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Ingabe nawe unemithambo yegazi emincane emaphashini akho? Ake sixoxe nge-Pulmonary Arterial Hypertension (PAH)!

Ingabe nawe unemithambo yegazi emincane emaphashini akho? Ake sixoxe nge-Pulmonary Arterial Hypertension (PAH)!

Ingabe ngezinye izikhathi uzizwa uphelelwa umoya? Noma uzizwa ukhathele ngendlela engavamile ngisho nalapho uhamba ibanga elifushane? Wake waphawula ukuthi iminwe yakho nezindebe zakho ziphenduka zibe luhlaza okwesibhakabhaka kanye nokuqina noma ubuhlungu esifubeni sakho? Ungakunaki lokhu njengezinto ezivamile. Ngoba ngezinye izikhathi, ngemuva kwalezi zimpawu, kungase kube nesimo sempilo esidinga ukunakwa. Esinye sezimo ezinjalo yi -Pulmonary Arterial Hypertension (PAH) . Nakuba igama lingase lizwakale liyesabeka kancane, ake sixoxe ngalo kalula nangendlela ongayiqonda.

Kuyini i-Pulmonary Arterial Hypertension (PAH)? Kalula nje...

Kalula nje, i-Pulmonary Arterial Hypertension (PAH) yisimo lapho imithambo yegazi emincane emaphashini akho (imithambo yegazi yamaphaphu) incipha khona. Cabanga ngakho njengepayipi lamanzi elivalekile, futhi kunzima ukuthi amanzi adlule kulo. Lapho le mithambo yegazi incipha, igazi alikwazi ukugeleza kahle emaphashini akho. Lokhu kubangela ukuthi ingcindezi engaphakathi kwale mithambo yegazi, noma ingcindezi yegazi, ibe phezulu kakhulu . Le mithambo yegazi yileyo ethwala igazi elingenawo umoya-mpilo lisuka enhliziyweni yakho liye emaphashini akho, lapho lihlanzwa khona.

Ngakho-ke kwenzekani uma lokhu kwenzeka? Uhlangothi lwesokudla lwenhliziyo yakho kufanele lusebenze kanzima kunokujwayelekile ukuze lupompe igazi liye emaphashini. Kufana nokuphakamisa imithwalo esindayo bese ukhuphuka intaba. Lapho inhliziyo kufanele ithwale lo mthwalo owengeziwe ngokuhamba kwesikhathi, iqala ukuba buthaka kancane kancane. Uma ingelashwa kahle, lesi simo, i-PAH, singabangela uchungechunge lwezinkinga hhayi nje enhliziyweni nasemaphashini akho, kodwa nasemzimbeni wakho wonke.

Khumbula, i-PAH uhlobo olulodwa nje oluthile lomfutho wegazi ophakeme emaphashini , okuyisimo lapho ingcindezi emithanjeni yegazi yamaphaphu ikhuphuka ngenxa yanoma yisiphi isizathu.

I-PAH iwuthinta kanjani umzimba wakho?

Umfutho Wegazi Ophakeme Wemithambo Yenhliziyo Yamaphaphu (i-PAH) ubeka ingcindezi ohlangothini lwesokudla lwenhliziyo yakho. Lokhu kungenxa yokuthi le ngxenye yenhliziyo ipompa igazi elingenawo umoya-mpilo liye emaphashini. Ngokuhamba kwesikhathi, lokhu kucindezela okuphezulu kungaholela ekuhlulekeni kwenhliziyo ohlangothini lwesokudla .

Akukhona lokho kuphela, i-PAH iphinde yehlise ijubane lokugeleza kwegazi phakathi kwenhliziyo namaphaphu. Lokhu kusho ukuthi igazi elincane lifinyelela emaphashini ukuze lithole umoya-mpilo omusha. Ngenxa yalokho, umoya-mpilo omncane ulethwa kwezinye izitho nezicubu zomzimba wakho. Eqinisweni, yonke ingxenye yomzimba wethu idinga umoya-mpilo ukuze iphile. Uma ingatholi ngokwanele, kuvela izinkinga.

Lesi simo esibizwa ngokuthi i-PAH sibi kangakanani?

I-Pulmonary Arterial Hypertension (PAH) iyisimo esibi kakhulu, ngezinye izikhathi esisongela impilo . Kodwa-ke, uma sitholakala kusenesikhathi futhi selashwa ngokushesha, ungaphila impilo ende nengcono. Yingakho kubalulekile ukunaka izimpawu.

Ubani othinteka kakhulu yi-PAH?

I-PAH ingathinta abantu abadala banoma yimuphi ubudala. Kodwa-ke, ivame kakhulu kwabesifazane , abavame ukutholakala bephakathi kweminyaka engama-30 nengama-60. Kutholakale nokuthi amadoda angaphezu kweminyaka engama-65 abathola i-PAH angaba nengozi enkulu yokuthola lesi sifo.

Lesi simo singathinta nezinsana ezincane. Uma kwenzeka ezinsaneni ezisanda kuzalwa, sibiza ngokuthi yi -Persistent Pulmonary Hypertension in the Neonate (PPHN) .

Ivame kangakanani i-PAH?

Uma kuqhathaniswa nezinye izinhlobo zomfutho wegazi ophezulu wamaphaphu, njengomfutho wegazi ophezulu wamaphaphu obangelwa yisifo senhliziyo noma isifo samaphaphu, i-PAH ayisona isimo esivamile kakhulu . Ngisho nasezweni elifana ne-United States, kutholakala amacala amasha angu-500 kuya ku-1,000 kuphela e-PAH minyaka yonke. Emazweni aseNtshonalanga, izinga lokutheleleka licishe libe ngu-25 ngesigidi.

Ziyini izimpawu ze-Pulmonary Arterial Hypertension (PAH)?

Ungase ungabi nazo izimpawu ezigabeni zokuqala ze-PAH. Iningi labantu liqala ukuzwa izimpawu njengoba isifo siqhubeka. Ezinye zalezi zimpawu zifaka:

  • Ukushintsha kombala weminwe noma izindebe: Njengokungathi igazi alinawo umoya-mpilo.
  • Ubuhlungu besifuba noma ukuqina: Njengokungathi othile ucindezela isifuba sakho.
  • Ukujuluka noma ukuquleka: Lokhu kungenzeka uma ukugeleza kwegazi kuya ebuchosheni kuncipha.
  • Ukukhathala: Ukuzizwa ukhathele kakhulu , hhayi nje ukukhathala.
  • Ukushaya kwenhliziyo okushesha kakhulu noma okushaya ngamandla.
  • Ukuphelelwa umoya: Lokhu kuyanda ngokuhamba kwesikhathi. Ngisho nokwenza imisebenzi emincane kungabangela ukuphelelwa umoya.
  • Ukuvuvukala (Ukuvuvuka): Ukuvuvukala kungase kuqale emilenzeni nasemaqakaleni, bese kusakazekela esiswini nasentanyeni.

Uma zingelashwa, lezi zimpawu ze-PAH zizoba zimbi kakhulu ngokuhamba kwesikhathi. Ungase uzithole ungakwazi ukwenza ngisho nemisebenzi yansuku zonke eyisisekelo ngaphandle kokuphefumula noma ukuphumula.

Yiziphi izimbangela ze-Pulmonary Arterial Hypertension (PAH)?

Imbangela eyinhloko ye-PAH ukulimala kolwelwesi lwemithambo yegazi emaphashini akho. Kodwa-ke, akucaci ngaso sonke isikhathi ukuthi yini ebangela lo monakalo.

