Ke luhi nei ʻoe i ka lā a pau a ʻaʻohe ikaika e hana i kekahi mea? Manaʻo pinepine mākou no ka mea hana nui mākou, ʻaʻole mākou e ʻai pono, a ʻaʻole mākou e hiamoe nui. Akā, ua ʻike anei ʻoe aia paha kekahi kumu hohonu no kēia mau mea a pau i loko o ko mākou kino? Ua lohe anei ʻoe i nā hale hana ikehu liʻiliʻi i loko o ko mākou kino? ʻO kēia nā mea a mākou e kapa nei he mitochondria. Inā ʻaʻole hana pono kēia mau mea, hiki ke kū mai nā pilikia nui a mākou e noʻonoʻo ʻole ai. No laila e kamaʻilio kākou e pili ana i kēia me nā kikoʻī a me ka maʻalahi i kēia lā.
He aha kēia mau mitochondria?
I ka ʻōlelo maʻalahi,
ua like nā mitochondria me nā ʻenekini liʻiliʻi a i ʻole nā mea kanu mana i loko o kēlā me kēia cell o ko mākou kino. E noʻonoʻo, inā he kūlanakauhale nui ko mākou kino, ʻo kēia mau mitochondria nā mea kanu mana e hāʻawi i ka uila i kēlā kūlanakauhale. Ma ka hoʻohana ʻana i ka meaʻai a mākou e ʻai ai a me ka oxygen a mākou e hanu ai, hana kēia mau mitochondria liʻiliʻi i 90% o ka ikehu e pono ai ko mākou kino e holo, lele, noʻonoʻo, hana,
a i ka pōkole, ola. ʻOi loa aku i nā ʻōpū e hana mau ana a koi aku i ka ikehu hou aʻe, e like me ko mākou
puʻuwai, lolo, a me nā ʻiʻo, he mau tausani o kēia mau mitochondria. No ka mea, pono kēlā mau ʻōpū i ka 'current' hou aʻe ma mua o nā mea ʻē aʻe.
No laila he aha kēia mau maʻi mitochondrial?
E noʻonoʻo, he aha ka mea e hiki mai ana inā e pau koke ka hana pono ʻana o kēlā mau hale mana aʻu i ʻōlelo ai a pau ka hana ʻana i ka ikehu lawa? E pōʻeleʻele ke kūlanakauhale holoʻokoʻa, a e pilikia pū nā hana o ko mākou kino. ʻO ia ka manawa e kū mai ai nā kūlana i kapa ʻia ʻo
'Nā Maʻi Mitochondrial' . He
mau maʻi mau kēia, ʻo ia hoʻi, hiki ke mau i ke ola holoʻokoʻa. ʻO ka hapa nui o ka manawa, he genetic lākou, ʻo ia hoʻi
, ua hoʻoilina ʻia mai nā mākua a i nā keiki. I kekahi manawa hiki ke loaʻa kēia mau hōʻailona i ka wā hānau, a i kekahi manawa hiki ke ʻike ʻia ma hope o ke ola.
He aha nā kumu o kēia mau maʻi?
ʻO ka hapa nui o ka manawa, ʻo ke kumu nui o kēia he genetic. ʻO ia hoʻi, kekahi mau hemahema i loko o nā genes a mākou e hoʻoilina ai mai ko mākou mau mākua mai. Hiki ke hana ʻia kēia ma kekahi mau ʻano nui.
