Kua pāngia koe e ngā mamae rerekē, e te pupuhi rānei i ngā wāhanga rerekē o tō tinana, inā koa i ngā wāhi pēnei i ō taringa, i ō ihu rānei? Kāore pea ēnei e tupu noa iho. I tēnei rā, kei te kōrero tātou mō tētahi āhuatanga kāore i te tino kōrerohia engari he mea nui kia mōhiotia: Te Mate Pūkahukahu Hoki-Muri . Ahakoa he uaua te ahua o te ingoa, me wehewehe kia māmā noa iho.
He aha tēnei āhuatanga?
He whakarāpopototanga noa iho, he mate hauora onge te Relapsing Polychondritis e pā ana ki te kiriuhi o tō tinana. Kei roto ko te mumura (te pupuhi, te whero, me te mamae) i roto i te kiriuhi, ka arahi pea ki te hekenga haere , te ngoikore rānei o ēnei kiko i roto i te wā.
Tērā pea kei te whakaaro koe, he aha rawa te kiriuhi ? He kiko honohono motuhake te kiriuhi e kitea ana puta noa i tō tinana. Whakaarohia ngā wāhanga ngāwari engari pakari o ō taringa, o te pito rānei o tō ihu—arā, ko te kiriuhi. Kei roto hoki i ō hononga, i tō korokoro, me tō ara manawa (trachea).
Ko te Polychondritis e hoki whakamuri ana ka pā ki:
- Te kiriuhi i roto i ō taringa .
- Te kiriuhi i roto i tō ihu .
- Te arai (tō pouaka reo).
- Tō pūhā (te ara o te puku).
Ahakoa he ingoa hangarau anō tō tēnei mate pērā i te Chronic atrophic polychondritis , te Generalized or systemic chondromalacia , te Meyenburg-Altherr-Uehlinger syndrome , te Relapsing perichondritis , te Von Meyenburg disease rānei, ko te mea e mōhiotia whānuitia ana ko te Relapsing Polychondritis .
Ko wai ka pāngia e tēnei mate, ā, he pēhea te noa o tōna whanaketanga?
Ka pāngia te tangata katoa e tēnei mate, engari ko te nuinga ka tīmata i waenga i te 40 me te 60 tau te pakeke .
Mō tōna horapa, he tino onge tēnei mate . E ai ki ngā rangahau, tata ki te kotahi i roto i te 285,000 tāngata ka pāngia. Nā te mea he iti noa te wāhanga o te taupori e pāngia ana, kāore i te maha ngā kōrero mō tēnei mate i roto i te hapori whānui.
He aha i pēnei ai?
Ko tētahi pātai e tino pātaihia ana, "He aha tēnei i puta ai?" Ki te pono, kāore anō kia tautuhia e ngā kaipūtaiao te tino pūtake o te Relapsing Polychondritis.
Heoi, he maha ngā tohunga e whakarōpū ana i tēnei mate hei mate pūnaha ārai mate . Tērā pea ka whakaaro koe he aha te mate pūnaha ārai mate. I roto i ngā kupu ngāwari, he pūnaha ārai mate tō tinana e mahi ana pērā i te ope taua, e whawhai ana ki ngā iroriki hei pupuri i tō hauora. I roto i te mate pūnaha ārai mate, ka tīmata hē tēnei "ope" ki te whakaeke i ō ake pūtau me ō kiko hauora . Mō te Relapsing Polychondritis, ka aro te pūnaha ārai mate ki tō kiriuhi, ahakoa kāore anō kia mārama te pūtake o tēnei urupare.
He aha ngā tohu?
Ko te Polychondritis e hoki whakamuri ana, kāore e mau tonu; ka puta mai i roto i ngā wā, i ngā mura rānei . Kia puta mai ngā tohu, ka roa pea mō ētahi rā, wiki rānei i mua i te memeha haere, ā, ka hoki anō i ētahi wā i roto i ngā tau.
Ngā tohu tuatahi:
Ki te tini, ka tīmata te mate me te mamae, te ngawari, te pupuhi, me te whero i roto i te taringa kotahi, i ngā taringa e rua rānei. He mea nui, ahakoa e pā ana ēnei tohu ki te kiriuhi o roto, o waho hoki o te taringa, kāore te taringa e kitea i te nuinga o te wā. I ētahi wā, ka ngawari, ka piko ngā taringa, ka kiia ko ngā "taringa ngoikore". Hei tauira, ki te pāngia koe e te mamae me te whero ohorere i roto i te taringa kotahi, ā, ka memeha haere i muri i ētahi rā, ā, ka whai muri i tētahi atu taringa i muri i ētahi marama, he āhuatanga tēnei o tēnei mate.
