A châng chuan i taksa peng hrang hrangah natna mak tak tak leh hring dup pawh i nei thei bawk a ni lawm ni? A bik takin i beng leh hnar ang hmunah te. Hengte hi random thil mai a ni lo mai thei. Vawiin hian kan sawi dawn a, natna hriat tur awm lo, mahse hriat a pawimawh em em a ni. Hei hi
Relapsing Polychondritis an ti a . A hming hi a buaithlak deuh nachungin, awlsam takin i hrethiam ang u.
He natna hi eng nge ni?
A awlsam zawngin sawi ila,
Relapsing Polychondritis hi natna hmuh tur awm lo tak a ni a, kan taksaa
cartilage a nghawng a ni. Thil thleng chu cartilage chu a
inflamed (swelling, redness, leh pain) a ni a, hun kal zelah cartilage chu
a atrophy zauh zauh (melt leh wear away) a ni. Tunah chuan he cartilage hi eng nge a nih i ngaihtuah mai thei. Cartilage hi kan taksa chhunga inzawmna (connective tissue) bik a ni. I hre reng em, kan beng bulah khawih la, kan hnar hmalam chu khawih rawh. Chu hmunah chuan chu hmun tlemte, mahse a chak deuh deuh chu a awm a, chu chu cartilage a ni. Hengte hi kan ruhkawr, kan kawr, leh kan thluak (trachea)-ah hmun tam takah hmuh tur a awm a. He `Relapsing Polychondritis` natna hian a nghawng ber chu:
- I beng chhunga cartilage thlengin .
- I hnar chhunga cartilage thlengin .
- I larynx (kan thusawina box) chu i rilruah a awm a .
- I thlipui (trachea) .
He natna hi hming dang engemaw zatin an ko a, mahse damdawi lam deuh deuh an ni: `Chronic atrophic polychondritis`, `Generalized or systemic chondromalacia`, `Meyenburg-Altherr-Uehlinger syndrome`, `Relapsing perichondritis`, `Von Meyenburg disease`. Mahse, a hming hman tam ber chu `Relapsing Polychondritis` tih a ni.
Hei hi tuin nge dawng thei ang? Engtiang chiahin nge a hluar?
Hetiang dinhmun hian tu pawh a nghawng thei a ni. Mahse,
kum 40 leh 60 inkar mite zingah a intan tlangpui a, a hluar danah chuan a takah chuan
natna hmuh tur awm lo tak a ni . Zirchiangtute sawi dan chuan mi sanghnih leh sawmriat leh panga (285,000) zinga pakhat velin a nghawng a ni. Chumi awmzia chu mipui tam takah mi tlemte chauh a nghawng tihna a ni. Chuvang chuan he natna hi khawtlang nunah sawi a hlawh vak lo.
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
Mi tam takin zawhna an neih chu, "Engvangin nge he natna hi a lo awm?" Dik tak chuan scientist te hian Relapsing Polychondritis hi eng nge a thlen tih
chiang takin an la hre lo . Mahse, scientist thenkhat chuan
autoimmune disease niin an ngai.Tunah chuan, "He autoimmune natna hi eng nge ni?" A awlsam zawngin kan taksa hian immune system a nei a. A hna chu hnam dang natna hrik doin natna laka min humhim hi a ni. Kan taksaah sipai team kan neih ang mai a ni. Mahse autoimmune natnaah chuan kan sipaite ngei pawhin
kan cell leh tissue hrisel tak takte chu an rawn bei sual tan thin . Relapsing Polychondritis-ah hian immune system hian hetiang hian kan cartilage hi a bei niin an ngai. Mahse, engvangin nge hetiang thil hi a thlen tih erawh a la chiang lo.
Hei hi eng symptoms nge ni?
Relapsing polychondritis hi a tlangpuiin a awm chhunzawm zel a ni lo. Episode emaw flare emaw angin
a lo kal a, a kal zel bawk . Symptoms a lan chuan ni engemaw zat emaw, kar engemaw zat emaw a awm thei. Tichuan an kal bo ta a. Mahse, kum tam tak chhungin symptoms a lo lang leh thei a ni.
A lan chhuah hmasak ber: Mi tam tak tân chuan he natna hi
beng pakhat emaw, beng pahnih emawa natna, hnim hring, hring, leh sen hring aṭangin a inṭan a ni . Pawimawh tak chu heng symptoms te hian beng chhung leh pawna cartilage a nghawng a,
mahse earlobe erawh a nghawng lo . A chang chuan beng chu a
floppy thei bawk . Ni khat chu i thianpa Sunil-a chu a beng na, a sen leh a hring chhuak thut mai ang tih han ngaihtuah teh. Allergy mai mai niin a ngai a. Ni rei lo te chhungin a bo ta a ni. Mahse thla engemaw zat hnuah chuan beng dang chu a lo awm leh ta a. Hetiang hian he natna lan chhuah dan hi a lo lang tan thei a ni.
