Uvame ukwenzani uma ingane yakho inomkhuhlane, umkhuhlane, noma isifo esifana ne-chickenpox? Ngezinye izikhathi sicabanga ukuthi, "O... mnike nje i-aspirin encane." Kodwa bewazi ukuthi ukunikeza i-aspirin ngesikhathi esinjengaleso kungaba yingozi kakhulu enganeni yakho? Namuhla sikhuluma ngesimo esingakhulunywa ngaso kakhulu, kodwa esibucayi kakhulu esibangela lokho. Leso yi-Reye's Syndrome, noma i-Reye's Syndrome .
Kalula nje, iyini i-Reye's Syndrome?
I-Reye's Syndrome yisifo esingavamile kodwa esibi kakhulu esibangela ukuvuvukala kwesibindi nobuchopho. Singathinta noma ubani wanoma yimuphi ubudala, kodwa sivame kakhulu ezinganeni nakubantu abadala abasebasha abalulama ekuthelelekeni ngegciwane njenge-flu noma i-chickenpox.
Ucwaningo lodokotela luthole ukuthi ingozi enkulu yalokhu ukunikeza ingane i-aspirin noma eminye imithi efanayo, okungukuthi, imithi equkethe ama-salicylates, ngesikhathi sokutheleleka ngegciwane.
Ngenxa yalesi sizathu, odokotela batusa kakhulu ukugwema ngokuphelele i-aspirin ezinsaneni nasezinganeni ezincane ezisalulama ekuthelelekeni ngamagciwane.
Kungani lesi simo senzeka?
Odokotela abakaqondi ngokugcwele imbangela eqondile ye-Reye's Syndrome, kodwa bayazi ukuthi ezinye izingane zinamathuba amaningi okuba nalesi simo uma zinikwa i-aspirin ngesikhathi sokutheleleka ngegciwane.
Ngaphezu kwalokho, ezinye izingane zisengozini enkulu yokuthola lesi sifo. Lokhu kufaka phakathi:
- Uma benesifo sofuzo esihlobene nenqubo yokuqhekeka kwama-fatty acid emzimbeni (i-Fatty Acid Oxidation Disorder).
- Uma uke wachayeka kunoma yimaphi amakhemikhali anobuthi njengemithi yokunciphisa upende, imithi yokubulala izinambuzane, kanye nemithi yokubulala ukhula.
Uma kwenzeka i-Reye's Syndrome, amangqamuzana omzimba ayavuvukala bese amafutha eqala ukuqongelela ngaphakathi kwawo. Ngesikhathi esifanayo, izinga likashukela egazini liyehla ngokuzumayo. Izinto eziyingozi njenge-ammonia kanye ne-asidi ziyanda egazini. Lezi zinguquko zingabangela umonakalo omkhulu esibindini ikakhulukazi ebuchosheni, ngoba lezi zitho ziyavuvukala kakhulu.
Ziyini izimpawu? Sizibona kanjani?
Izimpawu ze-Reye's Syndrome zivame ukuvela ezinsukwini ezi-3 kuya kwezi-5 ngemuva kokuqala kokutheleleka ngegciwane. Lezi zimpawu zingahluka kancane kuye ngobudala, ngakho-ke kubalulekile ukukunaka lokhu.
Ake sibheke lezi zici etafuleni ukuze kube lula ukuziqonda.
| Isenzakalo / Iqembu Lobudala | Izimpawu ezibonwayo |
|---|---|
| Izimpawu Zokuqala | |
| Izingane ezingaphansi kweminyaka emibili ubudala | Uhudo kanye nokuphefumula okusheshayo |
| Izingane ezincane kanye nentsha | Ukuhlanza okuqhubekayo kanye nokulala okungajwayelekile |
| Izimpawu Ezinzima | |
| Izinguquko zokuziphatha | Ukucasuka okungazelelwe, ulaka, kanye nentukuthelo. |
| Isimo sengqondo | Ukudideka, ukubona noma ukuzwa izinto ezingekho (ukubhula). |
| Izinguquko zomzimba | Ubuthakathaka noma ukuba ndikindiki ezithweni, ukuxhuzula , ukulahlekelwa ukwazi. |
Lesi yisimo esiphuthumayo! Uma ubona noma yiziphi zalezi zimpawu ezinzima, njengokushintsha okukhulu kokuziphatha, ukuquleka, noma ukulahlekelwa ingqondo, yisa ingane yakho eMnyangweni Wezimo Eziphuthumayo (ETU) wesibhedlela ngaphandle kokulibala . Lokhu kungaba yingozi empilweni, ngakho-ke ukuxilongwa nokwelashwa ngokushesha kubalulekile.
