E hia te nui o te āwangawanga o te whaea, o te pāpā rānei ina titiro rātou ki tētahi pēpi hou, ā, ka kite i ētahi panoni iti i roto i tōna tinana? I ētahi wā, ahakoa he mea tino onge, ka pā ki tā tātou pēpi, ka tino pouri ai tātou. I tēnei rā, ka kōrero tātou mō tētahi āhuatanga kāore i te tino rangona, engari he mea tino nui kia mōhiotia. Ka huaina tēnei e tātou ko (Urogenital Sinus).
He aha tēnei (Urogenital Sinus)? Kia mārama noa iho?
He whakarāpopototanga noa iho, ko te Sinus Urogenital he hapa whānau i roto i te pūnaha mimi me te pūnaha whakaputa uri o te wahine. Inaianei, tirohia, e toru ngā pūaha o te pēpi wahine hei putanga i ngā para i te tinana: ko tētahi ko te rectum, te wāhi e puta mai ai te tūtae, ko tētahi ko te pūaha urethral, te wāhi e puta mai ai te mimi, ā, ko te tuatoru ko te tenetene . Heoi, e rua ngā pūaha o te pēpi e pāngia ana e te Sinus Urogenital. Ko tētahi ko te rectum, te wāhi e puta mai ai te tūtae, ā, ko tētahi he pūaha noa mō te urethra me te tenetene. Ko te tikanga ka puta mai te mimi, ka hono atu ki te tenetene mai i te wāhi kotahi.
Ka puta tēnei āhuatanga (Urogenital Sinus) i ngā wāhanga tōmua o te whanaketanga o te kukune. Whakaarohia, mō te wā poto rawa i te wāhanga kukune, ko ngā pūnaha e toru – te ara whekau (rectum), te ara ira tangata (te tara), me te ara mimi (te pūkahukahu mimi) – e hono katoa ana ki tētahi kōhao me tētahi whakatuwheratanga kotahi. Ka karangatia tēnei e mātou ko ( Cloaca ). I te tipu haere o te kukune , ka wehe ēnei pūnaha e toru, ka hanga i ngā whakatuwheratanga e toru (te tara, te urethra , me te nono). Engari i ētahi wā, mō tētahi take, kāore te ara mimi me te pūnaha whakaputa uri – inā koa ko te urethra me te tara – e wehe tika ana, engari ka mau tonu i tētahi whakatuwheratanga kotahi. Ka karangatia taua whakatuwheratanga noa ko (Urogenital Sinus). Ka karangatia hoki tēnei e ētahi tāngata ko (Persistent Urogenital Sinus - PUGS).
He aha te nuinga o te wā ka puta ai te Sinus Urogenital?
I te wā e whanake ana, ka noho tēnei wāhi (e kiia nei ko te Urogenital Sinus) hei urethra me te kiri e karapoti ana i te pūaha o te tara (vulvar vestibule). Ko te urethra te ngongo e puta ai te mimi i tō tinana. Ko te kiri e karapoti ana i te pūaha o te tara (vulvar vestibule) ko te kiri kei roto o te labia, i waenganui i te urethra me te pūaha o te tara.
Kei hea te tūnga o te Sinus Urogenital i roto i te tinana?
E hono ana tēnei (Urogenital Sinus) ki te urethra me te tenetene.
He momo sinus urogenital?
Ae, e rua ngā momo matua o te Sinus Urogenital. He mea tino nui te tautuhi i tēnei mō te whakamahere maimoatanga.
1. Hononga-iti / Hononga-iti: I tēnei momo, ka hono te urethra me te tenetene ki te pūaha o waho o te tinana, arā, i te pito raro. Nō reira, he poto rawa tēnei ara noa. I tēnei take, he rite tonu te rahi me te tūnga o te urethra me te tenetene ki te mea noa. He āhua iti ake te kino o tēnei mate.
2. Hononga-teitei / Huinga-teitei: I tēnei wā, ka honoa te urethra me te tenetene i tawhiti atu i te whakatuwheratanga o waho o te tinana, arā, i te tihi. Kātahi ka tino roa tēnei ara noa. Ko tēnei momo huihuinga-teitei te mea tino kino. Nā te mea, ka puta pea ētahi atu raruraru me tēnei. Hei tauira, ka taea te tū te nono ki mua rawa atu i te mea noa i roto i te tinana.
He pēhea te onge o tēnei mate (Urogenital Sinus)?
