Yu dɔn ɛva fil wan strenj pen we nɔ klia na yu bɛlɛ ɔ yu bak? Wi kin tink se na at atak ɔ smɔl injury na in bak. Bɔt tide wi go tɔk bɔt wan sik we kin kam wit di sem kayn sik, we nɔ kin apin smɔl, bɔt i rili impɔtant fɔ mek wi ɔl no bɔt. dεn kכl dis rεtropεritoneal fibrosis. Sɔmtɛm dɛn kin kɔl am bak Ɔmɔnd in sik.
Wetin na Retroperitoneal Fibrosis? Fɔ tɔk am simpul wan...
fכ simpul wan, rεtroperitoneal fibrosis na
di fכmeshכn fכ tisu we lεk ska (fibrosis) rawnd di כgan dεm na di spεs we dεn kכl rεtroperitoneum, di spεs bihayn wi bεlε. I tan lɛk skata we de fɔm na wi skin, bɔt i kin apin insay wi bɔdi. Bikɔs na wan sik we de go bifo, di sayn dɛm lɛk pen ɛn di urine we nɔ de kɔmɔt kin go wɔs as tɛm de go.
Okay, so wetin na dis retroperitoneum?
bכku pan di כgan dεm we de insay wi bεlε (lεk di liva, bεlε, intestכn) de rawnd wan mεmbran we de protεkt we dεn kכl di pεritoneum.
di spεs bihayn dis pεritoneum, we de tכwεd di spayna, dεn kכl am di rεtropεritoneum. Dis eria na di say we wi:
- Kidni dɛn
- Pat dεm na di urinary system
- Big big blɔd vesel dɛn we de kɛr blɔd go ɛn kam na di leg (fɔ ɛgzampul, di inferior vena cava) .
- imכtant כgan dεm lεk di adrenal gland dεm de de.
Aw dis kin afɛkt wi bɔdi?
as wi bin dכn tכk, fibrosis כ ska tisu de bכku sכmtεm, i de afekt di כgan dεm εn כda strכkchכ dεm na di rεtropεritoneum.
Bɔku tɛm, dis kin mɔs afɛkt di ureters, di tiub dɛm we de kɛr urine frɔm wi kidni to di blad. Imajin wetin kin apin we da tik tik de fɔm rawnd dɛn tiub dɛn ya ɛn tayt? I tan lɛk we yu de swɛt wata paip, we de mek di urine nɔ flɔ. If dis kכndyushכn kin bi siriכs,
kכmplikεshכn dεm we de mek yu layf de pan denja lεk we di kidni dεm nכ de wok fayn kin apin.
Udat kin gɛt di sik we dɛn kɔl retroperitoneal fibrosis?
Dis sik
kin mɔs pan man dɛm wae ol bitwin 40 ɛn 60. Dis min se man dɛm wae gɛt midul ej kin gɛt smɔl smɔl risk. Apat frɔm dat, sɔm ɔda tin dɛn de we kin mek pɔsin gɛt dis sik:
- Fɔ di wan dɛn we de wok wit tin dɛn lɛk asbest (bikɔs dɛn de ɛkspos to dɛn).
- Fɔ pipul dɛn we de smok ɛnFɔ di wan dɛn we de yuz tin dɛn we dɛn mek wit tabak .
Wetin kin mek dis apin? Di tin dɛn we kin mek pɔsin gɛt Ɔmɔnd in sik
Bɔrku tɛm,
e kin tranga fɔ fɛn wan patikyula kɔz fɔ dis. Insay mɛrɛsin, wi kin kɔl am
idiopathic . Dat min se "we dɛn nɔ no wetin mek i du." Bɔt sɔm kayn tin dɛn de we i kin apin as kɔmplikeshɔn fɔ ɔda sik. Sɔm pan di tin dɛn we kin mek i apin na:
- Sɔm mɛrɛsin (wi go tɔk bɔt dis smɔl).
