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Iyini i-Acute Chest Syndrome? Kalula nje...
Kulungile, manje bheka. Le 'Acute Chest Syndrome' iyinkinga engaba yingozi yesifo se-sickle cell ('SCD') . Kalula nje, yilapho uba nobuhlungu besifuba, ukukhwehlela, umkhuhlane, amazinga aphansi omoya-mpilo egazini lakho, kanye nezinto ezingavamile, ikakhulukazi uketshezi, eziqala ukwakheka ezicutshini zamaphaphu ('amaphaphu ayangena').Lesi simo singaba sibi kakhulu ngokushesha okukhulu . Eqinisweni, lesi Acute Chest Syndrome' siyimbangela ehamba phambili yokulaliswa esibhedlela futhi ngezinye izikhathi ukufa kwabantu abanesifo se-sickle cell . Ngakho-ke, kubaluleke kakhulu ukuqaphela lokhu.Manje ungase uzibuze ukuthi iyini iSickle Cell Disease (SCD). Ake sikukhumbuze kancane ngayo. Yisifo esibangelwa ufuzo . Lokho kusho ukuthi sizuzwe njengefa. Sithinta iphrotheni emaseli ethu abomvu egazi ebizwa ngokuthi i-hemoglobin . Ngenkathi amaseli abomvu egazi omuntu ophilile eyindilinga, amaseli abomvu egazi omuntu one-SCD abunjwe njengesikela (njengenyanga). Ngakho la maseli amise okwesikela awakwazi ukudlula emithanjeni yethu yegazi emincane kalula. Ngemuva kwalokho, i-hemoglobin ayikwazi ukuthwala umoya-mpilo emzimbeni wonke ngendlela efanele. Lena yinkinga enkulu nge-SCD.
Ivame kangakanani i-Acute Chest Syndrome?
Eqinisweni, i-'Acute Chest Syndrome' iyisimo esivame kakhulu kubantu abanesifo se-sickle cell ('SCD'). Ngokwezibalo, cishe ingxenye yabantu abane-'SCD' bazobhekana nalesi simo okungenani kanye empilweni yabo . Nakuba kubonakala sengathi sivame kakhulu ezinganeni ezincane eziphakathi kweminyaka engu-2 no-4 , singaba sibi kakhulu kubantu abadala kunasezinganeni . Kutholakale nokuthi abantu abane-'SCD' kanye ne-asthma basengozini enkulu yokuthola i-'Acute Chest Syndrome' kunabanye.Kungani kwenzeka i-Acute Chest Syndrome? Ziyini izimbangela?
Ososayensi abakakwazi ukusho ngokuqinisekile ukuthi yini ngempela ebangela i-'Acute Chest Syndrome'. Kodwa bakholelwa ukuthi kungenzeka ukuthi ibangelwa yisici esisodwa noma ngaphezulu. Ake sibheke ukuthi ziyini:- I-Bone marrow necrosis:Ubuwazi ukuthi umongo wamathambo uyingxenye ethambile, ethambile emathanjeni ethu amakhulu? Uma lo mongo wamathambo ufa ngandlela thile (okubizwa ngokuthi 'i-necrosis'), izingcezu zawo ezincane zingaphuka zingene egazini futhi zihambe emzimbeni wonke. Uma lezi zingcezu ziya emaphashini, zingadala 'i-Acute Chest Syndrome'.
- Ukuminyana kwamafutha: Esinye isizathu esingaba khona sokwehluleka komongo wethambo okukhulunywe ngaso ngenhla ukuminyana kwamafutha . Kalula nje, lokhu kwenzeka lapho inhlayiya yamafutha (cabanga ngayo njengethonsi lamafutha) inamathela emthanjeni wegazi futhi ivimbele ukugeleza kwegazi . Lokhu kungaholela nase-Acute Chest Syndrome.
