Uma udokotela ekutshela ukuthi ingane yakho encane inesifo senhliziyo esibizwa ngokuthi "i-Shone's Complex," ungase uzizwe ushaqekile, wesaba futhi udidekile . Kuvamile kakhulu. Kungenzeka ukuthi awukaze uzwe ngaleli gama ngaphambili. "Siyini lesi sifo? Kuzokwenzekani enganeni yami?" Ungase ube nemibuzo eminingi engqondweni yakho. Ungakhathazeki. Ake sixoxe ngalokhu kalula nangokucacile. Iyini i-Shone's Complex? Ake siqonde kahle ukuthi yenzani enganeni.
Kalula nje, iyini le-Shone's Complex?
I-Shone's Complex yisifo senhliziyo esizalwa naso . Okwenzekayo kulokhu ukuthi kukhona ukuvinjelwa ezindaweni ezingaphezu kweyodwa endleleni yokugeleza kwegazi eya ohlangothini lwesobunxele lwenhliziyo yengane yethu. Cabanga nje, uhlangothi lwesobunxele lwenhliziyo yethu yilona oluthatha igazi elihlanzekile, elicebile ngo-oksijini emaphashini bese lilipompa umzimba wonke. Njengenjini yamanzi. Manje kwenzekani uma kukhona ukuvinjelwa noma izilonda kule ndlela yokugeleza kwegazi? Kuba nzima ngenhliziyo ukungenisa igazi, futhi kuba nzima ukupompa igazi emzimbeni. Yilokho okwenzekayo ku-Shone's Complex.
Lesi simo sibizwa ngokuthi i-Shone's Complex, ngemuva kukadokotela owasichaza okokuqala. Nakuba ethole izinkinga ezine zenhliziyo ezihlobene naso, odokotela sebethole ukuthi kunezinkinga eziningana ezengeziwe.
Yiziphi izinkinga zenhliziyo ezingahlotshaniswa ne-Shone's Complex?
Ukuze kutholakale ukuthi une-Shone's Complex, ingane kumele okungenani ibe neziphambeko ezimbili kweziyisishiyagalombili zenhliziyo esizoxoxa ngazo ngezansi. Ake sibone ukuthi ziyini. Amanye amagama angase abonakale eyinkimbinkimbi kancane, kodwa ngizowachaza kalula.
| Isici Senhliziyo | Kalula nje, kwenzekani ngalokhu? |
|---|---|
| I-Cor triatriatum | Kwakha ulwelwesi olwengeziwe ngaphakathi kwegumbi eliphezulu kwesobunxele senhliziyo (i-atrium yesobunxele). Lokhu kuhlukanisa igumbi libe izingxenye ezimbili, kuvimbela igazi ukuthi ligeleze liye ekamelweni elingezansi (i-ventricle yesobunxele). |
| Indandatho ye-Supravalvular mitral | Indandatho yezicubu ezinemicu ikhula ngaphezu kwevalvu ye-mitral enhliziyweni. Lokhu kunciphisa isikhala lapho ivalvu ivuleka khona, kuvimbele ukugeleza kwegazi. |
| I-valve ye-mitral yeparachute | Ngokuvamile, kunemisipha emibili (imisipha ye-papillary) esiza i-valve ye-mitral ukuthi ivuleke futhi ivaleke. Kulesi sici, kunomunye kuphela. Kufana nokuthi zonke izintambo zeparashuti ziqoqene endaweni eyodwa. Lokhu kungabangela ukuthi i-valve inciphe noma igazi livuza emuva. |
| I-ventricle yesobunxele engaphansi kwepulasitiki | "I-Hypoplastic" isho ukuthi ayikhuli kahle. Lapha, i-ventricle yesobunxele, igumbi eliyinhloko lokupompa lenhliziyo, ayikhuli kahle. Incane. Ngakho ayikwazi ukupompa igazi kahle. |
| I-stenosis ye-Subaortic | Izicubu ezengeziwe ziyanqwabelana ngaphansi kwevalvu ye-aorta, epompa igazi lingene ku-aorta, okwenza indawo ibe ncane. Lokhu kuncipha kwenza kube nzima ngenhliziyo ukupompa igazi. |
| I-valve ye-aorta ye-bicuspid | Ngokuvamile, ivalvu ye-aorta inama-flap amathathu. Kodwa izingane ezinalesi sici zinezimbili kuphela. Lokhu kungabangela ukuthi ivalvu inciphe noma ivuza igazi. |
| I-annulus ye-valve encane ye-aortic | Indandatho eqinile (i-annulus) ezungeze isisekelo se-aortic valve iba ncane kunokujwayelekile, ngakho-ke inani legazi elingadlula ku-valve liye ku-aorta liyancishiswa. |
| Ukuhlangana kwe-aorta | Ukuncipha kwe-aorta, umthambo wegazi oyinhloko othwala igazi uye emzimbeni, kubangela ukuthi inhliziyo isebenze kanzima ukupompa igazi endaweni encishisiwe. |
Into ebalulekile ukuthi uma kukhona amaphutha amabili noma ngaphezulu kwalawa ayisishiyagalombili, yilokho odokotela abakubiza ngokuthi i-Shone's Complex. Esikhathini esiningi, kuba nokuvinjelwa okukodwa endleleni yokungena kanye nokuvinjelwa okukodwa endleleni yokuphuma.
