Koj puas xav tias koj nkees thiab qaug zog heev txhua hnub yam tsis muaj laj thawj? Koj puas xav tias koj tsis muaj zog? Los yog koj poob phaus nrog rau kev tsis noj mov? Txawm hais tias peb feem ntau xav txog cov no ua kev qaug zog ib txwm muaj, qee zaum qhov no tuaj yeem yog ib qho tsos mob ntawm qee yam loj dua. Qhov ntawd yog tus mob uas peb tab tom tham txog hnub no, Addison's Disease. Tsis txhob txhawj, peb yuav tham txog txhua yam hauv cov lus yooj yim.
Hais yooj yim xwb, kab mob Addison yog dab tsi?
Xav txog tias peb lub cev yog ib lub Hoobkas uas nyuaj heev thiab zoo kawg nkaus. Hauv lub Hoobkas no, muaj ib pawg neeg xa xov uas ua kom txhua yam sib npaug thiab khiav zoo. Peb hu lawv
cov tshuaj hormones . Nyob rau saum peb lub raum, muaj ob lub qog me me, peb hu lawv
cov qog adrenal . Ob lub qog me me no tsim ntau hom tshuaj hormones uas tseem ceeb rau peb lub neej. Yog li, yog tias vim li cas cov qog adrenal no tsis tuaj yeem tsim cov tshuaj hormones uas xav tau, qhov ntawd yog qhov peb hu ua Addison's Disease lossis Primary Adrenal Insufficiency. Qhov no yog ib qho mob tsis tshua muaj. Nws cuam tshuam txog li ib ntawm ib lab tus tib neeg. Tab sis qhov zoo tshaj plaws yog tias
yog tias koj raug kuaj pom zoo thiab noj tshuaj kho mob uas tus kws kho mob tau sau tseg, koj tuaj yeem ua neej nyob ib txwm tsis muaj teeb meem. Cia peb kawm txog ob qho ntawm cov tshuaj hormones tseem ceeb tshaj plaws.
Muaj ob hom tshuaj hormones tseem ceeb uas raug txo qis hauv lub cev hauv Addison tus kab mob. 1.
Cortisol: Qhov no kuj hu ua 'hormone kev ntxhov siab'. Cov tshuaj hormones no yog siv los npaj lub cev los daws kev ntxhov siab, txawm tias lub hlwb lossis lub cev. Tsis tas li ntawd, nws pab tswj
cov ntshav siab thiab lub cev siv cov protein, carbohydrates, thiab rog li cas. 2.
Aldosterone: Cov tshuaj hormones no tswj cov ntsev (sodium) thiab potassium hauv lub cev los ntawm peb lub raum. Yog tias qhov no tsis ua kom raug, cov ntsev hauv lub cev txo qis thiab cov ntshav siab pib poob qis.
Cov tsos mob ntawm tus kab mob Addison yog dab tsi?
Cov tsos mob ntawm tus kab mob no maj mam tshwm sim, qeeb heev. Yog li ntawd, qee zaum nws yuav siv sijhawm los kuaj mob. Vim tias ntau cov tsos mob no zoo ib yam li lwm yam kab mob, nws yog ib qho tseem ceeb heev uas yuav tsum mus ntsib kws kho mob kom
paub tseeb.
