Ngaba wakha wazibuza ukuba kutheni amazinyo akho etshintsha umbala kangaka, okanye eqhekeka okanye ephuka lula? Ngamanye amaxesha, nokuba awuyazi isizathu, inokuba yingxaki nge-enamel yamazinyo akho. Yiloo nto siza kuthetha ngayo namhlanje. Inzima kancinci, kodwa masizame ukuyichaza ngokulula.
Yintoni i-(Amelogenesis Imperfecta)? Masifumanise ngokulula!
Ngamafutshane, i-(Amelogenesis Imperfecta) sisifo semfuza . Okwenzekayo koku kukuba isigqubuthelo esiqinileyo esikhuselayo phezulu kwamazinyo akho, oko kukuthi, i-enamel, asiphuhli kakuhle. Cinga ngayo, yile enamel ekhusela iindawo ezibuthathaka ngaphakathi kwamazinyo ethu. Xa une-(Amelogenesis Imperfecta), nokuba ubungakanani be-enamel alwanelanga, okanye i-enamel eyenziweyo ayinamandla ngokwaneleyo. Ngenxa yoku, amazinyo akho anokutshintsha umbala aze abe buthathaka . Ukuchaneka, le enamel yinxalenye yezinyo efana nekhaka elikhuselayo. Ngoko ke xa kukho ingxaki ngayo, inempembelelo enkulu kwizinyo.
Le meko ingakwenza uzive uneentloni ngoncumo lwakho kwaye woyike nokuya kugqirha ukuba wenze ingozi encinci ngamazinyo akho. Ixhaphakile kakhulu. Kodwa ngomonde nexesha, kukho unyango olunokuqinisa amazinyo akho kwaye luphucule inkangeleko yawo. Musa ukuphelelwa lithemba!
Ziziphi iintlobo eziphambili ze (Amelogenesis Imperfecta)?
Kukho iintlobo ezine eziphambili zale meko. Makhe sijonge ukuba ziyintoni, ngokweenkcukacha ezithe vetshe:
- Uhlobo 1 — I-Hypoplastic: Le yimeko ebizwa ngokuba yi -enamel hypoplasia . Oku kuthetha ukuba akwenziwanga i-enamel eyaneleyo. I-enamel onayo inokuba yincinci, njengeglasi ebhityileyo. Oku kunokubangela ukuba amazinyo akho abe mancinci kunesiqhelo, abe nemiphezulu erhabaxa kwaye mhlawumbi abe nemingxunya.
- Uhlobo 2 — Hypomaturation: Olu hlobo lwenzeka xa iiproteni ezinceda i-enamel yakho ikhule zingaphuhli kakuhle. Cinga ngayo njengaxa isamente ingapholi kakuhle xa usakha indlu. Nangona i-enamel yakho isondelelene nobukhulu obuqhelekileyo, inokuthamba kakhulu kwaye iqhekeke lula . Njengesiqwenga setshokholethi.
- Uhlobo 3 — I-Hypocalcified: Olu hlobo lwenzeka xa i-enamel yakho ingavelisi i-calcium eyaneleyo ukuyiqinisa, okanye ukuyiqinisa. I-enamel isenokuba nobukhulu obuqhelekileyo, kodwa inokuqhekeka kwaye iguge ngokulula. Inokuqhekeka nokuba kucinezelwe kancinci, njengebhisikithi.
- Uhlobo lwesi-4 — Hypomaturation/hypoplasia/taurodontism: Kolu hlobo, ungabona iingxaki nge-enamel yamazinyo akho eziqhelekileyo kwiintlobo zoku-1 nezesi-2. Oku kuthetha ukuba i-enamel inokuba ncinci kwaye ithambe. Kwakhona, i-taurodontismOku kunokunxulunyaniswa nemeko ebizwa ngokuba yi "protrusion of the jaw." Oku kwenzeka xa umzimba wezinyo lakho mkhulu kakhulu kwaye iingcambu zimfutshane kakhulu. Olu lwalamano lungaqhelekanga lwamazinyo lunokwenza kube nzima koogqirha ukukhetha iindlela zonyango.
Ixhaphake kangakanani le meko?
(Amelogenesis Imperfecta) sisifo esingaqhelekanga kakhulu . Umzekelo, eMelika, sichaphazela umntu omnye kuphela kwabayi-14,000. Asiqhelekanga kangako naseSri Lanka. Ngoko ke usenokungaqhelanga ukuva ngaso.
Zithini iimpawu ze-(Amelogenesis Imperfecta)?
Ukuba une-Amelogenesis Imperfecta, ungazibona ezi mpawu kumazinyo akho. Jonga ukuba unayo na enye okanye ezingaphezulu kwezi:
- Ukutshintsha kombala: Amazinyo anokuba mhlophe njengetshokhwe, angwevu, atyheli, okanye abe mdaka. Ngamanye amaxesha, kunokubakho amabala okanye umbala utshintshe.
