Khawucinge nje, usempilweni entle kwaye ngequbuliso enye yeengalo okanye imilenze yakho iyaphelelwa ngamandla uze uphelelwe ngamandla. Okanye umzimba wakho wonke uba buthathaka kangangokuba awukwazi ukuhamba. Kuqhelekile ukuba uzive usoyika kakhulu xa kwenzeka into efana nale. Abantu abaninzi bacinga ukuba oku kungenxa yokudinwa okanye enye into. Nangona kunjalo, ngamanye amaxesha kunokubakho isizathu sezonyango emva koku ekufuneka sixoxwe nzulu. Namhlanje sithetha ngemeko yezonyango engaqhelekanga kodwa ebaluleke kakhulu ekufuneka siyiqaphele.
Ngamafutshane, yintoni iPrimary Periodic Paralysis (PPP)?
I-Primary Periodic Paralysis, okanye i-PPP ngamafutshane, liqela leemeko ezingaqhelekanga ezichaphazela izihlunu zethu ngequbuliso. Okwenzekayo kukuba, ngaphandle kwesilumkiso , izihlunu zakho ziba buthathaka, ziqine, okanye zingasebenzi ngokupheleleyo. Le meko inokuhlala imizuzu embalwa kwabanye abantu, ngelixa kwabanye inokuhlala iintsuku.
Isizathu esiphambili soku sikumaseli ethu emisipha. Khawuthelekelele ukuba iiseli zethu zemisipha zinemijelo emincinci. Ezi mijelo kulapho iiminerali ezibalulekileyo ezifana nepotassium, i-sodium, kunye ne-calcium zingena khona ziphume kwiiseli. Ukuze umsipha usebenze kakuhle, ubungakanani bezi minerali ngaphakathi nangaphandle kweseli kufuneka bulingane ngokugqibeleleyo. Okwenzekayo kumntu one-PPP kukuba olu lungelelwano lulahlekile ngenxa yesiphene kwezi mijelo. Emva koko izihlunu azikwazi ukusebenza kakuhle.
Uninzi lwexesha, ezi mpawu ziqala ebuntwaneni okanye ebusheni, kodwa abanye abantu basenokungabonakalisi zimpawu de babe neminyaka engama-60 okanye engama-70 ubudala.
Ziziphi iintlobo eziphambili zesi sifo?
I-PPP yahlulwe yaba ziintlobo ezininzi eziphambili. Olu hlu luphenjelelwa kakhulu kukuba loluphi uphazamiseko lwemijelo yeminerali olukhoyo kwiiseli zakho zemisipha.
| Uhlobo lwemeko yezonyango | Kwenzeka ntoni (ngamagama alula) |
|---|---|
| Ukukhubazeka Kwexesha Eliphantsi Kwe-Hypokalemic (hypoKPP) | Okwenzekayo koku kukuba inqanaba le-potassium egazini lehla kakhulu ngequbuliso. |
| Ukukhubazeka Kwexesha Eliphezulu Kwe-Hyperkalemic (hyperKPP) | Okwenzekayo koku kukuba amanqanaba e-potassium egazini anyuka kakhulu ngequbuliso. |
| I-Paramyotonia Congenita | Apha, ibhalansi yesodium kunye nepotassium kwiiseli zemisipha iyaphazamiseka. |
| Isifo sika-Andersen-Tawil (ATS) | Kule meko, inkqubo yokungena nokuphuma kwe-potassium kwiiseli ayisebenzi kakuhle. Inqanaba le-potassium egazini linokuba phezulu, liphantsi, okanye liqhelekile. |
Ngamanye amaxesha, ubuthathaka bemisipha bunokubangelwa zezinye iimeko. Umzekelo yiThyrotoxic Periodic Paralysis (TPP) . Le yimeko apho i-thyroid gland ivelisa i-thyroid hormone eninzi kakhulu. Oku kuhamba namanqanaba aphantsi e-potassium egazini, anokubangela iimpawu ezifana neHypoKPP.
