Ke manaʻo nei ʻoe i kekahi manawa ua luhi loa, ua poniuniu , a ua pōwehiwehi iki kou ʻike? ʻOiai ke manaʻo nei mākou he mau mea maʻamau kēia, i kekahi manawa ʻo ke kumu ma hope o kēia he hōʻiliʻili ʻana o ke koko i loko o ko mākou kino. Ua kapa ʻia kēia ʻo Secondary Polycythemia i ka ʻepekema lapaʻau. Mai makaʻu i kou lohe ʻana i kēia inoa, he ʻano kakaikahi kēia. I ka ʻōlelo maʻalahi, ʻo ia hoʻi, ua hana kou kino i nā hunaola koko ʻulaʻula ma mua o ka mea e pono ai . No laila e kamaʻilio kākou e pili ana i kēia me nā kikoʻī, me ka maʻalahi loa.
No ke aha e mānoanoa ai ke koko penei? He aha nā kumu?
ʻO ke ʻano o ka huaʻōlelo "lua" ʻo ia hoʻi "lua." No laila ua hāʻawi ʻia kēia maʻi i kēlā inoa no ka mea ʻaʻole ia he mea e kū pololei ana, akā , ma muli o kekahi maʻi a kumu ʻē aʻe .
E noʻonoʻo i kēia ʻano, lawe nā hunaola koko ʻulaʻula i ka oxygen i nā ʻiʻo o ko kākou kino. Inā no kekahi kumu e loaʻa ai i ka lolo a i ʻole nā puʻupaʻa kahi hōʻailona ʻaʻole lawa ka oxygen i ke kino, hana nā puʻupaʻa i kahi hormone i kapa ʻia ʻo 'Erythropoietin' a i ʻole ' EPO' . Hele kēia hormone 'EPO' i ko kākou iwi iwi a haʻi iā ia e "hana i nā hunaola koko ʻulaʻula hou aʻe, ʻaʻole lawa ka oxygen i ke kino." No laila hoʻomaka ka iwi iwi e hana i nā hunaola koko ʻulaʻula hou. Ke piʻi ka nui o nā hunaola koko ʻulaʻula ma kēia ʻano, mānoanoa mālie ke koko. He paʻakikī i kēia koko mānoanoa ke hele ma waena o nā kīʻaha koko liʻiliʻi ('capillaries') i loko o ko kākou kino. ʻO ia ke kumu e piʻi ai ka pilikia o nā maʻi koʻikoʻi e like me ka ' stroke' .
I kēia manawa, e nānā kākou i nā kumu nui o kēia.
| ʻAno kumu | Nā Laʻana |
|---|---|
| Nā kumu e pili ana i ke ʻano o ka nohona |
|
| Nā maʻi o ka ʻōnaehana hanu | |
| Nā kūlana olakino ʻē aʻe |
He aha ka ʻokoʻa ma waena o ka Polycythemia mua a me ke lua?
Ua lohe paha ʻoe i ka 'Primary Polycythemia.' ʻOiai ua like ke kani ʻana o kēia mau mea ʻelua, aia kahi ʻokoʻa nui ma waena o nā mea ʻelua.
I ka ʻōlelo maʻalahi, ua like ko kākou iwi me kahi hale hana e hana ana i nā hunaola koko.
- ʻO ka Polycythemia Mua: ʻO kēia ka wā e hana ai ka hale hana ponoʻī (ka iwi iwi) i nā hunaola koko ʻulaʻula he nui loa ma kāna iho, me ka ʻole o nā hōʻailona o waho. ʻO ka maʻamau, hana ʻia kēia e kahi loli genetic (`mutation`).
- ʻO ka Polycythemia Lua: Maanei, ke hana maikaʻi nei ka hale hana (iwi iwi). Eia nō naʻe, ma muli o nā hōʻailona hewa a pono ʻole paha mai waho (e laʻa, mai nā puʻupaʻa) e haʻi ana iā ia e "hana hou aku," hana ia i nā hunaola koko ʻulaʻula he nui loa.
No ka hoʻokaʻawale ʻana ma waena o nā mea ʻelua, hoʻāʻo nā kauka no kahi gene i kapa ʻia ʻo `JAK2`. He nui ka poʻe me `Primary Polycythemia` i hoʻāʻo ʻia he `maikaʻi` no kēia gene. Eia naʻe, ʻaʻole kēia e hana ma `Secondary Polycythemia`.
He aha nā hōʻailona o kēia maʻi?
Hiki ke ʻokoʻa nā hōʻailona o ke koko i kēlā me kēia kanaka. ʻAʻole paha i loaʻa i kekahi poʻe kekahi mau hōʻailona. Eia naʻe, ʻo kēia nā hōʻailona maʻamau.
- Luhi
- ʻEha poʻo
- Pōʻino
- ʻIke pōwehiwehi
- ʻAʻohe ʻono
- Ka nāwaliwali o ke kino
- Hoʻemi ʻia ka noʻonoʻo noʻonoʻo
ʻO ka mea nui, ʻaʻole i hoʻokumu ʻia kēia mau hōʻailona e ke koko wale nō. Hiki ke loaʻa nā hōʻailona ʻē aʻe (ke kuʻi, ka pōkole o ka hanu) ma muli o ke kumu kumu (e laʻa, ka maʻi māmā).