- Incinci ngendlela engaqhelekanga: Oku kunokubangela izithuba phakathi kwamazinyo akho.
- Umphezulu urhabaxa, unemingxuma, okanye unemiqolo. Olu rhabaxa lunokuviwa xa luchukunyiswa.
- Ukubhitya nokuqhekeka lula nokuguguleka. Nokuba uluma into encinci, iqhekeza lezinyo lingaphuma.
- Uvelwano kwizinto ezishushu nezibandayo. Usenokuziva amazinyo akho ephelelwa ngamandla xa usitya i-ayisikhrim okanye usela iti eshushu.
- Ukungalingani: Usenokuba nokuluma okuvulekileyo, apho amazinyo akho aphezulu nawasezantsi angadibani xa uvala umlomo wakho. Oku kuthetha ukuba kukho umsantsa phakathi kwamazinyo akho angaphambili nokuba umlomo wakho uvaliwe.
Zithini izizathu ze-(Amelogenesis Imperfecta)?
I-Amelogenesis I-Imperfecta yenzeka xa kukho utshintsho , okanye utshintsho, kwenye okanye ngaphezulu kwezakhi zofuzo ezilawula uphuhliso lwe-enamel yezinyo lakho. Olu tshintsho lwezakhi zofuzo lunokubangela iingxaki ekuphuhlisweni kwamazinyo akho omntwana kunye namazinyo akho amadala. Uninzi lwabantu luzuze olu tshintsho kumzali omnye okanye bobabini.
Ukwenziwa kwe-enamel yinkqubo entsonkothileyo kakhulu. Iphenjelelwa ziijini ezahlukeneyo. Ngokukodwa, kukho iijini ezilawula indlela iiproteni kunye neeminerali ezidibana ngayo ukwenza i-enamel. Ukuba kukho ingxaki encinci ngezi jini, i-amelogenesis imperfecta inokwenzeka. Ezinye zezona nguqu zixhaphakileyo kwi-amelogenesis imperfecta zinxulumene nezi jini:
- `(FAM83H)`
- `(ENAM)`
- `(MMP20)`
- `(AMELX)`
La magama anzima kancinci, kodwa la ngamanye amagama eejini asetyenziswa ngoogqirha xa bethetha ngale meko.
Oku kudluliselwa njani kwizizukulwana ngezizukulwana?
Nangona utshintsho lwemfuza lunokwenzeka ngokungazi, oko kuthetha ukuba ngaphandle kwesizathu, uninzi lwabantu abane-Amelogenesis Imperfecta bayifumana njengelifa le meko. Ngokuxhomekeke kuhlobo lwe-Amelogenesis Imperfecta, ipateni yelifa ingaba ngolu hlobo lulandelayo:
- I-Autosomal dominant: Kwimeko enjalo, kufuneka uzuze i-gene eguquliweyo komnye wabazali bakho ukuze uvelise i-Amelogenesis Imperfecta. Oku kuthetha ukuba ukuba umama okanye utata une-gene, umntwana naye unokuyifumana. Le yindlela uninzi lweentlobo ze-Amelogenesis Imperfecta ezizuzwa ngayo njengelifa.
- I-Autosomal recessive: Kwimeko enjalo, kufuneka uzuze i-gene eguquliweyo kubazali bobabini ukuze uphuhlise i-Amelogenesis Imperfecta. Le meko iya kuvela kuphela ukuba abazali bobabini bayayifumana i-gene.
- I-X-linked: Kule meko, utshintsho lufunyanwa nge -chromosome ye-X , hayi i-chromosome ye-Y. Njengoko usazi, abasetyhini bane-chromosome ezimbini ze-X (XX), kwaye amadoda ane-chromosome enye ye-X kunye nenye ye-Y (XY). Amakhwenkwe ane-X-linked (Amelogenesis Imperfecta) adla ngokuba neengxaki kunye neempawu ezininzi kunamantombazana.
Ziziphi iingxaki ezinokubakho ze-Amelogenesis Imperfecta?
Iingxaki nge-enamel yamazinyo zibonakalisa izicwili ezibuthathaka ezingaphantsi, ezibizwa ngokuba yi-dentine , kwaye zandisa umngcipheko weengxaki zamazinyo. (Amelogenesis Imperfecta) yandisa umngcipheko we:
- Iimbobo okanye ukubola kwamazinyo. Ngenxa yokuba i-enamel ibuthathaka, iintsholongwane zinokungena lula.
- Ukuguguleka kwamazinyo.
- Isifo seentsini. Usulelo lweentsini lunokwenzeka kuba kunzima ukucoca amazinyo akho ngokufanelekileyo.
- Intlungu yamazinyo.
