Lu leh kawng hnunglam na fo... Hei hi Chiari Malformation a ni thei.

I lu hnunglam atanga tan a, i kawr hnuai lam pan thin natna mak tak i nei fo thin em? He natna hi a bik takin i khuh emaw, i thawk hah emaw, thil rit tak i chawi emaw hian a pung em? A châng chuan i lu a buai , i kal laiin i balance a hloh a, a nih loh leh i kut a hrual ṭhîn em? Hengte hi lu na pangngaiah i ngai a nih pawhin a chang chuan chhan thup dang a awm thei bawk. Chu chu chutiang dinhmun hmuh tur awm lo mahse pawimawh tak zinga mi a ni.

A awlsam zawngin Chiari Malformation chu eng nge ni?

Hei hi hming hi a buaithlak deuh a, mahse a awlsam zawngin i sawi ang u. Kan thluak hi kan lu ruh chhungah venhim a ni. He luruh hnuai lamah hian, kawr leh luruh inzawmna hmunah chiah hian kan ruhro (spinal cord) luhna tur khur a awm a. Hei hi damdawi lam tawng chuan ``foramen magnum'' an ti a.

Chiari malformation an tih dinhmunah chuan kan thluak hnuai lam, a bik takin cerebellum an tih chu foramen magnum kaltlangin, spinal cord awmna hmunah chuan a nawr emaw, a hrual emaw a ni. Hmun tenau zawka dah theih aia lian zawk dah tum ang maiin ngaihtuah ang che.

He compression hian thluak leh ruhro vel a kal kual thin cerebrospinal fluid (CSF) kal dan a tibuai a ni. Hei hi tui pipe block ang mai a ni. Hei hian thluak leh ruhro hmun thenkhatah pressure a siam a, symptom hrang hrang a thlen thin.

Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?

A tam zawkah chuan Chiari malformation hi pianpui natna a ni . Chumi awmzia chu naute chu nausen pum chhunga a lo seilian laiin thluak leh luruh hmasawnna lama chhiatna a awm vang a ni tihna a ni. Hei hi a chhan chu mi thenkhat chuan luruh chhungah hmun pangngai aia tlem zawk posterior fossa an tih vang a ni a, chu chu thluak awmna hmun a ni. Mahse zirchiangtute chuan engvangin nge hetiang thil hi a thlen tih erawh an la chiang lo.

A chang chuan hei hi genetic cause vang pawh a ni thei.

A tlem berah chuan he dinhmun hi pian hnuah, chu chu puitlin hunah a thleng thei a ni . A chhan chu:

• Thluak natna (brain tumor) a ni.
• Lu hliam hian thluaka tuiin a khat sac (cyst) emaw thisen zam (hematoma) emaw a thlen thei a ni.
• ``Hydrocephalus'' an tih, thluaka tui awmkhawmna a ni.
• Spinal cord nena inzawm natna dang tethered cord syndrome te pawh a awm thei.

Hetiang dinhmun hi chi hrang hrang a awm em?

Ni e, he natna hi a nasat dan leh thluak hmun thenkhat a nghawng nasat dan azirin chi hrang hrangah then a ni.

Type I natna lan chhuahna langsar ber berte chu engte nge ni?

Type I vei zawng zawng hian symptoms an nei vek dawn lo. Mahse, symptoms a awm tak tak a nih chuan, a then chu:

• Occipital lu na leh kawng na:Hei hi a symptom ber leh langsar ber a ni. Khuh, thawk hah emaw, thil rit tak tak chawi emaw hian a na zual thin.
• Dizziness and Balance Problems: Luak hahna, i kal laiin i muhil dawn ang maia luak chhuak.
• Muscle chak lohna.
• Kut leh kea rilru hahna emaw thil dang danglam tak emaw .
• Mit lama harsatna: mit hmuhna (blurred vision), mit hmuhna pahnih (double vision).
• Swallowing harsatna.
• Beng chhunga ri (tinnitus) leh hriatna lama harsatna nei.
• Mut harsatna: Mut theih lohna, emaw, mut laiin thawk rei lo (sleep apnea).
• Nausea leh luak chhuak.

Engtin nge hei hi i hmuh theih, Doctor?

I natna lan chhuah dan i sawi zawh chuan i doctor chuan uluk takin a enfiah hmasa ang che, a bik takin neurological exam . Hei hian i balance, muscle chakna, reflexes leh sensation te a check ang.

Tichuan, he dinhmun chungchangah hian rinhlelhna a awm chuan test engemaw zat nei turin an refer ang che a, chu chu finfiah turin an refer ang che.

• MRI (Magnetic Resonance Imaging) Scan: Hei hi Chiari malformation hriat theihna atana test tha ber leh pawimawh ber a ni. MRI hian thluak leh ruhro insiam dan chu chiang takin a hmu thei a. Thluak hi engzat nge a compress tih leh `CSF` fluid luang chhuak a tikhawlo em tih chiang takin a hmu thei a ni.
• Cine MRI: Hei hi MRI chi khat bik a ni. Video ang mai a ni. CSF chu thluaka a kal kual vel chu real-time-in i hmu thei a, chu chu live-in i hmu thei a ni.
• CT (Computed Tomography) Scan: Hei hian luruh ruh chhunga thil dik lo awm leh awm loh a enfiah thei a ni.

Enkawlnate chu engte nge ni?

Enkawlna chu i neih chi hrang hrang, i natna lanchhuahna nasat dan leh i nitin nun a nghawng danah a innghat a ni.

1. No Symptoms: Type I i vei a, symptoms i neih loh chuan, emaw, an tibuai lo che a nih chuan enkawlna engmah i mamawh lo mai thei . I doctor chuan i dinhmun enfiah turin regular check-up nei turin a rawn lut ang che.

2. Damdawi: 1.1.Lu na leh kawng na ang chi symptom i neih chuan i doctor chuan a control theih nan painkiller (NSAID) leh muscle relaxant a pe thei che a ni.

3. Surgery: Damdawi hmanga thunun theih loh symptom na tak tak i neih chuan, emaw, scan-a thluak emaw, ruhro emaw a chhiat a nih chuan doctor chuan zai a rawt thei ang.

Surgery tum ber pahnih chu:

• Thluak leh ruhro (spinal cord) a pressure tihziaawmna.
• CSF fluid kal dan tur siam that leh.

Surgery tih tam ber chu Posterior Fossa Decompression Surgery a ni . Chutah chuan surgeon chuan ruh bul atanga ruh te tak te a la chhuak a, chutah chuan a kawr nen a inhmu a ni. Hei hian thluak leh ruhro tan hmun a siam tam zawk a ni. Thluak (dura) vel membrane pawh hawn a ni a, a hmunah patch an sewn bawk. Hei hian cerebrospinal fluid (CSF) chu zalen takin a luang thei a ni.

Hydrocephalus (thluak-a tui awm) i vei bawk a nih chuan, a tui tam zawk paih chhuah nan shunt dah a ngai mai thei.