Ua hoʻi mai anei kāu keiki mai ka pāʻani ʻana a ʻōlelo akula, "E Māmā/Pāpā, ʻeha ma ʻaneʻi, me he puʻupuʻu liʻiliʻi lā"? A i ʻole paha e loaʻa iā ʻoe iho kekahi mau puʻupuʻu liʻiliʻi a me nā puʻupuʻu ma nā ʻāpana like ʻole o kou kino. ʻO ka hapa nui o ka manawa, nalo lākou i loko o kekahi mau lā. Eia naʻe, i kekahi manawa, inā hoʻomau ka puʻupuʻu, a inā paha e ʻike ʻia ana e nui aʻe ana, he manaʻo maikaʻi ke nānā iki iā ia. I kēia lā e kamaʻilio mākou e pili ana i kahi puʻupuʻu like, akā he mea kakaikahi iki, e hana ʻia ana i loko o nā iwi. Ua kapa ʻia kēia ʻo `(Aneurysmal Bone Cyst)` a i ʻole `(ABC)` no ka pōkole.
Ua ʻike anei ʻoe i ke ʻano o kēia "Aneurysmal Bone Cyst (ABC)"?
I ka ʻōlelo maʻalahi, ʻo `(Aneurysmal Bone Cyst)` he puʻupuʻu maikaʻi ʻole, ʻaʻole maʻi kanesa e ulu ana i loko o ko kākou mau iwi. He mau lua liʻiliʻi i piha i ke koko (cysts) i loko o kēia puʻupuʻu. ʻO ka huaʻōlelo "Aneurysmal" e pili ana i kahi puʻupuʻu i loko o ka paia o kekahi o ko kākou mau kīʻaha koko. ʻO "Cyst" e pili ana i kahi lua i piha i ka wai. No laila, ke hoʻohui ʻoe i kēia mau mea ʻelua, hiki iā ʻoe ke hoʻomaopopo i ke ʻano o kēia mea āpau, ʻeā?
He mea kākaʻikahi loa kēia ʻano i kapa ʻia ʻo `(ABC)`. He mea kākaʻikahi nō hoʻi nā puʻupuʻu iwi, a i waena o lākou, aia kēia `(ABC)` i loko o kahi pakeneka liʻiliʻi loa. Hoʻopilikia nui kēia ʻano i nā keiki a me nā ʻōpio ma lalo o 20 mau makahiki .
Ma hea kahi e ulu nui ai kēia mau mea?
Hiki i kēia mau puʻupuʻu ke hana i loko o kekahi iwi i loko o ke kino, akā ʻo ka mea maʻamau ka loaʻa ʻana ma kēia mau wahi:
- ʻO ka iwi nui ma kou ʻūhā (Femur)
- Iwi ʻūhā (Tibia)
- ʻO ka iwi ma ka lima luna `(Humerus)`
- ʻO ka Vertebrae i loko o ka iwi kuamoʻo
- Nā iwi i loko o kou pelvis
ʻO kēia nā wahi e hiki ai iā ʻoe ke ʻike pinepine i kēia mau hua '(ABC)'.
Aia kekahi mau ʻano 'ABC'?
ʻAe, aia ʻelua ʻano nui o nā "Aneurysmal Bone Cysts".
1. ʻABC mua: Ma kēia, ulu ka puʻupuʻu ma kāna iho, me ke kumu ʻole.
2. ʻABC lua: Hana ʻia kēia ke loaʻa iā ʻoe kekahi maʻi pili iwi a i ʻole ka puʻupuʻu, a ulu kēia ʻ(ABC)` ma muli o ia mea.
ʻO kekahi mau maʻi iwi a me nā maʻi ʻaʻai e hiki ai ke hana i ka ABC lua:
- ʻO ka dysplasia fibrous
- ʻO ka puʻupuʻu pūnaewele nui
- ʻOsteoblastoma
- ʻO ke kondrosarcoma
- ʻOsteosarcoma
ʻIke ʻia ka lua `(ABC)` me nā kūlana ʻē aʻe e like me kēia.
He aha nā hōʻailona o kēia? Pehea ʻoe e ʻike ai?