- Ukutheleleka : Ukutheleleka okuhlukahlukene, ikakhulukazi i-pneumonia ebangelwa amagciwane noma ama-virus , kungabangela i-acute chest syndrome. Ukutheleleka kuyimbangela eyinhloko yalesi simo ezinganeni ezincane . Kodwa-ke, kubantu abadala , kungenzeka kakhulu ukuthi kubangelwe yi-fat embolism.
Yiziphi izimpawu zomuntu one-Acute Chest Syndrome?
Izimpawu ze-'Acute Chest Syndrome' zingahluka kumuntu nomuntu. Kunomehluko othile, ikakhulukazi phakathi kwezingane ezincane nabantu abadala. Izingane ezincane zivame ukukhombisa izimpawu eziningi zokutheleleka:- Ukukhwehlela
- Imfiva
- Ukwehla kokuhlushwa kwe-oxygen egazini (i-hypoxemia)
- Isivinini sokuphefumula esingavamile (i-tachypnea)
- Ukuphefumula (umsindo ovela esifubeni lapho uphefumula)
- Ubuhlungu besifuba , ikakhulukazi lapho uphefumula, bungakhula.
- Ubuhlungu obukhulu, obungazelelwe ezingalweni, emilenzeni, nasemhlane obubangelwa ukuvaleka kokugeleza kwegazi (okubizwa nangokuthi inkinga ye-vaso-occlusive).
- Ukuqongelela koketshezi emaphashini nasesifubeni (i-pleural effusion).
- Ubunzima bokuphefumula (ukuphelelwa umoya).
I-Acute Chest Syndrome ihlolwa kanjani? (Ukuxilongwa)
Ukuqashelwa kusenesikhathi kwe-'Acute Chest Syndrome' kungasindisa impilo yomuntu.Uma une-SCD futhi ulaliswe esibhedlela, kuzodingeka uhlolwe njalo futhi wenze izivivinyo ezidingekayo. Kunezivivinyo eziningana ezingasiza odokotela ukuthi baxilonge le nkinga:- Ukuhlaziywa kwegesi yegazi lemithambo: Lokhu kungalinganisa amazinga e-acidity (pH), i-oxygen, kanye ne-carbon dioxide egazini lakho.
- Ukuhlolwa kwegazi: Ukubalwa kwegazi okuphelele kungakunikeza ulwazi mayelana namaseli akho abomvu egazi, amaseli amhlophe egazi, nama-platelet.
- I-X-ray yesifuba: Lokhu kungasetshenziswa ukuhlola izifo zamaphaphu noma ukunqwabelana kwalezo zinto ezingavamile (ezingena) esikhulume ngazo ngaphambili.
- Ukukhula: Lokhu kuhlolwa kusiza ekutholeni izinhlobo ezahlukene zokutheleleka ngokuhlola igazi lakho, i-mucus, noma olunye uketshezi lomzimba.
Yiziphi izindlela zokwelapha i-Acute Chest Syndrome?
Kulesi simo , ukuqala ukwelashwa kusenesikhathi kuyindlela engcono kakhulu yokuvimbela izinkinga ezinkulu . Izindlela zokwelapha zifaka:- Ukumpontshelwa igazi: Lokhu kuhilela ukususa elinye igazi lakho bese unikeza igazi noma izingxenye zalo kumnikeli.
- Uketshezi lwe-IV: Lokhu kusiza ukuvimbela ukuphelelwa amanzi emzimbeni (ukugcinwa kwamanzi), okungenza isifo se-sickle cell sibe sibi kakhulu futhi kwandise ubuhlungu.
- Izibulali-zinhlungu: Imithi efana ne-'ketorolac' noma i-'opioids' inganikezwa ukulawula ubuhlungu.
- I-Incentive Spirometer: Le divayisi encane ikusiza ukuthi uphefumule ngokujulile. Isiza ukugcina amaphaphu akho ehlanzekile futhi esebenza kahle.