| ʻAno Hoʻoilina | I ka ʻōlelo maʻalahi... |
|---|
| Hoʻoilina Recessive Autosomal | I kēia hihia, hoʻoilina ke keiki i kahi gene kīnā (gene mutated) mai ka makuahine a me ka makuakāne. A laila, loaʻa i kēlā me kēia keiki i loko o ka ʻohana he 25% ka manawa e loaʻa ai ka maʻi. |
| Hoʻoilina Mana Autosomal | ʻO ka mea e hana ʻia ma ʻaneʻi, ua hoʻoilina ke keiki i kahi gene kīnā mai hoʻokahi makua wale nō, ʻo ka makuahine a i ʻole ka makuakāne. A laila, loaʻa i kēlā me kēia keiki i loko o ka ʻohana he 50% ka manawa e loaʻa ai ka maʻi. |
| Hoʻoilina Mitochondrial | He mea kūikawā iki kēia. Loaʻa i nā Mitochondria kā lākou DNA ponoʻī. Ma kēia hoʻoilina, loaʻa i kahi makuahine me ka mitochondria kīnā ʻole he 100% ka manawa kūpono e hoʻoilina ai kāna mau keiki āpau i kēia maʻi. |
| Nā Hoʻololi Kaulike | He mea kākaʻikahi loa, hiki ke hana ʻia kahi mutation ke hoʻokumu hou ʻia nā genes o ke keiki, me ka ʻole o ka hewa o nā mākua. |
Eia kekahi, hiki ke pili ka hana ʻole o ka mitochondrial me kekahi mau maʻi, e like me ka maʻi Alzheimer, muscular dystrophy, diabetes, a me kekahi mau ʻano maʻi kanesa.
He aha nā hōʻailona o kēia mau maʻi?
ʻO kēia kahi e huikau ai nā kānaka he nui. Hiki ke ʻokoʻa loa nā hōʻailona o kēia mau maʻi mai kekahi kanaka a i kekahi. ʻO ke kumu, ʻokoʻa nā hōʻailona ma muli o ke kino i hoʻopilikia ʻia. ʻOiai he mau hōʻailona palupalu
loa kekahi poʻe, hiki i kekahi ke loaʻa nā hōʻailona koʻikoʻi.
Hiki ke ʻike ʻia kēia mau hōʻailona i kēlā me kēia makahiki. Eia kekahi, no ka mea ua like kēia mau hōʻailona me nā maʻi maʻamau ʻē aʻe, hiki i kekahi manawa ke paʻakikī ke ʻike i ka maʻi.
Hōʻike ka papa ma lalo nei i kekahi o nā hōʻailona e hiki ke kū mai.
| ʻŌnaehana/ʻōkana i hoʻopilikia ʻia | Nā hōʻailona hiki ke loaʻa |
|---|
| Ka ulu ʻana a me nā ʻiʻo | Ka ulu ʻole ʻana, ka nāwaliwali o nā ʻiʻo, a me ka luhi i ka wā e hoʻoikaika kino ai. |
| ʻO ka lolo a me nā aʻalolo | Nā pilikia aʻo, nā lohi o ka ulu ʻana, ka maʻi autism spectrum, nā migraines, nā hopu ʻana, ka hahau ʻana, a me ka dementia. |
| Nā kino sensory | Nā hemahema o ka ʻike a me ka lohe. |
| Nā kino kūloko | Maʻi puʻuwai, puʻupaʻa a i ʻole ke akepaʻa, ka maʻi diabetes, nā pilikia thyroid. |
| ʻŌnaehana hoʻoheheʻe | Paʻakikī i ke ale ʻana, ʻeha ka ʻōpū, ka maʻi pākīkī a i ʻole ka paʻa ʻana o ka ʻōpū, ka luaʻi ʻana. |
Pehea e ʻike ai i ka maʻi?
E like me kaʻu i ʻōlelo ai ma mua, hiki ke ʻokoʻa loa nā hōʻailona o kēia mau maʻi, no laila hiki ke paʻakikī iki ke ʻike pono i ke ʻano o ka maʻi.
ʻAʻole hiki ke ʻike ʻia me kahi hoʻāʻo hoʻokahi. ʻO ia ke kumu e nānā ai ke kauka i kahi maʻi a hoʻouna iā lākou no kekahi mau hoʻāʻo like ʻole.
Nā hoʻokolohua i hana pinepine ʻia
- He loiloi pono o ka mōʻaukala lapaʻau o ka ʻohana .
- Ke hana ʻana i kahi hoʻokolokolo kino a me ka neurological piha.
- Ke ʻike ʻana i nā loli kemika i loko o ke kino ma o nā hoʻāʻo koko a me ka mimi (hoʻokolohua Metabolic).