ʻO ka hapa pinepine, ʻike ʻia nā hōʻailona ma ke ʻano he mau loli i kou lima, wāwae, ʻūhā, a i ʻole ke kua. ʻO kēia mau mea:
- Iā ʻoeHiki iā ʻoe ke hoʻopā iā ia me kou lima, a aia paha he puʻupuʻu a he puʻupuʻu paha i ʻike ʻia.
- Aia paha he ʻeha ma ia wahi. I kekahi manawa hiki ke hoʻonui koke ʻia kēia ʻeha.
- E ʻike ʻoe i ka pehu ʻana a puni ka wahi i loaʻa ai ka puʻupuʻu.
E noʻonoʻo, hoʻi mai kāu keiki mai ka pāʻani ʻana i kekahi lā a ʻōlelo ʻo ia ua ʻeha kona wāwae. Aia kahi pehu liʻiliʻi a me kahi puʻupuʻu hiki iā ʻoe ke ʻike ma kou lima. Inā ʻaʻole ia e nalowale ma hope o ʻelua a ʻekolu paha lā, a piʻi mālie ka ʻeha, a laila pono ʻoe e hopohopo iki.
ʻOi aku hoʻi, inā ulu kēia puʻupuʻu `(ABC)` i loko o ka iwi kuamoʻo a kaomi i nā aʻalolo o ka iwi kuamoʻo, hiki ke ʻike ʻia nā hōʻailona ʻē aʻe:
* Mālie
* He manaʻo e like me nā ʻanuʻu e holo ana a puni, a i ʻole nā pine a me nā nila (Paresthesia)
* Nāwaliwali o nā ʻiʻo
* I kekahi mau hihia, hiki iā ia ke alakaʻi i ka maʻi lolo .
No laila, inā loaʻa iā ʻoe nā hōʻailona e like me kēia me ka ʻeha o ke kua, he mea nui loa ia e ʻimi koke i ke kōkua lapaʻau.
No ke aha i hoʻokumu ʻia ai kēia ʻano ʻABC? He aha ke kumu?
ʻO kaʻoiaʻiʻo, ʻaʻole i loaʻa i nā loea lapaʻau ke kumu pololei o kēia mau ʻano maʻi ʻaʻai (ABC). Eia nō naʻe, aia kekahi mau kumu i manaʻo ʻia e kōkua i ko lākou hanana ʻana:
- Hiki paha ke kumu o kekahi mau pilikia me nā kīʻaha koko i loko o nā iwi.
- Hiki paha ke kumu o kekahi mau loli i loko o nā genes e kaohi ana i ke ʻano o ka ulu ʻana a me ka māhele ʻana o kā mākou mau cell.
ʻO kēia nā pilikia nui e kānalua ʻia nei i kēia manawa.
He aha nā pilikia e hiki mai ana mai kēia?
ʻO kēia kūlana i kapa ʻia ʻo "Aneurysmal Bone Cyst" hiki ke hana i kekahi mau pilikia .
- ʻOiai inā hana kēia i nā keiki, hiki iā ia ke hoʻopilikia i ka ulu ʻana o ko lākou iwi . ʻO ke ʻano kēia, no ka laʻana, ʻoi aku ka pōkole o kekahi lima a wāwae paha ma mua o kekahi.
- Inā ulu mālie ka puʻupuʻu a hoʻonāwaliwali i ka iwi, nui aʻe ka manawa e haki ai ka iwi . ʻOiai he hāʻule iki wale nō hiki ke haki ka iwi.
No laila, he mea nui e mālama pono i kēia.
Pehea e ʻike ai nā kauka i kēia?
Ke ʻike ʻoe a i ʻole kāu keiki i ke kauka me kēia mau hōʻailona, ʻo ka mea mua āna e hana ai, ʻo ia ka hana ʻana i kahi hoʻokolokolo kino piha . E nānā pono ʻo ia i nā puʻupuʻu āu e ʻike ai a i ʻole e hoʻopā ai.