Amacala lapho kungatholakali khona imbangela (i-Idiopathic PAH)

Ngezinye izikhathi, asikho isizathu esiqondile esingatholakala . Thina odokotela sikubiza ngokuthi “i-idiopathic” i-pulmonary arterial hypertension . Kufana nemfihlakalo.

Izimbangela ezaziwayo

Kodwa-ke, ngezinye izikhathi, kunezimbangela ezicacile. Ezinye zezimbangela ezaziwayo ze-PAH zifaka:

  • Ezinye izimo zezokwelapha:
  • Isifo senhliziyo esizalwa naso
  • Izifo zokugcina i-Glycogen
  • Ukutheleleka nge-HIV
  • Isifo sesibindi
  • Izifo ezizenzakalelayo njenge -lupus
  • Umfutho wegazi ophezulu we-portal (ukwanda kwengcindezi emithanjeni yegazi eholela esibindini)
  • I-hemangiomatosis yama-capillary emaphashini (ukukhula okungajwayelekile kwama-capillary emaphashini)
  • Isifo se-veno-occlusive se-pulmonary (ukuvaleka kwemithambo emaphashini)
  • I-Schistosomiasis (ukutheleleka okubangelwa yi-parasite)
  • I-Scleroderma (ukuqina kwesikhumba kanye nezicubu ezixhumeneyo)
  • Ukuguqulwa kwezakhi zofuzo:
  • Ngokuvamile, lokhu kungenxa yokuguquka kwezakhi zofuzo zakho ze-BMPR2 . Lesi sakhi sofuzo silawula inani lamaseli kwezinye izicubu emzimbeni wethu. Ngakho-ke, lapho lesi sakhi sofuzo siguqulwa, amaseli emithanjeni yegazi emincane emaphashini akho angakhula kakhulu. Lapho la maseli egcwele, izimbobo emithanjeni yegazi ziba zincane.
  • I-PAH ingasebenza ngemindeni. Siyibiza ngokuthi i-PAH ezuzwa njengefa . Cishe abantu abangu-80% abanalesi simo banezinguquko ku-gene ye-BMPR2.
  • Abanye abantu baphatha lesi sakhi sofuzo esishintshiwe, kodwa abakaze babe ne-PAH.
  • Abanye abantu bangaba ne-PAH yize kungekho muntu emndenini wabo onayo, ngenxa yokuguquka kwezakhi zofuzo. Lokhu kubizwa ngokuthi i-PAH engavamile .
  • Eminye imithi nemithi:
  • Amanye amaphilisi okunciphisa umzimba , njengomuthi omdala othi “fen-phen,” asevinjelwe manje, kodwa angabangela i-PAH eminyakeni eminingi ngemva kokusetshenziswa.
  • Izidakamizwa zokuzijabulisa , isibonelo i-cocaine ne-methamphetamine.

I-Pulmonary Arterial Hypertension (PAH) ihlolwa kanjani ?

I-PAH ingaba nzima ukuyixilonga ngoba izimpawu ze-PAH zifana nezezinye izifo eziningi. Udokotela wakho uzokwenza ukuhlolwa ngokomzimba futhi akhulume nawe ngezimpawu zakho kanye nomlando wezokwelapha. Bazokwenza izivivinyo eziningana (kufaka phakathi izivivinyo zezithombe kanye nokuhlolwa kwegazi) ukuthola ukuthi une-hypertension yamaphaphu, futhi uma kunjalo, uhlobo luni.

Udokotela wakho angakudlulisela kudokotela wamaphaphu noma kudokotela wenhliziyo . Laba ochwepheshe bazokwenza izivivinyo ezikhethekile ukuhlola ukusebenza kwenhliziyo namaphaphu akho. Bazonquma ukuthi une-PAH noma olunye uhlobo lomfutho wegazi ophezulu wamaphaphu. Bazohlola nokuthi isimo sakho sibi kangakanani.

Kunezindlela zokwelapha ezithile ze-PAH ezingatholakali kwezinye izinhlobo zomfutho wegazi ophezulu wamaphaphu. Ngakho-ke, ithimba lakho lezokwelapha lidinga ukwazi okuningi ngangokunokwenzeka ngalokho okwenzekayo emaphashini akho nasenhliziyweni yakho. Lolu lwazi luzobasiza ukuthi bakhe uhlelo lokwelashwa olungcono kakhulu kuwe.

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-PAH?

Ithimba lakho lezokwelapha lizosebenzisa inhlanganisela yezivivinyo ukuze linqume ezinye izifo futhi lixilonge i-PAH.

Uma udokotela wakho esola ukuthi kungenzeka ukuthi une-PAH ngemva kokuhlolwa kwakho ngokomzimba, ukuhlolwa kokuqala abazokuyala yi- transthoracic echocardiogram . Lokhu kuhlolwa kuhlola isakhiwo kanye nokusebenza kwenhliziyo yakho iyonke.

Ezinye izivivinyo zingafaka:

  • Ukuhlolwa kwegazi: Hlola ukusebenza kwezitho zomzimba, amazinga ama-hormone, bese uthola izifo eziyisisekelo. Ikakhulukazi ukuhlolwa okufana nephaneli ephelele ye-metabolic kanye nenani eliphelele legazi .
  • I-CT scan yesifuba: Ukuhlola nokususa ezinye izimo ezifana nesifo sezinso. (Mhlawumbe isifo sezinso esihlokweni sokuqala kufanele sibe yisifo samaphaphu. I-CT chest scan ibheka amaphaphu nezitho zesifuba. Ake sithi sibheka isimo samaphaphu.
  • I-X-ray yesifuba: Ukubona ukuthi imithambo yenhliziyo noma yamaphaphu yakho inkulu yini kunejwayelekile.
  • I-MRI Yenhliziyo: Hlola isimo se-ventricle yesokudla yenhliziyo yakho (lena yigumbi lenhliziyo elipompa igazi liye emaphashini).
  • I-Polysomnogram (PSG): Ukuhlolwa kwe-sleep apnea, okungase kube kubi kakhulu i-PAH. I-PSG uhlobo lokuhlolwa kokulala okwenziwa ebusuku.
  • Ukuhlolwa kokusebenza kwamaphaphu: Bona ukuthi amaphaphu akho asebenza kahle kangakanani.
  • Ukuskena komoya/ukugeleza kwegazi emaphashini (VQ): Kuhlola amahlule egazi emaphashini. Lokhu kuhlolwa kungasusa isimo esibizwa ngokuthi i-chronic thromboembolic pulmonary hypertension .
  • Ukufakwa kwe-catheter kwenhliziyo kwesokudla: Kukala ingcindezi emithanjeni yegazi emaphashini akho (ingcindezi yemithambo yegazi yamaphaphu). Lokhu kuhlolwa kubalulekile ukuze kutholakale i-PAH ngokuphelele.
  • Ukuhlolwa kokuhamba ngezinyawo kwemizuzu eyisithupha: Bona ukuthi ungakubekezelela kangakanani ukuvivinya umzimba nokuthi ingakanani i-oxygen ejikeleza egazini lakho uma uhamba.

Khuluma nodokotela wakho mayelana nokuthi yiziphi izivivinyo okudingeka uzenze nokuthi ungazilungiselela kanjani .

Yiziphi izindlela zokuhlola i-Pulmonary Arterial Hypertension?