Ētahi atu tohu:
- Te hinga o te kiriuhi ihu: Ka taea e tēnei te arahi ki te "ira ihu nohoanga," te wāhi e papatahi ai te piriti o te ihu, e rite ana ki te nohoanga hoiho.
- Mamae hononga : Tērā pea ka pāngia koe e ngā mamae e rite ana ki te mate rumatiki .
- Te pupuhi o te ihu .
- Te mamae o te uma e tata ana ki te wheua o te uma.
- Te mamae o ngā kanohi me te whero .
- Te pānga o te taringa o roto: Ka hua ake pea tēnei i te ngaronga o te rongo , te tangi o ngā taringa ( tinnitus ), te pororaru rānei (whatiwhati).
- Ngā uauatanga manawa: Ka puta tēnei mēnā ka pā te mate ki te trachea. Tērā pea ka pā te uauatanga kōrero mēnā ka pā te larynx.
He mea nui: Ki te uaua te manawa, he āhuatanga hauora nui tēnei. Tena koa whakapā atu ki ngā ratonga ohorere, haere rānei ki te hōhipera tata tonu atu.
Ngā tohu onge:
Ahakoa kāore i te tino kitea, ka pāngia pea ētahi tāngata e:
- Ngā raruraru o te takirere ngākau.
- E ngunguru ana te ngākau.
- Te ngaronga o te tirohanga.
- Mate whatukuhu.
Me pēhea te tautuhi i tōna mate?
Mena kei a koe ēnei tohu, me toro atu koe ki tētahi tohunga hauora. Kāore he whakamātautau kotahi, he whakamātautau tuturu mō te Relapsing Polychondritis; kāore he whakamātautau toto, he matawai rānei e taea te whakaū tonu me te tino pono 100%.
E whakapae ana ngā tākuta i tēnei mate mēnā e toru ngā tohu e pā ana ki a koe i te roanga o te wā, pērā i te mumura o te kiriuhi taringa, te mumura o te kiriuhi ihu, me te mamae o ngā hononga e puta tahi ana i te wā kotahi.
Hei āwhina i te tautuhi mate, ka tūtohu pea tō tākuta:
- He koiora o te kiriuhi taringa.
- Ngā whakamātautau toto hei whakakore i ētahi atu mate me te aroturuki i ngā tohu o te mumura.
He aha ngā maimoatanga?
Engari, kāore he rongoā tuturu mō te Relapsing Polychondritis. Kāore he maimoatanga i tēnei wā hei whakakore katoa i te mate.
Heoi, ehara tēnei i te kī kāore e taea te mahi i tetahi mea. Ko ngā whāinga matua o te maimoatanga ko:
- Whakahaerehia ngā tohu (whakaitihia te mamae me te pupuhi).
- Whakaitihia te mōrearea o ngā raruraru.
Ko te tikanga ka tīmata te maimoatanga me ngā rongoā pēnei i:
- Colchicine: He maha ngā wā e whakamahia ana hei rongoā mō te kauti.
- Corticosteroids: Hei tauira, ko te Prednisone , he rongoā kaha e whakamahia ana hei whakaiti i te mumura.
- Dapsone: He rongoā e whakamahia ana i ētahi wā hei whawhai i te mumura.
- Ngā rongoā anti-inflammatory kore-steroidal (NSAID): Ka āwhina ēnei ki te whakahaere i te mamae me te whakaiti i te pupuhi.
Mena he kino rawa atu tō āhua, ka tohua pea e tō tākuta:
- Ngā rongoā ārai mate: Pērā i te Cyclophosphamide , i te Azathioprine rānei. Ka mahi ēnei mā te pehi i te pūnaha ārai mate e kaha rawa ana te mahi.
- Methotrexate: He rongoā ārai mate e whakamahia ana mō ngā āhuatanga pēnei i te mate rumatiki.
I roto i ngā take tino kino, ka hiahiatia pea te wawaotanga pokanga:
- Pokanga takirere ngākau: Mena kua pakaru ngā takirere ngākau.
- Tracheostomy: Mena he nui te aukati o tō ara manawa, me whakatuwhera tika te kaki hei āwhina i te manawa.
- Ngā tikanga whakahaere ara hau:
- Te whakatakotoranga o te stent: Ka whakauruhia he ngongo iti (te stent laryngeal, te stent tracheal rānei) hei pupuri i te ara manawa kia tuwhera tonu.
- Te whakawhanui i te ara manawa: Te whakamahi i tētahi taputapu rite ki te poihau hei whakawhanui i ngā ara manawa kua kuiti.
- He pokanga hei hanga anō i te trachea, i te larynx rānei.
Ka taea te ārai i tēnei āhuatanga?
Nā te mea kāore anō kia mōhiotia te tino pūtake o te Relapsing Polychondritis , he uaua ki te tūtohu i ngā rautaki ārai motuhake. I tēnei wā, kāore he huarahi motuhake hei ārai i te tīmatanga o tēnei mate.
He mate whakamate tēnei āhuatanga, ā, he aha te tirohanga whakamua?
Ahakoa te ahua taumaha o tēnei tātaritanga, kia mōhio koe he pai te roanga o te oranga mō te hunga e pāngia ana e te Relapsing Polychondritis. E whakaatu ana ngā rangahau e tata ana ki te 95% o ngā tūroro e ora tonu ana i ngā tau e waru i muri i te tātaritanga.
Heoi anō, ka taea e ia te arahi ki ngā raruraru e morearea ana ki te ora, inā koa ko te uaua o te manawa. Tērā anō hoki te mōrearea o te rongo tuturu, te ngaronga rānei o te tirohanga. Nō reira, he mea nui kia tūpato ki ngā tohu me te piri tonu ki tāu mahere maimoatanga.
He āhuatanga tēnei mō te wā katoa?
He mate mau tonu te Polychondritis e hoki whakamuri ana. Ko te tikanga, ehara i te mea ka memeha noa iho; he tukanga whakahaere mō te wā katoa.
Heoi, mā te maimoatanga tika, ka taea e koe te whakaiti i te auau me te kaha o ngā putanga mai o te mate. He mea nui kia mahi tahi koe me tō rōpū hauora ki te whakawhanake i tētahi mahere tiaki whaiaro.
He aha taku e pātai atu ai ki taku tākuta?
Mena kua tāpaetia koe kei te pāngia e te Relapsing Polychondritis, anei ētahi pātai hei pātai atu māu ki tō tākuta:
- "E pēhea ana te kino o tōku āhua i tēnei wā?"
- "He aha ngā rongoā e tika ana mō taku mate?"
- "Me whai whakamātautau motuhake ahau mō ōku kanohi, taringa, pūnaha manawa, ngākau, whatukuhu rānei?"
- "Me kōrero ahau ki ētahi atu tohunga (hei tauira, ngā taote pokanga ENT, ngā tākuta rumatiki)?"
- "He whakarerekētanga āhua noho whaiaro kei a au hei tautoko i te hauora o tōku kiriuhi?"
- "Kei te haere tonu ngā whakamātautau haumanu , ngā rangahau hou rānei e pā ana ki tēnei mate?"
Mā te pātai i ēnei pātai ka āwhina i a koe kia pai ake te māramatanga me te whai wāhi atu ki te tiaki i a koe.
Āhea ahau me rapu awhina hauora tonu?
Mena kei a koe te Relapsing Polychondritis, he mea nui kia haere tonu koe ki te tirotiro me tō kaiwhakarato hauora.
Hei tāpiri atu, ki te pāngia koe e te uauatanga ohorere ki te manawa, ki te rerekētanga o te tirohanga, ki te raru rānei ki te whakarongo, kaua e tatari mō tō wā tirotiro e whai ake nei. Rapua tonutia he awhina hauora, nā te mea he tohu pea ēnei o ngā take nui e hiahia ana kia rongoatia wawetia.
Whakarāpopototanga o ngā kōrero matua
Ko te tumanako ka āwhina tēnei tirohanga whānui mō te Relapsing Polychondritis i a koe kia mārama ake ai ki tō haerenga hauora. Anei ngā mea nui hei ako:
- He mate onge te Polychondritis hoki whakamuri, e tohuhia ana e te mumura me te pirau o te kiriuhi wheua.
- Ko ngā taringa me te ihu te nuinga o te wā ka pā ki tēnei mate, engari ka pā pea hoki ki te korokoro, te ara rere o te manawa, me ngā hononga.
- Ahakoa kāore i te tino mōhiotia te take, e kiia ana he tukanga autoimmune.
- Ahakoa kāore he rongoā tuturu, kei reira ngā maimoatanga whai hua hei whakahaere i ngā tohu me te whakaiti i ngā raruraru.
- Nā te mea he morearea ngā raruraru manawa, kia mataara, me te rapu tohutohu hauora wawe tonu mō ngā tohu hou, ngā tohu kino rānei.
Mena kei te pāngia koe, tetahi atu rānei e mōhio ana koe, me toro atu ki te tākuta i taua wā tonu. Ko te noho mōhio me te whai whakaaro nui te mea nui ki te oranga hauora ki Nirogi Lanka.
Polychondritis Hokihoki, Kirita, Mamae taringa, Pupuhi ihu, Uaua ki te manawa, Mamae hononga, Mate ārai mate, Mumura, Mate onge