A laila, hiki ke hana ʻia nā hoʻokolohua kiʻi e like me kēia e hōʻoia hou aku:
- Nānā iwi
- ʻIke CT (ʻIke Tomography i hoʻopili ʻia)
- ʻO ke kiʻi MRI (ʻO ke kiʻi Magnetic Resonance Imaging)
- Nā kukuna X
Hiki i kēia mau scan ke hōʻike i nā mea he nui, e like me ke ʻano o ka puʻupuʻu, kona nui, a me kona hopena ma ka iwi.
Eia kekahi, i kekahi manawa e hoʻoholo paha ke kauka e hana i kahi biopsy . ʻO ke ʻano kēia o ka lawe ʻana i kahi hāpana liʻiliʻi o ka ʻiʻo mai ka puʻupuʻu a nānā iā ia ma lalo o kahi microscope. ʻO kēia ke hōʻoia inā loaʻa i ka puʻupuʻu nā hunaola kanesa a ʻaʻole paha.
He aha nā lāʻau lapaʻau no kēia? (Lāʻau lapaʻau)
ʻO ka nūhou maikaʻi, aia nā lāʻau lapaʻau no kēia kūlana "ABC". Aia ka lāʻau lapaʻau i kekahi mau kumu, e like me ka nui o ka puʻupuʻu, kona wahi, a me kou mau makahiki.
ʻoki kino
ʻO ka lāʻau lapaʻau maʻamau ka ʻoki ʻana i kapa ʻia ʻo curettage . Pili kēia i kahi kauka ʻokiʻoki orthopedic e ʻoki ana i ka ʻili a puni ka puʻupuʻu, e wehe ana i nā cysts a me ka uhi o ka puʻupuʻu. A laila hoʻopiha ʻia ka wahi me ka iwi, he iwi i hoʻopili ʻia mai kahi mea hāʻawi a i ʻole mai kahi ʻāpana ʻē aʻe o kou kino.
Nā lāʻau lapaʻau ʻoki ʻole
I nā hihia kahi hiki ʻole ke ʻoki ʻana, a i ʻole ma waho aʻe o ke ʻoki ʻana, aia kekahi mau lāʻau lapaʻau ʻē aʻe e like me:
- ʻO ka embolization arterial: Pili kēia i ke ālai ʻana i nā kīʻaha koko e hoʻolako ana i ke koko i ka puʻupuʻu. ʻO kēia ke kumu o ka nalowale ʻana o ke koko i ka puʻupuʻu a hoʻomaka e emi.
- ʻInikini Doxycycline : Hoʻokomo ʻia kēia lāʻau lapaʻau i loko o ka puʻupuʻu, e hoʻemi ana a hoʻōki i ka ulu ʻana o ka puʻupuʻu.
- Nā lāʻau hoʻoikaika iwi: Hiki ke hāʻawi ʻia nā lāʻau lapaʻau e like me Denosumab (Prolia®) e hoʻoikaika i nā iwi.
- Lapaʻau radiation: Hoʻohana ʻia kēia e luku i nā cell i loko o ka puʻupuʻu. Eia nō naʻe, hoʻohana pinepine ʻia inā ʻaʻole i holo pono nā lāʻau ʻē aʻe.
- Sclerotherapy: He ʻano hana kēia no ka hoʻokomo ʻana i kahi lāʻau i loko o ka puʻupuʻu. Hoʻemi kēia lāʻau i ka puʻupuʻu.
E koho kāu kauka i ka lāʻau lapaʻau maikaʻi loa nāu.
Pehea ka lōʻihi e hoʻōla ai? (Hoʻōla)
ʻO ka manawa hoʻōla nou a i ʻole kāu keiki e pili ana i ke ʻano o ka lāʻau i hana ʻia. No ka laʻana, ma hope o ka curettage, hiki i ka iwi ke hala i ʻekolu a ʻeono mahina e ho'ōla ai.Hiki ke lōʻihi ka manawa, no laila he mea nui e nīnau i kāu kauka i ka mea e manaʻo ai, ka mea e hana ai, a me nā mea e hana ʻole ai i kou wā e hoʻōla ai ma hope o ke ʻoki ʻana.
Āhea wau e pono ai e ʻike hou i ke kauka?
