Kua rongo pea koe, "Āe, kua pāngia taua taitama e te toto totoka." Kua pupuhi ohorere rānei tō waewae, kua mamae? I tēnei rā ka kōrero tātou mō tētahi mate e kiia nei ko te 'Thrombophilia' ka pā mai pea ēnei momo mate. Kaua e mataku ina rongo koe i tēnei ingoa, he mate tēnei ka pā ki te tini o te tangata. Koia te mea nui kia mōhio koe ki tēnei.
He aha te Thrombophilia?
Ko te Thrombophilia he āhuatanga e tere ake ai te totoka, e ngāwari ake ai hoki i te toto noa. Ka kiia tēnei e ngā tākuta he āhuatanga 'hypercoagulable'. Ko te tikanga he nui ake te kaha o te totoka ki te totoka. Ka taea tēnei te puta mai i te ira, te mea rānei i whiwhihia. Whakaarohia te aha ka puta ina tapahia tō ringa ki te maripi? Ka ngaro he toto iti, ā, i muri i tētahi wā ka puta he totoka toto ki taua wāhi, ka mutu te toto. He tukanga tiaki tēnei i roto i tō tātou tinana. I muri i te ora o te patunga, ka whakarewahia anō e te tinana te totoka totoka ka tangohia. Engari he mea anō ka tupu ki te tangata whai Thrombophilia. Ahakoa kāore e hiahiatia ana e te tinana, ka puta he totoka totoka i roto i ngā uaua. Kāore rānei ngā totoka totoka e puta mai ana e whakarewahia ana, e tangohia tika ana. Ko te raruraru nui ko te haere o ēnei totoka totoka i roto i ngā uaua ka aukati i te oko toto e arahi ana ki tētahi okana nui. Nā te mea ka whiwhi ia pūtau i roto i tō tātou tinana i te hāora e hiahiatia ana e ia mai i te toto. Ki te aukatia te uaua totoka, kāore e taea te kawe hāora. Ka taea e tēnei te arahi ki ngā āhuatanga kino pēnei i
te mate ngakau me te whiu .
E rua ngā momo matua o te thrombophilia:
E ai ki tā mātou i kōrero ai i mua ake nei, ka taea te wehewehe i tēnei āhuatanga kia rua ngā momo matua i runga i te āhua o tōna putanga mai. 1.
Thrombophilia Whiwhi: Koinei te momo tino noa. Ehara i te mea he mea tuku iho. Ka taea te puta mai i ētahi rongoā e tangohia ana e tātou, i tō tātou āhua noho, i ētahi atu mate rānei. Ko te mea tino noa, ā, he kino rawa atu o ēnei momo ko te
Antiphospholipid Syndrome . 2.
Thrombophilia Tuku Iho (Thrombophilia Ira/Tuku Iho): He āhuatanga ira tēnei ka riro mai i tō whaea, i tō pāpā, i a koe rānei. He pūmua kei roto i tō tātou tinana e whakahaere ana i te toto toto. Nā ēnei huringa ira, kāore pea aua pūmua e mahi tika. Kāore rānei e taea e te tinana te whakaputa i te iti o ngā pūmua e aukati ana i te toto toto.
Mena kua pāngia koe e ngā toto toto i mua i te 40 tau te pakeke, kua maha ngā materoto kua pāngia koe , mena rānei he hītori toto toto kei roto i tō whānau, tera pea kei a koe tēnei thrombophilia tuku iho.
He aha ngā momo thrombophilia whānau?
He rerekē ngā momo o tēnei mate ira. Me titiro tātou ki ētahi o ngā momo matua.
| Momo Thrombophilia Ira | He whakamārama māmā mōna |
|---|
| Te Thrombophilia o te Tauwehe V o Leiden | Koinei te momo ira tino kitea. Ka pā ki te 1% ki te 5% o te taupori. Ka whakanui ake i te tūponotanga o te whakawhanake i te toto totoka i roto i te uaua hohonu o te waewae (Deep Vein Thrombosis - DVT) mō te wā tuatahi. |
| Te totoropiria o te prothrombin | Koinei te tuarua o ngā momo e tino kitea ana. He nui ake te mōrearea o te pulmonary embolism, te DVT, me te materoto. |
| Te korenga o te pūmua C | He ahua onge tēnei. He nui te tūponotanga o te toto totoka anō. Mena ka riro mai tēnei mate i ngā mātua e rua, ka taea te whakararu i te ora. |
| Te Kore o te Pūmua S | He onge anō hoki tēnei. Heoi anō, he onge ake te āhua (i tukuna iho i ngā mātua e rua) ka pā mai pea ngā raruraru toto totoka mōrearea ki te ora o ngā pēpi hou. |
| Te ngoikore o te antithrombin | He onge hoki tēnei (e pā ana ki te 1 i roto i te 500 ki te 5,000 tāngata). Engari he nui ake te mōrearea o te hunga whai mate pēnei ki te whakawhanake i ngā toto totoka i ērā atu mate ira. Neke atu i te 80% o te hunga whai mate pēnei ka whakawhanake i te iti rawa i te kotahi totoka i te 50 tau te pakeke. |
He aha ngā tohu o te toto totoka?
I te nuinga o te wā, kāore pea koe e mōhio kei a koe te thrombophilia. Ka puta noa te raruraru ina puta he toto totoka, ā, ka puta ngā tohu. Ka rerekē ēnei tohu i runga i te wāhi i puta ai te toto totoka.
| Wāhanga tinana | Ngā tohu hei tumanako |
|---|
| Roro | - Ngā mate hopuhopu
- Te ānini ohorere, te mamae nui
- He uaua ki te kōrero me te kite
- Te ahua o te ngoikore i tetahi taha o te tinana
|
| Ngākau | |
| Ngā pūkahukahu | |
| Waewae, Ringa rānei | - Pupuhi ohorere
- Mamae nui
- Te mahana ki te pā atu
|
| Puku | |
He aha ngā take me ngā āhuatanga mōrearea e pā ana ki te whakawhanaketanga o te thrombophilia?
Haunga ngā take ira, he maha atu anō ngā take me ngā āhuatanga mōrearea ka hua ake ai te thrombophilia, ka piki ake rānei te mōrearea o te toto totoka.
Ngā take matua:
- Te Mate Ārai-phospholipid
- Te Whakapūngao Toto i roto i te Pūnaha Toto (DIC), he mate toto onge
- Hepatitis
- Mate HIV
- Mate ate
Ngā āhuatanga e whakanui ake ai i te mōrearea:
- Taumaha rawa: Ko te momona tetahi o ngā tino take mōrearea o te toto totoka.
- Te Hapūtanga: Mā ngā huringa homoni o te tinana i te wā e hapū ana ka piki ake te totoka.
- Te whakamahinga o ngā hua tupeka: Ka kino te momi hikareti i ngā uaua toto, ā, ka māmā ake te hanga o ngā totoka.
- Ētahi atu mate: Ngā āhuatanga pēnei i te mate huka, te mate pukupuku, te mate ngakau, me te atherosclerosis.
- Te noho i te tūranga kotahi mō te wā roa: Ina noho i te hōhipera i muri i te pokanga, i runga i te rererangi roa, i te pahi rānei, i te noho rānei i te mahi, ka heke te rere o te toto i roto i ngā waewae, ā, ka puta he toto totoka.
- Kei te pokangahia.
- Te tango i ngā pire ārai whānau, i te rongoā whakakapinga homoni rānei (HRT) kei roto ko te homoni estrogen.
- He hītori whānau mō ngā toto totoka.
- Te koroheketanga.
- Ngā materoto kāore e kitea te take.
- He nui atu i te kotahi te toto totoka i mua i te 40 tau te pakeke.
Kia maumahara, ahakoa kei a koe tētahi, neke atu rānei o ēnei āhuatanga mōrearea, ehara i te mea ka pāngia koe e te toto totoka. Engari he mea nui kia mōhio koe ki ēnei āhuatanga, kia whai hoki i ngā tohutohu a tō tākuta.
Me pēhea taku mōhio mēnā kei a au tēnei āhuatanga?
Ina he toto totoka tōu, ā, kei te rongoatia koe mōna, tera pea ka whakapae tō tākuta he thrombophilia koe. Kātahi ka whakahaerehia e rātou ētahi whakamātautau hei whakaū i te mate.
- Tō hītori hauora: Ka pātaihia koe mō ngā toto kua pupū ake i mua, mēnā kua pāngia tētahi o tō whānau e ēnei toto, mēnā rānei kua pāngia koe e ētahi materoto.
- Whakamātautau Tinana: Ka tirohia mēnā he pupuhi me te mamae i puta mai i te toto totoka.
- Ngā Whakamātautau Toto: Ka mahia ngā whakamātautau toto motuhake hei rapu i ngā āhuatanga ira, i ētahi atu ngoikoretanga pūmua rānei e hua ai te thrombophilia.
- Ētahi atu whakamātautau: Tērā pea ka mahia ngā whakamātautau pēnei i te matawai ultrasound, te matawai CT , te angiogram rānei hei kimi i te wāhi tika o te toto totoka.
Ko wai te tangata me mahi i tēnei whakamātautau?
Kāore ēnei whakamātautau e mahia ana mō te katoa. Tērā pea ka tonoa ēnei whakamātautau e tō tākuta i roto i ēnei āhuatanga e whai ake nei:
- Mena he toto totoka tōu i mua i te 50 tau te pakeke.
- Mena he maha ngā tāngata o tō whānau he hītori o te toto totoka.
- Mena ka puta he toto totoka, kāore he āhuatanga mōrearea e kitea ana.
- Mena ka puta he toto totoka ki ngā wāhi rerekē (hei tauira, ngā ringa, te puku).
- Mena he maha ngā wā ka mate pāwera koe.
- Ki te hiahia koe ki te mōhio mēnā kei roto tō whānau i te mōrearea.
He aha ngā maimoatanga mō te thrombophilia?
Kāore he rongoā mō te thrombophilia whānau. Engari ka taea te
whakahaere pai, te ārai i ngā toto totoka me te noho i te oranga noa. Ko ngā kōwhiringa maimoatanga e whakawhirinaki ana ki te momo thrombophilia kei a koe, mēnā kua puta he toto totoka, me te kaha o te mate.
