Uma ubheka ingane yakho esanda kuzalwa, uke waphawula ukuthi isikhumba esiswini sayo sishwabene njenge-prune? Noma isisu sayo sibukeka sikhulu ngendlela engavamile? Kujwayelekile ukuthi noma yimuphi umama noma ubaba esaba uma ebona lezi zinto. Kodwa lokhu kungaba uphawu lwesimo esingavamile esibizwa ngokuthi i-Prune Belly Syndrome. Ungakhathazeki, sizoxoxa ngakho konke ngokucacile nangokulula.
Iyini i-Prune Belly Syndrome?
Kalula nje, i-Prune Belly Syndrome yisimo esingavamile kakhulu esiba khona lapho kuzalwa (esizalwa naso). Leli gama livela eqinisweni lokuthi isikhumba esiswini salaba bantwana sibukeka sishwabene futhi sibukeka njenge-prune. Lokhu kubangelwa yizici ezintathu eziyinhloko.
1. Imisipha yesisu ebuthakathaka noma engekho: Imisipha yesisu yomntwana ayikakhuli ngokugcwele, okwenza isikhumba esiswini sibonakale sigobile futhi sishwabene.
2. Amasende angakafiki phansi: Kubafana, amasende awazange ehle emzimbeni aye emasendeni lapho kufanele abe khona.
3. Izinkinga zesistimu yomchamo: Kunezinkinga ngendlela uhlelo lomchamo lwengane, okungukuthi, izinso kanye nesinye, olwakheka ngayo.
Ngaphezu kwalezi zinkinga ezintathu eziyinhloko, lesi simo singathinta nezinye izingxenye zomzimba womntwana. Isibonelo, inhliziyo, amaphaphu, amathumbu, kanye nohlelo lwamathambo kungathinteka. Lokhu kubizwa nangokuthi i-Triad Syndrome noma i-Eagle-Barrett Syndrome.
Sivame kangakanani lesi simo?
Lesi yisimo esingavamile kakhulu. Sithinta cishe ingane eyodwa kwezingu-30,000 kuya kwezingu-40,000 ezisanda kuzalwa. Okuphawuleka kakhulu ukuthi amaphesenti angama-95 alesi simo abikwa kubafana .
Yiziphi izimpawu eziyinhloko zalesi sifo?
Kunezimpawu ezingaphezu kuka-50 ze-Prune Belly Syndrome. Kodwa-ke, lezi zimpawu zingahluka kusuka kumntwana kuya kumntwana. Udokotela wakho uzohlola ingane yakho futhi enze izivivinyo ezidingekayo ukuqinisekisa isimo.
Ake sibheke ezinye zezici eziyinhloko ezivame ukubonakala.
| Isibonakaliso | Incazelo elula |
|---|---|
| Ukushwabana kwesikhumba sesisu | Isikhumba sibonakala somile futhi sishwabene ngenxa yemisipha yesisu ebuthakathaka noma engekho. |
| Isisu esikhulu | Ngenxa yokuthi isikhumba esiswini sincane, izinto ezifana namathumbu angaphakathi zingabonakala. Isisu sibukeka sikhulu. |
| Amasende angakafiki phansi | Kwabafana, amasende awazange ehlele esinqeni lapho kufanele abe khona (amasende angavuki) . |
| Izinkinga zesistimu yomchamo | Izinkinga ezifana nokuvaleka komgudu womchamo, ukwandiswa kwezinso noma esinyeni, kanye ne -vesicoureteral reflux . |
| Ezinye izinkinga zomzimba | Izinkinga zesistimu yokugaya ukudla, ukukhubazeka kwenhliziyo, i-scoliosis , kanye ne-clubfoot nazo zingabonakala. |
Kungani lokhu kwenzeka? Iyini imbangela?
Abacwaningi abakasitholi ngempela isizathu salokhu okwamanje, kodwa kunemibono eminingana ephakamisa ukuthi kungaba yimbangela.
- Izinkinga zesinyi: Abanye abantu bakholelwa ukuthi lesi simo sibangelwa ukungajwayelekile kwesinyeni okwenzeka ngesikhathi umntwana ekhula esibelethweni. Umchamo awukwazi ukugeleza kahle futhi uyanqwabelana, okubangela ukuba isinyi, ama-ureter, nezinso zivuvuke. Njengoba isinyi sikhula, sibeka ingcindezi emisipheni yesisu, okubangela ukuba iphele amandla.
- Inkinga yokukhula kwemisipha: Abanye bakholelwa ukuthi imbangela eyinhloko ukuthi imisipha yesisu somntwana ayikhuli kahle.
- Izimbangela Zezakhi Zofuzo: Kukholelwa ukuthi lesi simo singase sibe nethonya lezakhi zofuzo, njengoba sibonakala ezinganeni zakubo. I-Prune Belly Syndrome iyabonakala nasezinganeni ezinezimo zezakhi zofuzo ezifana ne-Trisomy 18 (i-Edwards syndrome) kanye ne-Down syndrome (i-Trisomy 21).
Yiziphi izinkinga ezingaba khona ngenxa yalesi simo?
Kunemiphumela emibi eminingi kanye nezinkinga ezihambisana ne-Prune Belly Syndrome. Iyahlukahluka kusuka kusana kuya kosana. Lezi yizinkinga eziyinhloko ezingabonakala.
- Ukuqunjelwa: Ubunzima bokukhipha indle ngenxa yemisipha yesisu ebuthakathaka.
- Ukukhubazeka kwamathambo: izinto ezifana nokukhumuka kwesinqe, ukulahleka kwezandla, iminwe, noma izinzwane.
- Izifo zomgudu womchamo: Ukuvela njalo kwezifo zomgudu womchamo (UTIs).
- Ukungazali noma umdlavuza: Ukwehluleka ukwehla emasendeni kungaholela ekungazali noma engcupheni yomdlavuza esikhathini esizayo.
- Ukukhula kwamaphaphu okunciphile: Amaphaphu awakhuli kahle (i-pulmonary hypoplasia).
- Ukwehluleka kwezinso okungapheli: Lena inkinga enzima kakhulu.
Ungasithola kanjani lesi simo?
Ezimweni eziningi, lesi simo singatholakala kusenesikhathi ngesikhathi sokuhlolwa kwe-ultrasound (i-fetal ultrasound) okwenzayo ngesikhathi sokukhulelwa kwakho. Ukuhlolwa kuvumela udokotela ukuthi abone:
- Ukukhubazeka kwamathambo noma kwemisipha
- Izinkinga zenhliziyo
- Ukuthuthukiswa kwamaphaphu aphansi
- Izinkinga zesistimu yokugaya ukudla
- Isinyi siyavuvukala.
- Izinso ziyakhula.
Ngemva kokuzalwa kwengane, udokotela angase asole ukuthi ingane inalesi simo ngokuyibuka nje. Ukuqinisekisa lokho kusola, kungenziwa izivivinyo eziningana, ezifana nalezi:
- Ukuhlolwa kwegazi
- Ukuskena nge-ultrasound
- I-X-ray
- Ukuskena kwe-CT
- Ukuskena kwe-MRI
- I-voiding cystourethrogram (VCUG) - Lokhu kuhilela ukufaka uketshezi olukhethekile esinyeni bese uthatha ama-X-ray ngenkathi umntwana echama ukuze kuhlolwe ukusebenza kohlelo lomchamo.
Iphathwa kanjani?
Ukwelashwa kwalokhu kuyahlukahluka kuye ngengane. Ithimba lochwepheshe lizosebenzisana ukuthuthukisa uhlelo lokwelashwa olufanele kakhulu lwengane. Lokhu kuzocabangela izici eziningi, okuhlanganisa ubudala bengane, isimo sempilo, ubucayi besimo, kanye nezifiso zabazali.
- Amacala amancane: Ezinye izingane ezinezimpawu ezingezimbi kangako zingase zizuze kuma -antibiotic kuphela ukuvimbela noma ukwelapha izifo zomchamo.
- Ukuhlinzwa: Kodwa-ke, izingane eziningi zizodinga ukuhlinzwa kaningi ukulungisa udonga lwesisu, izitho zangasese, isinye, kanye nezinye izingxenye zesimiso somchamo.
Into ebaluleke kakhulu ukuthi ukwelashwa ngakunye kunqunywa ngokutadisha ngokucophelela isimo somntwana futhi kuqondene ngqo nalowo mntwana.