- MRI scan (ʻoi aku hoʻi no nā pilikia o ka lolo).
- ʻO kahi hoʻāʻo ECG (Electrocardiogram) a i ʻole Echocardiogram e nānā i ka hana o ka puʻuwai.
- Nā hoʻāʻo DNA kūikawā e ʻike i nā kīnā genetic .
- I kekahi mau hihia, pono paha e lawe i kahi ʻāpana liʻiliʻi o ke ʻiʻo a i ʻole ka ʻili no ka hoʻāʻo ʻana (biopsy) .
He aha nā lāʻau lapaʻau no kēia?
ʻO kahi nīnau a ka poʻe he nui e nīnau ai, inā paha he lāʻau lapaʻau piha no kēia. ʻO ka ʻoiaʻiʻo,
ʻaʻohe lāʻau lapaʻau kūikawā no nā maʻi mitochondrial. Akā, mai makaʻu i kēlā. Nui nā lāʻau lapaʻau i loaʻa e kāohi i nā hōʻailona a hoʻolohi i ka holomua o ka maʻi. Aia ka lāʻau lapaʻau i ka maʻi o ka mea maʻi, nā ʻōpū i hoʻopilikia ʻia, a me ke koʻikoʻi o ka maʻi. ʻOiai inā ʻelua mau kānaka me ka maʻi like i loaʻa ka lāʻau like, ʻaʻole paha e hana like.
ʻO kekahi o nā ʻano lapaʻau nui:
- Nā huaora a me nā mea hoʻohui: Kōkua kekahi mau huaora i ka hana mitochondrial.
- Hoʻoikaika Kino: ʻOi aku ka hoʻoikaika kino. Pono e hana ʻia kēia ma lalo o ke alakaʻi a kāu kauka a mea hoʻoponopono kino paha.
- Hoʻōla kino , hoʻōla hana, a me ka hoʻōla ʻōlelo : Kōkua kēia i ka mea maʻi e hana maʻalahi i nā hana o kēlā me kēia lā.
Eia kekahi, ua ʻōlelo ʻia nā mea maʻi e noho mamao aku mai kekahi mau mea. Eia kekahi laʻana, he mea nui loa ka pale ʻana i nā mea e like me ke anuanu loa a i ʻole ka wela, ka pōloli, ka hiamoe ʻole, ke kaumaha,
ka puhipaka, a me ka inu ʻona .
Leka Lawe-Home
- Ua like nā Mitochondria me nā mea kanu mana liʻiliʻi e hāʻawi ana i ka ikehu i nā ʻāpana o ko mākou kino.
- ʻO nā maʻi i hoʻokumu ʻia e ka hana pono ʻole o kēia mau mea he lōʻihi ka manawa a hoʻoilina pinepine ʻia ma ke ʻano genetic.
- He ʻokoʻa loa nā hōʻailona a hiki ke komo pū me ka nāwaliwali o nā mākala, ka ulu ʻole ʻana, ka hemahema o ka ʻike a me ka lohe, a me nā maʻi puʻuwai.
- ʻOiai ʻaʻohe lāʻau lapaʻau kūikawā no kēia mau maʻi, hiki iā ʻoe ke ola i kahi ola maikaʻi ma ka kaohi ʻana i nā hōʻailona a me ka hoʻololi ʻana i kou nohona.
- Inā loaʻa iā ʻoe a i ʻole kekahi o kou ʻohana kēia maʻi, he mea nui loa ia e kamaʻilio me kāu kauka e pili ana i ke aʻo ʻana i nā ʻano genetic ma mua o ka loaʻa ʻana o nā keiki. ʻO ka mea maikaʻi loa e hana ai, ʻaʻole e hopohopo, akā e kiʻi i ka ʻōlelo aʻoaʻo lapaʻau kūpono.
Mitochondria, Mitochondria, Maʻi Mitochondrial, Maʻi Genetic, Ikehu, Nā Kelepona, Nā Hōʻailona, Lapaʻau
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