| Cov tsos mob | Ib qho lus piav qhia yooj yim txog qhov xwm txheej |
|---|
| Kev qaug zog tas li thiab cov leeg tsis muaj zog | nkees heev thiab xav tias tsis muaj sia nyob txawm tias tsis tau ua dab tsi los xij. |
| Tsis qab los noj mov thiab poob phaus | Tsis qab los noj mov, ua rau poob phaus maj mam. |
| Kev ua kom daim tawv nqaij tsaus zuj zus (Hyperpigmentation) | Cov tawv nqaij xim av/dub ntawm cov cheeb tsam uas raug tshav ntuj thiab cov uas tsis raug tshav ntuj. Qhov kev hloov pauv no tuaj yeem pom tshwj xeeb tshaj yog ntawm lub hauv pliaj, hauv caug, lub luj tshib, cov qhov txhab, cov kab me me, thiab cov pos hniav. |
| Ntshav siab qis (Hypotension) | Ntshav siab qis. Qhov no tuaj yeem ua rau kiv taub hau thiab tsaus muag, tshwj xeeb tshaj yog thaum sawv ntsug. |
| Kev ntshaw ntsev ntau dhau | Thaum ntsev raug tshem tawm ntawm lub cev, muaj lub siab xav noj cov khoom noj ntsev tas li. |
| Lwm yam nta | Cov ntshav qab zib qis (Hypoglycemia), xeev siab, ntuav, mob plab, raws plab, tsis muaj peev xwm daws tau kev ntxhov siab, chim siab, qhuav dej, thiab mob pob qij txha. |
Tseem Ceeb: Cov tsos mob no kuj tuaj yeem tshwm sim los ntawm lwm yam kab mob. Yog li ntawd, yog tias koj muaj ib yam dab tsi zoo li no, nco ntsoov mus ntsib koj tus kws kho mob hauv tsev neeg kom tau txais lus qhia.
Dab tsi yog cov ua rau muaj tus kab mob Addison?
Qhov ua rau muaj qhov no yog
tus kab mob autoimmune . Hais yooj yim xwb, peb lub cev tiv thaiv kab mob (lub cev tiv thaiv kab mob) ua yuam kev tawm tsam thiab rhuav tshem peb cov qog adrenal. Qhov no yog qhov ua rau muaj li ntawm 70% ntawm cov neeg mob. Tsis tas li ntawd, tej zaum yuav muaj lwm yam ua rau.
- Kev kis kab mob: Kab mob ntsws ,Cov kab mob hnyav thiab ntev mus ntev, xws li HIV thiab qee cov kab mob fungal, tuaj yeem ua rau cov qog adrenal puas tsuaj.
- Mob qog noj ntshav: Cov qog noj ntshav los ntawm lwm qhov tuaj yeem kis mus rau cov qog adrenal (qhov no tsis tshua muaj).
- Kev los ntshav sab hauv: Kev los ntshav hauv cov qog adrenal.
- Cov yam ntxwv caj ces: Kuj tseem muaj kev pheej hmoo ntawm kev mob no vim muaj qee yam mob caj ces.
- Kev Phais Mob: Tej yam zoo li kev phais mob kom tshem tawm cov qog adrenal.
Tus kws kho mob kuaj mob li cas?
Thaum koj mus ntsib kws kho mob, nws yuav mloog koj cov tsos mob kom zoo thiab kuaj koj lub cev, tshwj xeeb tshaj yog nrhiav seb puas muaj cov xim tsaus ntawm koj daim tawv nqaij thiab cov pos hniav. Tom qab ntawd, lawv yuav ua ntau qhov kev kuaj mob kom paub tseeb tias koj tau kuaj mob.
- Kev kuaj ntshav: Cov no kuaj xyuas cov sodium (ntsev), potassium, thiab cortisol hormones hauv lub cev. Hauv tus kab mob Addison, cov sodium tej zaum yuav qis thiab cov potassium tej zaum yuav siab.
- Kev kuaj mob ACTH: Qhov no yog qhov kev kuaj tseem ceeb uas siv los kuaj mob. Hauv qhov kev kuaj no, ib hom tshuaj hormones hu ua ACTH, uas raug tso tawm los ntawm lub hlwb, raug muab ua ib qho kev txhaj tshuaj, thiab tom qab ntawd ntsuas qib cortisol hauv cov ntshav. Hauv ib tus neeg noj qab haus huv, qib cortisol siab. Txawm li cas los xij, rau ib tus neeg uas muaj kab mob Addison, cov qog adrenal tsis ua haujlwm, yog li qib cortisol tseem qis.