- Ukwelashwa komoya-mpilo okwengeziwe: Uma izinga lomoya-mpilo egazini liphansi, kunikezwa umoya-mpilo.
- Ama-antibiotic: Uma lesi simo sibangelwa ukutheleleka ngamagciwane, kunikezwa ama-antibiotic.
- Ama-antiviral: Uma imbangela iwukutheleleka ngegciwane, kunikezwa imithi efanele yokulwa namagciwane.
Ingabe ingozi yokuthola i-Acute Chest Syndrome ingancishiswa?
Uma unesifo se-sickle cell (SCD), kubalulekile ukukhuluma nethimba lakho lezokwelapha ngezindlela zokuvimbela i-Acute Chest Syndrome. Bangase basikisele izinto ezinjengalezi:- Ukufutha ibhodlela njalo: Nakuba kungase kubonakale kuyinto elula, lokhu kusiza ukugcina izindlela zakho zokuphefumula zihlanzekile futhi kunciphisa ukunqwabelana koketshezi olungadingekile emaphashini akho.
- Ukuvivinya umzimba njalo: Lokhu kungandisa amandla amaphaphu akho.
- Ukumpontshelwa igazi njalo: Abanye abantu bangase bakudinge lokhu.
- Ukuthatha imithi efana ne-'Hydroxyurea' noma i-'L-glutamine': Le mithi ingasiza ekunciphiseni ubuhlungu futhi inciphise ingozi yokulaliswa esibhedlela njalo. Kodwa-ke, le mithi kufanele ithathwe kuphela ngaphansi kweseluleko sikadokotela.
Uyini umbono (ukululama) womuntu onalesi simo?
Kubalulekile ukufuna ukwelashwa ngokushesha uma kwenzeka i-'Acute Chest Syndrome'. Ukwehluleka ukwenza kanjalo kungaholela ezinkingeni ezinkulu ezifana nalezi:- I-Acute Respiratory Distress Syndrome (ARDS): Lesi yisimo esibi samaphaphu esingasongela ukuphila.
- Isimo sengqondo esishintshile.
- Ukulimala kwezinso.
- Ukungasebenzi kahle kwesibindi.
- Ukwehluleka kwezitho eziningi.
- Ukwehluleka kokuphefumula okuphelele.
- Ubuhlungu obukhulu kakhulu.
- Ngeshwa, ngisho nokufa kungenzeka.
Ngokwezibalo, izinga lokufa kwabantu abadala ngenxa ye-'Acute Chest Syndrome' licishe libe ngu-4% . Phakathi kwezingane, leli nani licishe libe ngu -1% . Lokhu kusho ukuthi izimpilo eziningi zingasindiswa ngokwelashwa kusenesikhathi.Futhi, khumbula ukuthi noma ngabe i-'Acute Chest Syndrome' yelashwa futhi yelapheka ngempumelelo, umuntu one-'SCD' angase aphinde abhekane nalesi simo esikhathini esizayo .
Nginesifo se-sickle cell. Yini okufanele ngiyenze uma ngiba nezimpawu ze-Acute Chest Syndrome?
Lena yinto ebaluleke kakhulu. Uma une-SCD futhi uqala ukuzwa noma yiziphi izimpawu ze-Acute Chest Syndrome (ubuhlungu besifuba, ukuphelelwa umoya, ukukhwehlela, umkhuhlane), ungalibali umzuzu bese ucela iseluleko sezokwelapha ngokushesha .- Tshela odokotela ukuthi unesifo se-sickle cell uma uya ekamelweni lezimo eziphuthumayo noma kwesinye isikhungo sezokwelapha.
- Cela i-X-ray yesifuba ngokushesha . Lokhu kungaqinisekisa ngokushesha ukuthi une-Acute Chest Syndrome bese uqala ukwelashwa ngokushesha.
Khumbula, ukuthatha isinyathelo ngokushesha ngesikhathi esinjengalesi kungasiza kakhulu ekusindiseni impilo yakho.
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