- Tayp dɛm fɔ kansa , mɔ di Hodgkin lymphoma ɛn non-Hodgkin lymphoma.
- Di kɔndishɔn dɛn we pɔsin kin gɛt infɛkshɔn .
- Radiation therapy fɔ tin dɛm lɛk kansa.
- Damej pan di tisu dɛm na da eria de, ilɛksɛf na bikɔs ɔf ɔpreshɔn ɔ ɔda aksidɛnt.
Us kayn mɛrɛsin kin mek dis sik?
Dɛn dɔn si se dis sik kin apin we dɛn de yuz sɔm mɛrɛsin fɔ lɔng tɛm. Na sɔm ɛgzampul dɛn ya:
- Beta- blɔk na wan klas ɔf drɔgs we dɛn kin yuz fɔ mɛn at sik . Sɔm ɛgzampul dɛn na prɔpranɔlɔl, mɛtoprolɔl, ɛn atenɔlɔl.
- Dopamine antagonist na drɔgs wae dɛn kin yuse fɔ trit mɛntɛl sik ɛn nɔs. Ɛgzampul dɛn: mɛtildopa, pɔrgolyd.
- Hydralazine tablɛt fɔ ay blɔd prɛshɔn.
- Mɛrɛsin lɛk ergotamine, we dɛn kin yuz fɔ maygren.
- Sɔm mɛrɛsin dɛn we de mek pɔsin fil pen, mɔ di mɛrɛsin dɛn we de mek pɔsin fil pen ɛn NSAID .
Impɔtant: If yu de yuz dis kayn mɛrɛsin, nɔ panik. Nɔto ɔlman go gɛt dis sik. Bɔt i impɔtant fɔ no bɔt dis ɛn tɔk to yu dɔktɔ bɔt am.
Wetin na di sayn dɛm fɔ dis?
Di sayn dɛm kin difrɛn frɔm wan pɔrsin to ɔda pɔrsin. I dipen pan usay di fibrosis de ɛn aw i siriɔs.
We yu bigin, yu kin fil pen na yu bɛlɛ, yu bɔdi we de dɔŋ, ɔ yu flanks. Dis pen kin bi vague, min se e tranga fɔ pinpoint "ya ɛn de," ɛn e kin bi jɛnɛral pen. Ɔda sayn dɛn we de sho se yu gɛt dis sik na:
- I at fɔ muv yu leg ɛn muv rawnd.
- Hydrocele: Dis na wan sik we di man in tɛstikul dɛn kin swel.
- di leg dεm de swεla, di leg dεm de pen, כ di kכla na di skin na di leg dεm de chenj.
- Di urine we de kɔmɔt na di bɔdi dɔn go dɔŋ.
Wetin na di prɔblɛm dɛn we kin apin we pɔsin gɛt Ɔmɔnd in sik?
if di rεtroperitoneal fibrosis de go bifo, we min se di ska tisu de inkrεs εn bigin fכ kכmprεs di כgan dεm,
difrεn k כmplikεshכn dεm kin apin. Sɔm pan dɛn na:
- Anemia: Dis min se di nכmba fכ di rεd bכdi sεl dεm na di bכdi de dכn, כ jכs "blכd dεficiency".
- Anuria: Dis na wan sik we dɛn nɔ de pas urine atɔl. Dis na imejensi.
- Bɔdi we de it.
- Jandis: Di yay ɛn di skin kin yɔlɔ.
- Nɔs ɛn vɔmit.
- Nyurolɔjik kɔmplikeshɔn dɛn.
- Di day we di intestinal tisu de day (nɛkrɔsis).
- We yu de lɔs yu wet.
Aw dɛn kin no se pɔsin gɛt rεtroperitoneal fibrosis?
If yu gɛt dɛn sik ya, go to dɔktɔ ɛn dɛn go chɛk yu. Dis kin inklud:
- Fɔ ɛgzam fɔ yu bɔdi: Di dɔktɔ go fil yu bɛlɛ fɔ chɛk if yu gɛt ɛnitin we nɔ fayn, lɛk we yu gɛt lumps.