Ngezinye izikhathi lezi zimpawu zingadidaniswa ne-meningitis, ukusabela kwesifo sikashukela, noma ubuthi. Uma usola ukuthi kukhona into enobuthi (isb. i-herbicide), shayela ngokushesha i-National Poisons Information Centre e-Colombo National Hospital ukuze uthole iseluleko.
Udokotela usithola kanjani lesi sifo ngqo?
Akukho ukuhlolwa okukodwa okuqondene ngqo ne-Reye's Syndrome, ngakho odokotela bavame ukubheka ngokucophelela izimpawu nomlando bese benza izivivinyo eziningana ukuze banqume ezinye izimo.
Phakathi kwazo:
- Ukuhlolwa kwegazi nomchamo: Lokhu kuhlola izinto ezifana nokusebenza kwesibindi, ushukela egazini, kanye namazinga e-ammonia.
- Ukuhlolwa kwezinkinga ze-metabolism yamafutha: Kuhlolwa igazi okukhethekile ngalokhu.
- Ukubhoboza Umgogodla/Ukushaya Ithambo: Lokhu kuhlolwa kwenziwa ukuze kulinganiswe ingcindezi ebuchosheni nasemgogodleni kanye nokuhlola ukutheleleka.
- Ukuhlolwa Kwesibindi: Lokhu kusiza ekunqumeni izinga eliqondile lomonakalo kumaseli esibindi.
- Ama-CT noma ama-MRI scan: Lokhu kungabheka ukuvuvukala kobuchopho bese kuthola ukuthi kukhona yini ezinye izinkinga.
Ingabe ikhona indlela yokwelapha lokhu?
Akukho ukwelashwa okuqondile okungayimisa ngokuphelele i-Reye's Syndrome. Kodwa-ke, odokotela bangayiphatha le nkinga ngokungenisa isiguli esibhedlela, ukuvimbela izimpawu ezinzima, futhi ikakhulukazi ukulawula ukuvuvukala kobuchopho. Nazi ezinye izinto okufanele zenziwe:
- Uketshezi olufakwa emthanjeni (IV) kanye nokudla okunomsoco.
- Ama-diuretics yimithi esusa amanzi amaningi nosawoti emzimbeni futhi inciphise ukuvuvukala.
- Imithi yokuvimbela ukopha.
- Uma kwenzeka isimo esinjengokuphuma kwegazi esibindini, kunikezwa i-vitamin K, i-plasma, nama-platelet ukusiza ekuqhekekeni kwegazi.
Kungaba yini imiphumela yesikhathi eside?
Izindaba ezinhle ukuthi ngentuthuko kwezesayensi yezokwelapha, lesi sifo manje singatholakala kusenesikhathi, futhi izinga lokufa lehle lisuka ku-50% laya ngaphansi kuka-20%. Lokhu kusho ukuthi iningi lezingane nabantu abadala abasebasha abathola lesi sifo bayalulama ngokugcwele.
Ukuthi umuntu ululama kahle kangakanani kanye nengozi yokulimala kobuchopho isikhathi eside kuncike ekutheni ubuchopho buvuvukele kangakanani . Ingozi yokulimala kobuchopho iphakeme uma izimpawu ziba zimbi ngokushesha, okuholela ekuqulekeni.
Umlayezo Wokuya Nawe Ekhaya
- Ungalokothi unike izingane kanye nabantu abasha i-aspirin uma benesifo esibangelwa amagciwane njenge-flu, umkhuhlane, noma i-chickenpox.
- Ngaphambi kokunikeza ingane yakho noma yimuphi umuthi, hlola ukuthi uqukethe i-aspirin noma ama-salicylates. Uma ungabaza, qiniseka ukuthi ubuza udokotela wakho.
- Uma ingane yakho ibonisa izimpawu ezifana nokuhlanza okuqhubekayo, ukozela ngokweqile, kanye nokushintsha kokuziphatha ngemva kokutheleleka ngegciwane, ungazinaki.
- Uma ubona izimpawu ezinzima njengokuquleka noma ukulahlekelwa ingqondo, thatha ingane yakho uye e-Emergency Treatment Unit (ETU) esibhedlela ngokushesha. Ukwelashwa okusheshayo kungasindisa izimpilo futhi kunciphise umonakalo wesikhathi eside.











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