Tlemte i kal lai te, stairs i chhoh lai te angin i chau tawh lo em ni? Thâwk lak harsa i ti mai mai em? ‘Hei hi i tar hunah a thleng thin’ tiin i ngaihtuah mai thei. Mahse khuh zawng zawng ni lo, khuh zawng zawng hi thil pangngai a ni lo. Vawiin hian natna pakhat, hetiang symptoms thlen thei, chu chu a pawi deuh hlek a, mahse fimkhur a pawimawh hle. Chu chu Pulmonary Fibrosis a ni .
Pulmonary Fibrosis (PF) hi eng nge ni tak tak?
A awlsam zawngin, hei hi i lung chhunga tissue nalh tak takte chu a khauh zauh zauh a, hliam a siam a ni. Kan vunah hian hliam kan tuar a, chutiang bawk chu kan lung chhungah pawh a thleng thin. He scarring hian lungs chu a elasticity a hloh tir a, chu chuan a inflate emaw deflate tha thei lo emaw a ni.
Kan thawh hian oxygen chu lung chhunga boruak bawm (alveoli) te tak teah a lut a. Heng air sacs vel tissue te hi a khauh chuan oxygen hi thisenah a lut tha lo hle. Hei hian thaw hahdam a ti harsa a, kan thaw a tlachham thin. He natna hi a tlangpuiin a zual zel a, hun kal zelah a zual zel a ni.
Idiopathic pulmonary fibrosis (PF) tih hi eng nge ni?
A châng chuan doctor-te chuan lung khauh leh hliam chhan chiang tak an hmu thei lo. Chu chu Idiopathic Pulmonary Fibrosis kan tih chu a ni. "Idiopathic" tih thumal hi 'a chhan hriat loh' tihna a ni. Dik tak chuan Pulmonary Fibrosis vei tam zawk hian he idiopathic type hi an nei a ni.
He natna lan chhuah dan engte nge ni? Engtin nge i hriat chian?
Heng symptoms te hi a tir lamah chuan hmuh tur a awm lo mai thei a, mahse hun kal zelah a pung zauh zauh thin. Chûngte chu kum upa lam aṭanga lo awm inthlâk danglamna pangngai mai mai niin i ngai mai thei. Mahse heng symptoms te hi ngaihven a pawimawh hle.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Thâwk a tawi | Thâwk lak harsa i ti thei a, a bîk takin kea kal emaw, stairs chhoh ang chi hna awlsam tak tak i tih lai emaw chuan. Natna a zual zel chuan ding reng chung pawhin thawk harsa i ti mai thei. |
| Cough vawt (dry cough) awm reng | Cough awm reng, tithinur thei, dry cough hi mucus tel lovin a awm thin. |
| Chau | Hna engmah thawk lo mah la, chau leh chau takin i inhria fo thin. |
| A taksa rihna tlahniam nghal | Beih lovin i thau a tlahniam a, chhan hriat lohvin. |
| Kut zungtang clubbed tak tak te | Kut zungtang leh ke ruhte chu a zungbun a, nail vel vun chu a lo hring chhuak ta a ni. |
| Vun sen/sem (Cyanosis) 1.1. | Thisena oxygen level a tlahniam chuan hmui, mit vel emaw, kut zungtang emaw chu a sen, a sen emaw, a var emaw a lo ni ta a ni. |
Engvangin nge hetiang natna hi a lo awm? A chhante chu engte nge ni?
