Ingaba i-cartilage yakho iyanyibilika? Masifunde ngesi sifo singaqhelekanga (i-Relapsing Polychondritis)?

Ngamanye amaxesha unokufumana iintlungu ezingaqhelekanga kunye nokudumba kwiindawo ezahlukeneyo zomzimba wakho, akunjalo? Ingakumbi kwiindawo ezifana neendlebe zakho kunye nempumlo. Ezi zisenokungabi zizinto nje ezingaqhelekanga. Namhlanje siza kuthetha ngesifo esingavamanga kangako, kodwa kubaluleke kakhulu ukwazi ngaso. Oku kubizwa ngokuba yiRelapsing Polychondritis . Nangona eli gama liyinkimbinkimbi kancinci, masiliqonde ngokulula.

Yintoni le sifo?

Ngamafutshane, i-Relapsing Polychondritis sisifo esingaqhelekanga esichaphazela i-cartilage emizimbeni yethu. Okwenzekayo kukuba i-cartilage iyavuvukala (ukudumba, ukubomvu, kunye nentlungu) kwaye ngokuhamba kwexesha, i-cartilage iyaphela kancinci (iyanyibilika kwaye iphele). Ngoku usenokuba uzibuza ukuba yintoni le cartilage. I-Cartilage sisicwili esikhethekileyo esidibanisayo emizimbeni yethu. Uyakhumbula, chukumisa iindlebe zethu, chukumisa umphambili wempumlo yethu. Kukho loo ndawo iguquguquka kancinci, kodwa inamandla kuloo ndawo, yi-cartilage. Ezi zifumaneka kwiindawo ezininzi kumalungu ethu, emqaleni, nakwi-trachea. Esi sifo 'seRelapsing Polychondritis' sichaphazela kakhulu:

• Kwi-cartilage endlebeni zakho.
• Kwi-cartilage empumlweni yakho.
• Ingxolo yakho (ibhokisi esithetha kuyo) ikwindawo yakho yomqala .
• Umbhobho wakho womoya (i-trachea) .

Esi sifo sibizwa ngamanye amagama amaninzi, kodwa singonyango ngakumbi: `Chronic atrophic polychondritis`, `Generalized or systemic chondromalacia`, `Meyenburg-Altherr-Uehlinger syndrome`, `Relapsing perichondritis`, `Von Meyenburg disease`. Nangona kunjalo, igama elisetyenziswa kakhulu yi`Relapsing Polychondritis`.

Ngubani onokuyifumana le nto? Ixhaphake kangakanani?

Le meko inokuchaphazela nabani na. Nangona kunjalo, idla ngokuqala kubantu abaphakathi kweminyaka engama-40 ukuya kwengama-60. Ngokwendlela exhaphake ngayo, eneneni sisifo esingaqhelekanga . Ngokutsho kwabaphandi, sichaphazela malunga nomntu omnye kubantu abangamakhulu amabini anamashumi asibhozo anesihlanu amawaka (285,000). Oku kuthetha ukuba sichaphazela inani elincinci kakhulu labantu kuluntu olukhulu. Yiyo loo nto esi sifo singathethwa kakhulu kuluntu.

Kutheni oku kusenzeka? Yintoni unobangela?

Umbuzo abantu abaninzi abanawo ngowokuba, "Kutheni esi sifo sisenzeka?" Ukuba ndithetha inyani, izazinzulu azikafumani ukuba yintoni kanye kanye ebangela iRelapsing Polychondritis. Nangona kunjalo, ezinye izazinzulu zikholelwa ukuba sisifo esibangelwa kukuzimela komzimba.Ngoku usenokuba uzibuza, "Yintoni le sifo sokuzikhusela komzimba?" Ngamafutshane, imizimba yethu inenkqubo yokuzikhusela komzimba. Umsebenzi wayo kukusikhusela kwizifo ngokulwa neentsholongwane zasemzini. Kufana nokuba neqela lamajoni emizimbeni yethu. Kodwa kwizifo zokuzikhusela komzimba, amajoni ethu ngempazamo aqala ukuhlasela iiseli zethu eziphilileyo kunye nezicubu . Kwi-Relapsing Polychondritis, kucingelwa ukuba inkqubo yokuzikhusela komzimba ihlasela i-cartilage yethu ngale ndlela. Kodwa, akukacaci ukuba kutheni oku kusenzeka.