Yiziphi izimpawu uma ingane yami inalesi simo?
Ezinye izingane ezinalesi simo, uma zinzima kakhulu, ziqala ukukhombisa izimpawu cishe ngokushesha ngemva kokuzalwa . Lokhu kungenxa yokuthi inhliziyo yengane ayikwazi ukupompa igazi elanele emzimbeni. Kodwa-ke, ngezinye izikhathi, izimpawu zingavela ngesikhathi sobuntwana noma ngisho nasebusheni.
Bheka lezi zimpawu enganeni yakho:
- Ubunzima bokuthola isisindo: Ukungatholi isisindo ngendlela efanele.
- Ukuzizwa ukhathele ngenkathi uphuza ubisi: Ngemva kokuphuza ubisi, uqala ukujuluka futhi ube nobunzima bokuphefumula.
- Ukwehla kokukhishwa komchamo : Ukukhipha umchamo omncane kunokujwayelekile.
- Ukushaya kwenhliziyo okubuthakathaka: Ukushaya kwenhliziyo kubuthakathaka kakhulu, ikakhulukazi ezandleni nasezinyaweni.
- Umehluko ekucindezelweni kwegazi phakathi kwezingalo nemilenze: Umfutho wegazi ezingalweni uphakeme kunasemilenzeni.
- Ukuqongelela kwe-lactic acid egazini.
Uma ingane yakho inesinye noma ngaphezulu salezi zimpawu, kubaluleke kakhulu ukukhuluma nodokotela wakho ngokushesha okukhulu.
Kungani lokhu kwenzeke enganeni yami? Iyini imbangela yalokhu?
Manje ungase uzibuze, "Kungani lokhu kwenzeke enganeni yami? Ingabe kuyiphutha lami?" Empeleni, odokotela abakayitholi imbangela ethile yalokhu. Esikhathini esiningi, kwenzeka ngezikhathi ezithile. Asinalo ulwazi olwanele lokusho ngokuqinisekile ukuthi kuyisici sofuzo noma sendawo ezungezile.
Nakuba olunye ucwaningo lubonisa ukuthi kungase kube ufuzo, indlela okudluliswa ngayo emindenini iyinkimbinkimbi kakhulu. Ngakho-ke kudingeka ucwaningo olwengeziwe ukuze kuqondwe ngokugcwele lokhu.
Ngakho-ke sicela ukhumbule, lokhu akulona iphutha lakho. Asinawo amandla okulawula lezi zinto.
Yiziphi izinkinga ezingaba khona ngenxa yalesi simo?
I-Shone's Complex ingabangela izinkinga ezithile, yingakho ukwelashwa okusheshayo nokuqapha isikhathi eside kubalulekile.
- Umfutho wegazi ophezulu wamaphaphu: Ukwanda okungavamile komfutho wegazi emithanjeni yegazi ethwala igazi liye emaphashini.
- Izigqi zenhliziyo ezingavamile: Izigqi zenhliziyo ezingavamile.
- Ukwehluleka kwenhliziyo: Isimo lapho inhliziyo ingakwazi ukupompa igazi elanele emzimbeni.
Odokotela bakuthola kanjani lokhu?
Odokotela basebenzisa izivivinyo eziningana ukuze baxilonge lesi sifo.
- I-echocardiogram yengane esanda kuzalwa: Lokhu kuskena okukhethekile okwenziwa ngesikhathi ingane isesesibelethweni. Kungabona izinkinga zenhliziyo ngaphambi kokuba ingane izalwe.
- I-Transthoracic echocardiogram (TTE): Ukuhlolwa kwenhliziyo nge-ultrasound okwenziwa ngemva kokuzalwa komntwana. Lokhu kuhlolwa kusetshenziselwa kakhulu ukuxilonga i-Shone's Complex.
- Ukuskena kwe-CT yenhliziyo noma i-MRI: Lokhu akuvamile ukwenziwa yiwo wonke umuntu, kodwa kwezinye izimo, lokhu kuhlolwa kungasiza ekuhlinzekeni ngolwazi olujulile mayelana nesakhiwo senhliziyo.
Ngokuvamile, lesi sifo sitholakala ngaphambi noma ngemva kokuzalwa. Kodwa-ke, ngezinye izikhathi lesi sifo sitholakala okokuqala ebuntwaneni noma ebusheni, lapho izimpawu zincane futhi zingabi zimbi kangako. Ezimweni ezinjalo, udokotela angase athumele ukuhlolwa okwengeziwe ngenxa yomsindo ongavamile (ukububula kwenhliziyo) ozwakalayo lapho kulalele inhliziyo.
