Koj puas tau muaj ib qho mob txawv txawv, tsis meej pem hauv koj lub plab lossis nraub qaum qis? Peb yuav xav tias nws yog mob plawv lossis raug mob nraub qaum me me. Txawm li cas los xij, hnub no peb yuav tham txog ib qho mob uas tuaj yeem muaj cov tsos mob zoo sib xws, uas yog qhov tsis tshua muaj, tab sis nws tseem ceeb heev rau peb txhua tus kom paub txog. Qhov no hu ua retroperitoneal fibrosis. Nws kuj qee zaum hu ua Ormond's disease.
Retroperitoneal Fibrosis yog dab tsi? Hais yooj yim xwb...
Hais yooj yim xwb, retroperitoneal fibrosis yog
qhov tsim cov nqaij zoo li caws pliav (fibrosis) nyob ib puag ncig cov kabmob hauv qhov chaw hu ua retroperitoneum, qhov chaw tom qab peb lub plab. Nws zoo li ib qho caws pliav tsim rau ntawm peb daim tawv nqaij, tab sis nws tshwm sim hauv peb lub cev. Vim tias nws yog ib qho mob uas zuj zus tuaj, cov tsos mob xws li mob thiab tso zis tsawg dua tuaj yeem hnyav zuj zus raws sijhawm.
Zoo, yog li qhov retroperitoneum no yog dab tsi?
Ntau yam ntawm cov kabmob hauv peb lub plab (xws li lub siab, lub plab, cov hnyuv) raug ib puag ncig los ntawm daim nyias nyias hu ua peritoneum.
Qhov chaw tom qab peritoneum no, mus rau tus txha nraub qaum, hu ua retroperitoneum. Thaj chaw no yog qhov chaw uas peb:
- Cov raum
- Cov ntu ntawm lub cev tso zis
- Cov hlab ntsha loj uas nqa ntshav mus rau thiab los ntawm ob txhais ceg (piv txwv li, qhov qis dua vena cava)
- Cov kab mob tseem ceeb xws li cov qog adrenal nyob ntawd.
Qhov no cuam tshuam li cas rau peb lub cev?
Raws li tau hais lawm, fibrosis, lossis cov nqaij caws pliav, maj mam tsim, cuam tshuam rau cov kabmob thiab lwm yam qauv hauv retroperitoneum.
Feem ntau, qhov no feem ntau cuam tshuam rau cov ureters, cov raj uas nqa cov zis los ntawm peb lub raum mus rau lub zais zis. Xav txog seb yuav muaj dab tsi tshwm sim thaum cov nqaij tuab ntawd tsim nyob ib puag ncig cov raj no thiab nruj? Nws zoo li nias lub yeeb nkab dej, thaiv cov zis ntws. Yog tias qhov mob no hnyav zuj zus,
cov teeb meem txaus ntshai xws li kev ua tsis tau haujlwm ntawm lub raum tuaj yeem tshwm sim.
Leej twg yuav muaj feem mob retroperitoneal fibrosis ntau dua?
Tus mob no
feem ntau tshwm sim rau cov txiv neej hnub nyoog ntawm 40 thiab 60 xyoo. Qhov no txhais tau tias cov txiv neej hnub nyoog nruab nrab muaj feem yuav mob ntau dua me ntsis. Tsis tas li ntawd xwb, muaj ntau yam ua rau mob ntxiv:
Dab tsi ua rau qhov no? Ua rau muaj tus kab mob Ormond
Feem ntau,
nws nyuaj rau nrhiav qhov ua rau qhov no. Hauv kev kho mob, peb hu nws ua
idiopathic . Qhov ntawd txhais tau tias "tsis paub ua rau." Txawm li cas los xij, muaj qee kis uas nws tshwm sim ua ib qho teeb meem ntawm lwm yam mob. Qee qhov ua rau muaj xws li:
- Qee cov tshuaj (peb yuav tham txog qhov no me ntsis).
- Hom mob qog noj ntshav , tshwj xeeb tshaj yog Hodgkin lymphoma thiab non-Hodgkin lymphoma.
- Cov mob kis kab mob .
- Kev kho mob hluav taws xob rau tej yam xws li mob qog noj ntshav.
