Kua pāngia koe e te mamae upoko nui, pumau tonu, kāore i memeha mō ngā rā? Kāore rānei i te mōhiotia e koe he wā pōhēhē, he ngoikore, he ngoikore tinana hōhonu rānei? Ahakoa e warewarehia ana ēnei tohu, he tohu whakatūpato pea ēnei mō tētahi mate kino kei raro. I tēnei rā, kei te kōrero tātou mō tētahi kaupapa hauora uaua engari he mea nui e pā ana ki tō roro me tō taurakira: te CNS Vasculitis.
He aha te CNS Vasculitis? Me whakamārama tātou.
I roto i ngā kupu māmā, ko te ( CNS Vasculitis ) he mumura o ngā oko toto i roto i tō Pūnaha Io Matua (CNS) — te whatunga kei roto ko tō roro me tō taurakira. Pērā i te pupuhi o tō kiri i muri i te whara, ka pupuhi ēnei oko toto nui, ka aukati i te rere o te toto. Ka kīia pea tēnei e ngā tākuta ko te angitis tuatahi o te pūnaha io matua , ko te angitis granulomatous rānei.
Whakaarohia tō pūnaha io matua hei pokapū whakahaere matua mō tō tinana. Mā tēnei pūnaha e whakahaere ngā mea katoa mai i ō nekehanga ā-ringa—pēnei i te pato i tō waea pūkoro—ki ngā tukanga aunoa pēnei i te pao o tō ngākau me te manawa. Ina pāngia ngā uaua toto o tēnei wāhi nui, he mea nui tēnei e hiahia ana kia aro nui atu tō kaiwhakarato hauora ki Nirogi Lanka.
He momo rerekē te CNS Vasculitis?
Ae, e rua ngā wāhanga matua o tēnei e whakarōpūhia ana e ngā tohunga hauora:
1. Te Vasculitis Matua o te CNS: Ka puta motuhake tēnei, arā, kāore i puta mai i tētahi atu mate, i tētahi atu āhuatanga pūnaha rānei.
2. Te Vasculitis Tuarua o te CNS: He hua tēnei nō tētahi atu raruraru hauora. He maha ngā wā ka puta mai i ngā mate pūnaha ārai mate (inā he whakaekenga hē tō pūnaha ārai mate i tō ake tinana) me ngā mate pūnaha rānei.
Te Mōhio ki ngā Tohu
Ka rerekē ngā tohu o te CNS Vasculitis i ia tangata, i ia tangata, engari ko ngā tohu whakatūpato noa ko:
- Ngā ānini nui, pumau: He rerekē ki ngā ānini taumaha noa, he kaha tonu ēnei, ā, ka roa mō ngā rā.
- Te pōhēhē, ngā huringa hinengaro rānei: Te ngaro ohorere o te mahara, te uaua rānei ki te arotahi.
- Te ngenge, te mākūkū, ngā panonitanga o te kare ā-roto: Ngā kare ā-roto rerekē o ō ringaringa me ō waewae.
- Ngoikore tinana: He kare ā-roto o te ngenge nui, te ngaro rānei o te kaha o ngā uaua.
- Ngā huringa tirohanga: Te tirohanga pōuri, te tirohanga takirua rānei.
- Ngā Āwangawanga: Te wiri ohorere, te ngaromanga rānei o te māramatanga, te kore rānei e mōhiotia.
- Encephalopathy: Ngā huringa o te whanonga, te tuakiri, te hinengaro rānei.
Ki te pāngia koe e tētahi o ēnei tohu, he mea nui kia rapu awhina hauora tonu. Nā te mea ka taea e ēnei tohu te taupatupatu ki ētahi atu mate, he mea nui te tātaritanga ngaio hei tautuhi i te pūtake.
Ngā raruraru pea
Nā te mea ka aukati te mumura i te rere o te toto, ka pā pea he kino roa ki te roro me te taurakira. Ko ngā raruraru nui pea ko:
- Ngā whiu
- Ngā whakaekenga ischemic poto (TIA) (e kiia ana ko ngā "whiu-iti")
- Ngā aneurysms roro
He āhuatanga ohorere hauora ēnei.Ki te whakapae koe kei te pāngia koe e te whiu, e te aneurysm rānei, haere ki te rūma whawhati tata, waea atu rānei ki te 911 tonu.
