PPMS (Primary Progressive Multiple Sclerosis) hi eng nge ni? I symptoms te chu zawi zawiin a zual zel a nih chuan i hriat tur

A châng chuan kea kal harsa i nei em, i ke ruhte a ti na a, a nih loh leh chhan awm lovin i chau reng em? Heng symptoms te hi a intan thut lo va, hun kal zelah zawi zawiin a pung zel ang tih pawh i hria em? Tichuan, vawiin a kan sawi tum PPMS an tih hi i hriat chian a pawimawh hle. Hei hi thupui buaithlak deuh mahse, awlsam takin, in hriatthiam theih angin kan sawi dawn a ni.

PPMS hi eng nge ni mai?

Okay, a hmasain PPMS chu eng nge a nih kan en ang. PPMS tih thumal hi `Primary Progressive Multiple Sclerosis` tihna a ni. Hei hi natna chi khat `Multiple Sclerosis` ( MS ) a ni.

A awlsam zawngin, Multiple Sclerosis (MS) hi kan taksa immune system , natna laka min humhimtu system chuan kan nervous system ngei pawh a rawn bei sual a ni. Hei hian thluak, ruhro leh taksa peng dangte inkara thu kal dan a tibuai a ni.

Tunah chuan MS chi hnih a awm tawh a.

1. Relapsing-Remitting MS (RRMS): Hei hi natna lan chhuah dan a lo zual thut (hei hi `relapse` kan ti) a, chutah chuan hun engemaw chen hnuah a natna a lo tha leh emaw, a bo vek emaw (`remission`) a ni. Ruah sur ang mai a ni a, a rawn on nghal a, a tla thla a, a rawn on leh leh ta a ni.

2. Primary Progressive MS (PPMS): Tunlaia kan sawi chi hrang hrang PPMS hi a danglam hle. Hetah hian symptoms hi a lo chhuak nghal lo va, a reh leh ta lo. Chu ai chuan hun kal zelah symptoms chu a zual zauh zauh thin. Drizzle ang maiin a hnim deuh a, chutah chuan a hnim tak zet a ni. A châng chuan, symptoms a flare thei a, mahse chu chu a tlem hle.

MS vei zinga 10% vel chuan he MS chi hi an nei a, chu chu PPMS an ti a ni.

PPMS natna lan chhuahna berte chu engte nge ni?

PPMS-ah chuan a tir lamah chuan a symptoms hi a langsar vak lo mai thei. Mahse hun kal zelah an na zual sauh sauh a. Heng symptoms te hi mi hrang hrangah a inang lo thei. I natna lan chhuahna bulpui ber berte chu han thlir ila.

Engvangin nge PPMS hi a lo awm? A chhan chu eng nge ni?

Dik tak chuan MS emaw PPMS emaw awm chhan dik tak hi hriat chian a la ni lo a, mahse zirchiangtute chuan thil hrang hrang inzawmkhawm niin an ngai.

• Genetic predisposition: I chhungkuaa mi pakhatin MS a vei chuan nang pawhin i vei theihna chance tlem i nei a ni. Mahse hei hi risk tlem tak a ni. Chumi awmzia chu nu leh pate’n an neih vang mai maia naupangte’n an neih a rinawm loh tihna a ni.
• Environment factors: Virus thenkhat emaw bacteria infection emaw nena inzawmna hian MS lo awm danah nghawng engemaw zat a nei niin an ngai bawk.
• Immune system activation: Kan sawi tawh ang khan hetah hian thil thleng chu kan immune system ngei hian kan nerve cells chhehvela protective covering (`myelin sheath`) chu a tichhia a ni He chhiatna hian nerve kaltlangin thuchah inthlunzawmna a tibuai a ni.

Engtin nge PPMS hi hmuhchhuah a nih?

PPMS finfiah thei tur test pakhat mah a awm lo. Doctor chuan i natna lan chhuah dan te, i damdawi lam chanchin te, leh test engemaw zat result te uluk taka enfiahin natna hi a hriat theih nan a hmang thin. Chumi awmzia chu hun engemaw chen la ngai process a ni tihna a ni.