Odokotela baxilonga umfutho wegazi ophezulu wamaphaphu ngokulinganisa ingcindezi emithanjeni yegazi emaphashini akho. Izindlela zokuxilonga ziwukuthi ingcindezi yemithambo yegazi yamaphaphu emaphashini akho ingaphezu kwamamilimitha angu-20 e-mercury (20 mmHg) uma uphumule . Leli nani lilinganiswa ngokufaka i-catheter yenhliziyo efanele .

Yiziphi izindlela zokwelapha i-Pulmonary Arterial Hypertension (PAH)?

Imigomo eyinhloko yokwelashwa kwe-PAH ukulawula ukuqhubeka kwesifo nokukunikeza impilo engcono. Akukho ukwelashwa okukodwa okulingana nakho konke kwe-PAH. Udokotela wakho uzosebenza nawe ukuze anqume ukwelashwa okungcono kakhulu kwezidingo zakho ezithile.

Uhlelo lwakho lokwelashwa nge-PAH lungafaka:

  • I-Balloon atrial septostomy (BAS): Le nqubo ivame ukwenziwa ezinganeni ezinezinkinga zenhliziyo ezizalwa nazo, kodwa ngezinye izikhathi isetshenziselwa abantu abadala abane-PAH. I-septostomy isiza ekunciphiseni ingcindezi ohlangothini lwesokudla lwenhliziyo, ivumela umoya-mpilo owengeziwe ukuthi ujikeleze egazini. Ingenziwa futhi njengebhuloho eliya ekufakweni kwamaphaphu.
  • Ama-calcium channel blockers: Le mithi isiza ukwehlisa umfutho wegazi emithanjeni yegazi yamaphaphu akho kanye nasemzimbeni wakho wonke.
  • Imithi yokwehlisa uketshezi: Eyaziwa nangokuthi “amaphilisi amanzi,” le mithi isiza ukususa uketshezi oluningi emzimbeni futhi inciphise ukuvuvukala.
  • Ukwelashwa nge-oxygen: Lokhu kwelashwa kungadingeka uma ungenawo umoya-mpilo owanele egazini lakho. Umoya-mpilo owengeziwe ungasiza uma uphumule, ulele, noma uzivocavoca.
  • Ama-vasodilator e-pulmonary: Le mithi isiza imithambo yegazi emaphashini akho (imithambo ye-pulmonary) ukuthi iphumule futhi ivuleke kabanzi. Lokhu kunciphisa ukucindezeleka enhliziyweni yakho futhi kusiza ekunciphiseni izimpawu zakho.

Kwabanye abantu abane-PAH enzima , ukufakelwa amaphaphu kungaba yindlela yokugcina. Lokhu kuhlinzwa kungakunika iphaphu elilodwa noma amabili amasha. Ukufakelwa inhliziyo namaphaphu nakho kungakunikeza inhliziyo entsha.

Yimiphi imithi enikezwa i-PAH?

Imithi yokwelapha i-PAH iza ngezindlela ezahlukene:

  • Imithi yomlomo: Le mithi isiza ukukhulula imithambo yegazi emaphashini futhi ivimbele ukuncipha. Le mithi ingakusiza futhi ukuthi ube nomzimba osebenzayo.
  • Imithi ephefumulwayo: Yelapha ubunzima bokuphefumula.
  • Iphampu yokumpompa ephathekayo: Lokhu kungasiza ukuvula imithambo yegazi nokwandisa ukugeleza kwegazi. Lokhu kungasiza ekuthuthukiseni izimpawu zakho.
  • Imithi yokwelapha nge-intravenous (IV): Ivula imithambo yegazi futhi inciphise izimpawu ezifana nobuhlungu besifuba kanye nobunzima bokuphefumula.

Nazi ezinye zemithi ezivunyelwe yi-US Food and Drug Administration (FDA) ezigulini ze-PAH:

  • I-Ambrisentan (ngomlomo)
  • I-Bosentan (ngomlomo)
  • I-Epoprostenol (IV)
  • I-Iloprost (ukuphefumula)
  • I-Macitentan (ngomlomo)
  • I-Riociguat (ngomlomo)
  • I-Selexipag (ngomlomo)
  • I-Sildenafil (ngomlomo)
  • I-Tadalafil (ngomlomo)
  • I-Treprostinil (ngomlomo, ukuhogela, iphampu, IV)

Imiphumela emibi yemithi ye-PAH

Eminye imiphumela emibi evamile yemithi esetshenziswa ukwelapha i-PAH ihlanganisa:

  • Ukuzizwa unesizungu noma ubuthakathaka.
  • Ukuzwa ukufudumala ebusweni, entanyeni, noma ezandleni (ukushawa).
  • Izimpawu zesisu ezifana nokuqunjelwa, isicanucanu, ukuhlanza kanye nohudo.
  • Ikhanda elibuhlungu (ikhanda elibuhlungu).
  • Umfutho wegazi ophansi (i-Hypotension) .
  • Ukuvuvukala kwemilenze namaqakala (i-Pedal edema) .
  • Ukuqhuma kwesikhumba.
  • Ukuzwa kokuminyana kwendlela yokuphefumula ephezulu.

Eminye imithi ingaba nemiphumela emibi eyengeziwe. Khuluma nodokotela wakho mayelana nendlela yokuphatha noma yimiphi imiphumela emibi. Kwezinye izimo, udokotela wakho kungadingeka ashintshe umthamo womuthi wakho.

Ingabe i-Pulmonary Arterial Hypertension (PAH) ingelapheka ngokuphelele?

Nakuba imithi yamanje ingalawula ukuqhubeka kwe-PAH, ayikwazi ukuguqula umonakalo osuvele ukhona . Kodwa-ke, abacwaningi baphenya ngemithi emisha abacabanga ukuthi ingayiguqula i-PAH. Imithi enjalo ingalungisa umonakalo kumaseli e-endothelial agudle imithambo yegazi emaphashini akho.

Khuluma nodokotela wakho ukuze ufunde kabanzi mayelana nocwaningo lwakamuva kanye nezivivinyo zemitholampilo zokwelapha i-PAH.

Yiziphi izinto ezandisa ingozi yomuntu yokuthola i-Pulmonary Arterial Hypertension (PAH)?

Izici eziningana ezandisa ingozi yokuthola i-PAH yilezi:

  • Isifo sezicubu ezixhumeneyo .
  • I-Down syndrome .
  • Umlando womndeni womfutho wegazi ophezulu wamaphaphu.
  • Ukutheleleka nge-HIV .
  • Ukusebenzisa imithi yokwehlisa isisindo efana ne-“fen-phen” (dexfenfluramine kanye ne-phentermine).
  • Ukusetshenziswa kwezidakamizwa ezingekho emthethweni (izidakamizwa zasemgwaqweni).

Uma othile emndenini wakho ene-PAH, buza udokotela wakho mayelana nokuhlolwa kwezakhi zofuzo. Uma kutholakale ukuthi une-PAH, kuwumqondo omuhle ukucela umndeni wakho ukuthi nawo ucabangele ukuhlolwa kwezakhi zofuzo.

Ungakuvimbela Kanjani Umfutho Wegazi Ophakeme We-Pulmonary Arterial (PAH)?

Asikwazi ukulawula ezinye izinto eziyingozi ze-PAH (njengokuguqulwa kwezakhi zofuzo). Kodwa-ke, ukuyeka izidakamizwa ezingekho emthethweni kunganciphisa ingozi yakho hhayi ye-PAH kuphela, kodwa nezinye izinkinga eziningi zempilo. Futhi, khuluma nodokotela wakho ngaphambi kokuthatha noma yimiphi imithi yokwehlisa isisindo.

Kuye ngezici zakho eziyingozi, udokotela wakho angase ancome ukuhlolwa kwe-PAH kokuvimbela.