- Kev puas tsuaj rau cov nqaij ntawm thaj chaw ntawd, txawm yog vim phais lossis lwm yam xwm txheej.
Cov tshuaj twg ua rau muaj qhov no?
Tau pom tias qhov mob no tuaj yeem tshwm sim thaum siv qee yam tshuaj ntev. Nov yog ob peb yam piv txwv:
- Cov tshuaj beta- blockers yog ib pawg tshuaj siv los kho kab mob plawv . Piv txwv li suav nrog propranolol, metoprolol, thiab atenolol.
- Cov tshuaj dopamine antagonists yog cov tshuaj siv los kho mob hlwb thiab xeev siab. Piv txwv li: methyldopa, pergolide.
- Cov ntsiav tshuaj Hydralazine rau cov ntshav siab.
- Cov tshuaj xws li ergotamine, uas yog siv rau mob taub hau migraines.
- Qee cov tshuaj tua kab mob, tshwj xeeb tshaj yog cov tshuaj analgesics thiab NSAIDs .
Tseem Ceeb: Yog tias koj siv hom tshuaj no, tsis txhob ntshai. Tsis yog txhua tus yuav muaj tus mob no. Tab sis nws yog ib qho tseem ceeb kom paub txog qhov no thiab tham nrog koj tus kws kho mob txog nws.
Cov tsos mob ntawm qhov no yog dab tsi?
Cov tsos mob yuav txawv ntawm ib tus neeg mus rau ib tus neeg. Nws nyob ntawm qhov twg ntawm cov fibrosis thiab nws hnyav npaum li cas.
Thaum ntxov, koj yuav hnov mob hauv koj lub plab, nraub qaum qis, lossis sab nraub qaum. Qhov mob no tuaj yeem tsis meej, txhais tau tias nws nyuaj rau txheeb xyuas "ntawm no thiab qhov ntawd," thiab nws tuaj yeem yog qhov mob dav dav. Lwm cov tsos mob suav nrog:
- Nws nyuaj rau txav koj ob txhais ceg thiab txav mus los.
- Hydrocele: Qhov no yog ib qho mob uas cov txiv neej lub noob qes o.
- Ob txhais ceg o, mob hauv ob txhais ceg, lossis hloov xim ntawm daim tawv nqaij ntawm ob txhais ceg.
- Cov zis tso tawm tsawg dua.
Tej yam teeb meem uas yuav muaj los ntawm tus kab mob Ormond yog dab tsi?
Yog tias retroperitoneal fibrosis loj zuj zus, uas txhais tau tias cov nqaij caws pliav loj hlob thiab pib nias cov kabmob,
ntau yam teeb meem tuaj yeem tshwm sim. Ib txhia ntawm lawv yog:
- Kab mob ntshav tsis txaus (Anemia): Qhov no txhais tau tias cov qe ntshav liab hauv lub cev tsawg zuj zus, lossis tsuas yog "tsis muaj ntshav txaus".
- Anuria: Qhov no yog ib qho mob uas tsis muaj zis tawm kiag li. Qhov no yog ib qho xwm txheej ceev.
- Lub cev khaus.
- Jaundice: Qhov muag thiab daim tawv nqaij daj.
- Xeev siab thiab ntuav.
- Cov teeb meem ntawm lub paj hlwb.
- Kev tuag ntawm cov ntaub so ntswg hauv plab (necrosis).
- Poob phaus.
Yuav kuaj mob retroperitoneal fibrosis li cas?
Yog koj muaj cov tsos mob no, mus ntsib kws kho mob thiab lawv yuav kuaj koj. Qhov no yuav suav nrog:
- Kev kuaj lub cev: Tus kws kho mob yuav kov koj lub plab kom paub seb puas muaj qhov txawv txav, xws li muaj pob.
- Kev kuaj ntshav: Cov no tuaj yeem ntes tau cov cim qhia ntxov ntawm kab mob raum thiab cov teeb meem xws li ntshav tsis txaus.
- Kev kuaj ultrasound ntawm lub raum (raum): Yog tias cov tsos mob qhia txog teeb meem ntawm lub raum, qhov kev kuaj no tuaj yeem soj ntsuam qhov mob fibrosis thiab lwm yam teeb meem.
