Bɔku tɛm yu kin gɛt wan strenj pen we kin bigin na yu ed bak ɛn travul go dɔŋ yu nɛk? Dis pen kin bɔku mɔ we yu kɔf, sniz, ɔ es sɔntin we ebi? Sɔntɛnde, yu kin fil lɛk se yu de tɔn ed , yu nɔ kin balans we yu de waka, ɔ yu an dɛn kin swɛ? Ivin if yu tink se dis na nɔmal ed pen, sɔntɛnde ɔda rizin kin de we ayd biɛn dɛn. Dat na wan pan dɛn rare bɔt impɔtant kɔndishɔn dɛn we yu fɔ no bɔt.
Fɔ tɔk am simpul wan, wetin na Chiari Malformation?
Dis na smɔl kɔmplikɛt nem, bɔt lɛ wi kip am simpul. Wi bren de protɛkt insay wi skel. na di bכtכm pat pan dis sכkul, jכs usay di nεk mit di sכkul, wan ol de we wi spεnal kכd de kכmכt. dis dεn kכl am di ``foramen magnum'' insay mεdikal tεm dεm.
insay wan kכndishכn we dεn kכl Chiari malfכmeshכn, di lכw pat pan wi bren, spεshal wan di pat we dεn k כl sεribεl , dεn de push כ sכk dכn tru di foramen magnum, insay di spεs usay di spεnal kכd de. Tink bɔt am lɛk we yu de tray fɔ fit sɔntin we big pas aw i go fit insay smɔl ples.
Wi sɛribɛl na in de kɔntrol wi muvmɛnt, balans we wi de waka, kɔntrol aw wi de tinap, ɛn to sɔm mak wi atɛnshɔn. So we dis pat afɛkt, prɔblɛm dɛn we gɛt fɔ du wit dis kin kam.
dis kכmpreshכn de ambɔg di fכ fכlכ fכ di sεribrospεnal fכluid (CSF), we de sכkכt rawnd di bren εn di spεnal kכd. Dis tan lɛk wata paip we dɔn blok. Dis kin put prɛshɔn pan sɔm pat dɛn na di bren ɛn spɛshal kɔd, ɛn dis kin mek pɔsin gɛt difrɛn sayn dɛn.
Wetin mek dis de apin? Wetin na di rizin dɛn?
Bɔku tɛm, Chiari malfɔmeshɔn na wan sik we dɛn bɔn wit . dis min se di kכndyushכn de apin biכs fכ difεkt na di divεlכpmεnt fכ di bren εn sכkul we di pikin de gro na di bεlε. dis na biכs sכm pipul dεn gεt sכm sכm pas nכmal spεs na di sכkul we dεn kכl di posita fכs, we na di say we di bren de. Bɔt di wan dɛn we de stɔdi bɔt dis stil nɔ shɔ wetin mek dis kin apin.
Sɔntɛnde dis kin bi bikɔs ɔf wan jɛnɛtik kɔz.
Na smɔl tɛm nɔmɔ dis sik kin apin afta dɛn bɔn am, dat na we pɔsin big . I kin bi bikɔs ɔf:
- Wan tumbu we de na di bren.
- If yu wund yu ed, i kin mek yu gɛt sak we ful-ɔp wit wata (cyst) ɔ blɔd klot (hematoma) na di bren.
- wan kכndyushכn we dεn kכl ``hydrocephalus'', we na di wata we de kכmכt na di bren.
- כda kכndyushכn dεm we de fכm di spεnal kכd lεk tεthered cord syndrome.
Difrɛn kayn dis sik de?
Yes, dis kכndyushכn kin sheb to difrεn men tכp dεm dipכnt pan aw i siriכs εn aw di pat dεm na di bren de afekt.
| Kayn | Simpul ɛksplen |
|---|---|
| Tayp I. Tayp I | Dis na di kayn we we kɔmɔn pas ɔl ɛn we nɔ rili siriɔs . na di lכw pat pan di sεribra nכmכ dεn de push insay di spεnal kanal. Sɔm pipul kin liv wae nɔr gɛt ɛni sayn. Bɔku tɛm, dɛn kin no am bay we dɛn de du MRI skan fɔ ɔda rizin. |
| Tayp II | dis dεn kכl am bak `(Arnold-Chiari malformation).` na ya, dεn de push כl tu di sεribεl εn di bren stεm dכn. bכku tεm dεn kin si dis tכgeda wit di bכn difεkt `(spina bifida).` |
| Tayp III | Dis na wan kayn tin we nɔ kin apin so ɔltɛm ɛn we kin rili siriɔs . di pat dεm na di bren de kכmכt na di sכkul εn go insay di bak pat na di nεk. Dis kin mek pɔsin in layf de pan denja. |
| Tayp IV | Dis na tin bak we nɔ kin apin so ɔltɛm. insay dis kes, di sεribכl nכ de divεlכp ful wan. Ɔ, di pat dɛn nɔ de. |
Wetin na di sayn dɛm wae kin kam pan pɔrsin wae gɛt tayp I?
Nɔto ɔlman we gɛt Tayp I go gɛt di sik. Bɔt if di sayn dɛn kin apin, sɔm pan dɛn na:
- Oksipital ed pen ɛn nɛk pen:Dis na di men ɛn kɔmɔn sayn. Di pen kin bɔku we yu de kɔf, sniz, ɔ es ebi ebi tin.
- Diziz ɛn Balɛns Prɔblɛm: Fɔ fil diziz, lɛk se yu go fɔdɔm we yu de waka.
