Kei te mōhio koe ki ngā mate Prion: Te whakaekenga puku ki te roro?

Kei te mōhio koe ki ngā mate Prion: Te whakaekenga puku ki te roro?

Physician Reviewed — Not Medical Advice

Whakaarohia mēnā ka tīmata tētahi o ō rātou whanaunga ki te pāngia e ngā huringa ohorere, tere o te mahara, te āhua, me te taunga tinana. Kua rongo kē koe i tētahi rōpū mate roro tino onge, tere te whanake, me te uaua e uaua ana ki te tautuhi i ngā mate, tae noa ki ngā tākuta? E mōhiotia ana ēnei mate ko ngā Mate Prion.

He Kupu Māmā: He aha ngā Mate Prion?

Ko ngā mate prion he rōpū mate e pā ana ki tō roro me tō pūnaha io. Ka taea e rātou te whakararu i te hinengaro , te whakararuraru nui rānei i te whakahaere nekehanga, ā, he maha ngā wā ka tere te heke o te āhua. He tino onge ēnei mate; hei tauira, tata ki te 350 ngā mate e pūrongohia ana i ia tau i te United States.

Nā, he aha te take o ēnei? He pūmua tūturu ngā prion i roto i tō roro. Mō ngā take e rangahauhia tonutia ana e ngā kaipūtaiao, ka taea e ēnei pūmua te takai hē, te piri tahi, ā, ka rerekē. Ko te mea tino morearea ko te mea ka taea e te prion kotahi te takai hē te akiaki i ngā pūmua hauora tata kia takai hē anō hoki. He rite ki te pānga domino e meinga ai ēnei pūmua rerekē kia kohia, ā, ka mutu ka whakangaro i ngā pūtau roro (ngā neuron). Ko tēnei whakangaromanga tonu te mea e whakaoho ana i ngā tohu.

He tokomaha te hunga e whakapoauau ana i ngā mate prion me te mate a Alzheimer ( te mate a Alzheimer ). Ahakoa ka taea e ēnei e rua te whakararu i te mahara, he rerekētanga nui: Ko te mate a Alzheimer ka puhoi haere i roto i ngā tau maha. He rerekē, i roto i te mate prion, ka tere te kino haere o te āhua i roto i te wā poto rawa, i roto i ētahi marama. Hei tāpiri, pērā i te mate a Alzheimer, kāore anō kia kitea he rongoā mō ngā mate prion i tēnei wā.

He aha ngā momo matua o ngā mate Prion?

Ka pāngia te tangata me te kararehe e ngā mate prion. Kei raro nei ngā momo matua e pāngia ai te tangata.

Ingoa Mate Whakaahuatanga Poto
Te mate Creutzfeldt-Jakob (CJD) Koinei te momo tino noa i roto i te tangata, ka puta i te nuinga o te wā i roto i te hunga neke atu i te 60 tau te pakeke.
Momo CJD (vCJD) Ka pā pea tēnei ki te hunga rangatahi, ā, kua honoa ki te kai mīti mai i ngā kau kua pangia e te "Mate Kau Pōrangi".
Gerstmann-Sträussler-Scheinker syndrome He mate ira tino onge, he mate tuku iho.
Te kore moe whānau whakamate He mate tuku iho anō hoki, e tohu ana i te kore e taea te moe nui, kāore e taea te rongoā.
Kurū I horapa haeretia i roto i ngā iwi o Papua Niu Kini mā te kai tangata, ā, i horapa haere i ngā wā o mua; engari kua kore noa iho ināianei.

He aha ngā tohu o te mate Prion?

Ka puta ohorere pea ngā tohu o ngā mate prion. Ko ngā tohu matua ko ngā huringa tere o tō wairua, tō mahara, me tō nekehanga tinana.

Te Rohe Pānga Ngā Tohu Ka Kitea
Hinengaro me te Whanoke Te manukanuka nui, te pouri rānei
Ngā huringa ohorere o te whanonga, o te tuakiri rānei
Te tere haere o te mate wareware
Te Tinana me te Pūkaha Te ngaronga o te taurite (ataxia)
Te hikoi pōturi
Te ngaronga o te mana whakahaere uaua, te oho ohorere, te wiri rānei
Kōrero pōturi
Te uaua ki te horomi
Ētahi atu Tohu Ngā mate hopuhopu
Ngā raruraru tirohanga

Ngā Take me ngā Take Mōrearea

I roto i te nuinga o ngā wā, pērā i te CJD tūpono noa, ka puta te mate me te kore he take mārama. Heoi anō, kua tautuhia ētahi āhuatanga mōrearea.