Test tih thin thenkhat chu hetiang hi a ni.

PPMS hi kum 40 leh 50 inkar vel a ni tlangpui a, mahse kum eng pawhah a awm thei.

PPMS enkawl dan tur chu engte nge ni?

PPMS hi damdawi a la awm lo. Mahse, natna zual zel tur tikhawtlai thei leh a natna lan chhuah dan enkawl a nun awlsam zawk thei enkawlna a awm.

Enkawlna hi chi hnih ah then theih a ni:

1. Natna tidanglam thei damdawi (DMTs) .

Heng damdawi te hian natna avanga nerve chhiatna tihziaawmna leh natna zual zelna rate tihziaawmna hmangin hna an thawk a ni. PPMS atana DMT pawmpui ber pakhat chu ocrelizumab (Ocrevus®) a ni. He damdawi hian natna lan chhuahna rate a control thei a, eng emaw chen chu.

2. Symptoms enkawl dan tur

Hei hi a pawimawh hle. Nitin nun tichhe thei symptoms control nan enkawlna hrang hrang hman a ni.

• Physiotherapy : Exercise leh enkawlna dangte hian taksa ruh nghet lo, chak lohna leh balance lama harsatna awmte a tiziaawm thei a ni.
• Occupational Therapy: Nitin hna (e.g., incheina, chaw siam) awlsam zawka siam dan leh hmanrua te a zirtir thin.
• Damdawi: I doctor chuan i natna lan chhuah dan tur damdawi chi hrang hrang a pe thei a, chu chu zun control lama harsatna, natna, hahna, leh lungngaihna te hi a ni .

I doctor chuan i tana tha tur treatment plan a siam ang. Enkawlna eng pawh i tan hmain i doctor nen a nghawng tha lo awm thei te chu sawipui hmasa phawt ang che.

PPMS nena kan awm hian eng nge beisei tur?

PPMS hi i nitin nunah nghawng lian tak a nei thei a ni. Symptoms a zual zel chuan i himna tur leh accident laka inven nan inthlak danglamna engemaw zat i siam a ngai mai thei.

Entîr nân, kea kal harsatna i neih hunah kea kal emaw, wheelchair emaw i hman a ngai mai thei. Hengte hi hman hi hnehna a ni lo tih hre reng la, i zalenna vawng reng tur leh i tih tur i tih theihna tura puitu che a ni tih hre reng ang che.

Hetiang natna khirh tak nena nun hian taksa leh rilru lamah pawh nghawng a nei thei che a ni. Lungngaihna leh lungkhamna awm hi thil pangngai a ni. Hetiang hunah hian rilru lam hriselna lama thurawn petu nena inbiakna leh i rintlak mi pakhat hnena i rilru put hmang sawi chu hahdamna nasa tak a ni thei.

PPMS hian dam chhung hi direct-in a nghawng lo a, mahse natna avanga harsatna awm chuan nunphung a nghawng thei a ni.

Engtikah nge Doctor ka hmuh ang?

PPMS i neih chuan doctor nen inbiak reng a pawimawh. Damdawi lam thurawn zawng la, a bik takin:

• I symptoms a nasat lutuk a, nitin hnathawhna a nghawng a nih chuan.
• Paralysis, ke ruh chhunga natna awm reng emaw, rilru hahna emaw a awm chuan.
• Balance hloh vanga i tlu a, i hliam a nih chuan ETU (Emergency Treatment Unit) ah kal nghal rawh.
• Enkawlna avanga side effects a nasat chuan.

I doctor zawh tur zawhna

• PPMS emaw MS chi dang emaw ka nei em?
• Engtin nge ka symptoms te hi ka enkawl theih ang?
• Physics therapy nge occupational therapy hmanga enkawlna ka mamawh em?
• Damdawi i rawt te hian eng side effect nge a neih?
• Wheelchair ang maia mobility aid ka mamawh dawn em?