Iyini ikusasa labantu abane-Pulmonary Arterial Hypertension (PAH)?

Ngokuthuthuka kokwelashwa, abantu abane-PAH baphila isikhathi eside kunanini ngaphambili. Isikhathi osiphila ngaso sincike ezintweni eziningi, okuhlanganisa nobunzima besimo sakho nokuthi usheshe utholakale unesifo. Khuluma nodokotela wakho ngesimo sakho esithile.

Into ebaluleke kakhulu ukuqhubeka nokwelashwa kwakho nokulandela imiyalelo kadokotela wakho ngokucophelela. Kunezinto ezimbalwa ongazenza ukuze uthuthukise amathuba akho okusinda:

  • Yenza ikhithi yezimo eziphuthumayo. Kunezinsiza ezithile nolwazi okufanele uhlale unalo. Buza udokotela wakho ukuthi yini okufanele uyifake ekhithini yakho, futhi ungalokothi uphume ekhaya ungayisebenzisi.
  • Thola imijovo yesizini njengoba kunconywe udokotela wakho. Kubaluleke kakhulu ukuzivikela emkhuhlaneni kanye nase-pneumonia.
  • Gcina wonke ama-aphoyintimenti okulandelela. Ukuhlolwa njalo kubalulekile ukuze kuhlolwe ukusebenza kwamaphaphu akho kanye nenhliziyo yakho futhi kulinganiswe inqubekela phambili yokwelashwa kwakho.
  • Phuza imithi yakho njengoba nje udokotela wakho ekuyalele, ngesikhathi esifanayo nsuku zonke. Ungayishintshi indlela othatha ngayo imithi yakho ngaphandle kweseluleko sikadokotela wakho.

Yiziphi izinguquko zendlela yokuphila okudingeka ngizenze?

Landela iseluleko sikadokotela wakho mayelana nanoma yiziphi izinguquko zendlela yokuphila ofuna ukuzenza. Ngokuvamile, nanka amanye amathiphu abalulekile:

  • Gwema ama-hot tub, ama-sauna, kanye nokuya ezindaweni eziphakeme.
  • Cabanga ngokulawula inzalo. Ukukhulelwa kungaba yingozi kubantu abane-PAH. Khuluma nodokotela wakho uma uhlela ukukhulelwa noma uma ungase ukhulelwe.
  • Vivinya umzimba futhi uhlale umatasa ngangokunokwenzeka. Khuluma nodokotela wakho ngokuthi yikuphi ukuzivocavoca okuphephile kuwe nokuthi kufanele wenze umsebenzi ongakanani nsuku zonke. Buza udokotela wakho ngaphambi kokuqala uhlelo olusha lokuzivocavoca.
  • Landela ukudla okunempilo kwenhliziyo. Lokhu kufaka phakathi ukudla okunamafutha agcwele aphansi, amafutha e-trans, kanye ne-sodium.
  • Yeka ukubhema nokusebenzisa imikhiqizo kagwayi. Futhi, gwema intuthu ebhemayo.
  • Funa ukwesekwa, ungazami ukuhamba uhambo lwakho lwe-PAH wedwa. Buza udokotela wakho ngamaqembu okusekela kanye nezinsiza.

Kufanele ngishayele nini udokotela wami ucingo?

Shayela udokotela wakho uma unemibuzo elandelayo:

  • Uma izinga lokushaya kwenhliziyo lingaphezu kwama-beats angu-120 ngomzuzu (izinga lokushaya kwenhliziyo elisheshayo).
  • Uma ukutheleleka kokuphefumula noma ukukhwehlela kuba kubi kakhulu.
  • Uma uvame ukuzizwa unesizungu noma uphelelwe amandla.
  • Uma uzwa ubuhlungu esifubeni noma ungakhululeki ngomsebenzi womzimba.
  • Uma uzizwa ukhathele kakhulu noma ukwehla kwamandla akho okwenza imisebenzi evamile.
  • Ukucanuzela noma ukuphelelwa yisifiso sokudla.
  • Ukungahlaliseki noma ukudideka.
  • Uma ukuphefumula kwakho kuba kubi kakhulu, ikakhulukazi uma uzizwa uphelelwa umoya lapho uvuka.
  • Uma ukuvuvukala emaqakaleni akho, emilenzeni, noma esiswini kuba kubi kakhulu.
  • Ubunzima bokuphefumula ngesikhathi semisebenzi evamile noma lapho uphumule.
  • Ukukhuluphala (amakhilogremu amabili ngosuku noma amakhilogremu amahlanu ngesonto).

Kufanele ngiye nini eMnyangweni Wezimo Eziphuthumayo (i-ETU) ?

Uma unezinye zalezi zinto, iya ekamelweni lezimo eziphuthumayo noma ushayele inombolo yakho yezimo eziphuthumayo yendawo:

  • Uma izinga lokushaya kwenhliziyo (ukushaya okungu-120-150 ngomzuzu) linganciphi.
  • Ukuquleka, okubangela ukulahlekelwa ukwazi.
  • Izinkinga ezivela kuphampu yakho ye-IV noma yokumpompa (njengokutheleleka, ukuphuma kwe-catheter, ukuvuza kwesisombululo, ukopha, ukungasebenzi kahle kwephampu ye-IV).
  • Uma ukuphefumula okuncane kungapheli ngisho nangemva kokuphumula.
  • Ubuhlungu besifuba obungazelelwe nobunzima.
  • Ikhanda elibuhlungu ngokuzumayo futhi elinzima.
  • Ubuthakathaka obungazelelwe noma ukukhubazeka kwezingalo noma imilenze.

Ekugcineni, umyalezo okufanele uwukhumbule

Ukucindezeleka Kwemithambo Yemithambo Yenhliziyo Yamaphaphu (i-PAH) kuyisifo esishintsha impilo. Uma wena noma othandekayo wakho nisanda kutholakala ukuthi ninayo lesi sifo, zinike isikhathi sokufunda ngalesi simo nokuthi yini ongayilindela. Buza udokotela wakho ngezinsiza ezichaza ukuthi i-PAH isebenza kanjani nokuthi ukwelashwa kungasiza kanjani.

Enye yezinsiza ezibaluleke kakhulu ongaba nazo ukusekelwa abanye empilweni yakho. Ungazami ukuphatha lesi simo wedwa. Uma umndeni wakho nabangani bakho bengekho, buza udokotela wakho ngamaqembu okusekela kanye nezinsiza zomphakathi.

Uma othandekayo wakho etholakale enalesi sifo, yenza konke ongakwenza ukuze uzizwe esekelwa futhi umsize axhumane nabanye. Ukugula kungasenza sizizwe sihlukanisiwe ngezindlela ezithile, kodwa kungasisondeza futhi. Sebenzisa lesi sikhathi ukwakha umphakathi ongakusiza wena noma othandekayo wakho ukuthi niqhubekele phambili.


Umfutho wegazi ophezulu we - pulmonary arterial, i-PAH, umfutho wegazi ophezulu we-pulmonary, ukuphelelwa umoya, isifo senhliziyo, isifo samaphaphu, izimpawu

Frequently Asked Questions (FAQ)

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-PAH?

Ithimba lakho lezokwelapha lizosebenzisa inhlanganisela yezivivinyo ukuze linqume ezinye izifo futhi lixilonge i-PAH.

Yimiphi imithi enikezwa i-PAH?