Zithini iimpawu zoku?

I-polychondritis ephinda ibuyele esiqhelweni ayisiyonto iqhubekayo. Iza ize iphele ngeziqendu okanye ngokuqhambuka. Xa iimpawu zivela, zinokuhlala iintsuku okanye iiveki ezimbalwa. Emva koko ziyaphela. Nangona kunjalo, iimpawu zinokuphinda zibuye emva kweminyaka emininzi. Iimpawu zokuqala: Kubantu abaninzi, esi sifo siqala ngentlungu, ukuthamba, ukudumba, kunye nokubomvu kwindlebe enye okanye zombini . Okubalulekileyo, ezi mpawu zichaphazela i-cartilage ngaphakathi nangaphandle kwendlebe, kodwa kungekhona i-earlobe . Ngamanye amaxesha indlebe isenokutyibilika . Khawuthelekelele ukuba ngenye imini, umhlobo wakho uSunil ngequbuliso unendlebe ebuhlungu, ebomvu, nevuvukileyo. Wayecinga ukuba yi-allergy nje. Yaphela kwiintsuku ezimbalwa. Kodwa emva kweenyanga ezimbalwa, enye indlebe yaphinda yafana. Le yindlela iimpawu zoku ezinokuqala ngayo ukubonakala. Ezinye iimpawu:

• Ukuvaleka kwe- cartilage yempumlo: Oku kunokubangela ukuba ibhulorho yempumlo iwe, nto leyo ebangela imeko ebizwa ngokuba yi-saddle nose deformity (impumlo ifana ne-saddle emqolo wehashe).
• Intlungu yamalungu : Intlungu yamalungu , efana ne -arthritis , inokubakho.
• Ukuxinana kwempumlo .
• Intlungu embindini wesifuba , kufutshane nethambo lesifuba .
• Intlungu yamehlo kunye nokubomvu .
• Ukuba indlebe yangaphakathi ichaphazelekile: Ukulahlekelwa kukuva, ukukhala rhoqo ezindlebeni (i-tinnitus) ,Izinto ezifana nesiyezi (vertigo) zinokwenzeka.
• Ubunzima bokuphefumla: Oku kwenzeka xa umphimbo womoya (i-trachea) uchaphazelekile. Ubunzima bokuthetha bunokubakho xa umphimbo womlomo uchaphazelekile.

Kubalulekile: Ubunzima bokuphefumla bunokuba yingozi, ngoko funa ingcebiso kagqirha ngokukhawuleza.

Iimpawu ezingaqhelekanga: Ezi azibonakali rhoqo, kodwa abanye abantu banokuzibona:

• Iingxaki zevalvu yentliziyo.
• Isandi sentliziyo esingaqhelekanga (Intliziyo ikhalaza).
• Ukulahleka kombono.
• Isifo sezintso.

Phi ? Oogqirha bayifumana njani le nto?

Ukuba unale mpawu, kungcono ukubona ugqirha. Nangona kunjalo, akukho vavanyo lunye olunokuxilonga iRelapsing Polychondritis. Oko kukuthi, akukho vavanyo lunye lwegazi okanye iskeni esinokukuxelela ukuba "le yiRelapsing Polychondritis." Ugqirha uya kucinga ukuba unesifo ukuba ubuneempawu ezintathu kwezi mpawu ixesha elide. Umzekelo, ukuba uneempawu ezidibeneyo ezifana nokudumba kwe-cartilage endlebeni yakho, ukudumba kwe-cartilage empumlweni yakho, kunye nentlungu yamalungu, ugqirha wakho unokukucinga oku. Ngamanye amaxesha, ukunceda ukuqinisekisa ukuxilongwa:

• I-biopsy ingenziwa ngokuthatha iqhekeza le-cartilage endlebeni .
• Kunokwenziwa uvavanyo lwegazi oluninzi (ukuqinisekisa ukuba azikho ezinye iimeko zonyango kwaye kukhangelwe iimpawu zokudumba).