Zithini izizathu kunye nezinto "ezibangela" le meko?
I-PPP ibangelwa sisiphene semfuza . Ngamafutshane, ibangelwa sisiphene kwimfuza ezilawula imijelo kwiiseli zemisipha esithethe ngazo ngaphambili. Uninzi lwexesha, umntwana ufumana esi gene siphene komnye wabazali bakhe. Nangona kunjalo, kunqabile kakhulu ukuba umntwana abe nesi sifo nokuba abazali abanaso esi gene.
Ngoku makhe sijonge ukuba yintoni enokubangela obu buthathaka bemisipha. Oku kunokwahluka kumntu nomntu.
- Ukutya: Ukutya kakhulu ukutya okutyebileyo kwi-potassium (kwi-hyperKPP) okanye kwi-potassium ephantsi (kwi-hypoKPP). Kwakhona, ukutya ukutya okune-carbohydrate eninzi (isitatshi/iswekile).
- Ukuzilolonga : Xa uphumle emva kokuzilolonga kakhulu.
- Ukuphumla: Ukuhlala kwindawo enye ixesha elide, xa uvuka kusasa, okanye emva kokulala.
- Ezinye izizathu: Uxinzelelo, ukuchatshazelwa ngumkhuhlane ogqithisileyo, ukusela utywala, kunye namayeza athile (umz., amayeza okukhulula izihlunu, amanye amayeza e-asthma, amayeza okudambisa iintlungu).
Ziziphi iimpawu eziphambili?
Uphawu oluphambili kukuphelelwa ngamandla kwemisipha okanye ukukhubazeka ngokupheleleyo. Oku kunokuchaphazela ingalo okanye umlenze omnye ngexesha, okanye umzimba wonke ngamanye amaxesha.
Ukongeza kolu phawu luphambili, abanye abantu banokubona nezinye iimpawu xa bebona obu buthathaka:
- Ubuthathaka bemisipha yobuso
- Intlungu yemisipha kunye nokuqina kwayo
- Ukubetha kwentliziyo okungaqhelekanga
- Ubunzima bokuphefumla okanye ukuginya
I-HypoKPP (uhlobo lwe-potassium ephantsi)
Iimpawu zinokuvela rhoqo kanye ngemini, okanye zingabikho rhoqo ngonyaka. Zinokuhlala iyure enye okanye ezimbini, okanye zihlale iintsuku ezimbini okanye ezintathu. Ekuhambeni kwexesha, izihlunu zinokuba buthathaka ngonaphakade.
I-HyperKPP (uhlobo lwe-potassium eyongeziweyo)
Ubuthathaka bunokuthatha ixesha elifutshane, kodwa bunokwenzeka rhoqo. Iimpawu zinokuvela ngequbuliso, kwaye ngamanye amaxesha zihlale imizuzu embalwa. Nokuba akukho buthathaka, ungaziva ukuqaqamba kwemisipha okanye ukuqina.
Isifo sika-Andersen-Tawil (ATS)
Ukongeza kubuthathaka bemisipha, kukho nezinye iimpawu zomzimba ezibonakala.
- Ukubetha kwentliziyo okukhawulezayo okanye okungaqhelekanga
- I-Scoliosis
- Iminwe eneentambo
- Zincinci kunezandla neenyawo eziqhelekileyo
- Utshintsho oluthile ebusweni (umz., ibunzi elibanzi, iindlebe ezisezantsi)
Indlela yokuxilonga ngokuchanekileyo esi sifo?
Ngenxa yokuba i-PPP yimeko engaqhelekanga kwaye iimpawu zayo zifana nezinye izifo eziqhelekileyo, kungathatha ixesha ukuxilonga isifo ngokuchanekileyo. Ke ngoko, ukuba unale mpawu, kungcono ukubona ugqirha ogxile kwizifo ezinxulumene nenkqubo yemithambo-luvo (i-Neurologist) .
Ugqirha wakho unokubuza imibuzo efana nale ukuze afumanise imeko:
- Ziqale nini ezi mpawu?