Imithi yokwelapha i-PAH iza ngezindlela ezahlukene:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ingabe nawe unemithambo yegazi emincane emaphashini akho? Ake sixoxe nge-Pulmonary Arterial Hypertension (PAH)!
Izifo NezimoJulayi 16, 2026

Ingabe nawe unemithambo yegazi emincane emaphashini akho? Ake sixoxe nge-Pulmonary Arterial Hypertension (PAH)!

Ingabe ngezinye izikhathi uzizwa uphelelwa umoya? Noma uzizwa ukhathele ngendlela engavamile ngisho nalapho uhamba ibanga elifushane? Wake waphawula ukuthi iminwe yakho nezindebe zakho ziphenduka zibe luhlaza okwesibhakabhaka kanye nokuqina noma ubuhlungu esifubeni sakho? Ungakunaki lokhu njengezinto ezivamile. Ngoba ngezinye izikhathi, ngemuva kwalezi zimpawu, kungase kube nesimo sempilo esidinga ukunakwa. Esinye sezimo ezinjalo yi -Pulmonary Arterial Hypertension (PAH) . Nakuba igama lingase lizwakale liyesabeka kancane, ake sixoxe ngalo kalula nangendlela ongayiqonda.

Kuyini i-Pulmonary Arterial Hypertension (PAH)? Kalula nje...

Kalula nje, i-Pulmonary Arterial Hypertension (PAH) yisimo lapho imithambo yegazi emincane emaphashini akho (imithambo yegazi yamaphaphu) incipha khona. Cabanga ngakho njengepayipi lamanzi elivalekile, futhi kunzima ukuthi amanzi adlule kulo. Lapho le mithambo yegazi incipha, igazi alikwazi ukugeleza kahle emaphashini akho. Lokhu kubangela ukuthi ingcindezi engaphakathi kwale mithambo yegazi, noma ingcindezi yegazi, ibe phezulu kakhulu . Le mithambo yegazi yileyo ethwala igazi elingenawo umoya-mpilo lisuka enhliziyweni yakho liye emaphashini akho, lapho lihlanzwa khona.

Ngakho-ke kwenzekani uma lokhu kwenzeka? Uhlangothi lwesokudla lwenhliziyo yakho kufanele lusebenze kanzima kunokujwayelekile ukuze lupompe igazi liye emaphashini. Kufana nokuphakamisa imithwalo esindayo bese ukhuphuka intaba. Lapho inhliziyo kufanele ithwale lo mthwalo owengeziwe ngokuhamba kwesikhathi, iqala ukuba buthaka kancane kancane. Uma ingelashwa kahle, lesi simo, i-PAH, singabangela uchungechunge lwezinkinga hhayi nje enhliziyweni nasemaphashini akho, kodwa nasemzimbeni wakho wonke.

Khumbula, i-PAH uhlobo olulodwa nje oluthile lomfutho wegazi ophakeme emaphashini , okuyisimo lapho ingcindezi emithanjeni yegazi yamaphaphu ikhuphuka ngenxa yanoma yisiphi isizathu.

I-PAH iwuthinta kanjani umzimba wakho?

Umfutho Wegazi Ophakeme Wemithambo Yenhliziyo Yamaphaphu (i-PAH) ubeka ingcindezi ohlangothini lwesokudla lwenhliziyo yakho. Lokhu kungenxa yokuthi le ngxenye yenhliziyo ipompa igazi elingenawo umoya-mpilo liye emaphashini. Ngokuhamba kwesikhathi, lokhu kucindezela okuphezulu kungaholela ekuhlulekeni kwenhliziyo ohlangothini lwesokudla .

Akukhona lokho kuphela, i-PAH iphinde yehlise ijubane lokugeleza kwegazi phakathi kwenhliziyo namaphaphu. Lokhu kusho ukuthi igazi elincane lifinyelela emaphashini ukuze lithole umoya-mpilo omusha. Ngenxa yalokho, umoya-mpilo omncane ulethwa kwezinye izitho nezicubu zomzimba wakho. Eqinisweni, yonke ingxenye yomzimba wethu idinga umoya-mpilo ukuze iphile. Uma ingatholi ngokwanele, kuvela izinkinga.

Lesi simo esibizwa ngokuthi i-PAH sibi kangakanani?

I-Pulmonary Arterial Hypertension (PAH) iyisimo esibi kakhulu, ngezinye izikhathi esisongela impilo . Kodwa-ke, uma sitholakala kusenesikhathi futhi selashwa ngokushesha, ungaphila impilo ende nengcono. Yingakho kubalulekile ukunaka izimpawu.

Ubani othinteka kakhulu yi-PAH?

I-PAH ingathinta abantu abadala banoma yimuphi ubudala. Kodwa-ke, ivame kakhulu kwabesifazane , abavame ukutholakala bephakathi kweminyaka engama-30 nengama-60. Kutholakale nokuthi amadoda angaphezu kweminyaka engama-65 abathola i-PAH angaba nengozi enkulu yokuthola lesi sifo.

Lesi simo singathinta nezinsana ezincane. Uma kwenzeka ezinsaneni ezisanda kuzalwa, sibiza ngokuthi yi -Persistent Pulmonary Hypertension in the Neonate (PPHN) .

Ivame kangakanani i-PAH?

Uma kuqhathaniswa nezinye izinhlobo zomfutho wegazi ophezulu wamaphaphu, njengomfutho wegazi ophezulu wamaphaphu obangelwa yisifo senhliziyo noma isifo samaphaphu, i-PAH ayisona isimo esivamile kakhulu . Ngisho nasezweni elifana ne-United States, kutholakala amacala amasha angu-500 kuya ku-1,000 kuphela e-PAH minyaka yonke. Emazweni aseNtshonalanga, izinga lokutheleleka licishe libe ngu-25 ngesigidi.

Ziyini izimpawu ze-Pulmonary Arterial Hypertension (PAH)?

Ungase ungabi nazo izimpawu ezigabeni zokuqala ze-PAH. Iningi labantu liqala ukuzwa izimpawu njengoba isifo siqhubeka. Ezinye zalezi zimpawu zifaka:

  • Ukushintsha kombala weminwe noma izindebe: Njengokungathi igazi alinawo umoya-mpilo.
  • Ubuhlungu besifuba noma ukuqina: Njengokungathi othile ucindezela isifuba sakho.
  • Ukujuluka noma ukuquleka: Lokhu kungenzeka uma ukugeleza kwegazi kuya ebuchosheni kuncipha.
  • Ukukhathala: Ukuzizwa ukhathele kakhulu , hhayi nje ukukhathala.
  • Ukushaya kwenhliziyo okushesha kakhulu noma okushaya ngamandla.
  • Ukuphelelwa umoya: Lokhu kuyanda ngokuhamba kwesikhathi. Ngisho nokwenza imisebenzi emincane kungabangela ukuphelelwa umoya.
  • Ukuvuvukala (Ukuvuvuka): Ukuvuvukala kungase kuqale emilenzeni nasemaqakaleni, bese kusakazekela esiswini nasentanyeni.

Uma zingelashwa, lezi zimpawu ze-PAH zizoba zimbi kakhulu ngokuhamba kwesikhathi. Ungase uzithole ungakwazi ukwenza ngisho nemisebenzi yansuku zonke eyisisekelo ngaphandle kokuphefumula noma ukuphumula.

Yiziphi izimbangela ze-Pulmonary Arterial Hypertension (PAH)?

Imbangela eyinhloko ye-PAH ukulimala kolwelwesi lwemithambo yegazi emaphashini akho. Kodwa-ke, akucaci ngaso sonke isikhathi ukuthi yini ebangela lo monakalo.