- Di mɔsul dɛn we wik.
- Di an ɛn fut dɛn we nɔ kɔmɔn ɔ ɔda tin dɛn we nɔ kɔmɔn .
- Prɔblɛm dɛn we yu de si: yu nɔ de si fayn, yu de si yu tu tɛm.
- I nɔ izi fɔ swɛla.
- Ring na di yes (tinnitus) ɛn nɔ de yɛri fayn.
- Prɔblɛm fɔ slip: Nɔ kin slip, ɔ fɔ stɔp fɔ blo fɔ shɔt tɛm we yu de slip (slip apnea).
- Nɔs ɛn vɔmit.
De impɔtant tin na dat, dɛn sayn ya kin difrɛn frɔm wan pɔrsin to ɔda pɔrsin. Ɛn nɔto ɔltɛm dɛn kin bi di sem. Sɔm de dɛn kin wɔs, sɔm de dɛn kin bɛtɛ.
Aw yu go fɛn dis, Dɔktɔ?
We yu dɔn tɔk bɔt yu sik dɛn, yu dɔktɔ go tek tɛm luk yu fɔs, mɔ fɔ chɛk yu nyurolɔjik . Dis go chɛk yu balans, yu mɔsul trɛnk, riflɛs, ɛn sɛns.
Dɔn, if ɛni dawt de bɔt dis kɔndishɔn, dɛn go rifer yu fɔ sɔm tɛst fɔ kɔnfirm am.
- MRI (Magnetic Resonance Imaging) Scan: Dis na di bεst εn imכtant tεst fכ no di Chiari malfכmeshכn. MRI kin si di strכkchכ fכ di bren εn spεnal kכd rili klia wan. i kin si εksakכt aw di bren de kכmprεs εn if di fכ fכlכ fכ `CSF` fכ fכlכ de bכku.
- Cine MRI: Dis na spɛshal kayn MRI. I tan lɛk fim. Yu kin si di CSF de muv rawnd di bren insay rial tɛm, dat na layf.
- CT (Computed Tomography) Scan: Dis kin chɛk fɔ ɛni abnɔmal tin na di bon dɛn na di skel.
Wetin na di tritmɛnt dɛn?
Di tritmɛnt kin dipen pan di kayn we aw yu gɛt, aw yu de fil bad, ɛn aw i kin afɛkt yu ɛvride layf.
1. Nɔ Simptom: If yu gɛt Tayp I ɛn yu nɔ gɛt ɛni simptom, ɔ if dɛn nɔ de mɔna yu, sɔntɛm yu nɔ nid ɛni tritmɛnt . Yu dɔktɔ go tɛl yu fɔ kam insay fɔ chɛk-ap ɔltɛm fɔ wach yu kɔndishɔn.
2. Mɛrɛsin:If yu gɛt sɔm sayn dɛn lɛk ed we de at ɛn yu nɛk pen, yu dɔktɔ kin gi yu mɛrɛsin fɔ mɛn yu pen (NSAID) ɛn tin dɛn we de mek yu mɔsul rilaks fɔ kɔntrol dɛn.
3. Ɔpreshɔn: If yu gɛt siriɔs sik dɛn we yu nɔ go ebul fɔ kɔntrol wit mɛrɛsin, ɔ if yu skan sho se yu bren ɔ yu spɛnal kɔd dɔn pwɛl, yu dɔktɔ go tɛl yu fɔ du ɔpreshɔn.
Di tu men gol dɛn fɔ ɔpreshɔn na:
- fכ ridyus di prεshכn pan di bren εn di spεnal kכd.
- rεstכr di fכlכ fכ CSF fכluid.
Di ɔpreshɔn we dɛn kin du mɔ na Posterior Fossa Decompression Surgery . Insay dis, di dɔktɔ we de du di ɔpreshɔn kin pul wan smɔl bon na di say we di skel de, usay i mit di nɛk. dis de mek mכr spεs fכ di bren εn di spεnal kכd. di mεmbran we de rawnd di bren (dura) dεn de opin bak εn dεn de siw wan pat insay in ples. dis de mek di sεribrospεnal fכluid (CSF) fכ fכlכ fri wan.
If yu gɛt haydrosɛfalɔs bak (wata we de bɔku na yu bren), yu kin nid fɔ mek dɛn put shunt fɔ pul di ɛkstra wata.
Mɛsej we dɛn kin kɛr go na os
- Chiari Malformation na strכkchכral difεkt we de kכz fכ di lכw pat pan di bren we dεn de push insay di spεnal kanal.
- Na Tayp I, we na di kayn we we dɛn kin gɛt mɔ, bɔku pipul dɛn nɔ kin gɛt ɛni sayn. Ivin if di sayn dɛm de, di men sayn na we yu ed de at na yu bak pat na yu ed ɛn yu nɛk.
- Di men tɛst we dɛn kin yuz fɔ no dis sik na MRI skan .
- If no sayn nɔ de, dɛn nɔ nid fɔ gɛt ɛni tritmɛnt. If sɔm sayn dɛn de, dɛn kin trit dɛn wit mɛrɛsin ɔ ɔpreshɔn.
- If yu gɛt ɛni dawt ɔ ɛni sayn, di bɛst tin fɔ du na fɔ go to yu dɔktɔ fɔ advays . I rili impɔtant fɔ du tin bay di advays we dɔktɔ gi yu pas fɔ fɛn infɔmeshɔn na di intanɛt.











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