Cabanga nje uma ungazelelwe waba nekhanda elibuhlungu, umbono ofiphele, kanye nokulahlekelwa ukuzwa? Ungase ucabange ukuthi lezi yizinkinga ezintathu ezingahlobene. Kodwa namuhla sikhuluma ngesimo esingavamile kakhulu esihlanganisa zonke lezi zimpawu ezintathu, kodwa esingaxoxwa kabanzi emphakathini. Lokhu kubizwa ngokuthi "i-Susac Syndrome." Leli gama lingase libe lisha kuwe. Kodwa kubaluleke kakhulu ukuqaphela lokhu.
Kalula nje, iyini iSusac Syndrome?
I-Susac Syndrome yisimo lapho uhlelo lokuzivikela lomzimba wethu, uhlelo lokuzivikela komzimba, luhlasela khona ngephutha imizimba yethu. Lokhu sikubiza ngokuthi isimo sokuzivikela komzimba. Cabanga ngebutho elivikela izwe elihlasela abantu balo ngephutha.
Kulesi sifo, amasosha omzimba wethu ahlasela imithambo yegazi emincane ezindaweni ezintathu ezibaluleke kakhulu emzimbeni wethu. Lezo zindawo ezintathu yilezi:
1. Ubuchopho
2. I -Retina
3. Indlebe yangaphakathi (i-Cochlea)
Uma lokhu kwenzeka, izindonga zangaphakathi zale mithambo yegazi ziyavuvukala. Njengoba nje ipayipi lamanzi livaleka, ukugeleza kwamanzi kule mithambo yegazi kuyancishiswa, futhi ngezinye izikhathi kungavinjelwa ngokuphelele. Lokhu kuncisha ubuchopho, amehlo, nezindlebe umoya-mpilo kanye nezakhamzimba ezikudingayo. Yilapho izimpawu zalesi sifo ziqala khona ukubonakala.
Yiziphi izimpawu eziyinhloko zalesi sifo?
Ku-Susac Syndrome, izimpawu ezihlobene nalezi zingxenye ezintathu eziyinhloko zingase zivele ndawonye noma ngokwahlukana. Kodwa ngokuvamile zonke izingxenye ezintathu ziyathinteka. Ake sibone ukuthi ziyini lezi zimpawu.
| Ingxenye ethintekile | Izimpawu ezingaba khona |
|---|---|
| 1. Ubuchopho |
|
| 2. Amehlo |
|
| 3. Indlebe Yangaphakathi |
|
Into ebalulekile ukuthi akubona bonke abantu ababhekana nazo zonke lezi zimpawu ngesikhathi esisodwa. Abanye abantu bangase babhekane nalezi zimpawu kanye bese bengaphinde babuye. Abanye bangase babe nalezi zimpawu iminyaka eminingana.
Kungani lokhu kwenzeka futhi ubani osengozini enkulu?
Njengoba sixoxile ngaphambili, imbangela eqondile yalokhu ayikatholakali . Okuwukuphela kwento eyaziwayo ukuthi kuyisimo sokuzivikela komzimba. Akusona isifo esizuzwa njengefa . Lokho kusho ukuthi abukho ubufakazi bokuthi izingane zizosithola uma abazali bazo benaso.
Kodwa-ke, izici ezithile zingakhomba abantu abasengozini yokuthola lesi sifo:
- Ubulili: Abesifazane banamathuba aphindwe kathathu okuthola lesi sifo kunabesilisa.
- Ubudala: Lezi zimpawu zivame ukuqala ukubonakala kubantu abaneminyaka ephakathi kuka-20 no-40 .
Odokotela bakuthola kanjani lokhu?
I-Susac Syndrome ingaba nzima ukuyixilonga ngoba izimpawu zayo zifana nezezinye izifo eziningi. Isibonelo, izimpawu zifana kakhulu nezezifo ezifana ne-Multiple Sclerosis (MS), isifo sohlangothi, kanye nokutheleleka kobuchopho (encephalitis). Ngakho-ke, udokotela angase acabange ngephutha ukuthi yisifo esihlukile.
Ngakho-ke, kwenziwa izivivinyo eziningana ezikhethekile ukuze kutholakale ukuxilongwa okunembile.
- Ukuhlolwa komzimba
- Ukuhlolwa kwe-neurological
- Ukuhlolwa kwamehlo
Ngaphezu kwalokho, lezi zivivinyo ezikhethekile zibaluleke kakhulu ukuqinisekisa lesi sifo.
| Ukuhlolwa | Ufunani kulokhu? |
|---|---|
| Ukuskena kwe-MRI (Umfanekiso Wokuqabulana Kwamagnetic) | Lokhu kuthatha izithombe eziningiliziwe zobuchopho. Kumuntu one-Susac Syndrome, izilonda ezimhlophe ezibukeka njenge-"snowballs" zingabonakala ku-corpus callosum, ingxenye yobuchopho exhumanisa izingxenye zobuchopho zesokudla nesobunxele. Lokhu kuyisibonakaliso esiyingqayizivele salesi sifo. |
| I-angiography ye-fluorescein | Lena inqubo ehlola imithambo yegazi ku-retina yeso. Kule nqubo, kufakwa idayi ekhethekile emthanjeni osengalweni bese kuthathwa izithombe zemithambo yegazi engaphakathi kweso. Lokhu kungabona ngokucacile ukuthi imithambo yegazi ivaliwe yini. |
| I-Audiogram | Lolu uhlobo lokuhlola olulinganisa ukuzwa. Abantu abane-Susac Syndrome bangase babe nobunzima bokuzwa, ikakhulukazi imisindo ephansi, futhi bangase babe nobunzima bokuqonda inkulumo. Lolu hlobo lokuhlola lungakubona lokhu. |
Iyini indlela yokwelapha?