- Blɔd tɛst: Dɛn tin ya kin no di fɔs sayn dɛm fɔ di kidni sik ɛn kɔmplikeshɔn dɛm lɛk anemia.
- Renal (kidney) ultrasound: If di sayn dɛm sho se yu gɛt prɔblɛm wit yu kidni, dis tɛst kin no if yu gɛt fibrosis ɛn ɔda prɔblɛm dɛm.
- CT skan: Dis kin no aw di fibrosis siriɔs. I kin ɛp bak fɔ pul ɔda tin dɛn lɛk we di limf no dɛn we dɔn swel na di groin ɔ ɔda tɔŋ dɛn.
Yu tink se i nid fɔ mek dɛn du bayɔpsi?
bכku tεm dεm, dεn kin no rεtropεritכnial fכbrosis wit blכd tεst εn di imej tεst dεm we wi bin dכn tכk bכt (ultrasound, CT scan). Bɔt insay sɔm spɛshal kes dɛn
, i kin nid fɔ tek bayɔpsi. Dis min se yu fɔ tek wan pat pan di tisu ɛn chɛk am ɔnda maykroskɔp. Dɛn kayn kes dɛn ya na:
- If pɔsin we dɛn tink se gɛt kansa ɔ infekshɔn.
- If di fɔs tritmɛnt nɔ wok fayn.
Us kayn tritmɛnt a nid?
Di bɛst tritmɛnt fɔ yu go dipen pan di say we di fibrosis de ɛn aw i siriɔs. Na di fɔs stej dɛm fɔ Ɔmɔnd in sik, yu tritmɛnt kin inklud:
- Kɔtikosterɔyd dɛn:Dɛn mɛrɛsin ya kin ridyus di inflamɛns na di bɔdi kwik kwik wan ɛn stɔp di divɛlɔpmɛnt fɔ di fibrosis.
- Immunomodulators: Dɛn mɛrɛsin ya de wok bay we dɛn de chenj di we aw di imyun sistɛm de wok. Dis kin ridyus di risk fɔ mek fibrosis kam bak tumara bambay. Bɔt bikɔs imyunomodulator kin tek sɔm mɔnt fɔ wok, dɛn kin gi dɛn wit kɔtikosterɔyd.
- Aw fɔ mɛn di mɛrɛsin: Sɔntɛnde, if na wan mɛrɛsin wae yu de tek na di fibrosis, yu dɔktɔ kin chenj di mɛrɛsin ɔr ridyus di doz.
If fibrosis dɔn go bifo, dɛn kin nid ɔda tritmɛnt dɛn:
- Ɔpreshɔn: I kin nid fɔ du ɔpreshɔn fɔ pul di fibrotic tisu ɛn fɔ mek ɛni damej pan di tisu dɛn we de rawnd am.
- Stent: As wi bin dɔn tɔk, if di ureter blok, dɛn kin put smɔl tin we tan lɛk tiub (stent) insay am fɔ mek i opin.
Aw wi kin mek di rεtroperitoneal fibrosis nכ de?
Bikɔs dis sik kin bi idiopathic,
i nɔ kin izi fɔ mek dɛn nɔ gɛt am kpatakpata. Bɔt bikɔs dɛn no se sɔm mɛrɛsin dɛn kin mek yu gɛt am, yu dɔktɔ go mɔs de wach yu fɔ si if yu gɛt fibrosis, mɔ if yu de tek dɛn fɔ lɔng tɛm.
Yu tink se dɛn kin ridyus di chans fɔ mek dis apin bak afta dɛn dɔn trit am?
If yu gɛt fɔ du ɔpreshɔn, sɔntɛnde dɛn kin rap wan layt we gɛt fat tisu rawnd di ureter we dɛn de du di ɔpreshɔn. Dɛn se dis kin mek i nɔ izi fɔ mek di fibrosis bigin bak.
Aw kwik a go fil fayn?
