I pum emaw, i hnungzang hnuai lam emaw-ah natna mak tak, chiang lo tak i nei tawh em? Heart attack emaw, hnungzang hliam tenau emaw niin kan ngai mai thei. Mahse, vawiin hian kan sawi dawn a, natna lan chhuah dan inang lo tak tak, a tlem deuh a, mahse kan zavaia kan hriat chian a pawimawh hle. Hei hi retroperitoneal fibrosis an ti a. Ormond natna an ti bawk.
Retroperitoneal Fibrosis hi eng nge ni? A awlsam zawngin...
A awlsam zawngin sawi ila, retroperitoneal fibrosis chu
kan pum hnung lama hmun, retroperitoneum an tih hmuna taksa peng hrang hrangte chhehvela scar ang chi tissue (fibrosis) lo awm hi a ni. Kan vunah hliam a lo awm ang mai a ni a, mahse kan taksa chhungah a thleng thin. Progressive condition a nih avangin natna leh zun chhuah tlahniam ang chi symptoms te hi hun kal zelah a na zual thei hle.
Okay, chuti a nih chuan he retroperitoneum hi eng nge ni?
Kan pum chhunga taksa peng tam tak (liver, stomach, intestines ang chi) hi peritoneum an tih, venhimna membrane-in a hual vel a ni.
He peritoneum hnung lama, ruhro lam hawia hmun hi retroperitoneum an ti a. He hmun hi kan:
- Kidney a ni
- Urinary system hmun thenkhat
- Thisen kalna kawng lian tak tak, ke atanga thisen phur leh chhuak (entir nan, inferior vena cava) .
- Chutah chuan taksa peng pawimawh tak tak, adrenal glands te chu a awm a.
Engtin nge hei hian kan taksa a nghawng?
Sawi tawh ang khan fibrosis emaw, scar tissue emaw chu a lo pung zauh zauh a, retroperitoneum chhunga taksa peng leh thil dangte a nghawng a ni.
A tam zawkah chuan hei hian ureters, kan kidney atanga bladder thlenga zun phurtu tube te a nghawng ber a ni. Chu tissue thuk tak chu heng tube chhehvelah hian a lo awm a, a tight chuan eng nge thleng ang tih han ngaihtuah teh? Tui pipe hrual ang mai a ni a, zun kalna tur a tikhawlo. Hetiang dinhmun hi a nasat chuan
nunna atana hlauhawm, kal (kidney failure) ang chi harsatna a awm thei a ni.
Tute nge retroperitoneal fibrosis vei tam zawk?
Hetiang dinhmun
hi mipa kum 40 leh 60 inkar zingah a tam ber a, hei hian mipa kum chanve vel chu a hlauhawmna a sang deuh tihna a ni. Chu bakah, risk factor dang engemaw zat a awm bawk:
Eng thilin nge hei hi a thlen? Ormond natna thlentu te
A tam zawkah chuan
hei hi a chhan chiang tak hmuh a harsa thin. Damdawi lamah chuan
idiopathic kan ti a. Chu chu "a chhan hriat loh" tihna a ni. Mahse, natna dang complication angin a lo awm fo thin. A chhan thenkhat chu:
- Damdawi thenkhat (hei hi tlem kan sawi leh ang).
- Cancer chi hrang hrang , a bik takin Hodgkin lymphoma leh non-Hodgkin lymphoma te.
- Infection awm dan tur.
- Cancer ang chi thilte tan radiation therapy hmanga enkawl a ni.
- Chu hmuna tissue te chhiatna, operation vang emaw, accident dang vang emaw pawh nise.
Eng damdawi chi hrang hrangin nge hetiang hi a thlen theih?
Damdawi thenkhat chu rei tak hman a nih chuan he natna hi a awm thei tih hmuhchhuah a ni. Entirna tlemte chu hetiang hi a ni:
- Beta- blockers hi lung natna enkawlna atana hman thin damdawi chi khat a ni . Entirnan, propranolol, metoprolol, leh atenolol te hi a ni.
- Dopamine antagonists hi rilru lam natna leh rilru hahna enkawlna atana hman thin damdawi a ni. Entirnan: methyldopa, pergolide tih te hi a ni.
- Hydralazine tablet hi thisen sang tan a ni.
- Damdawi ergotamine ang chi, migraine natna atana hman thin.
- Painkiller thenkhat, a bik takin analgesic leh NSAIDs te .