He tino onge te mate o te Sinus Urogenital. I te nuinga o te wā, e pāngia ana te 0.6 o roto i te 10,000 pēpi hou.
He aha ngā tohu o te Sinus Urogenital?
Ka rerekē ngā tohu o te Sinusitis Urogenital i runga i te kaha o te mate. Ko ētahi o ngā tohu e kitea nuitia ana ko:
- Kotahi anake te putanga mō te paru, me tētahi atu putanga e rite ana ki te tara me te urethra.
- Te pupuhi o te tara nā te nui o te mimi. Ka kiia hoki tēnei ko (Hydrocolpos).
- Tērā pea kua kati rawa te tenetene.
- I ētahi wā, kāore rawa he tara.
- Kāore te kōpū, ngā ovaries, ngā ngongo fallopian rānei i te whanake tika.
He aha ngā take o te mate pukupuku Urogenital?
Ki te pono, he uaua ki ngā tohunga hauora te tautuhi i te tino pūtake o te Sinus Urogenital.
I ētahi wā, ka hono pea tēnei ki tētahi āhuatanga e kiia nei ko te Congenital Adrenal Hyperplasia (CAH). He rōpū mate ira te CAH. Mena kei a koe te CAH, kāore tētahi, e rua rānei o ō repe adrenal e whakaputa i tētahi whākōkī e hiahiatia ana hei hanga homoni. Ka taea e tēnei te whakawhanake i ngā whekau ira tangata i tētahi āhua rerekē. Ka pā te CAH ki te tangata katoa, engari he nui ake te tūponotanga o ngā kōtiro ki te whai whekau ira tangata i tētahi āhua rerekē.
Ka taea hoki e te mate e kīia nei ko te virilization te take o te sinusitis urogenital. Ko te virilization te mea he nui rawa ngā homoni tāne (androgens) i roto i te tinana o te tama. Ko ngā androgens ngā mea e āwhina ana i te tinana kia pakeke, ā, ka pā hoki ki ngā mea pēnei i te hohonutanga o te reo, te huruhuru o te tinana, me te tipu o te uaua.
Me pēhea te tautuhi i te mate Sinus Urogenital?
He mea tino nui te (Urogenital Sinus) hei whakatau me pēhea te rongoā i te mate. Ka pā tēnei ki ngā ira tangata o tāu tamaiti, tae atu ki tōna tipu me tōna whanaketanga whānui.
I ētahi wā, ka kitea tēnei āhuatanga (Urogenital Sinus) e ngā tākuta i te wā o te tirotiro ultrasound i te wā kei roto tonu te pēpi i te kōpū. Heoi, i te nuinga o te wā, ka kitea tēnei āhuatanga e ngā tākuta i te wā o te whakamātautau tinana tuatahi i muri i te whānautanga o te pēpi. Kātahi ka whakahaerehia he whakamātautau toto hei ako atu mō te hauora whānui o te pēpi me ngā raruraru ira.
Tērā pea ka tonoa e te tākuta ētahi atu whakamātautau hei whakaū i te mate, hei ako atu rānei mō te whānuitanga o te Sinus Urogenital. Kei roto i ēnei ko:
- Ultrasound: Ka whakamahia e tēnei he ngaru oro auau teitei hei tango ataata, hei whakaahua rānei i ngā whekau o roto i te tinana. Ka taea e tēnei te whakaatu i ngā raruraru ki ngā whatukuhu, te pūkahukahu, te tara, me te pūkahukahu o tō pēpi. Ka taea hoki e ia te kite mēnā he puranga mimi kei roto i te tara (hydrocolpos).
- Ko te tākuta whakamuri-ira: He momo whakamātautau whakaahua anō hoki tēnei. I roto i tēnei whakamātautau, ka werohia e te tākuta he tae motuhake ki roto i te urethra/tenetene, ā, ka tangohia he hihi-X. Mā tēnei tae ka taea te tautuhi mārama i te rahi, te āhua, me te wāhi o ngā kiko me ngā whekau.
- Whakamātautau Whakaahua Āhua Aukume (MRI): Ka whakamahia e te MRI he aukume, he ngaru reo irirangi, me te rorohiko hei tango pikitia mārama o te tinana. Ka taea e tēnei te whakarato pikitia tino taipitopito o te Sinus Urogenital. Ka taea hoki te whakamahi i te MRI hei tirotiro i ngā raruraru o te hope me te tuaiwi o te tamaiti.