- Ngaba kukho omnye umntu kusapho onemeko efanayo?
- Kwenzeka ntoni xa kukho ubuthathaka?
- Ngaba wakha waziva ngathi ukutya okanye isenzo esithile sibangele oku?
Ukongeza, kunokwenziwa iimvavanyo ezininzi ukuqinisekisa isifo:
- Uvavanyo lwegazi: Jonga amanqanaba e-potassium, iihomoni ze-thyroid, nezinye izinto.
- I-Electromyography (EMG): Ukuvavanya ukusebenza kwezihlunu kunye nemithambo-luvo.
- I-Electrocardiogram (EKG): Ukujonga ukuba ukubetha kwentliziyo kubetha rhoqo na.
- I-Biopsy yeMisipha: Ukuthatha iqhekeza elincinci lemisipha uze ulihlolisise.
Indlela yokunyanga nokulawula?
Unyango oluphambili loku kukuchonga nokuphepha izinto ezibangela oku . Oku kuthetha ukwenza utshintsho oluthile kwindlela otya ngayo kunye nomthambo wakho.
Ukongeza, kukho amayeza okulawula amanqanaba e-potassium emzimbeni.
- Iyeza iDichlorphenamide (Keveyis) livunyiwe ukunyanga zombini i-hypoKPP kunye ne-hyperKPP.
- Ngamanye amaxesha oogqirha bacebisa nonyango olubizwa ngokuba yi -Acetazolamide (Diamox) .
- Izongezo zePotassium zinikwa abo baneHypoKPP.
- Umntu one-HyperKPP ngamanye amaxesha unokulawula ubuthathaka bakhe ngokusela isiselo esineswekile (umz., i-soda) kwangoko nje ukuba siqale.
Eyona nto ibalulekileyo kukuba, ungaze uyeke ukuthatha okanye ukuyeka amayeza wedwa. Yenza yonke into kuphela ngokwengcebiso kagqirha wakho. Ukuba ufumana ubuthathaka obukhulu ngequbuliso, ubunzima bokuphefumla, okanye iintlungu zesifuba, yiya kwiSebe leNgxamiseko (ETU) lesibhedlele esikufutshane ngoko nangoko.
Ungayilawula le meko kakhulu ngokwenza utshintsho oluncinci kwindlela ophila ngayo.
- Ukutya: Ukuba une-hyperKPP (i-potassium ephezulu), kuya kufuneka unciphise ukutya okune-potassium eninzi njengeebhanana, ii-dates, i-broccoli, kunye namandongomane. Ukuba une-hypoKPP (i-potassium ephantsi), kuya kufuneka unciphise ukutya okune-carbohydrate eninzi njengesonka, ipasta, irayisi kunye neelekese. Fumana icebiso elifanelekileyo kugqirha wakho malunga noku.
- Ukuzilolonga: Njengokuzilolonga kakhulu, akukho kuzilolonga nako kubi. Thetha nogqirha wakho malunga nomgangatho wokuzilolonga ofanelekileyo kuwe.
Umyalezo Wokuya Ekhaya
- I-Primary Periodic Paralysis (PPP) ayikokukhubazeka nje komzimba, sisiphene semfuza esenzeka kwiindlela ze-ion zeeseli zemisipha.
- Kukho izinto ezinokubangela le meko. Lumka ngezinto ezifana nokutya, umthambo, kunye noxinzelelo, kwaye uchonge kwaye uziphephe izinto ezikuchaphazelayo.
- Ukuba kuvela iimpawu, kubaluleke kakhulu ukubona ingcali ukuze ichonge isifo ngokuchanekileyo.
- Abantu abaninzi banokuyilawula ngempumelelo le meko baze baphile ubomi obuxakekileyo ngokutshintsha indlela abaphila ngayo kunye namayeza abawanikwe ngugqirha wabo.
- Landela icebiso likagqirha wakho rhoqo. Musa ukwenza izigqibo ngokwakho, njengokuthatha amayeza okanye ukutshintsha indlela otya ngayo.
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