- Ixhala: Usenokuziva uneentloni kwaye uxhalabile ngendlela abonakala ngayo amazinyo akho. Usenokude woyike nokuncuma esidlangalaleni.
Indlela yokuqaphela (i-Amelogenesis Imperfecta)?
Ugqirha wamazinyo unokuxilonga i-amelogenesis imperfecta ngexesha lovavanyo lwamazinyo. Ugqirha unokufumana umbono wemeko ngokujonga inkangeleko, umbala, kunye nokuthungwa kwamazinyo akho. Ekubeni le meko ichaphazela iintsapho, unokubuza ngembali yosapho lwakho yeengxaki zamazinyo, njengokuthi ingaba umama wakho, utata wakho, okanye abantakwenu baye baba neengxaki ezifanayo na.
Wena okanye umntwana wakho kusenokufuneka nihlolwe amazinyo nge-X-ray . Oku kuya kuvumela ugqirha ukuba afunde ngakumbi malunga nolwakhiwo lwamazinyo akho okanye omntwana wakho, umzekelo, ukuba i-enamel incinci kangakanani kunye nokuba injani imilo yeengcambu zezinyo.
Ngamanye amaxesha, uvavanyo lwemfuza lunokuqinisekisa utshintsho oluthile kunye nohlobo lwesifo. Oku kunokunceda ekucwangciseni unyango.
Iphathwa njani i-Amelogenesis Imperfecta?
Ngokuxhomekeke kwimeko yamazinyo akho nokuba ngamazinyo omntwana okanye angunaphakade, ugqirha wakho wamazinyo unokucebisa unyango oluhlukeneyo. Abantu abaninzi abane-Amelogenesis Imperfecta bafuna indibaniselwano yonyango ukukhusela nokuphucula ukubonakala kwamazinyo abo. Oku kunokuba yinkqubo yexesha elide.
Unyango luquka:
- Unyango lokubuyisela amazinyo kwimeko yawo: Olu nyango lulungisa amazinyo onakeleyo. Umzekelo, ungadinga isithsaba esinye okanye ezingaphezulu zamazinyo ukuze ugqume kwaye ukhusele amazinyo akho. Ezi zifana nesigqubuthelo esilingana namazinyo akho. Kwezinye iimeko, ukuba amazinyo akho onakele kakhulu, ukhetho olupheleleyo lokutshintshwa kwamazinyo olufana nokufakelwa ( izinyo lokufakelwa) kunye namazinyo okufakelwa (iseti yamazinyo okwenziwa) lolona khetho lubalaseleyo.
- Unyango lokuhombisa: Olu nyango luphucula inkangeleko yakho. Umzekelo, ukuba amazinyo akho atshintshile umbala, aqhekekile, okanye agugile ngenxa ye-amelogenesis imperfecta, ukubopha amazinyo ( ukwakha izinyo kwakhona ngezinto ezinombala wezinyo) kunye nee-veneers (izigqubuthelo ezibhityileyo ezincamatheliswe ngaphambili kwezinyo) kunokunceda. Ukongeza ekuncedeni ukuzinzisa izinyo, ii-crowns zikwaphucula inkangeleko yezinyo. Unyango lokwenza mhlophe lunokunceda ngamazinyo anombala.
- Unyango lwe-Orthodontic: Ukuba unamazinyo agobileyo ngenxa ye-Amelogenesis Imperfecta, okanye ukuba unengxaki yokuluma, kunokufuneka unxibe izixhobo zamazinyo ezifana neebraces okanye ii-aligner .
Eyona nto ibalulekileyo kukuthetha nogqirha wamazinyo uze wenze isicwangciso sonyango esikufaneleyo.
Yintoni onokuyilindela ukuba unayo (i-Amelogenesis Imperfecta)?
Ukuba ne-Amelogenesis Imperfecta (okanye ukuba nomntwana onesi sifo) kunokuba yinto ecaphukisayo necaphukisayo. Kuyaqondakala ukuba kunjalo. Iingxaki ze-enamel yamazinyo ziyandisa umngcipheko weengxaki ezininzi zamazinyo. Kusenokufuneka wenze unyango oluninzi ngokuhamba kwexesha. Kungathatha iminyaka ukugqiba unyango olupheleleyo.
Buza ugqirha wamazinyo wakho ukuba loluphi unyango olulungele amazinyo akho. Buza nangeshedyuli yonyango, njengoko inokwahluka kumntu nomntu. Ngale ndlela ungazi ukuba loluphi uhlobo lophuculo onokululindela kwaye luza kwenzeka nini. Umonde ubalulekile apha.
Ndingazinyamekela njani? Okanye ndingamnyamekela njani umntwana wam?
