I ke ruh zungbun atanga intan natna te tak te chu i taksa pum puiah zawi zawiin a darh thei a, i ke ruhte chu a ti na thei a, i ke ruh chu a tichak lo thei hial ang tih i ngaihtuah thei em? Thu hlauhawm tak a ni. Mahse hei hi neurological disorder hmuh tur awm lo tak
Guillain-Barré Syndrome (GBS) tih tak takna a ni. I pum chhunga natna hrik (jaundice ang chi) emaw thawkna lama natna (
khawsik ang chi) atanga i dam leh hnuah a lo awm fo thin.
A awlsam zawngin, Guillain-Barré syndrome (GBS) hi eng nge ni?
A awlsam zawngin sawi ila, GBS chu kan taksa invenna system,
immune system , chuan kan nerve te chu a rawn bei nghal mai a ni. Kan sipaite ngeiin kan mite an rawn beih palh ang mai a ni. Kan nerve te hi electrical wire ang maiin han ngaihtuah teh. Heng wire vel hi insulation atan plastic sheath a awm a ni lawm ni? Chutiang bawkin kan nerve pawh hi
myelin tih hming puin a hual vel a ni. GBS a lo awm chuan kan immune system chuan chu myelin sheath chu a bei thin. He sheath hi a chhiat chuan thluak atanga message lo lut chu taksa ruh (muscles) ah a thleng tha lo. Chumi rah chhuah chu taksa ruh chak lohna, rilru hahna, leh a châng chuan paralysis vek a ni.
Hei hi natna hrik kai theih emaw, thlahtute atanga lo chhuak emaw a ni lo. Mahse, emergency medical attention mamawhna dinhmun a ni . Chuvang chuan natna lanchhuahna hmasa ber a lo lan veleh damdawi lam pan vat a pawimawh hle.
GBS chi hrang hrangte chu engte nge ni?
GBS hi chi hrang hrang a awm a, mahse a chi khatna hi Sri Lanka-ah chuan a tam ber a ni.
| Natna chi hrang hrang | Specialty a ni |
|---|
| A rilru a hah lutuk chuan a rilru a buai em em a, a rilru a hah lutuk chuan a rilru a buai em em bawk a. AIDP . | Hei hi a tam ber chi a ni. Hetiang chi ah hian taksa chak lohna hi ke atanga intan a ni a, taksa pum puiah chunglam hawiin a darh thin. |
| Miller Fisher natna (MFS) natna a ni. | Hei hi Asia ramah chuan a awm fo thin. Mit tihchet harsat atanga tan hmasa ber a ni. Kea kal laiin balance hloh hi a symptom a ni bawk. |
| AMAN leh AMSAN chi hrang hrang | Hengte hi China leh Japan ang ramah a tam zawk. Symptoms hi chi dang aiin a na zawk thei. |
GBS vei chhan leh a hlauhawmna
GBS awm chhan dik tak erawh hriat a la ni lo. Mahse, doctor-te chuan natna hrik ṭhenkhatin kan nerve cell awm dan a tidanglam a, chu chuan immune system-in hmêlma anga a ngaih sual phah niin an ngai. GBS vei hmun thuma ṭhena hmun hnih vel chuan neurological symptoms a lo lan hma ni engemaw zat emaw, kar engemaw zat emaw chhungin pum natna, ril\am emaw, thawkna lam natna emaw, khawsik ang chi emaw an nei a ni.
GBS thlentu thil pawimawh thenkhat chu:- Campylobacter bacteria: He bacteria hi vawk tui lo hmanga kai a ni a, GBS thlentu ber nia ngaih a ni.
- Influenza virus a ni
- COVID -19 hri kai a ni
- Cytomegalovirus hmanga natna hrik pai a ni
- Epstein-Barr Virus atanga lo chhuak a ni
- Zika virus a ni
- Hepatitis A , B, C leh E te an ni
- HIV hrik pai a ni
- Surgery emaw accident emaw thenkhat
- A tlem berah chuan vaccine thenkhat (e.g. Johnson & Johnson leh AstraZeneca COVID-19 vaccine)
Hetiang natna vei zawng zawng hian GBS an vei vek dawn lo. Mi maktaduai khat zinga pakhat chauh hi hlauhawmah an awm.
Eng symptom nge i fimkhur tur?
GBS symptoms hi a lo lang nghal vat thei a, a chang chuan darkar tlemte emaw ni engemaw zat chhungin a na zual thei bawk.
| Symptom a ni | Hrilhfiahna |
|---|
| Numbness a awm | I ke ruh, ke ruh, kut zungtang leh kutphah-a rulhut rawn hrual ang maia tingling sensation. |
| Muscle chak lohna | Nunna nei lo hriatna, ke atanga intan a, zawi zawiin taksa chunglam thlenga darh thin. |
| Kal harsat | Ka kal laiin ka balance a hloh a, stairs chhoh pawh harsa ka ti hle. |
| Hmêl a inthlak danglam | Thusawi, chaw ei leh ei harsa a lo ni ta. Mit pahnihah thil pakhat emaw pahnih emaw i hmu thei (double vision). |
| Natna nasa tak a nei | Taksa taksa peng hrang hranga hliam, hliam na tak. He natna hi zan lamah a na zual thei hle. |
| Thil dang pawh a awm | Heart rate sang, thisen sang leh hniam, zun leh ek thunun theih loh, thawk harsa. |
Pawimawh tak: I damloh thut a, darkar tlemte chhunga a na zual a nih chuan, emaw, thawk emaw, ei emaw i harsat chuan damdawi in Emergency Department (ETU)-ah kal nghal rawh. Hei hi tihkhawtlai tur thil a ni lo.
He natna hi Doctor hian engtin nge a hriat chian?
GBS natna lan chhuah dan hi thluak lam natna dang nen a inang avangin doctor chuan natna dang a awm loh nan test eng emaw zat a kalpui ang.
- Zawhna zawh che: Engtin nge i natna lan chhuah dan leh engtikah nge a lo intan tih te, tun hnaia natna i neih leh neih loh zawh te.
- Nervous system test: Hei hian i taksa chakna, i kal dan, i balance leh i reflexes te a test thin.
- Spinal tap / Lumbar puncture: Hei hi i hnungzang hnuai lam ah needle te tak te tak te dahin i spinal cord vel a tui tlem te (cerebrospinal fluid) lak a, lab-ah test turin thawn a ni. He fluid-a protein level a san chuan GBS chhinchhiahna a ni.
- Neurological function test hrang hrang: 1.1.
- Electromyography (EMG): Hei hian nerve activity tehna atan muscle chhungah needle ang chi electrode tha tak tak dah a ni.
- Nerve conduction study: Hei hian vunah electrode dahin electrical current tlemte thawnin nerve impulse kal chak dan a teh a ni. He speed hi GBS ah chuan a slow a ni.
- MRI scan: I thluak emaw, i ruhro emaw MRI scan i nei thei bawk.
Enkawlnate chu engte nge ni?
GBS i vei tih hmuhchhuah a nih chuan enkawl tan nghal a ngai a ni. Hospital-a intensive care unit (ICU)-ah enkawl i ni fo ang. Enkawlna chi hnih a awm a, chungte chu: 1.
Plasma exchange / Plasmapheresis: I thisen chu machine bikah dah a ni a, i thisen liquid part (plasma) chu a inthen a. He plasma hian nerve tichhe thei antibody a pai a. Machine hian heng antibody tha lo te hi a paih chhuak a, thisen cell tha te chu i taksaah a dah leh thin. 2.
Immunoglobulin therapy: Mi hrisel hnen atanga antibody tha tak tak lak chhuah tam tak chu saline solution hmangin pek che a ni. Heng antibody tha te hian i taksa chhunga antibody tha lo te hnathawh a ti tlem a ni. Heng enkawlna lian ber berte bakah hian natna tidamtu, thisen tizautu damdawi te pek i ni ang a, a tul chuan tube hmangin chaw i ei theih loh avangin i chawm ang.
Thâwk harsatna a lo nasat chuan hun eng emaw chen chu ventilator-ah connect a ngai mai thei. I dam chhung hian physical therapy leh occupational therapy hmangin strength training i tih a ngai dawn a ni.
Dam lehna leh hmalam hun chu eng ang nge ni ang?
He natna hi a natna lan chhuah tirh atanga kar 2-3 hnuah a sang ber a thleng thin. Chumi hnuah chuan dam lehna chu zawi zawiin a intan thin.
- Damlo 80% vel chu thla 6 chhungin tanpuina awm lovin an kal thei a ni.
- Damlo 60% vel chuan kum khat chhungin taksa chakna zawng zawng an nei leh thei a ni.
- Recovery hian thla 6-12 inkar a awh thei a, thenkhat tan chuan kum 3 thleng a daih thei bawk.
GBS vei naupangte chu puitling aiin an dam chak zawk. GBS atanga i dam kim tawh chuan nun pangngai i hmang thei tawh ang.
Take-Home Thuchah a ni
- I ke atanga intan a, i taksa tizau thei chak lohna emaw i neih chuan ngaihthah suh.
- Heng symptoms te hi thawk harsa emaw, ei leh in emaw a awm chuan medical emergency a ni . Damdawi in pakhat Emergency Department (ETU) ah kal nghal rawh.
- GBS hi natna hmuh tur awm lo mahse na tak a ni thei. Mahse, enkawl tan hmasak a nih chuan mi tam zawk chuan an dam kim thei a ni.
- Hlauthawng suh. Heng symptoms te hi i neih chuan doctor pan vat la, thurawn la rawh.
Guillain-Barré Syndrome, GBS, neuropathy, ke ruh natna, ke ruh natna, taksa hriselna, myelin
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