Ngaba uhlala ufumana intlungu engaqhelekanga eqala ngasemva kwentloko yakho ize yehle entanyeni yakho? Ngaba le ntlungu iyanda ngakumbi xa ukhohlela, uthimla, okanye uphakamisa into enzima? Ngaba ngamanye amaxesha uziva unesizungu , ulahlekelwa yibhalansi yakho xa uhamba, okanye uziva ungenazintloni ezandleni zakho? Nokuba ucinga ukuba ezi ziintloko eziqhelekileyo, ngamanye amaxesha kunokubakho esinye isizathu esifihlakeleyo emva kwazo. Le yenye yeemeko ezinqabileyo kodwa ezibalulekileyo ekufuneka uziqaphele.
Ngamafutshane, yintoni iChiari Malformation?
Eli ligama elintsonkothileyo kancinci, kodwa masiligcine lilula. Ingqondo yethu ikhuselekile ngaphakathi kwekhakayi lethu. Emazantsi alo khakayi, kanye apho intamo idibana khona nekhakayi, kukho umngxuma apho intambo yomqolo wethu ingena khona. Oku kubizwa ngokuba yi-"foramen magnum" ngokwezonyango.
Kwimeko ebizwa ngokuba yiChiari malformation, inxalenye esezantsi yobuchopho bethu, ingakumbi inxalenye ebizwa ngokuba yi-cerebellum , ityhalelwa okanye icinezelwe phantsi nge-foramen magnum, kwindawo apho kukho khona umqolo. Cinga ngayo njengokuzama ukufaka into enkulu kunokuba inokungena kwindawo encinci.
I-cerebellum yethu yiyo elawula iintshukumo zethu, ibhalansi xa sihamba, ulawulo lokuma, kwaye ngandlela ithile ingqalelo yethu. Ngoko ke xa le nxalenye ichaphazeleka, iingxaki ezinxulumene noko zinokuvela.
Olu xinzelelo luphazamisa ukuhamba kolwelo lwe-cerebrospinal (CSF), olujikeleza ingqondo kunye nomqolo. Oku kufana nombhobho wamanzi ovalekileyo. Oku kubeka uxinzelelo kwiindawo zengqondo kunye nomqolo, okubangela iimpawu ezahlukeneyo.
Kutheni oku kusenzeka? Zithini izizathu?
Amaxesha amaninzi, i-Chiari malformation yimeko yokuzalwa . Oku kuthetha ukuba le meko yenzeka ngenxa yesiphene ekuphuhlisweni kwengqondo kunye nentloko ngelixa umntwana ekhula esibelekweni. Oku kungenxa yokuba abanye abantu banesithuba esincinci kunesiqhelo kwintloko ebizwa ngokuba yi-posterior fossa, apho ingqondo ikhona khona. Kodwa abaphandi abakaqiniseki ukuba kutheni oku kusenzeka.
Ngamanye amaxesha oku kunokubangelwa yimfuza .
Ayifane yenzeke le meko emva kokuzalwa, oko kukuthi, xa umntu emdala . Ingabangelwa zezi zinto zilandelayo:
- Umhlaza wobuchopho.
- Ukwenzakala entloko kunokubangela i-sac egcwele ulwelo (i-cyst) okanye i-blood clot (i-hematoma) engqondweni.
- Imeko ebizwa ngokuba yi-"hydrocephalus", ethetha ukuqokelelwa kwamanzi engqondweni.
- Ezinye iimeko ezinxulumene nomgogodla ezifana ne-tethered cord syndrome.
Ngaba kukho iintlobo ezahlukeneyo zale meko?
Ewe, le meko yahlulwe yaba ziintlobo ezininzi eziphambili ngokuxhomekeke kubukhali bayo kunye nomlinganiselo apho iindawo zobuchopho zichaphazeleka khona.
| Uhlobo | Ingcaciso elula |
|---|---|
| Uhlobo I | Olu lolona hlobo luxhaphakileyo nolungabalulekanga kangako . Yinxalenye esezantsi ye-cerebellum kuphela etyhalelwa kumjelo womqolo. Abanye abantu banokuphila ngaphandle kweempawu. Idla ngokufunyanwa ngengozi ngexesha le-MRI scan ngesinye isizathu. |
| Uhlobo II | Oku kukwabizwa ngokuba yi-`(Arnold-Chiari malformation).` Apha, zombini i-cerebellum kunye ne-brain stem zityhalelwa ezantsi. Oku kudla ngokubonakala kunye nesiphene sokuzalwa `(i-spina bifida).` |
| Uhlobo lwesithathu | Olu luhlobo olungaqhelekanga kakhulu nolunzima . Iindawo ezithile zobuchopho ziphuma ekhayeni ziye kungena ngasemva kwentamo. Oku kunokuba yingozi ebomini. |
| Uhlobo lwesine | Oku nako kunqabile kakhulu. Kwimeko enjalo, i-cerebellum ayikhuli ngokupheleleyo. Okanye, iindawo azikho. |
Ziziphi iimpawu eziqhelekileyo zohlobo lokuqala?
Ayingabo bonke abantu abane-Type I abaya kuba neempawu. Nangona kunjalo, ukuba iimpawu ziyabonakala, ezinye zazo ziquka:
- Intloko ebuhlungu yasemsebenzini kunye nentlungu yentamo:Olu lolona phawu luphambili noluqhelekileyo. Intlungu iyanda xa ukhohlela, uthimla, okanye uphakamisa izinto ezinzima.