Luluphi unyango lwale nto?

Ngelishwa, akukho nyango lwe-Relapsing Polychondritis. Oko kukuthi, akukho nyango okwangoku. Nangona kunjalo, oko akuthethi ukuba akukho nto inokwenziwa. Iinjongo eziphambili zonyango zezi:

• Ukunciphisa iimpawu (ukunciphisa iintlungu, ukudumba).
• Ukunciphisa umngcipheko weengxaki.

Unyango ludla ngokuqala ngamayeza anje:

• I-Colchicine: Eli liyeza elidla ngokunikezelwa kwi-gout.
• IiCorticosteroids: Umzekelo , i-prednisone . La ngamayeza anamandla anciphisa ukudumba.
• I-Dapsone: Eli liyeza elisetyenziselwa ukulwa nezifo.
• Amayeza angengo-steroidal alwa nokuvuvukala (ii-NSAID): La mayeza anceda ekunciphiseni iintlungu nokudumba.

Ukuba imeko imbi kakhulu, oogqirha banokukunika amayeza afana nala:

• Amayeza acinezela inkqubo yomzimba yokuzikhusela: Umzekelo , i-cyclophosphamide okanye i-azathioprineOko kwenziwa zezi zinto kukunciphisa umsebenzi wenkqubo yomzimba yokuzikhusela engasebenzi kakuhle.
• I-Methotrexate: Eli liyeza elithintela amajoni omzimba elisetyenziselwa ukunyanga izifo ezifana ne-arthritis.

Kwiimeko ezinzima kakhulu, utyando lunokufuneka:

• Utyando lwevalvu yentliziyo: Ukuba iivalvu zentliziyo zonakele.
• I-Tracheostomy: Ukuba umbhobho womoya uvalekile kakhulu, kunokufuneka kufakwe umbhobho ngqo usuka emqaleni ungene kumbhobho womoya.
• Iindlela zokuvula indlela yomoya:
• Ukubeka i-stent: Ityhubhu encinci, efana ne-stent ye-laryngeal, ifakwa kwi-larynx okanye kwi-trachea ukuze ihlale ivulekile.
• Ukwandiswa komoya: Isixhobo, esifana nebhaluni, sisetyenziselwa ukwandisa indlela yomoya enciphileyo.
• Utyando lokwakha kwakhona i-trachea okanye i-larynx .

Ngaba oku akunakuthintelwa ukuba kwenzeke?

Ekubeni unobangela ochanekileyo we-Relapsing Polychondritis ungaziwa , kunzima ukutsho indlela yokuyithintela. Okwangoku, akukho zicwangciso zithile zokuthintela .

Ingaba esi sifo siyabulala? Ingakanani iminyaka omele uyiphile?

Oku kunokuvakala kuyoyikisa, kodwa ubomi obulindelekileyo kubantu abane-Relapsing Polychondritis buhlala bulungile . Izifundo zibonisa ukuba ama-95% ezigulana asaphila emva kweminyaka esi-8 emva kokuba efunyenwe ene-HIV. Nangona kunjalo, inokubangela iingxaki ezisongela ubomi . Ubunzima bokuphefumla buyingozi kakhulu. Kukwakho nomngcipheko wokuva okanye ukulahleka kokubona okungapheliyo . Ke ngoko, kubaluleke kakhulu ukuqaphela iimpawu kwaye uthathe unyango njengoko luchazwe ngugqirha wakho.