A lan chhuah dan dangte:- Indentation of the nasal cartilage : Hei hian hnar bridge a tikehsawm thei a, chu chuan saddle nose deformity (hnar hi sakawr hnungzang chunga saddle ang mai a ni) an tih dinhmun a thlen thei a ni.
- Joint pain : Joint pain , arthritis ang chi hi a awm thei.
- Hnar natna (nasal congestion) a awm .
- A rilru chhungril lam , hnute ruh bulah natna .
- Mit na leh sen hring .
- Beng chhung lam a nghawng chuan: Hriatna hloh , beng chhunga ri reng (tinnitus) , .Luak chhuak (vertigo) ang chi thil a awm thei.
- Thâwk harsa: Hei hi thlipui (trachea) a nghawng chuan a thleng ṭhin. Larynx a nghawng chuan tawng harsa a awm thei bawk.
Pawimawh: Thâwk harsat hi thil pawi tak a ni thei a, chuvangin doctor thurawn la nghal rawh.
Symptoms hmuh tur awm lo: Hengte hi hmuh tur a tam lo hle a, mahse mi thenkhat chuan an tawng thei a ni:
- Heart valve lama harsatna nei.
- Thinlung ri danglam tak (Heart murmur).
- Mit hmuhna hloh.
- Kal natna.
Khawnge ? Doctor-te hian engtin nge hei hi an hmuh?
Heng symptoms te hi i neih chuan Doctor pan a tha ber. Mahse, Relapsing Polychondritis hriat theihna
tur test pakhat mah a awm lo . Chu chu, thisen test emaw scan emaw pakhat mah "hei hi Relapsing Polychondritis a ni" tih hriat theihna tur a awm lo tihna a ni.
Hetiang chhinchhiahna pathum tal hi rei tak i neih tawh chuan doctor chuan he natna hi i nei tih a ringhlel ang. Entirnan, i beng chhunga cartilage hring, i hnar a cartilage hring, leh ruh natna te ang chi symptoms inzawmkhawm i neih chuan
i doctor chuan hei hi a ringhlel mai thei. A châng chuan, diagnosis nemnghehna ṭanpui tûrin:
- Biopsy hi beng atanga cartilage chi khat lak atanga tih theih a ni .
- Thisen test eng emaw zat tih theih a ni (damdawi lam thil dang tih loh nan leh inflammation chhinchhiahna zawng turin).
Hei hi eng enkawl dan nge ni ang?
Vanduaithlak takin Relapsing Polychondritis hi
damdawi a awm lo . Chu chu damdawi a la awm lo tihna a ni. Mahse, chu chu engmah tih theih a ni lo tihna erawh a ni lo.
Enkawlna tum berte chu:- Symptoms tihziaawmna (natna tihziaawmna, hring dup).
- Harsatna awm thei tihziaawmna.
Enkawlna hi damdawi hmanga tan a ni tlangpui a, chungte chu:
- Colchicine: Hei hi gout natna damdawi pek fo a ni.
- Corticosteroids: Entirnan , prednisone . Hengte hi damdawi chak tak tak, inflammation tihziaawmna tur an ni.
- Dapsone: Hei hi natna hrik dona atana hman thin damdawi a ni.
- Non-steroidal anti-inflammatory drugs (NSAIDs): Hengte hian natna leh hliam tihziaawmna turin a pui a ni.
A natna hi a nasat deuh chuan doctor-te chuan hetiang damdawi hi an pe thei a ni:
- Immune system titawp thei damdawi: Entirnan , cyclophosphamide emaw azathioprine emawHengte hian an tih chu immune system tha lo hnathawh tihtlem hi a ni.
- Methotrexate: Hei hi immune-suppressing drug a ni bawk a, arthritis ang chi natna enkawlna atana hman thin a ni.
A nasat lutuk chuan operation neih a ngai mai thei:
- Heart valve surgery: Heart valve a chhiat chuan.
- Tracheostomy: Thlipui (windpipe) nasa taka a inkhar chuan thlipui (windpipe)-ah hian kawr atanga direct-a tube dah a ngai mai thei.
- Thlawhna kawng hawn dan tur:
- Stent dah dan: Tube te tak te, laryngeal stent ang chi chu larynx emaw trachea emaw ah dahin a inhawng reng thin.
- Airway dilation: Thlawhna kawng zim tawh chu tihzauh nan hmanraw, balloon ang chi hman a ni.