- Iingxaki zeSiyezi kunye neBalance : Ukuziva unesiyezi, ngokungathi uza kutyhafa xa uhamba.
- Ubuthathaka bemisipha.
- Ukuba ndindisholo okanye ezinye iimvakalelo ezingaqhelekanga ezandleni nasezinyaweni .
- Iingxaki zokubona: ukubona okufipheleyo, ukubona okuphindwe kabini.
- Ubunzima bokuginya.
- Ukukhala ezindlebeni (i-tinnitus) kunye nokuphazamiseka kokuva.
- Iingxaki zokulala: Ukungalali, okanye ukuyeka ukuphefumla okwethutyana ngelixa ulele (sleep apnea).
- Isicaphucaphu nokuhlanza.
Into ebalulekileyo kukuba ezi mpawu zinokwahluka kakhulu kumntu nomntu. Kwaye azifani rhoqo. Ngezinye iintsuku zinokuba zimbi, ngezinye iintsuku zinokuba ngcono.
Uyifumana njani le nto, Gqirha?
Wakuba uchaze iimpawu zakho, ugqirha wakho uza kuqala akuhlole ngononophelo, ingakumbi uvavanyo lwemithambo-luvo . Oku kuza kujonga ibhalansi yakho, amandla emisipha, amandla okusabela, kunye neemvakalelo zakho.
Emva koko, ukuba kukho amathandabuzo malunga nale meko, baya kukuthumela kwiimvavanyo ezininzi ukuze bayiqinisekise.
- I-MRI (Magnetic Resonance Imaging) Scan: Olu lolona vavanyo lubalaseleyo nolubaluleke kakhulu lokufumanisa i-Chiari malformation. I-MRI inokuyibona ngokucacileyo indlela ebunjwe ngayo ingqondo kunye nomqolo. Ingabona kakuhle ukuba ingqondo icinezelwe kangakanani kwaye nokuba ukuhamba kolwelo lwe-'CSF' kuthintelekile na.
- I-Cine MRI: Olu luhlobo olukhethekileyo lwe-MRI. Lufana nevidiyo. Ungayibona i-CSF ijikeleza ingqondo ngexesha langempela, oko kukuthi, ibukhoma.
- I-CT (Computed Tomography) Scan: Oku kunokujonga naziphi na iingxaki emathanjeni entloko.
Zithini iindlela zonyango?
Unyango luxhomekeke kuhlobo onalo, ubukhali beempawu zakho, kunye nendlela oluchaphazela ngayo ubomi bakho bemihla ngemihla.
1. Akukho zimpawu: Ukuba une-Type I kwaye awunazo iimpawu, okanye ukuba azikukhathazi, mhlawumbi awudingi naluphi na unyango . Ugqirha wakho uza kukuxelela ukuba uze kuhlolwa rhoqo ukuze ajonge imeko yakho.
2. Amayeza:Ukuba uneempawu ezifana neentloko ezibuhlungu kunye nentlungu yentamo, ugqirha wakho unokukunika ii-painkillers (NSAIDs) kunye ne-muscle relaxants ukuze uzilawule.
3. Utyando: Ukuba uneempawu eziqatha ezingenakulawulwa ngamayeza, okanye ukuba iiskeni zibonisa umonakalo engqondweni okanye emgogodleni, ugqirha wakho unokucebisa utyando.
Iinjongo ezimbini eziphambili zotyando zezi:
- Ukunciphisa uxinzelelo engqondweni nakwi-spinal cord.
- Ukubuyisela ukuhamba kolwelo lwe-CSF.
Olona tyando luqhelekileyo yiPosterior Fossa Decompression Surgery . Kule meko, ugqirha ususa iqhekeza elincinci lethambo kwisiseko sekhakayi, apho lidibana khona nentamo. Oku kudala indawo engakumbi yengqondo kunye nomqolo. I-membrane ejikeleze ubuchopho (dura) nayo iyavulwa kwaye kuthungelwe indawo. Oku kuvumela ulwelo lwe-cerebrospinal (CSF) ukuba luhambe ngokukhululekileyo.
Ukuba une-hydrocephalus (ukwakheka kwamanzi engqondweni), kunokufuneka ubeke i-shunt ukuze kususwe ulwelo olungaphezulu.
Umyalezo Wokuya Ekhaya
- I-Chiari Malformation sisiphene sokwakheka esibangelwa kukutyhalelwa kwenxalenye esezantsi yobuchopho kumjelo womqolo.
- Kwi-Type I, uhlobo oluqhelekileyo, uninzi lwabantu alunazo iimpawu. Nokuba zikhona iimpawu, uphawu oluphambili yintloko ebuhlungu ngasemva kwentloko nentamo.
- Uvavanyo oluphambili olusetyenziswayo ukufumanisa le meko yi -MRI scan .
- Ukuba akukho zimpawu, akukho mfuneko yonyango. Ukuba kukho iimpawu, zinyangwa ngamayeza okanye ngotyando.
- Ukuba unamathandabuzo okanye iimpawu, eyona nto ilungileyo onokuyenza kukubona ugqirha wakho ukuze akunike ingcebiso . Kubaluleke kakhulu ukwenza ngokweengcebiso zonyango kunokukhangela ulwazi kwi-intanethi.











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