- Kev thaij duab CT: Qhov no tuaj yeem ntsuas qhov hnyav ntawm fibrosis. Nws kuj tseem tuaj yeem pab tshem tawm lwm yam mob, xws li o ntawm cov qog ntshav hauv qhov chaw mos lossis lwm yam qog.
Puas tsim nyog yuav tsum tau kuaj nqaij me me (biopsy)?
Feem ntau, kev kuaj mob retroperitoneal fibrosis tuaj yeem kuaj tau los ntawm kev kuaj ntshav thiab kev kuaj duab uas tau hais los saum toj no (ultrasound, CT scan). Txawm li cas los xij, qee zaum tshwj xeeb
, yuav tsum tau kuaj biopsy. Qhov no txhais tau tias yuav tsum tau muab ib daim nqaij thiab kuaj nws hauv qab lub tshuab microscope. Cov xwm txheej zoo li no suav nrog:
- Yog tias muaj kev xav tias muaj mob qog noj ntshav lossis kab mob sib kis.
- Yog tias kev kho mob thawj zaug tsis ua tiav.
Kuv xav tau kev kho mob hom twg?
Cov kev kho mob zoo tshaj plaws rau koj yuav nyob ntawm qhov chaw thiab qhov hnyav ntawm cov fibrosis. Thaum ntxov ntawm tus kab mob Ormond, koj txoj kev kho mob yuav suav nrog:
- Cov tshuaj Corticosteroids:Cov tshuaj no sai sai txo qhov o ntawm lub cev thiab tiv thaiv kev loj hlob ntawm fibrosis.
- Cov Tshuaj Kho Mob Tiv Thaiv Kab Mob: Cov tshuaj no ua haujlwm los ntawm kev hloov pauv txoj kev uas lub cev tiv thaiv kab mob ua haujlwm. Qhov no tuaj yeem txo qhov kev pheej hmoo ntawm kev rov qab muaj fibrosis yav tom ntej. Txawm li cas los xij, vim tias cov tshuaj kho mob tiv thaiv kab mob tuaj yeem siv sijhawm ntau lub hlis los ua haujlwm, lawv yuav raug muab nrog rau corticosteroids.
- Kev tswj tshuaj: Qee zaum, yog tias qhov fibrosis yog los ntawm cov tshuaj uas koj noj, koj tus kws kho mob yuav hloov cov tshuaj lossis txo cov tshuaj noj.
Yog tias fibrosis tau nce qib, lwm yam kev kho mob yuav tsum tau ua:
- Kev Phais Mob: Tej zaum yuav tsum tau phais mob kom tshem tawm cov ntaub so ntswg fibrotic thiab kho txhua qhov kev puas tsuaj rau cov ntaub so ntswg nyob ib puag ncig.
- Stents: Raws li tau hais ua ntej, yog tias lub ureter raug thaiv, ib lub cuab yeej me me zoo li lub raj (stent) tuaj yeem muab tso rau hauv nws kom nws qhib.
Peb yuav ua li cas thiaj tiv thaiv tau qhov mob retroperitoneal fibrosis?
Vim tias qhov mob no feem ntau tsis paub tias yog vim li cas,
nws nyuaj rau tiv thaiv kom tsis txhob muaj mob. Txawm li cas los xij, vim tias qee cov tshuaj paub tias ua rau muaj mob, koj tus kws kho mob yuav saib xyuas koj cov tsos mob ntawm fibrosis, tshwj xeeb tshaj yog tias koj noj lawv ntev.
Puas muaj peev xwm txo tau qhov uas qhov no yuav tshwm sim dua tom qab kho tas?
Yog tias koj yuav tsum tau phais, qee zaum ib txheej ntawm cov nqaij rog yuav qhwv ib ncig ntawm cov hlab ntsha thaum lub sijhawm phais. Qhov no lawv hais tias ua rau nws nyuaj rau cov fibrosis rov tshwm sim dua.
Kuv yuav zoo siab sai npaum li cas?