Ukuba une-Amelogenesis Imperfecta, kufuneka ulumke ngakumbi ukuze ukhusele amazinyo akho. Oku kuquka:
- Ukucoca amazinyo akho rhoqo:Ungaphoswa kukubona ugqirha wamazinyo ukuze uhlolwe ubuncinci kabini ngonyaka, kwaye kunokufuneka uye rhoqo.
- Gcina imikhwa emihle yokucoca amazinyo: Kufuneka uhlambe amazinyo akho kabini ngemini, uhlambe i-floss yonke imihla, kwaye usebenzise i-toothpaste ethomalalisa ulusu kunye namanzi afudumeleyo ukuthintela ulusu olunolusu .
- Yitya ukutya okufanelekileyo kumazinyo akho: Ukutya okutyebileyo kwiivithamini A kunye no-D (ezifana neminqathe, ibhotolo, kunye neoyile yentlanzi) kulungile kwi-enamel yamazinyo akho. Ukutya okutyebileyo kwi -calcium (njengobisi, iyogathi, itshizi, kunye nentlanzi encinci eneqokobhe) nako kukhetho olufanelekileyo.
- Ziphephe ukutya neziselo ezinokonakalisa amazinyo akho: Zama ukuphepha ukutya okanye iziselo ezineswekile eninzi okanye i-asidi (itofi, itshokolethi, iziselo ezibandayo). Kwakhona, nciphisa ukutya kwakho ukutya okunzima kakhulu, okunzima ukukuhlafuna (iilekese, ii-ice cubes). Kukwangumbono olungileyo ukuhlala kude nokutya okunamathelayo okufana ne-caramel.
- Sela iintlungu zentlungu ukuba kuyimfuneko: Ukuba uqaqanjelwa lizinyo, yenza idinga lokubonana nogqirha wamazinyo. Okwangoku, ungathatha amayeza okuphelisa iintlungu athengiswa ngaphandle kwekhawuntara afana ne -acetaminophen (okanye i-paracetamol) kunye ne -ibuprofen . Kodwa musa ukuthatha la mayeza okuphelisa iintlungu kangangeentsuku ezingaphezu kwe-10 ngexesha ngaphandle kokuthetha nogqirha wakho okanye umboneleli wezempilo.
Ndifanele ndimbone nini ugqirha?
Ukuba ubona iimpawu zesifo esibizwa ngokuba yi-Amelogenesis Imperfecta, ezinje ngamazinyo atshintsha umbala, abuthathaka, okanye aqhekeke lula, bonana nogqirha wamazinyo ngokukhawuleza. Unyango lunokukhusela, lubuyisele, kwaye luphucule ukubonakala kwamazinyo akho - kodwa xa i-enamel iphelile, ayinakwakhiwa kwakhona. Ngoko ke, okukhona ufumana unyango ngokukhawuleza, kokukhona amathuba akho okugcina amazinyo akho esempilweni.
Ndingayibuza yiphi imibuzo ugqirha wam?
Kubalulekile ukuthetha nogqirha wakho ngale meko. Nazi ezinye zemibuzo onokuyibuza:
- Luhlobo luni lwe-Amelogenesis Imperfecta endinalo (okanye umntwana wam)?
- Luhlobo luni lonyango endiludingayo (okanye umntwana wam)?
- Ishedyuli yonyango lwam (okanye lomntwana wam) iya kuba njani? Iza kuthatha ixesha elingakanani?
- Zeziphi izinto ezikhethekileyo endinokuziqhelisa ukuze ndinyamekele amazinyo am (okanye omntwana wam)?
- Ziziphi ezinye iingxaki ezinokuvela kwixesha elizayo ngenxa yale meko?
Eyona nto ibalulekileyo ekufuneka uyikhumbule kweli nqaku!
Kulungile, ngoku unombono ongcono wento ebesithetha ngayo (i-Amelogenesis Imperfecta). Ukuba unale meko, kufuneka usebenzisane ngokusondeleyo nogqirha wamazinyo ohlala ejonga amazinyo akho. Nangona kunokuba yinto ecaphukisayo ukuba kufuneka unyamekele ngakumbi ukukhusela amazinyo akho, khumbula ukuba kukho unyango olunokunceda ukukhusela i-enamel onayo. Kwakhona, ukuba awonelisekanga luncumo lwakho, kukho unyango olunokuphucula inkangeleko yalo. Kungathatha ixesha, kodwa wena nogqirha wamazinyo ningathatha amanyathelo okunyamekela amazinyo enu. Ungakhathazeki, kulungile? Ngolwazi olufanelekileyo kunye nonyango, le meko inokulawulwa.
I- Amelogenesis Imperfecta, I-Enamel Yamazinyo, Izifo Zemfuza, Ukutshintsha Kombala Wamazinyo, Unyango Lwamazinyo, Impilo Yamazinyo, Iingxaki Zamazinyo











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