If yu de tek mɛrɛsin lɛk kɔtikosterɔyd, ɔ afta yu dɔn tek mɛrɛsin
, yu kin bigin fɔ fil fayn insay sɔm wiks. Bɔt if yu nid imyunomodulator, stent, ɔ ɔpreshɔn, i go tek smɔl tɛm fɔ mek yu wɛl.
Wetin na de luk fɔ pipul dɛm wae gɛt retroperitoneal fibrosis?
Bɔku pipul dɛn kin mek dɛn wɛl ful wan. Di bɛst chans fɔ mek di tritmɛnt go bifo na
we dɛn no di sik kwik kwik wan. Bɔt i impɔtant fɔ mɛmba se fibrosis kin kam bak sɔm mɔnt ɔ ia afta dɛn dɔn trit am.
Aw e tan lɛk fɔ liv wit Ɔmɔnd in sik?
Fɔ di wan dɛn we gɛt smɔl sik,
yu go nid fɔ kɔntinyu fɔ de ɔnda dɔktɔ. Dis min se yu go nid fɔ go to yu dɔktɔ ɔltɛm fɔ chɛk fɔ si if di sik de kam bak.
Wetin kin apin afta dɛn dɔn du di ɔpreshɔn fɔ kɔrɛkt di we aw di wata we de kɔmɔt na di wata we de urinary trakt?
Hydronephrosis kin apin we, insay sɔm dez afta dɛn dɔn du di ɔpreshɔn, dɔktɔ dɛn kin pul di urine we dɔn gɛda na yu kidni wantɛm wantɛm.Yu fɔ no bɔt di kɔmplikeshɔn we dɛn kɔl "urinary retention." We di urine we dɔn trɔp na di bɔdi kɔmɔt wantɛm wantɛm, dɛn tin ya kin apin:
- Ilektrolayt imbalans na di bɔdi.
- Di wata we nɔ de na di bɔdi.
- Hypovolemic shock (na wan kכndyushכn we de kכz bay we di bכdi de dכn).
Retroperitoneal fibrosis, ɔ Ormond’s disease, na wan sik we de mek tisu we tan lɛk ska de fɔm na di bak pat na di bɛlɛ. Pipul wae de tek sɔm mɛrɛsin kin gɛt dis sik. If dɛn dɔn no se yu gɛt dis sik, tɔk to yu dɔktɔ bɔt ɛni kwɛstyɔn ɔ tin we de mɔna yu. Dɛn de de fɔ ɛp yu.
Di tin dɛn we impɔtant pas ɔl fɔ mɛmba (Take-Home Message) .
Okay, so naw wi dɔn ɔndastand mɔ bɔt wetin na Retroperitoneal Fibrosis.
Pan ɔl we na sik we nɔ kin apin so ɔltɛm, i rili impɔtant fɔ no bɔt am.- mεmba se dis na tik tik we de fכm rawnd di כgan dεm we dεn se de insay di bכdi, tכwεd di spayna.
- Bɔku tɛm i kin afɛkt di ureters ɛn i kin pwɛl di kidni dɛn.
- Nɔto ɔltɛm de kɔz kin klia, bɔt tin lɛk sɔm mɛrɛsin, kansa, ɛn infɛkshɔn kin bi kɔz bak.
- I impɔtant fɔ go to dɔktɔ if yu gɛt sɔm sayn dɛn lɛk we yu nɔ de fil pen na yu bɛlɛ/bak ɛn yu nɔ de pis.
- Gud tritmɛnt dɛn de if dɛn no am kwik. So nɔ ignore di sayn dɛm.
- If yu gɛt ɛni kwɛstyɔn bɔt dis, nɔ fred fɔ aks yu dɔktɔ.
Wi op se dis infɔmeshɔn go ɛp yu. Stay wit wɛlbɔdi!
Retroperitoneal Fibrosis, Ormond in sik, kidni sik, bɛlɛ pen, urinary prɔblɛm, fibrosis, ɔpreshɔn
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