Doctor-te chuan heng hliamte hi lung a tihchhiat emaw, a dam tha lo emaw a inflammation avanga lo awm niin an ngai. A chhan awm thei engemaw zat a awm.
| Chhan | Entirna leh hrilhfiahna |
|---|---|
| Connective tissue natna a ni | Natna Rheumatoid Arthritis (RA ), Lupus , leh Scleroderma te pawhin lung a nghawng thei bawk. |
| Environment chhunga thil awmte nena inzawmna | Hun rei tak chhung asbestos leh silica ang chi leivut nena inzawmna. Tin, mold, bacteria, sava bawlhhlawh, emaw dander chi hrang hrang allergy ( Hypersensitivity Pneumonitis ) vang pawh a ni thei bawk. |
| Damdawi leh enkawl dan thenkhat | Damdawi thenkhat, Amiodarone , thinlung natna atana hman, Nitrofurantoin , natna hrik atana hman, Methotrexate , cancer atana hman, leh radiation therapy te pawh hian lung a tichhe thei bawk. |
| Meizial zuk | Meizial hi he natna vei theihna tur risk factor lian tak a ni. |
Tute nge he natna vei theihna sang zawk?
A chunga kan sawite bakah hian thil dang thenkhat chuan he natna vei theihna a tipung thei a ni:
- Kum 65 chunglam a nih vang a ni.
- Mipa nih hi.
- He natna vei chhungte hnai tak (nu leh pa, unau) neih.
- Genetic ( DNA ) inthlak danglamna avanga natna thenkhat neih.
Pulmonary Fibrosis natna avanga harsatna awm thei te chu engte nge ni?
Lung hian hna a thawk tha lo a nih chuan taksa pumpui a nghawng a ni. A bik takin thinlung hian a thawkrim zawk a ngai a ni. Hei hian harsatna hrang hrang a thlen thei a ni.
A pawimawh ber chu natna hi hriat hmasak a, enkawl tan a ni. Hei hian heng ang complication awm theihna a ti tlem thei a ni.
- Hypoxemia: Taksa tissue te hian oxygen mamawh zat an dawng lo.
- Pulmonary Hypertension : Pulmonary Hypertension : Lung lama thisen phurtu thisen kalna kawng hrang hranga pressure a sang chho zel a. Hei hian thinlungah phurrit rit tak a siam a ni.
- Lung infection leh lung tlu tawh.
- Thluak lam hawiRespiratory Failure: Puan hian taksain a mamawh oxygen a pe thei tawh lo.
- Heart Failure : Heart failure hi thinlungin hun rei tak chhung hna thawk nasa lutuk tura nawr luih a nih chuan a awm thin.
Engtin nge natna hi dik taka kan hriat theih ang? (Diagnosis) tih a ni.
Hei hi test khata hriat theih natna a ni lo. I doctor chuan i natna lan chhuah dan chu ngun takin a ngaithla ang a, i rilru chu stethoscope hmangin a ngaithla ang a, chutah chuan test eng emaw zat neih a rawt ang.
Test tih ber berte chu:
- Chest X-ray: A rilru a buai em em a, a rilru a hah em em bawk a.
- High-resolution CT (HRCT) scan: Hei hi special scan a ni a, CT scan pangngai aiin lung chhunga thil chiang zawk a lang thei.
- Pulmonary (lung) function test: Hei hian machine chhungah i puak lut a, chu chuan i lungin boruak a luh theih zat leh i thawk chhuah chak dan a teh a ni.
- Thisen test: Thisen test hi thisen oxygen level ang chi thil chi hrang hrang enfiah nan tih a ni.
- Bronchoscopy: Hnar chhung emaw, hmui emaw kaltlangin camera nei tube te tak te dahin lung chhung lam enfiah a ni.
- Biopsy: A chang chuan, lung atanga tissue te tak te tak te chu lakchhuah a ni a, enfiahin natna a awm tih finfiah a ni.
Hei hi eng enkawlna nge ni? A dam kim thei ang em?
Mi tam takin zawhna pakhat chu a dam kim thei ang em tih hi a ni. Dik tak chuan he natnain lungah hliam a siam hi tihdanglam theih a ni lo.