- Endoscopy: Ka whakamahia e te endoscopy tētahi ngongo angiangi, roa (endoscope) me te rama me te kāmera i tētahi pito. Ka whakauruhia tēnei endoscope ki roto i te urethra/tenetene noa hei tirotiro i te hanganga o roto.
Me pēhea te rongoā i te sinus urogenital?
Ko te huarahi anake hei rongoā i te mate Sinus Urogenital ko te pokanga hei wehe i te tara me te urethra o tō pēpi. I ētahi wā, inā koa mō ngā tamariki kua whakatōngia (nā te Congenital Adrenal Hyperplasia (CAH)) ā, kua kitea he mate whanaketanga moepuku koretake (DSD), tera pea he rerekē ngā whakaaro mō te mahi pokanga. Nō reira, i mua i te pokanga, me kōrero taipitopito koe ki te tīma hauora e rongoā ana i tō tamaiti. Ko te tikanga kei roto i tēnei tīma:
- He tākuta tohunga ki ngā mate o te pūnaha mimi me te pūnaha whakaputa uri ((Urologist)).
- He tākuta endocrinologist te tākuta e tohunga ana ki ngā mate e pā ana ki te pūnaha endocrine. Ko tō pūnaha endocrine te mea e hanga ana, e tuku ana hoki i ngā homoni.
Ko te tikanga ka mahia te pokanga i roto i te tau tuatahi o te pēpi . Ka mahia tēnei pokanga e te tākuta mimi.
Mō te mate hononga iti (Urogenital Sinus), ka whakahaerehia e te (Urologist) he pokanga e kiia nei ko te (Flap vaginoplasty). I roto i tēnei, ka hangaia e rātou he rua ngā pūaha motuhake ki waho o te tinana - tētahi mō te tenetene, me tētahi mō te urethra.
Mō te mate hononga teitei (Urogenital Sinus), ka whakahaerehia e te (Urologist) he pokanga e kiia nei ko te (Pull-through vaginoplasty). He pokanga uaua ake tēnei. I roto i tēnei, ka wehea e te (Urologist) te tenetene mai i te pūaha noa, ka hangaia he pūaha motuhake, ā, ka kati i taua pūaha noa. Kātahi ka rere tonu te mimi i te wāhi i mua ko te pūaha noa.
I ētahi wā o te hononga teitei (Urogenital Sinus), ka taea e te (Urologist) te mahi i tētahi tikanga e kiia nei ko te (Urogenital mobilization) me te (Flap vaginoplasty). I te wā o te (Urogenital mobilization), ka:
- Kua wehea te tōngāmimi.
- Ka wehea te urethra me te tenetene, ka nekehia ngātahitia, ka kawea ki te perineum.
- E honoa ana te pūkahukahu ki te pūkahukahu anal .
- Kātahi ka mahia te (flap vaginoplasty).
Tērā pea me mahi pokanga ētahi tamariki e kiia nei ko te Clitoroplasty me/ranei te Labiaplasty. Ko te Clitoroplasty he hanga anō i te kiko kia puta he clitoris noa. Ka ngana te taote pokanga ki te tiaki i te maha o ngā io kia taea ai e te tamaiti te whai oranga moepuku hauora ina pakeke haere. Ko te Labiaplasty he hanga anō i te labia, arā, ngā ngutu e karapoti ana i te tenetene.
Kia pēhea te roa o te wā e ora ai te pēpi i muri i te maimoatanga o te Sinus Urogenital?
Me noho tāu tamaiti ki te hōhipera mō ētahi rā i muri i te pokanga (Urogenital Sinus). Me tīmata te mamae ki te memeha i roto i te wiki, ā, me ora katoa te tamaiti i roto i te marama. Heoi, i runga i te kaha o te (Urogenital Sinus) o tāu tamaiti, ka whakamārama ake te tākuta o tāu tamaiti i tēnei.
Ka taea te ārai i te mate pukupuku Urogenital Sinus?
Mena kei roto i tō whānau tētahi mate e kiia nei ko te Congenital Adrenal Hyperplasia (CAH), ā, kei te hapu koe, kei te ngana rānei kia hapu, he mea nui kia kōrero koe ki tō tākuta. Hei ārai i te Urogenital Sinus, ka taea te hoatu homoni i mua i te whānautanga.
He aha taku e tumanako ai mēnā he mate pukupuku Urogenital tō taku tamaiti?