Umgomo oyinhloko wokwelapha lesi sifo ukulawula amasosha omzimba ethu, angasebenzi kahle. Okusho ukuthi, ukucindezela ukusebenza kwawo. Sibiza imithi enikezwa ngale njongo ngokuthi ama-immunosuppressants .
Lokhu kwelashwa kungadinga ukuthathwa isikhathi eside. Eminye yemithi evame ukusetshenziswa yile:
- Ama-Corticosteroids - isibonelo i-prednisone
- I-immunoglobulin efakwa emthanjeni (IVIG)
- I-Mycophenolate
- I-Azathioprine
- I-Cyclophosphamide
- I-Rituximab
Kunezindlela eziningana zokunikeza le mithi. Eminye inikezwa njengamaphilisi, eminye inikezwa njengomjovo, kanti eminye inikezwa ngemithambo yegazi (IV) njengesixazululo sikasawoti.
Kubaluleke kakhulu: Kubalulekile ukuthatha lo muthi njengoba nje udokotela wakho ekuyalele, kuze kube yilapho usuqedile. Uma weqa ukwelashwa noma uyeka ngokwakho, kunethuba elikhulu lokuthi izimpawu zakho zizophinde zivele.
Njengayo yonke imithi, lena ingaba nemiphumela emibi. Ngakho-ke khuluma nodokotela wakho ngakho ngokukhululekile ngaphambi kokuqala ukwelashwa. Uma kuvela imiphumela emibi, mtshele ngokushesha.
Singaba kanjani nethemba ngekusasa?
Nakuba igama elithi Susac Syndrome lingase lizwakale lesabisa, kunezindlela zokwelapha ezinhle kakhulu zalesi simo. Ikakhulukazi uma lesi sifo sitholakala futhi selashwa kusenesikhathi, imiphumela iba mihle kakhulu. Ukwelashwa kusenesikhathi kungavimbela ukulimala okungapheli ebuchosheni, emehlweni nasezindlebeni.
Kodwa-ke, uma ukwelashwa kwephuza, ngezinye izikhathi ukubona nokuzwa kungalahleka unomphela. Kodwa-ke, lokhu akuvamile kakhulu.
Lesi sifo asivamile ukuba yingozi empilweni. Okusho ukuthi, asifinyezi isikhathi sokuphila. Kodwa-ke, singathinta ikhwalithi yokuphila kwansuku zonke. Lapho izinto ezifana nokubona nokuzwa, okwakukuhle ngaphambili, zishintsha, kanye nezinguquko endleleni ocabanga futhi ukhumbula ngayo, kungaba nomthelela omkhulu ngokwengqondo. Ngakho-ke, ukukhuluma nomeluleki wezempilo yengqondo ngemva kokuxilongwa okunjengalokhu kuletha impumuzo kubantu abaningi.
Kufanele ngimbone nini udokotela?
Uma wena noma othile omaziyo ebhekana noshintsho olulodwa noma ngaphezulu ngesikhathi esisodwa, bona udokotela ngokushesha .
- Izinguquko ezingazelelwe embonweni (amabala amnyama, ukuzizwa sengathi umbozwe yikhethini).
- Ukulahlekelwa ukuzwa ngokuzumayo, isiyezi, noma ukukhala ezindlebeni.
- Ubunzima bokucabanga noma ukukhumbula (izinguquko ekusebenzeni kobuchopho).
- Izinguquko ezingachazeki ekuziphatheni noma ebuntwini .
- Uma lezi zimpawu ziphazamisa impilo yakho yansuku zonke .
Udokotela wakho angahlonza imbangela eqondile yalezi zimpawu futhi akunikeze ukwelashwa okudingekayo, okungasiza ekuvimbeleni izinkinga zesikhathi eside.
Umlayezo Wokuya Nawe Ekhaya
- I-Susac Syndrome yisifo esingavamile lapho amasosha ethu omzimba ehlasela khona imithambo yegazi emincane ebuchosheni, emehlweni nasezindlebeni.
- Izimpawu eziyinhloko zalesi sifo ziyizimpawu ezintathu: izinkinga zokusebenza kobuchopho (ikhanda elibuhlungu, ukudideka), izinkinga zokubona, kanye nezinkinga zokuzwa (isiyezi, ukulahlekelwa ukuzwa).
- Lesi akusona isifo esidluliselwa ngofuzo, futhi sivame kakhulu kwabesifazane.
- Ukubona udokotela ngokushesha nje lapho kuvela izimpawu nokuthola ukuxilongwa ngokushesha kungavimbela umonakalo ohlala njalo.
- Ukwelashwa kuhlanganisa imithi elawula amasosha omzimba (imithi yokucindezela amasosha omzimba), futhi kubaluleke kakhulu ukulandela imiyalelo kadokotela wakho.
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