Amacala lapho kungatholakali khona imbangela (i-Idiopathic PAH)

Ngezinye izikhathi, asikho isizathu esiqondile esingatholakala . Thina odokotela sikubiza ngokuthi “i-idiopathic” i-pulmonary arterial hypertension . Kufana nemfihlakalo.

Izimbangela ezaziwayo

Kodwa-ke, ngezinye izikhathi, kunezimbangela ezicacile. Ezinye zezimbangela ezaziwayo ze-PAH zifaka:

  • Ezinye izimo zezokwelapha:
  • Isifo senhliziyo esizalwa naso
  • Izifo zokugcina i-Glycogen
  • Ukutheleleka nge-HIV
  • Isifo sesibindi
  • Izifo ezizenzakalelayo njenge -lupus
  • Umfutho wegazi ophezulu we-portal (ukwanda kwengcindezi emithanjeni yegazi eholela esibindini)
  • I-hemangiomatosis yama-capillary emaphashini (ukukhula okungajwayelekile kwama-capillary emaphashini)
  • Isifo se-veno-occlusive se-pulmonary (ukuvaleka kwemithambo emaphashini)
  • I-Schistosomiasis (ukutheleleka okubangelwa yi-parasite)
  • I-Scleroderma (ukuqina kwesikhumba kanye nezicubu ezixhumeneyo)
  • Ukuguqulwa kwezakhi zofuzo:
  • Ngokuvamile, lokhu kungenxa yokuguquka kwezakhi zofuzo zakho ze-BMPR2 . Lesi sakhi sofuzo silawula inani lamaseli kwezinye izicubu emzimbeni wethu. Ngakho-ke, lapho lesi sakhi sofuzo siguqulwa, amaseli emithanjeni yegazi emincane emaphashini akho angakhula kakhulu. Lapho la maseli egcwele, izimbobo emithanjeni yegazi ziba zincane.
  • I-PAH ingasebenza ngemindeni. Siyibiza ngokuthi i-PAH ezuzwa njengefa . Cishe abantu abangu-80% abanalesi simo banezinguquko ku-gene ye-BMPR2.
  • Abanye abantu baphatha lesi sakhi sofuzo esishintshiwe, kodwa abakaze babe ne-PAH.
  • Abanye abantu bangaba ne-PAH yize kungekho muntu emndenini wabo onayo, ngenxa yokuguquka kwezakhi zofuzo. Lokhu kubizwa ngokuthi i-PAH engavamile .
  • Eminye imithi nemithi:
  • Amanye amaphilisi okunciphisa umzimba , njengomuthi omdala othi “fen-phen,” asevinjelwe manje, kodwa angabangela i-PAH eminyakeni eminingi ngemva kokusetshenziswa.
  • Izidakamizwa zokuzijabulisa , isibonelo i-cocaine ne-methamphetamine.

I-Pulmonary Arterial Hypertension (PAH) ihlolwa kanjani ?

I-PAH ingaba nzima ukuyixilonga ngoba izimpawu ze-PAH zifana nezezinye izifo eziningi. Udokotela wakho uzokwenza ukuhlolwa ngokomzimba futhi akhulume nawe ngezimpawu zakho kanye nomlando wezokwelapha. Bazokwenza izivivinyo eziningana (kufaka phakathi izivivinyo zezithombe kanye nokuhlolwa kwegazi) ukuthola ukuthi une-hypertension yamaphaphu, futhi uma kunjalo, uhlobo luni.

Udokotela wakho angakudlulisela kudokotela wamaphaphu noma kudokotela wenhliziyo . Laba ochwepheshe bazokwenza izivivinyo ezikhethekile ukuhlola ukusebenza kwenhliziyo namaphaphu akho. Bazonquma ukuthi une-PAH noma olunye uhlobo lomfutho wegazi ophezulu wamaphaphu. Bazohlola nokuthi isimo sakho sibi kangakanani.

Kunezindlela zokwelapha ezithile ze-PAH ezingatholakali kwezinye izinhlobo zomfutho wegazi ophezulu wamaphaphu. Ngakho-ke, ithimba lakho lezokwelapha lidinga ukwazi okuningi ngangokunokwenzeka ngalokho okwenzekayo emaphashini akho nasenhliziyweni yakho. Lolu lwazi luzobasiza ukuthi bakhe uhlelo lokwelashwa olungcono kakhulu kuwe.

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-PAH?

Ithimba lakho lezokwelapha lizosebenzisa inhlanganisela yezivivinyo ukuze linqume ezinye izifo futhi lixilonge i-PAH.

Uma udokotela wakho esola ukuthi kungenzeka ukuthi une-PAH ngemva kokuhlolwa kwakho ngokomzimba, ukuhlolwa kokuqala abazokuyala yi- transthoracic echocardiogram . Lokhu kuhlolwa kuhlola isakhiwo kanye nokusebenza kwenhliziyo yakho iyonke.

Ezinye izivivinyo zingafaka:

  • Ukuhlolwa kwegazi: Hlola ukusebenza kwezitho zomzimba, amazinga ama-hormone, bese uthola izifo eziyisisekelo. Ikakhulukazi ukuhlolwa okufana nephaneli ephelele ye-metabolic kanye nenani eliphelele legazi .
  • I-CT scan yesifuba: Ukuhlola nokususa ezinye izimo ezifana nesifo sezinso. (Mhlawumbe isifo sezinso esihlokweni sokuqala kufanele sibe yisifo samaphaphu. I-CT chest scan ibheka amaphaphu nezitho zesifuba. Ake sithi sibheka isimo samaphaphu.
  • I-X-ray yesifuba: Ukubona ukuthi imithambo yenhliziyo noma yamaphaphu yakho inkulu yini kunejwayelekile.
  • I-MRI Yenhliziyo: Hlola isimo se-ventricle yesokudla yenhliziyo yakho (lena yigumbi lenhliziyo elipompa igazi liye emaphashini).
  • I-Polysomnogram (PSG): Ukuhlolwa kwe-sleep apnea, okungase kube kubi kakhulu i-PAH. I-PSG uhlobo lokuhlolwa kokulala okwenziwa ebusuku.
  • Ukuhlolwa kokusebenza kwamaphaphu: Bona ukuthi amaphaphu akho asebenza kahle kangakanani.
  • Ukuskena komoya/ukugeleza kwegazi emaphashini (VQ): Kuhlola amahlule egazi emaphashini. Lokhu kuhlolwa kungasusa isimo esibizwa ngokuthi i-chronic thromboembolic pulmonary hypertension .
  • Ukufakwa kwe-catheter kwenhliziyo kwesokudla: Kukala ingcindezi emithanjeni yegazi emaphashini akho (ingcindezi yemithambo yegazi yamaphaphu). Lokhu kuhlolwa kubalulekile ukuze kutholakale i-PAH ngokuphelele.
  • Ukuhlolwa kokuhamba ngezinyawo kwemizuzu eyisithupha: Bona ukuthi ungakubekezelela kangakanani ukuvivinya umzimba nokuthi ingakanani i-oxygen ejikeleza egazini lakho uma uhamba.

Khuluma nodokotela wakho mayelana nokuthi yiziphi izivivinyo okudingeka uzenze nokuthi ungazilungiselela kanjani .

Yiziphi izindlela zokuhlola i-Pulmonary Arterial Hypertension?

Odokotela baxilonga umfutho wegazi ophezulu wamaphaphu ngokulinganisa ingcindezi emithanjeni yegazi emaphashini akho. Izindlela zokuxilonga ziwukuthi ingcindezi yemithambo yegazi yamaphaphu emaphashini akho ingaphezu kwamamilimitha angu-20 e-mercury (20 mmHg) uma uphumule . Leli nani lilinganiswa ngokufaka i-catheter yenhliziyo efanele .