  • Hītori Whānau : Tata ki te 15% o ngā mate he tuku iho, i puta mai i te whakarerekētanga o te ira `PRNP`.
  • Ngā Mate Pukupuku : He tino onge tēnei, engari ka puta pea mā te whakawhitinga kiko, mēnā rānei kāore i te tika te whakahoromata i ngā taputapu pokanga, nā te mea he ātete ngā prion ki te horoi paerewa.
  • Te Kai i te Mīti Pango: Mā te kai i te mīti mai i ngā kau e pangia ana e te "Mate Kau Pōrangi" (Bovine Spongiform Encephalopathy ) ka arahi pea ki te vCJD. Nā ngā ture pakari mō te whāngai kau me te koha toto kua tino whakaiti i tēnei mōrearea i te nuinga o ngā whenua.

Me pēhea te tautuhi i te mate Prion?

He uaua te tātaritanga i te mate prion nā te mea he rite tonu ngā tohu ki ētahi atu āhuatanga. Mena ka puta he tohu pēnei i te ngaronga o te mahara, ka whakakorea tuatahitia e tō tākuta ētahi atu take pea pēnei i te whiu, i te pukupuku roro rānei.

Ko ngā taputapu tātaritanga pea ko:

  • Werohanga Lumbar (Spinal Tap): Ka whakamahia he ngira hei kohi i te wai cerebrospinal (CSF) mai i tō tuaiwi hei whakamātautau mō ngā tohu pūmua motuhake e pā ana ki ngā mate prion.
  • MRI : Ka whakarato whakaahua taipitopito o te roro, e whakaatu ana pea i ngā tauira motuhake e pā ana ki ngā mate prion.
  • Matawai CT: Ka whakamahi i ngā hihi-X hei tiki whakaahua mārama o te roro.

Tuhipoka Hira:Ka taea anake te whakaū i te tautuhi mate mā te tango i te koiora o te roro. Heoi, nā te mea he tikanga whakaeke kino tēnei, he nui hoki te mōrearea, ka whakaarohia noa mēnā he whakapae kaha kei te taea te rongoā te mate taketake.

Te Maimoatanga me te Ārai

I tēnei wā, kāore he rongoā mō ngā mate prion. Ko te arotahi o te maimoatanga ko te tiaki mamae hei whakahaere i ngā tohu me te whakapai ake i te kounga o te oranga o te tūroro. Kei roto pea i tēnei ko ngā rongoā mamae, ngā rongoā ārai pouri, me ngā maimoatanga mō ngā raruraru whanonga, hinengaro rānei.

I te whanaketanga haere o te mate, ka hiahiatia te tiaki wā-katoa mō ngā tūroro, tae atu ki te whakamahi i ngā katitere, ngā wai IV, ngā ngongo whāngai rānei mēnā kāore e taea te horomi.

Ka taea e koe te ārai?

Kāore e taea te ārai i ngā momo ira. Heoi, hei whakaiti i te tūponotanga o te horapa mā te mate:

  • He tino pakari ngā tikanga a ngā hōhipera mō te whakamate i ngā taputapu pokanga.
  • Kaua te hunga whai mate prion e mōhiotia ana, he hītori whānau rānei e tuku i ngā okana, i ngā kiko rānei.
  • Me hoko tonu te mīti mai i ngā puna whaimana, pono hoki.

Kua tino whakahaeretia te horapa o te "Mate Kau Pōrangi" i roto i ngā mahi ahuwhenua o ēnei rā e ngā ture ā-ao mō te whāngai kararehe me te haumaru kai.

Karere Tangohia ki te Kāinga

  • He onge engari he kino, he tere te whanake haere o ngā mate prion.
  • Ko te rerekētanga matua mai i ngā mate pēnei i te mate a Alzheimer ko te tere rawa o te hekenga o te mahara, te whanonga, me te mahi tinana.
  • He uaua te tautuhi i te mate, ā, me whai rangahau haumanu motuhake.
  • Ahakoa kāore he rongoā, mā te whakahaere i ngā tohu ka whakamarie, ka tautoko hoki te tūroro.
  • Ki te puta he panoni ohorere, kāore i te mārama te āhua o tō mahi hinengaro, o tō mahi tinana rānei, whakapā atu ki tō tākuta, toro atu rānei ki tō tari urupare ohorere o te rohe.

Ngā mate Prion, Ngā Mate Prion, Te mate Creutzfeldt-Jakob, CJD, Ngā mate roro, Te pūnaha io, Te ngaronga o te mahara, Te mate wareware, Te mate kau porangi