Mahse, lungngai suh. Enkawlna chuan natna zual zel chu a tikhawtlai thei a, a lan chhuah dan a thunun thei a, i nunphung a tichangtlung thei bawk .
| Enkawl dan tur | Eng thil nge thleng? |
|---|---|
| Antifibrotic damdawi a ni | Nintedanib leh Pirfenidone ang damdawi te hian lung hliam rate a ti hniam a. |
| Corticosteroid hmanga tihdam theih a ni | Hengte hi a chang chuan lung chhunga inflammation tihziaawm nan an hmang thin. |
| Oxygen hmanga enkawlna | Thisena oxygen level a hniam chuan hnar chhunga tube te tak te dah hmangin extra oxygen pek a ni. |
| Pulmonary Rehabilitation hmanga enkawl a ni | Hei hi programme bik a ni a, thawk chhuahna exercise, taksa exercise, leh natna hriatna hmanga i chakna leh nunphung tihchangtlunna a ni. |
| Lung Transplant a ni | Natna na tak nei damlo thenkhat chuan criteria an tlin chuan lung transplant an dawng thei a ni. |
Engtikah nge doctor i hmuh ang? Engtikah nge Emergency Department (ETU) ah i kal ang?
Hemi chungchang chiang taka sawi hian i nunna chhanhimna kawngah a pui thei a ni.
Doctor hmu fo ang che.
A chunga kan sawi tawh ang chi, thawk hah, khuh reng, hna awlsam ber pawh tih harsat ang chi i neih chuan ngaihthah suh A rang thei ang bera doctor hmu la, hei hi sawipui rawh. Natna hi a hriat hma poh leh enkawl a awlsam zawk thin.
ETU-a kal nghal a ngaih hunah
Heng symptoms te hi i neih chuan hun khawhral suh la, damdawi in Emergency Treatment Unit (ETU) ah kal nghal la , 1990 ah call rawh.
| Rikrum! Damdawi inah kal nghal rawh. | |
|---|---|
| 🚨 Thâwk harsa na tak emaw, rang tak emaw | |
| 🚨 A rilru a na | |
| 🚨 Buaina emaw, hriatna danglam emaw | |
| 🚨 Vun, hmui, emaw nail emaw blue discoloration | |
He natna hian hmalam hun eng nge a thlen ang?
He natna hi a vei tih hmuhchhuah a nih hian hlauhna leh hmalam hun hriat chian loh hi thil pangngai a ni. ‘Eng chen nge ka dam a ngai ang?’ tih hi thil pangngai tak a ni bawk.
Mahse, damlo zawng zawng hi an inang vek lo tih hre reng ang che. Mi thenkhat tan chuan natna hi a zual zawi zawi hle a, kum tam tak chhung a ni. Mi dangte tan chuan a hmasawn chak deuh thei a, thla engemaw zat chhungin a kal zel thei bawk. Tuman chiang takin an sawi thei lo.
A pawimawh ber chu i doctor nen zalen taka inbiakna neih a, enkawlna dik tak dawng a, hei hi chakna leh chhungte thlawpna nena hmachhawn hi a ni. Tunlai enkawlna hian damlo dam rei zawng leh nunphung a tichangtlung hle a ni.
Natna vei midangte thil tawn atanga chakna i neih theih nan support group-ah i tel thei a ni.
Take-Home Thuchah a ni
- Pulmonary Fibrosis natna a ni a, chu chu kan taksa peng hrang hrangte a nghet a, a hliam a, thawk a harsat phah a ni.
- Thâwk harsa, khuh hring reng, leh hah lutuk te hi a lan chhuahna ber a ni. Hengte hi ngaihthah suh.
- He natna hi tihdam kim theih ni lo mah se, enkawlna \ha tak chuan natna kal zel dan a thunun thei a, nun \ha tak i neih theih phah a ni.
- Meizial i zuk chuan chawlhsan nghal a pawimawh . Tin, leivut leh chemicals, lung tana tha lo laka inven a pawimawh hle bawk.
- Nangmah emaw, i hriat tu emaw chuan heng natna lan chhuah dan hi i neih chuan, doctor thurawn la hmasa phawt ang che . Enkawlna atan chuan rang taka diagnosis a pawimawh hle.











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