- Trachea emaw larynx emaw siam thar lehna tur operation .
Hei hi a thleng lo thei lo em ni?
Relapsing Polychondritis awm chhan dik tak hriat a nih loh avangin , a ven dan tur sawi a harsa hle. Tunah hian
invenna tur ruahmanna bik a awm lo .
He natna hian thihna a thlen thei em? A dam rei zawng chu eng nge ni?
Hei hi hlauhawm tak angin a lang thei a, mahse
Relapsing Polychondritis vei te dam rei zawng hi a tlangpuiin a tha . Zirchianna atanga a lan dan chuan
damlo 95% chu an natna hmuhchhuah atanga kum 8 hnuah pawh an la dam a ni . Mahse,
nunna atana hlauhawm harsatna a thlen thei bawk .
Thâwk harsat hi a hlauhawm zual hle.
Tin , hriatna emaw mitdel emaw pawh a awm reng thei bawk . Chuvang chuan a natna lan chhuah dan ngaih pawimawh a, doctor-in a tih angin a enkawl dan tur i ei a pawimawh hle.
Hei hi eng chen nge a daih ang?
Relapsing Polychondritis hi
natna rei tak a ni a . Hei hian a awmzia chu lo thleng leh chhuak lo dinhmun a ni lo va,
dam chhung zawnga dinhmun a ni zawk tihna a ni . Mahse, enkawlna dik tak i neih chuan natna lan chhuah tamna chu i tihtlem thei a, a lan chhuah hunah a nasatzia pawh i tihtlem thei bawk. Chuvangin doctor nen inbia a, i tana tha tur treatment plan siam hi a pawimawh hle.
Doctor hnenah eng nge i zawh belh theih ang?
I doctor-in `Relapsing Polychondritis` i vei a tih chuan, a chungchang hriat belh duh chuan hetiang zawhna hi i zawt thei ang:
- "Doctor, ka dinhmun hi engtiang chiahin nge a nat?"
- "Eng damdawi nge ka tan a tha ber?"
- "Ka taksa peng hrang hrang, ka mit, beng, thawkna kawng, thinlung, leh kal (kidney) te hi special test neih a ngai em?"
- "Specialist dang (e.g., beng, hnar, ril specialist, joint specialist) ka hmu tur em ni?"
- "Ka cartilage tichak turin mimal takin ka tih theih tur a awm em, a nih loh leh he cartilage hloh hi tihziaawm nan?"
- "He natna chungchangah hian research thar emaw clinical trial thar emaw neih mek a awm em?"
Heng zawhnate hi zawh hian i dinhmun hriatthiamna tha zawk i nei thei a, i enkawlnaah pawh nasa takin i tel thei bawk.
Engtikah nge doctor ka hmuh vat ang?
Relapsing Polychondritis i vei a nih chuan doctor hnena
appointment neih reng a pawimawh hle. Tin,
thawk harsatna i neih chuan, i mit a danglam a, i hriatna i nei a nih chuan , i appointment lo awm tur chu nghak suh.
A rang thei ang bera damdawi lam thurawn zawng rawh . Chûngte chu a châng chuan enkawl vat ngai dinhmun a ni thei bawk.
Chuti a nih chuan, kan hriat reng tur thilte chu engte nge ni?
Tunah chuan kan sawi thin, `Relapsing Polychondritis` tih hi hriatthiamna engemaw chen i nei mai thei. A tawp berah chuan, hriat reng tur pawimawh tak takte chu hengte hi a ni:
- Relapsing Polychondritis hi natna hlauhawm tak a ni a, taksa chhunga cartilage te chu a inflamed a, a chhe vek thin.
- A tam zawkah chuan beng leh hnar hi target a ni a, mahse ril, trachea leh joint te pawh a nghawng thei bawk.
- Hei hi a chhan dik tak hi hriat chian a la ni lo a, mahse autoimmune condition a nih rinhlelh a ni.
- Damdawi famkim awm lo mah se, natna lan chhuah dan control leh harsatna tihziaawmna tur enkawlna a awm.
- Thâwk harsa ang chi thil hi a hlauhawm thei a, a natna lan chhuah dan ngaihven a, doctor pan vat a pawimawh.
Nangmah emaw, i hriat miin emaw heng symptoms te hi i neih chuan doctor pan a, thurawn lak hlau suh. Natna zawng zawng hriat chian hian nun hrisel tak i nei thei dawn a ni!
Relapsing Polychondritis, Cartilage, Beng na, Hnar hring, Thâwk harsa, Joint na, Autoimmune disease, Inflammation, Natna hmuh tur awm lo
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