Oku kuza kuhlala ixesha elingakanani?

I-Relapsing Polychondritis sisifo esingapheliyo . Oku kuthetha ukuba asiyomeko eza ize idlule, kodwa yimeko yobomi bonke . Nangona kunjalo, ngonyango olufanelekileyo, unokunciphisa ukuphindaphindeka kweempawu kwaye unciphise ubukhali beempawu xa zisenzeka. Ke ngoko, kubalulekile ukuthetha nogqirha wakho kwaye uphuhlise isicwangciso sonyango esikusebenzelayo.

Yintoni enye onokuyibuza ugqirha?

Ukuba ugqirha wakho uthi une-'Relapsing Polychondritis', ungabuza imibuzo efana nale ukuze ufunde okungakumbi ngayo:

• "Gqirha, imeko yam imbi kangakanani?"
• "Ngawaphi amayeza afanelekileyo kum?"
• "Ngaba kufuneka ndenze uvavanyo olukhethekileyo kumalungu am anje ngamehlo, iindlebe, inkqubo yokuphefumla, intliziyo, kunye nezintso?"
• "Ngaba kufuneka ndidibane nezinye iingcali (umz., ingcali yendlebe, impumlo, umphimbo, ingcali yamalungu)?"
• "Ngaba kukho into endinokuyenza mna ngokwam ukuqinisa i-cartilage yam, okanye ukunciphisa isantya sokulahleka kwe-cartilage?"
• "Ngaba kukho uphando olutsha okanye iimvavanyo zeklinikhi ezenziwayo kwesi sifo?"

Ngokubuza le mibuzo, ungayiqonda ngcono imeko yakho kwaye uthathe inxaxheba ngokukhutheleyo kunyango lwakho.

Ndifanele ndimbone nini ugqirha ngokukhawuleza?

Ukuba une-Relapsing Polychondritis, kubaluleke kakhulu ukuba uhlale udibana nogqirha wakho rhoqo . Kwakhona, ukuba unengxaki yokuphefumla, utshintsho embonweni, okanye ukuva , ungalindi de kube yintlanganiso yakho elandelayo. Funa ingcebiso kagqirha ngokukhawuleza . Ezi ngamanye amaxesha zinokuba ziimeko ezifuna unyango olukhawulezileyo.

Ngoko ke, zeziphi izinto ekufuneka sizikhumbule?

Usenokuba sele uyiqonda into ebesithetha ngayo, `i-Relapsing Polychondritis`. Okokugqibela, ezona zinto zibalulekileyo ekufuneka uzikhumbule zezi:

• I-Relapsing Polychondritis sisifo esingaqhelekanga apho i-cartilage emzimbeni ivuvukala ize yonakale.
• Amaxesha amaninzi, iindlebe kunye nempumlo zijoliswe kuzo, kodwa zinokuchaphazela neendawo ezifana nomqala, umphimbo, kunye namalungu.
• Isizathu esichanekileyo soku asikafunyanwa, kodwa kurhanelwa ukuba yimeko yokuzikhusela komzimba.
• Nangona kungekho nyango lupheleleyo, kukho unyango lokulawula iimpawu nokunciphisa iingxaki.
• Ngenxa yokuba izinto ezinje ngobunzima bokuphefumla zinokuba yingozi, kubalulekile ukuqaphela iimpawu kwaye ubone ugqirha ngokukhawuleza.

Ukuba wena okanye umntu omaziyo unezinye zezi mpawu, ungoyiki ukubona ugqirha aze afumane ingcebiso. Ukuzazi zonke izifo kuya kukunceda uphile ubomi obusempilweni! Ukuphinda ubuye kwi-Polychondritis, iCartilage, iintlungu zendlebe, ukudumba kwempumlo, ubunzima bokuphefumla, iintlungu zamalungu, isifo sokuzikhusela komzimba, ukudumba, izifo ezingaqhelekanga