Eia kekahi laʻana, inā ʻo ke kumu ʻo 'Sleep Apnea', hiki iā ʻoe ke ʻike i ka hiamoe nui i ke ao a me ka hānō ʻana i ka pō.
Pehea ʻoe e ʻike ai i kēia, e Kauka?
Ke haʻi aku ʻoe i kāu kauka e pili ana i kēia mau hōʻailona, ʻo ka mea mua āna e hana ai, ʻo ia ke nīnau iā ʻoe e pili ana i kāu mōʻaukala olakino piha. ʻO ia hoʻi, inā ʻoe e puhipaka ana, ua emi anei kou kaumaha i kēia manawa, ua loaʻa anei iā ʻoe ka ʻū, ka ʻū ʻana o ka umauma, ka paʻakikī o ka hanu ʻana, a i ʻole ka hānō ʻana i ka pō . E nīnau pū ʻo ia inā ua loaʻa i kekahi o kou ʻohana kēia mau maʻi.
A laila, hana ʻia kahi hoʻokolohua kino a, inā pono, ua ʻōlelo ʻia kekahi mau hoʻokolohua, e like me:
- Nā hoʻāʻo koko: E nānā i ka helu o nā kele koko ʻulaʻula, nā pae hormone EPO, a me nā pae oxygen i ke koko (hiki ke hana ʻia kēia me kahi hoʻāʻo Arterial Blood Gas - ABG).
- ECG (Electrocardiogram): E nānā i ka hana o ka puʻuwai.
- Nā Hoʻāʻo Kiʻi: Hiki i kahi X-ray umauma, CT scan, a i ʻole ultrasound scan ke nānā no ka pehu ʻana o ka puʻuwai, ke akepaʻa, a i ʻole ka spleen.
Ma o kēia mau hoʻokolohua e ʻike ai ke kauka i ke kumu maoli o kēia maʻi.
He aha nā lāʻau lapaʻau no kēia?
ʻO ka mea maikaʻi loa e pili ana i kēia, hiki ke ho'ōla ʻia ka polycythemia lua ma ka ʻike ʻana a me ka mālama ʻana i ke kūlana kumu i hoʻoulu ai i ka mānoanoa o ke koko .
ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ka hoʻopau ʻana i ke kumu o ke koko.
- Ke mālama nei i ke kumu kumu:
- Inā he mea puhi paka ʻoe: He mea nui e hoʻōki i ka puhi paka. E hāʻawi ke kauka i nā ʻōlelo aʻoaʻo a me nā lāʻau lapaʻau e pono ai no kēia.
- Inā ma muli o ka momona: E aʻo ʻia ʻoe e hoʻololi i kou nohona, hoʻoikaika kino, a hoʻemi i ke kaumaha.
- Inā loaʻa iā ʻoe kahi maʻi māmā e like me COPD: Hiki i ka lāʻau lapaʻau oxygen haʻahaʻa ke kōkua i ka hoʻihoʻi ʻana i nā pae oxygen i loko o ke kino.
- Inā ma muli o kahi puʻupuʻu: Hiki ke ho'ōla loa ʻia kēia maʻi ma ka wehe ʻana i ka puʻupuʻu ma ke ʻoki ʻana.
- Lapaʻau e hōʻoluʻolu i nā hōʻailona:
- Phlebotomy: Ua like kēia me ka hoʻoili koko. Ma kahi o ka hapalua paina a i ʻole ka paina o ke koko e wehe ʻia mai kahi aa koko, e hōʻemi ana i ka helu o nā hunaola koko ʻulaʻula a hoʻomāmā i ke koko. Hāʻawi kēia i ka hōʻoluʻolu koke mai nā hōʻailona e like me ke poʻo ʻeha a me ka poniuniu.
- Nā lāʻau lapaʻau: Hiki i kāu kauka ke kuhikuhi i nā lāʻau lapaʻau e like me ka aspirin e hōʻemi i ka ʻeha, a me nā antihistamines no nā hōʻailona e like me ka ʻeha.
He mea hoʻonāukiuki ke aʻo e pili ana i kekahi maʻi ʻē aʻe i kou wā e hana nei me kekahi. Akā e hoʻomanaʻo, ʻo ka hapa nui o nā maʻi e hoʻoulu ai i ka 'Secondary Polycythemia' ua ʻike nui ʻia a he nui nā lāʻau lapaʻau. No laila, inā mālama pono ʻia ke kumu kumu, ʻaʻole e hoʻopilikia kēia maʻi i kou ola.
Leka Lawe-Home
- ʻO ka polycythemia lua ka wā e hoʻonui ai nā hunaola koko ʻulaʻula o ke kino a mānoanoa ke koko ma muli o kekahi maʻi ʻē aʻe.
- ʻAʻohe mea ʻē aʻe kēia ma mua o kahi kīnā ma ka iwi iwi.
- ʻO ka puhi paka, ka momona, ka maʻi māmā, a me ka maʻi puʻuwai kekahi o nā kumu nui o kēia.
- ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ka mālama ʻana i ke kūlana kumu i hoʻoulu ai i ka mānoanoa o ke koko.
- Inā loaʻa iā ʻoe nā hōʻailona e like me ka luhi mau, ka ʻeha poʻo, a i ʻole ka dizziness, e kamaʻilio pono me kāu kauka e pili ana i ia mea.











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