Yog tias koj noj tshuaj xws li corticosteroids, lossis tom qab kev tswj hwm tshuaj
, koj yuav pib zoo dua hauv ob peb lub lis piam. Txawm li cas los xij, yog tias koj xav tau cov tshuaj immunomodulators, stents, lossis phais, nws yuav siv sijhawm ntev me ntsis kom rov zoo.
Cov neeg uas muaj retroperitoneal fibrosis yuav zoo li cas?
Feem ntau cov neeg rov zoo tag nrho. Lub sijhawm zoo tshaj plaws rau kev kho mob zoo yog
thaum kuaj pom tus kab mob thaum ntxov. Txawm li cas los xij, nws yog ib qho tseem ceeb uas yuav tsum nco ntsoov tias fibrosis tuaj yeem rov tshwm sim ntau lub hlis lossis ntau xyoo tom qab kev kho mob.
Nyob nrog tus kab mob Ormond zoo li cas?
Rau cov neeg uas muaj mob me me xwb,
koj yuav tsum tau mus ntsib kws kho mob tas li. Qhov no txhais tau tias koj yuav tsum mus ntsib koj tus kws kho mob tas li kom paub seb puas muaj cov cim qhia tias tus kab mob rov qab los.
Tom qab phais mob kom kho qhov kev thaiv ntawm txoj hlab zis, yuav muaj dab tsi tshwm sim?
Hydronephrosis tuaj yeem tshwm sim thaum, ob peb hnub tom qab phais, cov kws kho mob cia li tso cov zis uas tau sib sau ua ke hauv koj lub raum.Ceev faj txog qhov teeb meem hu ua "urinary retention." Thaum cov zis uas tau raug kaw hauv lub cev tawm los tam sim ntawd, cov hauv qab no tuaj yeem tshwm sim:
- Kev tsis sib npaug ntawm cov electrolyte hauv lub cev.
- Kev qhuav dej.
- Kev poob siab Hypovolemic (ib qho mob uas tshwm sim los ntawm kev txo cov ntshav ntim).
Kab mob retroperitoneal fibrosis, lossis Ormond's disease, yog ib yam mob uas cov nqaij zoo li caws pliav tsim nyob rau tom qab ntawm lub plab. Cov neeg uas noj qee yam tshuaj muaj feem yuav mob no ntau dua. Yog tias koj tau kuaj pom tias muaj tus mob no, nrog koj tus kws kho mob tham txog tej lus nug lossis kev txhawj xeeb uas koj muaj. Lawv nyob ntawd los pab koj.
Tej yam tseem ceeb tshaj plaws uas yuav tsum nco ntsoov (Cov Lus Qhia Coj Mus Tsev)
Zoo, yog li tam sim no peb nkag siab zoo dua txog Retroperitoneal Fibrosis yog dab tsi.
Txawm hais tias nws yog ib qho mob tsis tshua muaj, nws yog ib qho tseem ceeb heev uas yuav tsum paub txog nws.- Nco ntsoov, qhov no yog cov nqaij tuab uas tsim nyob ib puag ncig cov kabmob uas yuav tsum nyob hauv lub plab, mus rau tus txha nraub qaum.
- Feem ntau nws cuam tshuam rau cov zis thiab tuaj yeem ua rau lub raum puas tsuaj.
- Qhov ua rau tsis yog ib txwm meej, tab sis tej yam xws li qee yam tshuaj, mob qog noj ntshav, thiab kev kis kab mob kuj tuaj yeem yog cov ua rau.
- Nws yog ib qho tseem ceeb uas yuav tsum nrhiav kev pab kho mob yog tias koj muaj cov tsos mob xws li mob plab/mob nraub qaum me ntsis thiab tso zis tsawg dua.
- Yog tias kuaj pom ntxov ces yuav muaj kev kho mob zoo. Yog li ntawd, tsis txhob tso tseg cov tsos mob.
- Yog koj muaj lus nug txog qhov no, tsis txhob ntshai nug koj tus kws kho mob.
Peb vam tias cov ntaub ntawv no yuav pab tau koj. Nyob kom noj qab nyob zoo!
Retroperitoneal Fibrosis, Ormond's kab mob, kab mob raum, mob plab, teeb meem tso zis, fibrosis, phais mob
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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus