Kodi nthawi zonse mumadzimva wotopa komanso wopanda moyo? Chifukwa chimodzi cha izi chingakhale kusowa kwa magazi m'thupi, vuto lotchedwa kuchepa kwa magazi m'thupi. Ngati kuchepa kwa magazi kumeneku kumachitika chifukwa cha matenda ena, mungafunike kupatsidwa magazi pafupipafupi. Chifukwa chake, lero tikambirana za mankhwala atsopano omwe ayambitsidwa padziko lonse lapansi kuti athetse mavuto otere. Dzina la mankhwala amenewo ndi Reblozyl.
Kodi Reblozyl ndi mankhwala amtundu wanji?
Reblozyl ndi mankhwala omwe adavomerezedwa mu 2019. Kunena zoona, ndi a gulu la mankhwala otchedwa ``erythroid maturation agents (EMA)''. Chabwino, chabwino, mawu amenewo angamveke ovuta pang'ono. Mwachidule, mankhwalawa amathandiza maselo ofiira a magazi omwe amapangidwa mu mafupa athu kuti "akule", kutanthauza kuti, akhale maselo athanzi komanso okhwima. Mankhwalawa amagwiritsidwa ntchito makamaka pochiza kuchepa kwa magazi komwe kumachitika chifukwa cha matenda ena a magazi. Makamaka kwa akuluakulu omwe ali ndi matenda awiriwa: 1.
Beta-thalassemia: Anthu omwe amafunika kupatsidwa magazi nthawi zonse chifukwa cha vutoli. 2.
Myelodysplastic Syndromes (MDS): Izi zimadziwikanso kuti bone
marrow failure. Chifukwa chake, Reblozyl imaperekedwanso kwa anthu omwe amafunika kupatsidwa magazi nthawi zonse.
Tiyeni tiphunzire zambiri zokhudza beta-thalassemia ndi MDS.
Ngati mukumvetsa pang'ono za matenda awiriwa, zidzakhala zosavuta kumvetsetsa momwe mankhwala a Reblozyl amagwirira ntchito.
- Beta-thalassemia: Ganizirani maselo ofiira a m'magazi mwathu ngati magalimoto onyamula mpweya. Mpweya womwe uli m'galimoto iyi umayikidwa pa puloteni yotchedwa hemoglobin . Munthu amene ali ndi beta-thalassemia sapanga puloteni yokwanira ya hemoglobin iyi. Choncho maselo m'thupi salandira mpweya womwe amafunikira. Ndicho chifukwa chake zizindikiro monga kutopa kosalekeza ndi kufiira zimachitika.
- Matenda a Myelodysplastic (MDS): Uwu ndi mtundu wa khansa womwe umayambira mu fupa. Mafupa ndi fakitale yomwe imapanga maselo athu a magazi (maselo ofiira, maselo oyera, ndi ma platelet). Mwa munthu amene ali ndi MDS, kupanga kwa fakitale iyi kumasokonekera. Izi zikutanthauza kuti kupanga maselo amagazi athanzi komanso okhwima bwino kumachepa.
Muzochitika zonsezi, vuto lalikulu ndi kuchepa kwa maselo ofiira amagazi athanzi komanso ogwira ntchito bwino, zomwe zikutanthauzaKuchepa kwa magazi m'thupi kumachitika.
Reblozyl imagwira ntchito pothandiza maselo ofiira osakula bwino omwe sakukula bwino kuti akule bwino. Izi zimawonjezera kuchuluka kwa maselo ofiira athanzi, zimawonjezera hemoglobin, komanso zimapangitsa kuti thupi lizitha kunyamula mpweya. Chifukwa chake,
mungafunike kupatsidwa magazi pafupipafupi.
Koma kumbukirani izi: Reblozyl si njira yolowa m'malo mwa kupatsidwa magazi. Ndi mankhwala okhawo omwe amathandiza kuchepetsa kufunikira.
Kodi mankhwalawa amaperekedwa bwanji?
Reblozyl si piritsi lomwe mungamwe kunyumba. Ndi jakisoni yomwe imaperekedwa
milungu itatu iliyonse . Jakisoni iyi imaperekedwa ndi dokotala kapena namwino wophunzitsidwa bwino mu ofesi ya dokotala wanu, chipatala, kapena chipatala.
- Komwe mungapereke katemera: Katemerayu nthawi zambiri amaperekedwa pansi pa khungu la mkono, ntchafu, kapena mimba, pansi pa phewa.
- Kulandira katemera pa nthawi yake: Ndikofunikira kwambiri kupita kukatenga katemera tsiku lomwelo limene dokotala wakupatsani. Ngati mwaphonya tsikulo, imbani dokotala nthawi yomweyo ndikupempha upangiri tsiku lotsatira.
- Buku la zizindikiro: Ndibwino kulemba zizindikiro zanu (monga kutopa ndi chizungulire ) m'buku kapena pafoni yanu tsiku lililonse. Izi zidzakuthandizani kufotokozera dokotala wanu momwe mankhwalawo akukukhudzirani.
Mlingo wa mankhwala omwe mudzapatsidwa udzatsimikiziridwa ndi dokotala wanu kutengera kulemera kwanu komanso momwe thupi lanu limayankhira mankhwalawo.
Kodi zotsatirapo zake zingakhale zotani? Kodi mungathane nazo bwanji?
Monga mankhwala ena aliwonse, Reblozyl ingayambitse zotsatira zina zoyipa. Si aliyense amene amakumana nazo, koma ndikofunikira kuzidziwa. Gome ili pansipa likuwonetsa zina mwa zotsatira zoyipa zomwe zimafala kwambiri komanso momwe mungathanirane nazo.
| Zotsatira Zam'mbali | Momwe mungayendetsere |
|---|
| Kutopa kwambiri, chizungulire, kulephera kudziletsa thupi | Pewani kuyendetsa galimoto kapena kugwiritsa ntchito makina olemera mpaka mutadziwa bwino momwe mankhwalawa amakukhudzirani. |
| Kupweteka mutu, minofu kapena mafupa | Funsani dokotala wanu za mankhwala ochepetsa ululu omwe angathandize kuchepetsa zizindikirozi. Uzani dokotala wanu ngati zizindikiro zanu sizikusintha kapena zikuipiraipira. |
| Kusanza, kupweteka m'mimba, kutsegula m'mimba (kutupa m'mimba) | Yesetsani kudya zakudya zazing'ono m'malo modya zakudya zazikulu. Idyani zakudya zopanda thanzi monga buledi, makeke, ndi mpunga. Imwani madzi ambiri. Ngati zizindikirozi zikuipiraipira kapena sizikuchira, uzani dokotala wanu. |
| Kuthamanga kwa Magazi Kwambiri | Ndikofunikira kuchita masewera olimbitsa thupi ndikutsatira zakudya zabwino monga DASH. Yesani kuthamanga kwa magazi nthawi zonse. Ngati kuthamanga kwa magazi anu kuli kokwera kuposa 180/120 mmHg, pitani ku Dipatimenti Yothandiza Padzidzidzi (ETU) nthawi yomweyo. |
| Kuvuta kupuma, Kukumana ndi ziwengo | Funsani dokotala wanu pasadakhale za zizindikiro za ziwengo (monga ziphuphu pakhungu, kuyabwa, kutupa pankhope, kupuma movutikira). Ngati mukukumana ndi zizindikiro izi, imbani dokotala wanu nthawi yomweyo kapena pitani ku Dipatimenti Yoona za Zadzidzidzi (ETU) yapafupi . |
| Kuchulukana kwa madzi m'thupi (edema) | Ngati mukuona kutupa kulikonse m'manja, m'mapazi, kapena m'thupi lanu, uzani dokotala wanu. Iye adzakupatsani chithandizo chofunikira. |
Kodi pangakhale mavuto ndi mankhwala ena?
Inde. Kumwa Reblozyl kungayambitse mavuto ngati mumwa mankhwala ena. Makamaka, ngati mukumwa mankhwala obwezeretsa mahomoni a kusamba kapena mapiritsi oletsa kubereka, chiopsezo cha magazi kuundana chingachuluke.
Choncho, onetsetsani kuti mwauza dokotala wanu za mankhwala onse omwe mumamwa, kuphatikizapo omwe madokotala amakulemberani, mankhwala ogulitsidwa kunja kwa chipatala, mavitamini, mankhwala achikhalidwe, ndi mankhwala azitsamba .
Uthenga Wopita Nawo Kunyumba
- Reblozyl ndi mankhwala atsopano omwe amaperekedwa ngati jakisoni wochizira kuchepa kwa magazi m'thupi komwe kumachitika chifukwa cha matenda otchedwa beta-thalassemia ndi MDS.
- Izi zimathandiza makamaka maselo ofiira osakhwima kukula bwino.
- Mankhwalawa angathandize kuchepetsa kufunikira kwa kuikidwa magazi pafupipafupi, koma si m'malo mwa kupereka magazi.
- Katemerayu amaperekedwa ndi dokotala kapena namwino milungu itatu iliyonse.
- Zotsatirapo zina monga mutu, kutopa, ndi kupweteka kwa minofu zingachitike. Lankhulani ndi dokotala wanu za zizindikiro zachilendo zilizonse.
- Ndikofunikira kudziwitsa dokotala wanu za mankhwala ena onse omwe mukumwa.
Reblozyl, Anemia, Beta-Thalassemia, Matenda a Myelodysplastic, MDS, kuikidwa magazi, Luspatercept, hemoglobin
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