Ko te hua o tāu tamaiti e whakawhirinaki ana ki te rahi o tōna ihu urogenital. Ko te whāinga o te pokanga he hoatu ki tāu tamaiti te mahi me te āhua noa o ngā ira tangata. Ko te nuinga o ngā tamariki kua pokangahia ka taea te mimi noa i muri i te whakaoranga.
I te tipu haere o te pēpi, ka whaiti haere te tara (vaginal stenosis) ka poto haere hoki. Ka raru pea tēnei i te wā e moe ai.
Ahakoa he mate Sinus Urogenital tō te tamaiti, kāore e ārai i a ia kei hapu. Heoi, mēnā he whānui rawa te pokanga, he pai ake pea te pokanga cesarean i te wā e whānau ana. Ka kōrerohia tēnei e tō tākuta ki tāu tamaiti i te wā e tika ana.
Me pēhea taku tiaki i taku tamaiti?
Mā ngā tākuta o tāu tamaiti koe e tohutohu ki te huarahi pai hei rongoā i a ia. Ko te kaha o te (Urogenital Sinus) me ngā hua o te pokanga ka whakatau me pēhea koe e tiaki tonu ai i a ia.
Āhea ahau me toro atu ki te tākuta?
I muri i te pokanga, me haere tonu tāu tamaiti ki te tirotiro hauora kia mōhio ai kei te ora pai tōna tinana, ā, kei te mahi hoki ia e ai ki ngā tumanakohanga. Kia mahara ki te haere ki ēnei wā katoa.
Ki te kite koe i ētahi tohu hou, pērā i te kore e taea te pupuri i te mimi, kōrero ki te tākuta tamariki, ki te tākuta mimi rānei a tāu tamaiti.
He aha ngā pātai me pātai atu e au ki te tākuta o taku tamaiti?
Anei ētahi pātai ka taea e koe te pātai atu ki tō tākuta:
- He aha te momo Sinus Urogenital kei taku tamaiti?
- He aha te pokanga e taunaki ana koe?
- I tehea tau e taunakihia ana te pokanga?
- Ka mamae rānei taku tamaiti, kua mamae kē rānei ia?
- Me nui ake ngā pokanga e hiahiatia ana e te tamaiti i a ia e pakeke haere ana?
- E tumanako ana koe ka pāngia tāu tamaiti e ngā raruraru ki te urethra, ki te tara rānei i a ia e tipu ake ana?
- Ka pā tēnei ki te huringa paheketanga o taku tamaiti?
- Ka pā tēnei ki tōku kaha ki te hapu i tētahi tamaiti?
- Ka taea e taku tamaiti te whānau haumaru?
He mea nui: Kaua e wehi ki te pātai atu ki tō tākuta i ō pātai katoa, ahakoa te iti. Kei a koe te tika ki te mōhio mārama ki ngā mea katoa.
He aha te mate Urogenital whānui?
Ko te Mate Urogenital he mate e pā ana ki tō pūnaha mimi me te pūnaha whakaputa uri. Ko ētahi atu tauira ko:
- Ngā pukupuku pai.
- Hernia.
- Ngā Mate Tuku Iho (STI).
- Ngā mate pukupuku pērā i te mate pukupuku tōngāmimi, te mate pukupuku whēkau, te mate pukupuku kōpū rānei.
- Te mate pukupuku interstitial/te mamae o te pūkahukahu (IC/BPS).
Hei whakamutunga, ngā mea hei maumahara (Karere hei tango ki te kāinga)
He mea noa te ohorere me te mataku ina kitea he Sinus Urogenital tō tāu tamaiti. Engari kia maumahara, ka taea te rongoā i tēnei mate mā te pokanga hei wehe i te urethra me te tenetene o tāu tamaiti. Ko te tikanga me taea e tāu tamaiti te mimi marie.I a ia e pakeke haere ana, me pā mai anō hoki tōna paheketanga. Heoi, i ētahi wā, i a ia e pakeke haere ana, ka pāngia pea ia e te mamae i te wā e moe tāne ana.
Ko te mea nui, kāore koe e hiahia ki te aro atu ki ēnei mea ko koe anake. Kōrero ki te tākuta o tāu tamaiti. Ka taea e rātou te whakautu i ō pātai katoa, te whakamama i ō mataku, me te āwhina i a koe ki te whiwhi i te maimoatanga me te manaaki pai rawa atu mō tāu tamaiti.
` Ngā ihu mimi, ngā PUGS, ngā hapa whānautanga, te pūnaha mimi, te pūnaha whakaputa uri, te pokanga, te hauora o te tamaiti











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