- Ngā rongoā ārai toto toto: Koinei ngā maimoatanga matua. Ka mahi ēnei rongoā mā te aukati i te hanganga o ngā toto toto hou, me te whakaroa i te tipu o ngā toto toto kua puta. He rongoā tawhito a Heparin me Warfarin . Kei te wātea ngā rongoā hou ake, he māmā ake te tango. Tērā pea me tango e ētahi tāngata ēnei rongoā mō te toenga o ō rātou oranga.
- Ngā rongoā thrombolytic: Ka whakamahia ēnei i ngā wā ohorere me ngā wā kino anake. Hei tauira, mēnā he toto toto nui kei roto i ngā pukahukahu he mea mōrearea ki te ora, ka taea te hoatu i ēnei rongoā mā roto i te uaua hei whakarewa tere i te toto toto.
- Tōkena Kōpeke: Ka tohutohu pea tō tākuta kia mau koe i ēnei momo tōkena motuhake hei whakaiti i te pupuhi me te pupuri i te rere pai o te toto, inā koa mō te hunga he toto totoka kei roto i ō rātou waewae.
- Pokanga: He tino onge, ki te kore e taea te whakarewa i tētahi toto toto nui ki te rongoā, me pokanga pea hei tango.
Ngā mea ka taea e tātou te mahi hei whakaiti i te mōrearea
Ki te mōhio koe he thrombophilia tōu, kei te mōrearea rānei koe ki te whakawhanake i ngā toto totoka, he mea tino nui kia huri koe i tō momo noho.
- Āta karohia te momi hikareti.
- Kia mau tonu te taumaha tinana hauora.
- Whakakorikori tinana i ia rā, i ia rā. Ahakoa he mea ngāwari pēnei i te hikoi, he pai tonu te mahi i ia rā.
- I ngā haerenga roa: Ki te mea kei te haere koe i runga i te waka rererangi, i te pahi rānei mō te wā roa, whakatika ake i ia haora, i ia rua rānei, ka hikoi haere mō tētahi wā, me te rūrū i ō waewae.
- I muri i te pokanga: Whakatika i te moenga ka tīmata te hikoi ina whakaaetia koe e tō tākuta.
- Ngā rongoā kei roto te estrogen: Mena kei te tango koe i ngā rongoā kei roto te estrogen, pērā i ngā pire ārai whānau, kōrero ki tō tākuta mō tēnei mōrearea. Ka taea e ia te tūtohu i tētahi atu rongoā e tika ana māu.
- Tohutohu a te tākuta: Ki te mea kei te tango koe i te rongoā whakaiti toto, tangohia i te wā tika me te horopeta tika. Kaua rawa e mutu te tango i te rongoā me te kore e kōrero ki tō tākuta.
Āhea te wā hei kite i te tākuta
Mena he thrombophilia tōu, he mea nui kia mau tonu tō whakapā atu ki tō tākuta, kia tere hoki te mahi mēnā ka puta mai ētahi tohu.
Āhea me rapu tohutohu hauora: Tirohia tō tākuta,
haere rānei ki te Wāhanga Maimoatanga Ohotata (ETU) o te hōhipera i taua wā tonu. - He pupuhi hou, he mamae, he whero rānei i te waewae, i te ringa rānei.
- Te toto rerekē, pērā i te toto ihu, te toto i roto i te mimi, i te tūtae rānei, nā te tango i ngā rongoā whakaiti toto.
- Mena he feaa, he pātai rānei āu mō tō āhuatanga.
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- Te mamae ohorere o te uma , te uaua rānei ki te manawa (he tohu pea ēnei o te mate manawa, o te embolism pūkahukahu rānei).
- Te ānini nui ohorere, te uaua ki te kōrero, te ngoikore rānei o tetahi taha o te tinana (he tohu pea ēnei o te whiu).
- Te toto nui, tonu, nā te motu i puta mai.
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Karere Tangohia ki te Kāinga
- Ko te Thrombophilia he āhuatanga e tere ake ai te toto i te mea noa, e ngāwari ake ana hoki. Tērā pea he mea kei te whānau mai, he mea rānei ka puta ake i muri mai i te ao.
- He tokomaha ngā tāngata e pāngia ana e tēnei mate ka ora tonu, kāore he toto e pupū ake ana. Ka puta noa ngā tohu mēnā ka puta he toto i roto i te uaua, ā, ka aukati i te rere o te toto.
- Ka kino te toto totoka mēnā ka puta i roto i te roro, i te ngākau, i ngā pukahukahu, i ngā waewae rānei, nō reira he mea nui kia mōhio ki ngā tohu.
- Ahakoa kāore e taea te whakaora katoa i tēnei mate, ka taea te whakahaere pai, me te whakaiti i te mōrearea mā te tango i ngā rongoā e ai ki te tohutohu a tō tākuta, me te whai i tētahi momo noho hauora.
Thrombophilia, toto totoka, DVT, embolism pūkahukahu, thrombosis, toto totoka, whakangawari toto
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