He aha ngā take o te CNS Vasculitis?
E kiia ana te CNS Vasculitis he mate pūnaha ārai mate , ina he te aro o tō pūnaha ārai mate ki tō ake kiko hauora o ngā oko toto.
- He maha ngā wā ka kore e mōhiotia te pūtake tuturu o te mate pūkahukahu o te pūnaha io (CNS Vasculitis) .
- Ko te Vasculitis CNS Tuarua e hono ana ki ētahi atu mate mumura, tae atu ki:
- Lupus
- Granulomatosis me te polyangiitis
- Te granulomatosis eosinophilic me te polyangiitis (EGPA)
- Te polyangiitis moroiti
- Te mate a Behçet
- Te mate a Sjögren
- Ngā mate urutā: te huaketo Epstein-Barr, te huaketo varicella-zoster
- Ngā mate kitakita: Kohi, Syphilis
Ko wai kei te mōrearea?
Ahakoa ka taea e te tangata katoa te pāngia e te CNS Vasculitis, he nui ake te kitea i roto i ngā tāne i ngā tatauranga. Ahakoa he maha ngā wā ka kitea ai tēnei mate i roto i te hunga e 50 tau te pakeke, ka taea tonu te pā ki ngā tau katoa.
Me pēhea te tātaritanga?
Ko te tātaritanga he whakamātautau tinana hōhonu me te arotake i tō hītori hauora. Kia rite ki te whakaahua i te roa o te mau o ō tohu me te mea ka hoki mai anō. He maha ngā wā he tukanga tātaritanga rerekē te tātaritanga - me te whakakore i ētahi atu mate noa i te tuatahi. Ka tono pea tō tākuta:
- MRI (Whakaahua Āhua Aukume)
- Matawai CT
- Angiogram
- Ngā koiora
Tērā pea ka tukuna koe ki tētahi Tākuta Rheumatologist , he tohunga ki ngā mate mumura me ngā mate pūnaha ārai mate.
Ngā Tohu hei Āwhina i te Tātaritanga
Ko ngā "tohu" he tohu mō tētahi mate. Ka taea e tō tākuta te tautuhi i ēnei mā roto i ngā whakamātautau taiwhanga i runga i ō toto, i ētahi atu wai tinana rānei. Hei kite i ngā tohu o te Vasculitis o te Pūnaha Nervous Matua (CNS), ka whakamahia pea e tō tākuta ētahi whakamātautau motuhake:
- Ngā whakamātautau toto: Hei tirotiro mō te anemia.
- Whakamātautau ESR (Te Auau Whakatakotoranga Erythrocyte): He tohu e whakamahia ana hei kite i te mumura i roto i tō tinana.
- Whakamātautau pūmua C-reactive (CRP): Hei tirotiro i ngā tohu mumura e tukuna ana e te ate.
- Werohanga lumbar: He tikanga e kohia ai te wai o te tuaiwi roro hei tirotiro i te nui o ngā toto toto ma.
He aha ngā maimoatanga mō tēnei?
Ka tūtohu tō tākuta i ngā maimoatanga e aro ana ki te whakahaere i te mumura. Ko te whāinga matua i te rongoā i te CNS Vasculitis ko te whakaiti i te kino ki tō roro me tō taurakira. Ko te nuinga o ngā tūroro me whakamahi i te huinga o ngā Corticosteroids (rongoā hei whakaiti i te mumura) me ngā Immunosuppressants (rongoā hei pehi i te pūnaha ārai mate).
I te tīmatanga, me nui ake pea ngā horopeta rongoā e hiahiatia ana. I roto i te wā (i muri i ētahi marama), ka whakaitihia pea e tō tākuta te auau, te horopeta rānei o te maimoatanga. Ko te whāinga kia tae koe ki te wā "whakaora", arā, he iti noa iho ō tohumate, he ngaro rawa rānei.
Mena kei a koe te mate pukupuku CNS tuarua, me whai maimoatanga tāpiri koe hei whakahaere i te mate taketake i puta ai. Ma tō tākuta e whakamārama taipitopito tēnei tukanga ki a koe.