- Lwm yam kev kuaj mob: Qee zaum yuav muaj kev kuaj CT scan los xyuas seb puas muaj kev kis kab mob, mob qog noj ntshav, lossis los ntshav hauv cov qog adrenal.
Kev kho mob thiab kev tswj hwm
Kab mob Addison yog ib qho tsis muaj cov tshuaj hormones hauv lub cev, thiab kev kho mob yog muab cov tshuaj hormones uas tsis txaus rau sab nraud. Qhov no yog ib yam dab tsi uas yuav tsum tau ua thoob plaws lub neej.
- Cov ntsiav tshuaj Hydrocortisone: Cov no yuav tsum tau noj txhua hnub los hloov cov tshuaj cortisol.
- Cov ntsiav tshuaj Fludrocortisone: Cov no yuav tsum tau noj txhua hnub los hloov cov tshuaj hormone aldosterone.
Qhov tseem ceeb tshaj plaws yog noj cov tshuaj uas koj tus kws kho mob tau sau tseg, raws sijhawm, thiab tsis txhob ncua ib hnub. Txawm tias tsis noj ib zaug xwb los yeej txaus ntshai.
Yog tias koj muaj kev ntxhov siab, xws li muaj kev kis kab mob, phais mob, lossis muaj xwm txheej, koj cov tshuaj no yuav tsum tau nce ntxiv. Koj tus kws kho mob yuav qhia koj txog qhov no.
Qhov teeb meem txaus ntshai tshaj plaws: Addisonian Crisis
Qhov no yog
qhov xwm txheej ceev tshaj plaws thiab txaus ntshai tshaj plaws uas tuaj yeem tshwm sim hauv Addison's kab mob.Thaum lub cev muaj kev ntxhov siab heev (piv txwv li, muaj kev kis kab mob hnyav, muaj xwm txheej, phais), lub cev tsis muaj peev xwm tiv taus vim muaj cov tshuaj hormones tsawg. Cov tsos mob ces mam li loj zuj zus.
Cov tsos mob ntawm Addisonian crisis:- Mob sai sai , mob hnyav rau sab nraub qaum, plab, lossis ob txhais ceg
- ntuav thiab raws plab hnyav heev, ua rau lub cev qhuav dej
- Kev poob siab los ntawm kev ntshav siab qis heev
- Kev poob siab
- Kub taub hau thiab tsis muaj zog
Yog tias muaj cov tsos mob no tshwm sim, nws yog xwm txheej ceev hauv kev kho mob. Yuav tsum coj tus neeg mob mus rau Chav Kho Mob Ceev (ETU) ze tshaj plaws tam sim ntawd. Cov Lus Qhia Txog Kev Coj Mus Tsev
- Txawm hais tias tus kab mob Addison yog ib yam mob uas yuav kho tau mus ib txhis, yog tias kho tau zoo, ces yuav ua tau lub neej zoo li qub thiab noj qab nyob zoo .
- Tsis txhob tso tseg cov tsos mob xws li qaug zog tas li, tawv nqaij dub, tsis xav noj mov, thiab poob phaus. Tham nrog koj tus kws kho mob txog qhov no.
- Tsis txhob nco ib koob tshuaj uas koj tus kws kho mob tau sau tseg. Khaws cov tshuaj ntxiv nrog koj ib txwm.
- Ib txwm hnav daim npav ID kho mob lossis lub kauj tes uas qhia tias koj muaj tus kab mob Addison. Nws tuaj yeem pab cawm koj txoj sia thaum muaj xwm txheej ceev.
- To taub tias qhov teeb meem Addisonian yog ib qho xwm txheej ceev hauv kev kho mob. Nws yog ib qho tseem ceeb rau koj thiab koj tsev neeg kom paub txog nws cov tsos mob.
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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus