Xa ujonga amehlo omntwana wakho omncinci, ngaba wakha waphawula ukuba kukho into eyahlukileyo ngelihlo elinye? Mhlawumbi ingaphakathi lelihlo libonakala lingaqhelekanga, okanye intloko yomntwana ijikelwe kwelinye icala, okanye iliso elinye livuvukele. Kuqhelekile ukuba umzali azive esoyika xa ebona izinto ezinje. Namhlanje siza kuthetha ngemeko enokuchaphazela amehlo, into engaqhelekanga kodwa ebaluleke kakhulu ukuyazi. Leyo yimeko ebizwa ngokuba yi-'Morning Glory Syndrome '.
Yintoni le 'Morning Glory Syndrome'?
Ngamafutshane, i-'Morning Glory Syndrome' yimeko eyenzeka xa inxalenye yeliso lakho engaphakathi kweliso lakho, umqolo, ingakhuli kakuhle. Khawuthelekelele, umthambo oyintloko onxulumene nokubona ungaphakathi kweliso lethu, indawo apho udibana khona neliso, oko kukuthi, inxalenye ebizwa ngokuba yingcambu yemithambo-luvo, ekule meko, ikwimo ye-funnel. Kufana nokuba kukho intyatyambo ebizwa ngokuba yi-'Morning Glory', kwaye xa ugqirha ejonga kwi-'(Retina)' yeliso lakho, kubonakala ngathi ujonge kuloo ntyatyambo. Yiyo loo nto ibizwa ngokuba yi-'Morning Glory Syndrome'.
Oku kubangelwa yingxaki ekukhuleni kweliso ngelixa umntwana esesesibelekweni . Idla ngokuchongwa kwangethuba kakhulu, ngamanye amaxesha ngaphambi kokuba umntwana abe neminyaka emibini ubudala. Le 'Morning Glory Syndrome' (MGS) ibangela utshintsho kwisakhiwo ngaphakathi kweliso olunokuchaphazela umbono wakho. Ikwanyusa umngcipheko wokuba neengxaki ezahlukeneyo zamehlo ubomi bonke. Idla ngokuchaphazela iliso elinye kuphela, kodwa ayifane ichaphazele omabini amehlo.
Enye into kukuba, ngamanye amaxesha kunokubakho umahluko kuphela kwindlela elibonakala ngayo eli liso, oko kukuthi, ngaphandle kweempawu. Kwimeko enjalo, iingcali ziyibiza ngokuba yi-'Morning Glory Disk Anomaly'. Nangona kunjalo, ukuba lo mahluko kwindlela elibonakala ngayo uhamba neempawu, kuthiwa yi-'Morning Glory Syndrome'.
Ixhaphake kangakanani le meko?
I-Morning Glory Syndrome yimeko engaqhelekanga kakhulu . Kuqikelelwa ukuba ichaphazela abantwana abangaphezu kwama-63,000 abangaphantsi kweminyaka engama-20 ubudala. Enye into enomdla kukuba ixhaphake kabini kumantombazana kunamakhwenkwe. Kuthiwa ayixhaphakanga kubantu abamnyama.
Zithini iimpawu zoku?
Ayingabo bonke abantu abaneMorning Glory Syndrome (MGS) abaya kuba neempawu ezifanayo. Nangona kunjalo, kukho ezinye iimpawu eziqhelekileyo. Le meko inamathuba aphindwe kabini okuchaphazela iliso lasekhohlo kunelasekunene.
Iimpawu ezinxulumene namehlo:
- UmgamaI-Myopia : Oku kuthetha ukuba nangona izinto ezikufutshane zinokubonakala ngokucacileyo, izinto ezikude zibonakala zingacacanga.
- Iingxaki ezibonakalayo zokubona: Usenokuba nezikhewu okanye amabala angaboniyo (i-scotomas) kwindawo yakho yokubona. Nangona kuqhelekile ukuba wonke umntu abe nendawo encinci yokungaboniyo kwiliso ngalinye, le ndawo yokungaboniyo inokuba nkulu kunesiqhelo kwiliso elichaphazelekayo lomntu one-MGS.
- I-Strabismus: Iliso elinye okanye omabini ajikwa kwicala elahlukileyo. Sithi "amehlo anqamlezileyo".
- I-cornea emhlophe, yesilivere, emthubi, okanye emhlophe qhwa (iLeukocoria): Umbindi weliso, odla ngokubonakala umnyama, unokubonakala unombala owahlukileyo. Ukuba ubona oku, ngokuqinisekileyo kuya kufuneka ubone ugqirha ngoko nangoko.
Iimpawu ezenzeka kunye nezinye iimeko ezinxulumene noko:
Ukongeza kwezi mpawu zinxulumene namehlo, kukho nezinye iimeko zempilo ezinokubakho kunye neMorning Glory Syndrome (MGS). Ezi meko ziquka:
- I-Encephalocele (inxalenye yengqondo ephuma kwikhakayi)
- Isifo seMoyamoya (ukuncitshiswa kwemithambo yegazi ehambisa igazi engqondweni)
- `Isifo se-PHACE`
- ``I-Neurofibromatosis uhlobo 2 (NF2)''
- Isifo se-Aicardi
- `Uhlobo lwe-Chiari malformation I`
- `I-Duane syndrome` (ngamanye amaxesha ibizwa ngokuba yi-`Okihiro syndrome`)
La magama asenokuvakala entsonkothile kuwe, kodwa ukuba ugqirha urhanela ukuba une-MGS, uya kukhangela nezinye izifo ezifana nale.
Yintoni isizathu soku?
Enyanisweni, iingcali azikayiqondi kakuhle indlela iMorning Glory Syndrome (MGS) ekhula ngayo. Oku kungenxa yokuba yimeko engaqhelekanga kakhulu kwaye yaqala ukuchazwa kutshanje ngo-1969.
Nangona kunjalo, into eyaziwayo ziingcali kukuba unobangela we-MGS unxulumene nokuphazamiseka okuthile ekuphuhlisweni kweliso ngelixa umntwana esesesibelekweni . Oku kucingelwa ukuba kunxulumene nemithambo yegazi ehambisa igazi elisweni engakhuli kakuhle, okanye ukuphazamiseka ekuphuhlisweni kweliso nakwimithambo-luvo ye-optic.
Enye yezona zinto zibalulekileyo ezibonisa ukuba kukho iingxaki zemithambo yegazi kukuba i-MGS inamathuba aphindwe kabini okuchaphazela iliso lasekhohlo. Ngokwesiqhelo, umntwana osakhulayo esibelekweni unemingxuma emincinci phakathi kwamacala asekhohlo nasekunene entliziyo. Le mingxuma idla ngokuvaleka ngaphambi okanye kwiintsuku ezimbalwa emva kokuzalwa.
Nangona kunjalo, ukuba umntwana osesiswini uthambekele ekubeni namahlwili egazi amancinci (i-microemboli), loo mingxunya inokuvumela ukuba ihlwili legazi lihambe ukusuka kwicala lasekhohlo lentliziyo liye kwicala lasekunene. Ukusuka apho, linokuhamba liye engqondweni. Ukuba kukho ukuphazamiseka ekuphuhlisweni kwemithambo yegazi, ihlwili linokunamathela apho, lithintele ukuhanjiswa kwegazi kwaye lithintele izicubu ekukhuleni ngokufanelekileyo. Zezi ziganeko eziye zabonisa ukuba ukuphazamiseka ekuphuhlisweni kwemithambo yegazi kunegalelo kwi-MGS.
Nangona i-MGS inokwenzeka xa kukho iimeko zemfuza kunye nezifo ezidluliselwa kwilifa, uphando alubonisanga ukuba ezi meko zibangela i-MGS ngokuthe ngqo. Nangona kukho iingxelo zamalungu amaninzi osapho olunye afumana i-MGS, ayiqhelekanga kangako.
Zeziphi iingxaki ezinokwenzeka?
Eyona ngxaki ixhaphakileyo yeMorning Glory Syndrome (MGS) kukuqhekeka kwe-retina . Le meko inokwenzeka kubantu abafikelela kwi-40% abane-MGS. Le yingxamiseko yezonyango .
Ezinye iingxaki zingabandakanya:
- Ukubona okuphantsi: Ukubona okunciphileyo kakhulu.
- Iliso elivilaphayo (i-Amblyopia): Ngenxa yokuba umbono kwelinye iliso awukhuli kakuhle, ingqondo iqala ukungazinaki iimpawu ezivela kwelo liso.
- Ukuvuselelwa kwemithambo yegazi yeliso: Oku kunokuchaphazela umbono.
- Ukuqhekeka kwe-retinal (i-Retinoschisis) .
Uyibona njani le nto?
Ugqirha wamehlo, ingakumbi ingcali ye-retina, unokuxilonga i-Morning Glory Syndrome (MGS) esebenzisa iindlela ezahlukeneyo, kuquka ukubuza ngeempawu onazo wena okanye umntwana wakho kunye nemiphumo oyifumanayo.
Ugqirha uza kuhlola umbono wakho (okanye womntwana wakho), ajonge ngqo kwiliso elichaphazelekayo, kwaye mhlawumbi athathe imifanekiso ye-retina. Ezinye iiskeni ze-retina ezikhethekileyo nazo zinokuba luncedo kakhulu.
Uvavanyo olunokunceda ekuxilongweni kwezi:
- Uvavanyo lwamehlo: Oku kuquka izinto ezifana novavanyo lokubona ngamehlo, uvavanyo lwentsimi yokubona, kunye novavanyo lwesibane esiqhekekileyo.
- I-Optical Coherence Tomography (OCT): Oku kungathatha imifanekiso enqamlezileyo yangaphakathi kweliso.
- I-Fluorescein Angiography: Le ihlola imeko yemithambo yegazi ngaphakathi kweliso.
- I-Magnetic Resonance Imaging (MRI): Oku kunceda ukubona izakhiwo ezijikeleze ingqondo namehlo.
Ingaba oku kunganyangeka? Zithini iindlela zonyango?
I-Morning Glory Syndrome (MGS) yimeko eyenzeka xa ingaphakathi leliso lakho lingaphuhli kakuhle. Utshintsho lokukhula alunakulungiswa okanye lunyangwe, kwaye akukho nyango . Oko kuthetha ukuba akukho nyango ngqo lwe-Morning Glory Syndrome.
Kodwa ungakhathazeki. Nangona kungekho nyango ngqo lwe-MGS, iimpawu kunye neengxaki ezibangelwa yiyo zinokunyangwa .
Iinjongo eziphambili zonyango zezi zilandelayo:
- Ukulungisa ingxaki: Umzekelo, ukuba i-retina ihlukanisiwe, ingalungiswa ngotyando.
- Ukunciphisa impembelelo yengxaki: Ukunxiba i-eye patch ukuze uthintele iliso elivilaphayo ukuba lingabi mandundu.
- Ukuthintela ezinye iingxaki: Ukuba i-retina iyaqhekeka, kubalulekile ukuyilungisa ngokukhawuleza ukuze kuthintelwe umonakalo ongunaphakade kunye nokulahleka kokubona.
Iindlela zonyango zixhomekeke kwiingxaki zakho ezithile kunye nezinye izinto ezininzi. Ugqirha wakho uyakwazi ukukuxelela ukuba loluphi unyango olufanelekileyo kwimeko yakho kunye noko bakucebisayo.
Luhlobo luni lwekamva umntu onesi sifo anokulilindela?
I-Morning Glory Syndrome (MGS) idla ngokuchongwa ebuntwaneni. Yimeko ehlala ihleli, ehlala ihleli . Ayinakuphiliswa, iguqulwe, okanye ilungiswe. Ayisongeli ubomi, kodwa inokuchaphazela kakhulu umbono. Abantu abangaphezu kwesithathu abane-MGS bafumana ukuqhekeka kwe-retina.
Abanye abantu abane-MGS banokuba nombono "oqhelekileyo" (20/20) okanye umbono ophantse ube semgangathweni (phakathi kwe-20/20 kunye ne-20/70). Nangona kunjalo, uninzi lwabo alunawo . Uninzi lwabantu abane-MGS luwela kudidi "lokubona kancinci" (20/70 ukuya kwi-20/200) okanye "lokubona ngokusesikweni" (20/200 kunye nokulungiswa okufana neeglasi).
Kwelinye icala, abantu abane-MGS kwelinye icala kufuneka bajongwe ngokusondeleyo iliso labo elingachaphazelekanga, kuba elo liso likwasemngciphekweni omkhulu wokufumana iingxaki ezithile. Ngenxa yokuba i-MGS ibangela ukungaboni kakuhle (i-myopia), kukho umngcipheko wokuqhekeka kwe-retina, kwaye i-myopia yeyona nto iphambili ebangela ukuqhekeka kwe-retina, nokuba i-MGS ikhona okanye ayikho. Iliso elingachaphazelekanga lisenokuba semngciphekweni omkhulu wokufumana i-cataracts.
Ngenxa yokuba i-MGS ifunyaniswa isencinci, izigqibo zonyango zihlala zenziwa ngabazali okanye abagcini. Banendima ephambili ekuqapheleni iimpawu okanye iindlela zokuziphatha ezinokubonisa ukuba umntwana unengxaki yokubona enxulumene ne-MGS.
Ngaba oku kungathintelwa?
I-Morning Glory Syndrome (MGS) ayinakuthintelwa , kwaye akukho ndlela yokunciphisa umngcipheko wokuba ivele.
Ndingazinyamekela njani mna/umntwana wam?
Ukuba wena okanye umntwana wakho une-MGS, eyona nto ingcono onokuyenza kukugcina umbono wakho ubonakala kangangoko unako . Ingcali yakho yamehlo iya kukukhokela kwindlela yokwenza oku. Kubaluleke kakhulu ukulandela imiyalelo yakho yonyango ngononophelo, sebenzisa iiglasi zakho ozinikiweyo okanye ezinye iindlela zonyango njengoko kucetyisiwe, kwaye ubone ingcali yakho rhoqo ukuze ihlolwe.
Kufuneka ubone ugqirha nini kungekudala?
Ukuba une-MGS, usemngciphekweni omkhulu wokufumana ukuqhekeka kwe-retina. Le yingxamiseko yezonyango . Ke ngoko, kubalulekile ukufuna unyango ngokukhawuleza ukuba unezinye zeempawu ezilandelayo. Unyango olukhawulezileyo lunokuthintela umonakalo ongunaphakade kwaye lubuyisele umbono kwiliso elichaphazelekayo.
Iimpawu zokuqhekeka kwe-retinal zezi:
- Ukukhanya okukhawulezileyo (Photopsia): Njengokukhanya kombane.
- Amabala amnyama abonakala ngathi ayadada okanye adadayo abonakala ngaphezu kwesihlandlo esinye: (Kuqhelekile ukubona ezinye izinto ezidadayo phambi kwamehlo, kodwa ukuba zikhula ngequbuliso, kufuneka unikele ingqalelo).
- Umbono ofipheleyo: Oku kunokuvakala ngathi kuza amaza amnyama okanye ikhethini kwaye ivala indawo yakho yokubona.
- Umbono ofiphele ngequbuliso.
Ukuba ubona naziphi na kwezi mpawu, yiya esibhedlele ngokukhawuleza .
Yeyiphi imibuzo omele uyibuze ugqirha?
Usenokubuza ingcali yamehlo le mibuzo:
- I-MGS yam (okanye yomntwana wam) inzima kangakanani?
- Iza kuyichaphazela njani indlela endibona ngayo (okanye yomntwana wam)?
- Zeziphi izinto ekufuneka ndizijonge xa ndicinga ukuba umntwana wam unengxaki yokubona enxulumene ne-MGS yakhe?
- Ngaba kukho ezinye iimeko zempilo ezinokubangela i-MGS kum (okanye kumntwana wam)? Ngaba ndifuna ukuthunyelwa kwenye ingcali?
Okokugqibela, izinto ekufuneka uzikhumbule
Xa ufumanisa ukuba umntwana wakho okanye umntu omkhathalelayo uneMorning Glory Syndrome (MGS), imeko engaqhelekanga apho i-retina engasemva kweliso ingakhuli kakuhle, unokuziva ulusizi kwaye udanile. Akukho nyango luthe ngqo lwale meko.
Nangona kunjalo, nangona i-MGS ingenakunyangwa, uninzi lweengxaki ezibangelwa yiyo zinokunyangwa . Ukuba umntwana wakho une-MGS, thetha nogqirha wamehlo. Kukho izinto onokuzenza ukunciphisa iziphumo zale meko kwaye uyithintele ukuba ibe mandundu. Ukugcina umbono wakho yeyona nto ibalulekileyo . Ngokuhambela phambili kotyando lwamehlo kunye nolunye unyango namhlanje, kunokwenzeka ngakumbi kunangaphambili. Ngoko ke, musa ukuphelelwa lithemba. Ngeengcebiso zonyango ezifanelekileyo kunye nonyango, le meko inokulawulwa.
"Isifo seMorning Glory, i-MGS, izifo zamehlo, i-retina, izifo zamehlo zabantwana, ukukhubazeka kokubona, ukuhlukana kwe-retinal











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