Āhea ahau me toro atu ki te tākuta?
Kia tūpato ki ō tohumate, ā, kia mau ki te tuhi i ngā huringa katoa. Mēnā ka kite koe kei te piki haere te auau o ngā tohumate, kei te kaha haere rānei, whakapā atu ki tō tākuta tonu. Me whakamōhio atu hoki ki tō tākuta mēnā kei te whakaaro koe kāore tō mahere maimoatanga o nāianei e mahi ana pērā i te mea e tumanakohia ana.
Mā tō tākuta koe e tohutohu mō te auau e tika ana mō ngā wā tirotiro whai muri me ngā whakamātautau toto, whakamātautau tātaritanga rānei.
Mena ka pāngia koe e tētahi o ngā tohu e whai ake nei, rapua tonutia te āwhina ohorere, waea atu rānei ki te 911:
- Mena kei te whakapae koe i ngā tohu o tete whiu, te pakaru rānei o te aneurysm o te roro.
- Mena ka pāngia koe e te uaua ki te manawa.
- Mena ka rerekē ō tirohanga, ka ngaro rānei tō tirohanga.
He aha ngā mea ka tumanakohia e au mēnā kei a au te Vasculitis o te Pūnaha Nervous Matua?
Kāore he "rongoa" tuturu mō te CNS Vasculitis. Heoi, ina kitea e koe te huinga rongoā tika, ka taea e te tini o te tangata te noho mārire me te kore tohu mō te wā roa. Tērā pea ka noho ētahi tāngata mō ngā marama, mō ngā tau rānei kāore he tohu i mua i te putanga mai anō.
I te nuinga o te wā, kāore te CNS Vasculitis e tino pā ki te roanga o te oranga. Heoi, he uaua ki te whakawhanui i tēnei mea nā te mea ka taea e te mate te arahi ki ngā raruraru nui pērā i te whiu, i te aneurysm rānei. Mēnā ka puta ēnei raruraru, ka piki ake pea te mōrearea o ngā huihuinga morearea ki te ora.
Mena kei te āwangawanga koe mō tō hauora, mō te pānga rānei o te CNS Vasculitis ki tō oranga, tēnā kōrero mārire ki tō tākuta.
He mea whakamataku pea tētahi āhuatanga e pā ana ki tō Pūnaha Io Matua (CNS), inā koa ko te mōhio kei te kino tō ake pūnaha ārai mate ki tō roro me tō taurakira. Ko te rongo pai ko te nuinga o te hunga whai CNS Vasculitis ka kitea he tikanga maimoatanga hei pupuri i te āhua kia kore e pāngia. Kia kitea e koe te maimoatanga tika, ka āwhina tō tākuta i a koe ki te whakaiti i te pānga o te mate ki tō oranga o ia rā.
Kia maumahara, ehara i te mea kino te pātai mō tō hauora. Kōrerohia ō āwangawanga katoa ki tō tākuta. Mā rātou koe e whakautu, ā, mā rātou koe e āwhina kia māia ki ngā mea e tupu ana i roto i tō tinana me pēhea te whakahaere.
Te Take Matua
He mate kino te CNS Vasculitis, engari ka taea te whakahaere mā te maimoatanga tika. Ko te mea nui ko te rapu tohutohu hauora i te wā tonu ka puta ngā tohu, me te piri tonu ki te mahere maimoatanga kua whakaritea e koe. He mea nui te pupuri i tētahi hononga kaha me tō tākuta i a koe e noho ana me tēnei mate. Mā te whai i ā rātou tohutohu me te whakapuaki i ngā huringa ka pā ki a koe, ka taea e koe te ora angitu ahakoa tēnei tātaritanga. Kaua e mataku; ehara koe i te mea ko koe anake. Mā te aratohu hauora tika, ka taea te whakahaere pai i tēnei mate.
Ngā Kupumatua: Te Vasculitis o te CNS, Te Pūnaha Io Matua, te mumura o ngā oko toto, te roro, te taurakira, te mate pūnaha ārai mate, te ānini, Nirogi Lanka