Lezi ezinye zezinhlobo eziyinhloko zokuhlinzwa ezenziwayo:
- I-Vesicostomy: Kwenziwa imbobo encane ngesisu iye esinyeni, okuvumela umchamo ukuthi uphume ngayo.
- I-Orchiopexy: Amasende ehliswa ngokuhlinzwa emzimbeni bese efakwa esinqeni.
- I-Cystoplasty:Ukuhlinzwa okuyinkimbinkimbi kakhulu okwakha kabusha isinyi ngokuphelele.
Kwezinye izimo ezinzima kakhulu, ingane ingadinga nokufakelwa izinso .
Lizoba njani ikusasa lalaba bantwana?
Ukuphila kwalezi zingane kuncike ebunzimeni besifo. Ngokudabukisayo, phakathi kuka-10% no-25% wezingane ezizalwa nalesi simo zifela esibelethweni noma zife ngenxa yezinkinga emasontweni ambalwa okuqala okuphila.
Kodwa-ke, cishe ama-40% ezingane ezine-Prune Belly Syndrome zisebenza kahle izinso futhi zingaphila impilo ejwayelekile.
Abanye abangu-30% bazodinga ukufakelwa izinso ngesikhathi esithile empilweni yabo.
Ukuqapha nokulandelela impilo yonke yezokwelapha kubalulekile ezinganeni ezinalesi simo. Lokhu kungasiza ekuqapheni izinkinga zesistimu yomchamo nokunciphisa umonakalo ongaba khona ezinso.
Yiziphi izikhathi ezinhle kakhulu zokubona udokotela?
Izingane ezine-Prune Belly Syndrome zisengozini enkulu yokutheleleka kwe-urinary tract (UTIs), ngakho-ke uma ubona noma yiziphi izimpawu zokutheleleka kwe-urinary tract, shayela udokotela wakho ngokushesha.
| Izimpawu eziyisixwayiso zokutheleleka komgudu womchamo | |
|---|---|
| Umkhuhlane noma ukubanda | Isidingo sokuphuza njalo |
| Ukuzizwa unesidingo esikhulu sokuchama, kodwa kuphuma inani elincane kuphela | Ukushisa noma ubuhlungu lapho uchama |
| Ubuhlungu besisu noma umhlane ongezansi | Ukushintsha kombala womchamo (omnyama, ofiphele) |
| Iphunga elinamandla nelibi elivela emchameni | Igazi emchameni |
Ngaphezu kwalokho, funa iseluleko sezokwelapha uma ingane yakho inobunye ubunzima bokuchama noma ikhombisa ezinye izimpawu ezingavamile. Kubaluleke kakhulu futhi ukuyisa ingane yakho iyohlolwa okungenani kanye ngonyaka .
Ukunakekela ingane ezelwe inalesi simo kungaba yinselele. Kodwa khumbula, awuwedwa. Ukusebenza nodokotela kanye nethimba lochwepheshe abanolwazi ngalesi simo kungakunika wena kanye nengane yakho amandla nesiqondiso abasidingayo.
Umlayezo Wokuya Nawe Ekhaya
- I-Prune Belly Syndrome yisimo esingavamile kakhulu esenzeka lapho umuntu ezalwa.
- Izimpawu eziyinhloko ukugoba kwesikhumba esiswini, amasende angavuki kubafana, kanye nezinkinga zesistimu yomchamo.
- Lesi simo singatholakala ngisho nangaphambi kwesikhathi ngokusebenzisa ama-scan ngesikhathi sokukhulelwa.
- Izindlela zokwelapha ziyahlukahluka kuye ngesimo sengane, futhi kuvame ukudingeka ukuhlinzwa okuningi.
- Ukutheleleka komgudu womchamo kuyingozi kakhulu kulaba bantwana. Ngakho-ke qaphela ngaso sonke isikhathi. Bonana nodokotela ngokushesha nje lapho ubona ngisho nophawu oluncane kakhulu.
- Ingane idinga ukubhekwa kwezokwelapha impilo yayo yonke kanye nokulandelwa .
💬 Comments (0)
Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.
Engeza amazwana akho