Hiki i kēia kūlana i kapa ʻia ʻo "Aneurysmal Bone Cyst" ke hoʻi hou mai ma hope o ka mālama ʻia ʻana. No laila, inā manaʻo ʻoe he puʻupuʻu hou kou ma kahi i mālama mua ʻia, a inā ʻeha ʻoe, pono ʻoe e ʻike koke i ke kauka . Mai lawe māmā.
Pehea kēia? Hiki ke ho'ōla ʻia? (Prognosis)
He maʻi hiki ke mālama ʻia nā Aneurysmal Bone Cysts i ka hapa nui o nā hihia. He nūhou maikaʻi kēlā, ʻeā? Akā, e like me ka mea i ʻōlelo ʻia ma mua, aia ma kahi o 1 i loko o 5 mau kānaka ka manawa e loaʻa hou ai . ʻO ka hapa nui o ka manawa, hoʻi hou ia i loko o ka makahiki mua ma hope o ka mālama ʻana. ʻO ia ke kumu e ʻōlelo ai nā kauka he mea nui e hoʻomau i ka nānā ʻana (follow-up).
ʻO ka mea nui loa - nā mea e hoʻomanaʻo ai (Leka Lawe-Home)
ʻAe, no laila e hoʻomanaʻo aku kākou iā ʻoe i kekahi o nā mea nui e hoʻomanaʻo ai mai nā mea a kākou i kamaʻilio ai.
- He mea maʻamau ka loaʻa ʻana o nā puʻupuʻu a me nā ʻōhū ma kou kino. Hiki ke hana ʻia kēia inā ʻoe e kuʻi i ka puka a hāʻule paha i ka wā e pāʻani ana. Eia nō naʻe, inā ʻaʻole e nalowale kahi puʻupuʻu i loko o kekahi mau lā, hoʻomau, a i ʻole e ulu nui ana, pono ʻoe e ʻike i ke kauka .
- ʻAʻole ʻo 'Aneurysmal Bone Cyst (ABC)' he maʻi ʻaʻai . Mai hopohopo no ia mea. Eia nō naʻe, hiki iā ia ke hana i nā pilikia koʻikoʻi e like me ka haki ʻana o ka iwi.
- ʻO kēia kūlana ka mea nui e hoʻopilikia ai i nā keiki a me nā ʻōpio.
- Aia nā lāʻau lapaʻau maikaʻi no kēia, no laila mai hopohopo, a e ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe nā hōʻailona.
Inā loaʻa iā ʻoe a i ʻole kekahi o kou ʻohana kēia pilikia, e ʻoluʻolu e ʻike i ke kauka no ka ʻōlelo aʻo a me ka lāʻau lapaʻau. E noho olakino!
👩🏽⚕️ Nā nīnau hou aku (FAQs)
💬 He aha ka aneurysmal bone cyst (ABC)?
He ʻano ulu ʻole kēia no ka maʻi ʻaʻai e hana ʻia ana i loko o ka iwi, e hoʻopiha ana iā ia me ke koko a hana i kahi ʻano e like me ka huʻahuʻa. Ulu pinepine kēia mau mea ma nā iwi o nā wāwae o nā keiki ʻōpio.
💬 Pehea ka manaʻo o ka mea maʻi i ka wā e ulu ai kēia puʻupuʻu?
I ka ulu ʻana o ka puʻupuʻu, pehu ka iwi a puni a hoʻomaka e ʻeha. Lilo ka iwi i nāwaliwali loa, a hiki ke haki koke me ke kumu ʻole (pathologic fracture).
💬 Pehea e ho'ōla ai i kēia mau pu'upu'u?
Hoʻokomo mua ke kauka lapaʻau loea i loko o ka iwi a wehe i ka puʻupuʻu (curettage). A laila, hoʻohana ʻia ke kāpili iwi e hoʻopiha i ka hakahaka.
`ʻO ka cyst iwi, Aneurysmal Bone Cyst, ABC, Maʻi iwi pediatric, ʻEha iwi, Pehu iwi, Cyst iwi ʻaʻole maʻi kanesa











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