Yiziphi izindlela zokwelapha lokhu?
Ukuphela kwendlela yokwelapha i-Shone's Complex ukuhlinzwa . Okwamanje ayikho imithi engelapha lesi simo. Kodwa-ke, udokotela angase anikeze imithi yokulawula izimpawu zengane nokusekela ukusebenza kwenhliziyo kuze kube yilapho ehlinzwa.
Akukho ukuhlinzwa okuqondile kwalokhu. Esikhundleni salokho, odokotela bazonquma ukuthi yikuphi ukuhlinzwa okudingekayo ngokusekelwe kulokho ingane yakho enakho kanye nokuthi inhliziyo isebenza kahle kangakanani.
Ingane yakho ingadinga ukuhlinzwa okukodwa noma ngaphezulu kwalokhu okulandelayo:
- Ukususwa kwendandatho yezicubu ezengeziwe ezizungeze i-valve ye-mitral.
- Ukulungiswa kwevalvu ye-Mitral.
- Ukufakwa esikhundleni kwe-valve ye-Mitral (lokhu akuvamile kangako).
- Ukususwa kwezicubu ezisele ngaphansi kwevalvu ye-aorta.
- Ukwandisa ukuvuleka kwevalvu ye-aorta.
- Ukulungisa ingxenye encane ye-aorta.
Inqubo yokuhlinzwa
Ngezinye izikhathi odokotela bakwenza lokhu ngendlela ehleliwe . Okusho ukuthi, abakwenzi konke ngesikhathi esisodwa. Bakwenza ngezingxenye ezimbili, bahlukaniswe isikhathi. Isibonelo, ukuhlinzwa kokuqala kususa ukuvaleka kwendlela igazi eliphuma ngayo enhliziyweni. Bese, ukuhlinzwa kwesibili kususa ukuvaleka kwendlela igazi eligeleza ngayo enhliziyweni. Udokotela wakho uzochaza ukuthi zingaki ukuhlinzwa ingane yakho ezodinga nokuthi kwenziwa nini kahle.
Iyiphi impilo yengane yesikhathi esizayo kanye nesibikezelo sayo?
Impilo yesikhathi esizayo kanye nenhlalakahle yengane kuncike ezintweni eziningana:
- Ubunzima besifo: Ukuthi inkinga yenhliziyo imbi kangakanani.
- Isivinini sokwelashwa: Indlela ukwelashwa okuqalwa ngayo ngokushesha.
- Izinkinga: Kungakhathaliseki ukuthi kuzovela ezinye izinkinga noma cha.
- Ukuphindeka kwezinkinga: Ingabe ukukhubazeka kwenhliziyo okwelashwa ngaphambilini kuzophindeka ngokuhamba kwesikhathi?
Isibonelo, izinto ezifana nokugoba kwe-aorta zingaphinde zenzeke ngokuhamba kwesikhathi. Ngakho-ke, njengoba ingane yakho ikhula, kungase kudingeke ukuhlinzwa okwengeziwe. Udokotela wakho uzokunikeza ulwazi olwengeziwe ngalokhu kuye ngesimo sengane yakho.
Izifundo eziningi zikhombisile ukuthi izinga lokusinda isikhathi eside ngemva kokuhlinzwa lingaphezu kuka-75%, kuze kube yiminyaka engama-20 . Lokho kusho ukuthi izingane ezintathu kwezine ziphila kahle futhi ziphilile ngemva kokwelashwa.
Ungase ube nemibuzo eyinkulungwane engqondweni yakho ngemva kokuzwa ngokuxilongwa kwengane yakho. Lokho kuyinto evamile kakhulu. Bhala phansi imibuzo efika engqondweni yakho encwadini yamanothi. Uma uya kobona udokotela, mbuze yonke. Ithimba lezokwelapha lengane yakho lizokuchazela konke lokhu futhi likuqondise ukuthi yini okufanele uyenze ngokulandelayo.
Umlayezo Wokuya Nawe Ekhaya
- I-Shone's Complex iyisifo senhliziyo esingavamile esibangelwa ukuzalwa esibangela ukuthi ukugeleza kwegazi ohlangothini lwesobunxele lwenhliziyo kuvimbeke.
- Ukuze kutholakale ukuthi umntwana unalesi sifo, kufanele okungenani abe nokukhubazeka kwenhliziyo okungu-2 kwangu-8.
- Ukwelashwa kwalokhu kuphela ukuhlinzwa. Ukuhlinzwa kuvame ukuphumelela.
- Ngemva kokuhlinzwa, ingane izodinga ukulandelwa udokotela wenhliziyo impilo yayo yonke. Ungaphuthelwa yinoma yikuphi kwalokhu kuhlangana.
- Into ebaluleke kakhulu ukuthi lesi simo akusona iphutha lakho noma lomlingani wakho. Ungakhathazeki ngaso.











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