Pawimawh: Hetiang damdawi hi i hmang a nih chuan hlauthawng suh. Hetiang dinhmun hi mi zawng zawngin an tawng vek dawn lo. Mahse hei hi hriat chian a pawimawh a, i doctor nen pawh hemi chungchang hi sawipui a pawimawh.
Hei hi eng symptoms nge ni?
Mi tin hian natna lan chhuah dan a inang lo thei. Fibrosis awmna hmun leh a nasat danah a innghat.
A tir lamah chuan i pum, i hnungzang hnuai lam emaw, i flanks-ah emaw natna i nei thei. He natna hi a fiah lo thei a, chu chu "hetah leh khawiah pawh" pinpoint a harsa tihna a ni a, general ache a ni thei bawk. A lan chhuah dan dangte chu:
- I ke sawn leh che vel chu a harsa khawp mai.
- Hydrocele: Hei hi mipa testicles a lo hring chhuak thin a ni.
- Ke a hring, ke a na emaw, ke a vun rawng a inthlak emaw.
- Zun chhuah a tlahniam.
Ormond natna avanga harsatna awm thei te chu engte nge ni?
Retroperitoneal fibrosis a lo zual a, chu chu scar tissue a pung a, taksa peng hrang hrangte a compress tan tihna a nih chuan harsatna
hrang hrang a thleng thei a ni. Chung zinga ṭhenkhat chu:
- Anemia: Hei hian taksaa thisen sen (red blood cells) a tlahniam tihna a ni a, a nih loh leh "thisen tlakchhamna" mai mai a ni.
- Anuria: Hei hi zun a kal loh tak takna a ni. Hei hi emergency a ni.
- Taksa a itchy.
- Jaundice: Mit leh vun a sen.
- Nausea leh luak chhuak.
- Neurologic lama harsatna awm thei.
- Intestinal tissue thihna (necrosis) a awm.
- Rihna tihtlem.
Engtin nge retroperitoneal fibrosis hi an hriat theih?
Heng symptoms te hi i neih chuan doctor rawn la, an enfiah ang che. Hei hian a huam thei ang:
- Taksa enfiah: Doctor chuan i pum chu a hriat ang a, thil dik lo awm leh awm loh a enfiah ang a, chu chu lumps ang chi hi a ni.
- Thisen test: Hengte hian kal natna chhinchhiahna hmasa ber leh harsatna awm thei, thisen tlakchhamna (anemia) te a hmuchhuak thei a ni.
- Renal (kidney) ultrasound: A lan chhuah danin kal lama harsatna a awm tih a hriat chuan he test hian fibrosis leh harsatna dangte a zirchiang thei a ni.
- CT scan: Hei hian fibrosis nasat dan a teh thei. Tin, natna dang, groin-a lymph node hring emaw, tumor dang emaw pawh a awm loh nan a pui thei bawk.
Biopsy neih a ngai em?
A tam zawkah chuan retroperitoneal fibrosis hi thisen test leh a chunga kan sawi tak imaging test (ultrasound, CT scan) hmangin hriat theih a ni. Mahse, thil bik ṭhenkhatah chuan
, biopsy lak a ngai mai thei. Hei hian tissue chi khat la a, microscope hmanga enfiah tihna a ni. Chutiang case-ah chuan:
- Cancer emaw infection emaw rinhlelhna a awm chuan.
- A tir lama enkawlna a hlawhtlin loh chuan.
Eng ang enkawlna nge ka mamawh?
I tana enkawlna tha ber chu fibrosis awmna hmun leh a nasat danah a innghat ang. Ormond natna hmasa berah chuan i enkawlnaah hian:
- Corticosteroids te hi a hnuaia mi ang hian a ni.Heng damdawi te hian taksaa inflammation a tihziaawm thuai a, fibrosis lo awm tur pawh a titawp bawk.
- Immunomodulators: Heng damdawi te hian immune system hnathawh dan thlak danglamin hna an thawk a ni. Hei hian nakin lawkah fibrosis lo awm leh theihna a ti tlem thei a ni. Mahse, immunomodulators hian thla engemaw zat a daih theih avangin corticosteroids nen hian pek theih a ni.
- Damdawi enkawl dan: A chang chuan fibrosis hi damdawi i ei avanga lo awm a nih chuan i doctor chuan damdawi chu a thlak danglam thei a, a dose a ti tlem thei bawk.
Fibrosis a lo zual tawh chuan enkawlna dang a ngai mai thei:
- Surgery: Fibrotic tissue lakchhuah nan leh a chhehvela tissue chhiatna awm apiang siamthat nan operation neih a ngai mai thei.