Yiziphi izindlela zokwelapha i-Pulmonary Arterial Hypertension (PAH)?

Imigomo eyinhloko yokwelashwa kwe-PAH ukulawula ukuqhubeka kwesifo nokukunikeza impilo engcono. Akukho ukwelashwa okukodwa okulingana nakho konke kwe-PAH. Udokotela wakho uzosebenza nawe ukuze anqume ukwelashwa okungcono kakhulu kwezidingo zakho ezithile.

Uhlelo lwakho lokwelashwa nge-PAH lungafaka:

  • I-Balloon atrial septostomy (BAS): Le nqubo ivame ukwenziwa ezinganeni ezinezinkinga zenhliziyo ezizalwa nazo, kodwa ngezinye izikhathi isetshenziselwa abantu abadala abane-PAH. I-septostomy isiza ekunciphiseni ingcindezi ohlangothini lwesokudla lwenhliziyo, ivumela umoya-mpilo owengeziwe ukuthi ujikeleze egazini. Ingenziwa futhi njengebhuloho eliya ekufakweni kwamaphaphu.
  • Ama-calcium channel blockers: Le mithi isiza ukwehlisa umfutho wegazi emithanjeni yegazi yamaphaphu akho kanye nasemzimbeni wakho wonke.
  • Imithi yokwehlisa uketshezi: Eyaziwa nangokuthi “amaphilisi amanzi,” le mithi isiza ukususa uketshezi oluningi emzimbeni futhi inciphise ukuvuvukala.
  • Ukwelashwa nge-oxygen: Lokhu kwelashwa kungadingeka uma ungenawo umoya-mpilo owanele egazini lakho. Umoya-mpilo owengeziwe ungasiza uma uphumule, ulele, noma uzivocavoca.
  • Ama-vasodilator e-pulmonary: Le mithi isiza imithambo yegazi emaphashini akho (imithambo ye-pulmonary) ukuthi iphumule futhi ivuleke kabanzi. Lokhu kunciphisa ukucindezeleka enhliziyweni yakho futhi kusiza ekunciphiseni izimpawu zakho.

Kwabanye abantu abane-PAH enzima , ukufakelwa amaphaphu kungaba yindlela yokugcina. Lokhu kuhlinzwa kungakunika iphaphu elilodwa noma amabili amasha. Ukufakelwa inhliziyo namaphaphu nakho kungakunikeza inhliziyo entsha.

Yimiphi imithi enikezwa i-PAH?

Imithi yokwelapha i-PAH iza ngezindlela ezahlukene:

  • Imithi yomlomo: Le mithi isiza ukukhulula imithambo yegazi emaphashini futhi ivimbele ukuncipha. Le mithi ingakusiza futhi ukuthi ube nomzimba osebenzayo.
  • Imithi ephefumulwayo: Yelapha ubunzima bokuphefumula.
  • Iphampu yokumpompa ephathekayo: Lokhu kungasiza ukuvula imithambo yegazi nokwandisa ukugeleza kwegazi. Lokhu kungasiza ekuthuthukiseni izimpawu zakho.
  • Imithi yokwelapha nge-intravenous (IV): Ivula imithambo yegazi futhi inciphise izimpawu ezifana nobuhlungu besifuba kanye nobunzima bokuphefumula.

Nazi ezinye zemithi ezivunyelwe yi-US Food and Drug Administration (FDA) ezigulini ze-PAH:

  • I-Ambrisentan (ngomlomo)
  • I-Bosentan (ngomlomo)
  • I-Epoprostenol (IV)
  • I-Iloprost (ukuphefumula)
  • I-Macitentan (ngomlomo)
  • I-Riociguat (ngomlomo)
  • I-Selexipag (ngomlomo)
  • I-Sildenafil (ngomlomo)
  • I-Tadalafil (ngomlomo)
  • I-Treprostinil (ngomlomo, ukuhogela, iphampu, IV)

Imiphumela emibi yemithi ye-PAH

Eminye imiphumela emibi evamile yemithi esetshenziswa ukwelapha i-PAH ihlanganisa:

  • Ukuzizwa unesizungu noma ubuthakathaka.
  • Ukuzwa ukufudumala ebusweni, entanyeni, noma ezandleni (ukushawa).
  • Izimpawu zesisu ezifana nokuqunjelwa, isicanucanu, ukuhlanza kanye nohudo.
  • Ikhanda elibuhlungu (ikhanda elibuhlungu).
  • Umfutho wegazi ophansi (i-Hypotension) .
  • Ukuvuvukala kwemilenze namaqakala (i-Pedal edema) .
  • Ukuqhuma kwesikhumba.
  • Ukuzwa kokuminyana kwendlela yokuphefumula ephezulu.

Eminye imithi ingaba nemiphumela emibi eyengeziwe. Khuluma nodokotela wakho mayelana nendlela yokuphatha noma yimiphi imiphumela emibi. Kwezinye izimo, udokotela wakho kungadingeka ashintshe umthamo womuthi wakho.

Ingabe i-Pulmonary Arterial Hypertension (PAH) ingelapheka ngokuphelele?

Nakuba imithi yamanje ingalawula ukuqhubeka kwe-PAH, ayikwazi ukuguqula umonakalo osuvele ukhona . Kodwa-ke, abacwaningi baphenya ngemithi emisha abacabanga ukuthi ingayiguqula i-PAH. Imithi enjalo ingalungisa umonakalo kumaseli e-endothelial agudle imithambo yegazi emaphashini akho.

Khuluma nodokotela wakho ukuze ufunde kabanzi mayelana nocwaningo lwakamuva kanye nezivivinyo zemitholampilo zokwelapha i-PAH.

Yiziphi izinto ezandisa ingozi yomuntu yokuthola i-Pulmonary Arterial Hypertension (PAH)?

Izici eziningana ezandisa ingozi yokuthola i-PAH yilezi:

  • Isifo sezicubu ezixhumeneyo .
  • I-Down syndrome .
  • Umlando womndeni womfutho wegazi ophezulu wamaphaphu.
  • Ukutheleleka nge-HIV .
  • Ukusebenzisa imithi yokwehlisa isisindo efana ne-“fen-phen” (dexfenfluramine kanye ne-phentermine).
  • Ukusetshenziswa kwezidakamizwa ezingekho emthethweni (izidakamizwa zasemgwaqweni).

Uma othile emndenini wakho ene-PAH, buza udokotela wakho mayelana nokuhlolwa kwezakhi zofuzo. Uma kutholakale ukuthi une-PAH, kuwumqondo omuhle ukucela umndeni wakho ukuthi nawo ucabangele ukuhlolwa kwezakhi zofuzo.

Ungakuvimbela Kanjani Umfutho Wegazi Ophakeme We-Pulmonary Arterial (PAH)?

Asikwazi ukulawula ezinye izinto eziyingozi ze-PAH (njengokuguqulwa kwezakhi zofuzo). Kodwa-ke, ukuyeka izidakamizwa ezingekho emthethweni kunganciphisa ingozi yakho hhayi ye-PAH kuphela, kodwa nezinye izinkinga eziningi zempilo. Futhi, khuluma nodokotela wakho ngaphambi kokuthatha noma yimiphi imithi yokwehlisa isisindo.

Kuye ngezici zakho eziyingozi, udokotela wakho angase ancome ukuhlolwa kwe-PAH kokuvimbela.

Iyini ikusasa labantu abane-Pulmonary Arterial Hypertension (PAH)?

Ngokuthuthuka kokwelashwa, abantu abane-PAH baphila isikhathi eside kunanini ngaphambili. Isikhathi osiphila ngaso sincike ezintweni eziningi, okuhlanganisa nobunzima besimo sakho nokuthi usheshe utholakale unesifo. Khuluma nodokotela wakho ngesimo sakho esithile.

Into ebaluleke kakhulu ukuqhubeka nokwelashwa kwakho nokulandela imiyalelo kadokotela wakho ngokucophelela. Kunezinto ezimbalwa ongazenza ukuze uthuthukise amathuba akho okusinda:

  • Yenza ikhithi yezimo eziphuthumayo. Kunezinsiza ezithile nolwazi okufanele uhlale unalo. Buza udokotela wakho ukuthi yini okufanele uyifake ekhithini yakho, futhi ungalokothi uphume ekhaya ungayisebenzisi.
  • Thola imijovo yesizini njengoba kunconywe udokotela wakho. Kubaluleke kakhulu ukuzivikela emkhuhlaneni kanye nase-pneumonia.
  • Gcina wonke ama-aphoyintimenti okulandelela. Ukuhlolwa njalo kubalulekile ukuze kuhlolwe ukusebenza kwamaphaphu akho kanye nenhliziyo yakho futhi kulinganiswe inqubekela phambili yokwelashwa kwakho.
  • Phuza imithi yakho njengoba nje udokotela wakho ekuyalele, ngesikhathi esifanayo nsuku zonke. Ungayishintshi indlela othatha ngayo imithi yakho ngaphandle kweseluleko sikadokotela wakho.

Yiziphi izinguquko zendlela yokuphila okudingeka ngizenze?

Landela iseluleko sikadokotela wakho mayelana nanoma yiziphi izinguquko zendlela yokuphila ofuna ukuzenza. Ngokuvamile, nanka amanye amathiphu abalulekile:

  • Gwema ama-hot tub, ama-sauna, kanye nokuya ezindaweni eziphakeme.
  • Cabanga ngokulawula inzalo. Ukukhulelwa kungaba yingozi kubantu abane-PAH. Khuluma nodokotela wakho uma uhlela ukukhulelwa noma uma ungase ukhulelwe.
  • Vivinya umzimba futhi uhlale umatasa ngangokunokwenzeka. Khuluma nodokotela wakho ngokuthi yikuphi ukuzivocavoca okuphephile kuwe nokuthi kufanele wenze umsebenzi ongakanani nsuku zonke. Buza udokotela wakho ngaphambi kokuqala uhlelo olusha lokuzivocavoca.
  • Landela ukudla okunempilo kwenhliziyo. Lokhu kufaka phakathi ukudla okunamafutha agcwele aphansi, amafutha e-trans, kanye ne-sodium.
  • Yeka ukubhema nokusebenzisa imikhiqizo kagwayi. Futhi, gwema intuthu ebhemayo.
  • Funa ukwesekwa, ungazami ukuhamba uhambo lwakho lwe-PAH wedwa. Buza udokotela wakho ngamaqembu okusekela kanye nezinsiza.

Kufanele ngishayele nini udokotela wami ucingo?

Shayela udokotela wakho uma unemibuzo elandelayo:

  • Uma izinga lokushaya kwenhliziyo lingaphezu kwama-beats angu-120 ngomzuzu (izinga lokushaya kwenhliziyo elisheshayo).
  • Uma ukutheleleka kokuphefumula noma ukukhwehlela kuba kubi kakhulu.
  • Uma uvame ukuzizwa unesizungu noma uphelelwe amandla.
  • Uma uzwa ubuhlungu esifubeni noma ungakhululeki ngomsebenzi womzimba.
  • Uma uzizwa ukhathele kakhulu noma ukwehla kwamandla akho okwenza imisebenzi evamile.
  • Ukucanuzela noma ukuphelelwa yisifiso sokudla.
  • Ukungahlaliseki noma ukudideka.
  • Uma ukuphefumula kwakho kuba kubi kakhulu, ikakhulukazi uma uzizwa uphelelwa umoya lapho uvuka.
  • Uma ukuvuvukala emaqakaleni akho, emilenzeni, noma esiswini kuba kubi kakhulu.
  • Ubunzima bokuphefumula ngesikhathi semisebenzi evamile noma lapho uphumule.
  • Ukukhuluphala (amakhilogremu amabili ngosuku noma amakhilogremu amahlanu ngesonto).

Kufanele ngiye nini eMnyangweni Wezimo Eziphuthumayo (i-ETU) ?

Uma unezinye zalezi zinto, iya ekamelweni lezimo eziphuthumayo noma ushayele inombolo yakho yezimo eziphuthumayo yendawo:

  • Uma izinga lokushaya kwenhliziyo (ukushaya okungu-120-150 ngomzuzu) linganciphi.
  • Ukuquleka, okubangela ukulahlekelwa ukwazi.
  • Izinkinga ezivela kuphampu yakho ye-IV noma yokumpompa (njengokutheleleka, ukuphuma kwe-catheter, ukuvuza kwesisombululo, ukopha, ukungasebenzi kahle kwephampu ye-IV).
  • Uma ukuphefumula okuncane kungapheli ngisho nangemva kokuphumula.
  • Ubuhlungu besifuba obungazelelwe nobunzima.
  • Ikhanda elibuhlungu ngokuzumayo futhi elinzima.
  • Ubuthakathaka obungazelelwe noma ukukhubazeka kwezingalo noma imilenze.

Ekugcineni, umyalezo okufanele uwukhumbule

Ukucindezeleka Kwemithambo Yemithambo Yenhliziyo Yamaphaphu (i-PAH) kuyisifo esishintsha impilo. Uma wena noma othandekayo wakho nisanda kutholakala ukuthi ninayo lesi sifo, zinike isikhathi sokufunda ngalesi simo nokuthi yini ongayilindela. Buza udokotela wakho ngezinsiza ezichaza ukuthi i-PAH isebenza kanjani nokuthi ukwelashwa kungasiza kanjani.

Enye yezinsiza ezibaluleke kakhulu ongaba nazo ukusekelwa abanye empilweni yakho. Ungazami ukuphatha lesi simo wedwa. Uma umndeni wakho nabangani bakho bengekho, buza udokotela wakho ngamaqembu okusekela kanye nezinsiza zomphakathi.

Uma othandekayo wakho etholakale enalesi sifo, yenza konke ongakwenza ukuze uzizwe esekelwa futhi umsize axhumane nabanye. Ukugula kungasenza sizizwe sihlukanisiwe ngezindlela ezithile, kodwa kungasisondeza futhi. Sebenzisa lesi sikhathi ukwakha umphakathi ongakusiza wena noma othandekayo wakho ukuthi niqhubekele phambili.


Umfutho wegazi ophezulu we - pulmonary arterial, i-PAH, umfutho wegazi ophezulu we-pulmonary, ukuphelelwa umoya, isifo senhliziyo, isifo samaphaphu, izimpawu

Frequently Asked Questions (FAQ)

Yiziphi izivivinyo ezisetshenziswa ukuxilonga i-PAH?

Ithimba lakho lezokwelapha lizosebenzisa inhlanganisela yezivivinyo ukuze linqume ezinye izifo futhi lixilonge i-PAH.

Yimiphi imithi enikezwa i-PAH?

Imithi yokwelapha i-PAH iza ngezindlela ezahlukene:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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