- Stents: A hmaa kan sawi tawh ang khan ureter a block a nih chuan a chhungah hian tube ang chi device te tak te (stent) dahin a inhawng reng thei a ni.
Engtin nge retroperitoneal fibrosis lo awm tur hi kan ven theih ang?
Hetiang dinhmun hi idiopathic a nih fo avangin
ven kim a harsa hle. Mahse, damdawi ṭhenkhatin a thlen tih hriat a nih avangin i doctor chuan fibrosis symptoms i neih leh neih loh a enfiah mai thei che a, a bik takin hun rei tak i ei a nih chuan.
Enkawl hnuah hetiang thil thleng leh theihna hi a tlahniam thei ang em?
Surgery neih a ngai a nih chuan a chang chuan surgery neih chhung hian ureter chhungah thau tissue layer khat a inkhuh thin. Hei hian fibrosis lo awm leh a harsat phah niin an sawi.
Engtiang chiahin nge ka dam leh thuai ang?
Corticosteroids ang chi damdawi i ei a nih chuan, emaw, damdawi enkawl hnuah
, kar tlemte hnuah i dam leh tan mai thei. Mahse, immunomodulators, stent emaw, surgery emaw i mamawh chuan a dam leh theih nan hun rei vak lo a la ngai dawn a ni.
Retroperitoneal fibrosis vei te tan engtin nge an hmalam hun?
Mi tam zawk chuan damna famkim an nei thin. Hlawhtling taka enkawl theihna chance tha ber chu
natna hi a hmaa hriatchhuah a nih chuan a ni. Mahse, fibrosis hi enkawl a nih atanga thla emaw kum emaw hnuah a lo lang leh thei tih hriat reng a pawimawh.
Ormond natna nena nun chu eng ang nge ni?
Mild case nei tan chuan
doctor enkawlna hnuaia awm chhunzawm zel a ngai dawn a ni. Hei hian natna lo kir lehna chhinchhiahna enfiah turin doctor i pan fo a ngai dawn tihna a ni.
Urinary tract obstruction siamthat nan operation hnuah eng nge thleng?
Hydronephrosis hi operation hnu ni engemaw zat chhunga doctor-te’n i kal (kidney)-a zun awm tawh chu an chhuah nghal mai chuan a lo awm thei a ni."Urinary retention" an tih complication hi hre reng ang che. Taksa chhunga zun tang tawh chu a lo chhuah thut chuan a hnuaia mi ang hian a thleng thei a ni.
- Taksa chhunga electrolyte inthlauhna.
- Tui tlakchhamna (dehydration).
- Hypovolemic shock (thisen volume tlahniam avanga lo awm).
Retroperitoneal fibrosis, Ormond’s disease hi kan pum hnung lamah hliam ang chi tissue a lo awm thin a ni. Damdawi thenkhat ei thinte hian he natna hi an vei theihna a sang zawk. Hetiang natna hi i vei tih hmuhchhuah a nih chuan zawhna emaw, ngaihtuahna emaw i neih apiang chu i doctor nen sawiho rawh. I tanpui turin an awm reng a ni.
Thil pawimawh tak tak hriat reng tur (Take-Home Message) .
Okay, chuvangin tunah chuan Retroperitoneal Fibrosis chu eng nge a nih tih kan hrethiam tawh zawk.
Rare condition ni mahse, fimkhur a pawimawh hle.- Hei hi taksa chhunga awm tur taksa peng hrang hrang vel, ruhro lam hawia lo awm, tissue thicked tak a ni tih hre reng ang che.
- Ureter a nghawng fo a, kal a tichhia thei bawk.
- A chhan hi a chiang lo fo a, mahse damdawi thenkhat, cancer, leh natna hrik te ang chi te pawh hi a chhan a ni thei bawk.
- Vague abdominal/back pain leh zun chhuah tlem ang chi symptoms i neih chuan doctor advice lak a pawimawh.
- A hmaa hmuhchhuah a nih chuan enkawlna tha tak tak a awm. Chuvangin a symptoms te hi ngaihthah suh.
- Hemi chungchanga zawhna i neih chuan i doctor zawh hreh suh.
He thu hi i tan a \angkai ngei kan beisei. Hrisel takin awm rawh!
Retroperitoneal Fibrosis, Ormond natna, kal natna, pum na, zun lama harsatna, fibrosis, surgery
💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh