Kuvamile ukukhathazeka kancane uma ingane yakho ibona ngokuzumayo amabala amancane ansomi emzimbeni wayo, ikakhulukazi emilenzeni nasezinqeni zayo, ngemva kokudlala ngenjabulo. Ngezinye izikhathi lawa mabala angahambisana nobuhlungu besisu nobuhlungu bamalunga. Uma sibona into efana nale, sicabanga ngento eyodwa emva kwenye. Ngakho-ke namuhla sizokhuluma ngesimo esingabangela lezi zimpawu, kodwa isikhathi esiningi akusikho okufanele sikhathazeke ngakho, kodwa kubaluleke kakhulu ukuqaphela. Lokho yi-Henoch-Schonlein Purpura, noma i-HSP ngamafuphi.
Yini i-Henoch-Schönlein Purpura (HSP)?
Kalula nje, i-Henoch-Schonlein Purpura (HSP) yisimo lapho imithambo yegazi emincane emizimbeni yethu ivuvukala noma ivuvukala. Odokotela bakubiza lokhu ngokuthi "i- vasculitis ." Cabanga ngakho njengokucasuka nokuvuvukala kwemithambo yegazi emincane emizimbeni yethu. Lokhu kuvuvukala yikho okubangela zonke lezi zinkinga.
Uma imithambo yegazi ivuvukala ngale ndlela, amangqamuzana amancane egazi aqala ukuvuza. Njengoba nje ipayipi lamanzi livuza amanzi. Lawa mangqamuzana egazi angavuza esikhumbeni, ezithweni zangasese (njengezitho zangasese ezimanzi ngaphakathi kwemilomo nasemakhaleni ethu), noma ezithweni zangaphakathi. Uma evuza esikhumbeni, abangela lawo mabala ansomi, afana nokuklwebheka. Siwabiza lawo mabala ngokuthi `(purpura)`.
Ngokuvamile, lesi simo se-HSP sithinta imithambo yegazi esikhumbeni, emalungeni, emathunjini (emathunjini), nasezinso. Kodwa izindaba ezinhle ukuthi izingane eziningi ezithola i-HSP ziyalulama ngokuphelele phakathi namasonto ambalwa ngaphandle kwezinkinga zesikhathi eside . Ngakho-ke kubalulekile ukwazi iqiniso ngaphambi kokuba wethuke.
Yiziphi izimbangela ze-HSP?
Odokotela abakakwazi ukusho ngokuqinisekile ukuthi yini ebangela i-HSP. Kodwa bacabanga ukuthi kungenzeka ukuthi iqala ngemva kokutheleleka . Kungaba ukutheleleka kwebhaktheriya, igciwane, noma izinambuzane. Isibonelo, ezinye izingane zingase zibe nalesi simo ngemva komphimbo obuhlungu.
Ngaphandle kwalokho, kusolwa ukuthi kungabangelwa imithi ethile kanye nokungezwani nokudla. Abanye abantu bangase babe nokuthambekela kofuzo. Abacwaningi basafuna imbangela eqondile ye-HSP.
I-HSP yenzeka lapho amasosha omzimba ethu engasebenzi kahle. Sinohlobo olukhethekile lweprotheyini ebizwa ngokuthi `(Immunoglobulin A - IgA)` emizimbeni yethu. Umsebenzi wayo oyinhloko ukulwa nezifo nokusivikela ezifweni. Kodwa okwenzekayo emzimbeni womuntu one-HSP ukuthi le phrotheyini `(IgA)` ifakwa kuleyo mithambo yegazi emincane. Yilapho-ke leso simo `(vasculitis)` sivela khona, okubangela ukuba imithambo yegazi ivuvuke.
I-HSP uhlobo oluvame kakhulu lwe -vasculitis ezinganeni . Nakuba ingenzeka kunoma yimuphi ubudala, ivame kakhulu ezinganeni eziphakathi kweminyaka emi-2 neyi-6. Ivame kabili kubafana kunamantombazane. Ivame futhi ukwenzeka kaningi ekwindla nasebusika (okungukuthi, ngasekupheleni konyaka).
Ziyini izimpawu ze-HSP?
Manje ake sibone ukuthi yiziphi izimpawu ingane engase izibonise uma ine-HSP.
Amabala esikhumba `(Purpura)`
Lesi yisibonakaliso esiyinhloko nesisobala kakhulu se-HSP . Amabala amancane anombala onsomi abonakala njengemivimbo esikhumbeni. Lawa mabala awaphenduki abe mhlophe uma uwabuka (ukuqubuka okungashisi).
- Lezi zindawo zivame ukubonakala emilenzeni engezansi nasemaqakaleni .
- Ngezinye izikhathi la mabala angabonakala nasezandleni, ebusweni, nasezindaweni eziphakathi zomzimba, njengesifuba nesisu.
- La mabala angavela ngokuzumayo, noma anganda kancane kancane.
Ubuhlungu nokuvuvukala kwamalunga
Ezinganeni eziningi, ubuhlungu bamalunga nokuvuvukala kungase kwenzeke cishe isonto noma amabili ngaphambi kokuba kuvele ukuqubuka kwesikhumba .
- Ngokuvamile kuthinta amalunga amadolo namaqakala .
- Ngezinye izikhathi amalunga anjengendololwane nesihlakala nawo angathinteka.
- Lobuhlungu bungenza kube nzima ngengane ukuhamba.
Isisu esibuhlungu
Ukuphazamiseka kwesisu kuvame ukwenzeka ngemva kokuvela kokuqhuma kwesikhumba.
- Ungase ube nokuqaqamba kwesisu.
- Isicanucanu nokuhlanza .
- Ezinye izingane zingase zibe negazi endle yazo (igazi kuma-BM/endle). Lokhu kuyisibonakaliso okufanele sikhathazeke ngaso.
Imiphumela ezinso
Kwezinye izimo, i-HSP ingathinta nezinso .
- Inani elincane legazi noma iphrotheni lingadluliselwa ngomchamo .
- Ngezinye izikhathi umchamo ungase ubonakale ubomvu ngombala (i-hematuria).
- Nakuba lokhu kungekubi kakhulu ezimweni eziningi, kubaluleke kakhulu ukubona udokotela ukuze ahlole ukuthi kukhona yini umphumela ezinso.
Izimpawu ze-HSP zivame ukuhlala cishe inyanga , bese kuthi izingane eziningi zilulame zodwa.
Odokotela bayixilonga kanjani i-HSP ngokunembile?
Uma uyisa ingane yakho kudokotela, into yokuqala abayenzayo ukuhlola ingane kahle. Njengoba lawo mabala e-purpura ekhona cishe kuzo zonke iziguli ze-HSP, awusizo olukhulu kodokotela ekuxilongeni lesi sifo.
Ngaphezu kwalokho, udokotela angenza nezivivinyo ezifana nalezi:
- Ukuhlolwa kwegazi: Lokhu kungasetshenziswa ukuhlola ukusebenza kwezinso, ukuhlola izifo, kanye nokuhlola izinkinga zokujiya kwegazi.
- Ukuhlolwa komchamo: Hlola igazi noma amaprotheni emchameni. Lokhu kunganikeza umbono wokuthi izinso zithintekile yini.
- Ukuhlolwa kwendle: Hlola igazi elisendle.
- Ukuskena nge-ultrasound: Uma ingane yakho inobuhlungu obukhulu esiswini, lokhu kungasiza ekuqedeni ezinye izinkinga ngaphakathi esiswini, ikakhulukazi isimo esibizwa ngokuthi i-intussusception.
Ngemva kokwenza zonke lezi zivivinyo, udokotela unquma ukuthi une-HSP kanye nobunzima bayo.
Yiziphi izindlela zokwelapha i-HSP?
Esikhathini esiningi, i-HSP izixazulula yodwa ngaphandle kokwelashwa okuqondile . Yilezo izindaba ezinhle. Kodwa-ke, uma i-HSP ithinte izinso zakho, khona-ke ukwelashwa kungadingeka.
Ukuze usize ingane yakho ikhululeke futhi ilawule izimpawu, udokotela wakho angase ancome imithi efana nalokhu:
- Ama-antibiotic: Lawa anikezwa kuphela uma kucatshangwa ukuthi i-HSP ibangelwa ukutheleleka ngamagciwane.
- Imithi yokunciphisa ubuhlungu: Isibonelo, i-acetaminophen (njenge-paracetamol) ingasiza ekunciphiseni ubuhlungu bamalunga kanye nobuhlungu bomzimba.
- Imithi yokulwa nokuvuvukala: Isibonelo, imithi efana ne-ibuprofen ingasiza ekunciphiseni ubuhlungu nokuvuvukala emalungeni.
- Ama-Corticosteroids: Isibonelo, imithi efana ne-prednisone. Le mithi inikezwa kuphela uma ingane inobuhlungu obukhulu esiswini noma inesifo sezinso. Le mithi kufanele isetshenziswe kuphela ngaphansi kokuqondisa kukadokotela.
Izinto ongazenza ekhaya
Ngaphezu kwemithi, kunezinto ongazenza ekhaya ukuze ugcine ingane yakho ikhululekile:
- Vumela ingane yakho iphumule kahle: Nciphisa inani lokugijima nokudlala, bese uyikhuthaza ukuba ilale embhedeni futhi ifunde incwadi.
- Nikeza uketshezi oluningi ukuze uphuze:Ukunikeza izinto ezifana namanzi kanye nejusi yezithelo kungasiza ekuvimbeleni ukuphelelwa amanzi emzimbeni.
- Uma amalunga akho evuvukele futhi ebuhlungu: Ungawagcina ephakanyisiwe isikhashana, futhi mhlawumbe ubeke ne-ice pack kuwo uma udokotela wakho ekutshela ukuthi wenze kanjalo.
Into ebaluleke kakhulu ukuyisa ingane yakho kudokotela ngokushesha uma yenqaba ukudla noma ukuphuza, uma inezinhlungu zesisu ezinzima, noma uma ikhombisa izimpawu zezinkinga zezinso (isib. ukuncipha kokuchama, ukuvuvukala). Kungase kudingeke ukuthi ilaliswe esibhedlela ukuze ithole ukwelashwa.
Ingabe zikhona ezinye izinkinga ezingase zivele ngenxa ye-HSP?
Cishe ingxenye yezingane ezine-HSP ingaba nomthelela othile ezinso zazo. Ezimweni eziningi, lokhu kuwumphumela omncane nje futhi kuyaphela ngaphandle kokwelashwa okukhethekile. Kodwa-ke, akuvamile kakhulu, ezinye izingane zingase zibe nezimo ezibucayi njengokwehluleka kwezinso. Izingane ezinjalo zingadinga ukubona uchwepheshe wezinso (udokotela wezinso) ukuze zihlolwe okwengeziwe.
Esinye isimo sezokwelapha esingavamile kodwa esibucayi kakhulu yi-intussusception. Lokhu kwenzeka lapho ingxenye eyodwa yamathumbu ingena kwenye ingxenye . Lokhu kunganqamula ukuhlinzekwa kwegazi kuleyo ngxenye futhi kubangele ukuvaleka. Lesi yisimo esiphuthumayo esidinga ukwelashwa ngokushesha. Uma ingane yakho ivele ibe nobuhlungu obukhulu besisu obuqhubekayo, ihlanza, noma inegazi elifana nejeli esitulweni sayo, kufanele usole lokhu.
Ezinye izinto ezibalulekile okudingeka sizazi
- Ingxenye engcono kakhulu ukuthi, izingane eziningi ezithola i-HSP ziyalulama ngokuphelele phakathi nenyanga futhi azibi nezinkinga zesikhathi eside.
- Ezinye izingane zingase zibe ne-HSP futhi. Lokhu kuvame ukwenzeka ezinyangeni ezimbalwa ngemva kwesiqephu sokuqala. Kodwa-ke, uma kwenzeka futhi, kuvame ukuba kubi kakhulu kunesiqephu sokuqala .
Ngakho-ke, uthini umyalezo okufanele uthathwe ekhaya kukho konke lokhu?
Kulungile, ngakho-ke, kusukela kulokho esikhulume ngakho, lezi yizinto ezibaluleke kakhulu okufanele uzikhumbule:
- I-HSP yisimo esingathinta izingane ezincane, okubangela ukuvuvukala kwemithambo yegazi. Uphawu oluyinhloko amabala ansomi.
- Esikhathini esiningi, lokhu kuzophola ngokwakho.
- Ubuhlungu bamalunga, ukucasuka kwesisu, kanye nokulimala kwezinso kungenzeka.
- Uma ubona izindawo ezingajwayelekile emzimbeni wengane yakho, uma ikhala ngobuhlungu besisu, noma uma amalunga ayo ebuhlungu, nakanjani yiyise kudokotela. Ungesabi, kodwa funa iseluleko sezokwelapha ngokushesha.
- Landela imiyalelo kadokotela ngokucophelela. Nika ingane yakho ukuphumula nokuphuza okuningi.
- Iningi lezingane liyalulama ngokuphelele. Qaphela izinkinga ezingavamile.
Khumbula, awuwedwa. Odokotela bakhona ukukusiza wena nomntwana wakho. Ukwazi lolu hlobo lolwazi kuzokunika amandla amakhulu okuthatha isinyathelo ngesikhathi esifanele.
Ngakho-ke, ngithemba ukuthi lolu lwazi luzokusiza. Ngifisela ingane yakho ukululama okusheshayo!
👩🏽⚕️ Imibuzo eyengeziwe (ama-FAQ)
💬 Kuyini ukuqubuka okubomvu okungazelelwe (HSP) ezandleni nasezinyaweni zezingane?
I-Henoch-Schonlein Purpura (HSP) yisifo lapho imithambo yegazi emincane (ama-capillaries) athwala igazi emzimbeni wezingane ezincane ngokuzumayo avuvukala futhi aqhume njengekhabe, okubangela ukopha ngaphansi kwesikhumba. Lokhu kubangela amabala ansomi/abomvu esikhumbeni.
💬 Ingabe lesi sifo esibizwa ngokuthi i-Henoch-Schonlein Purpura siyalimaza izinso?
Yebo! Lokhu kuqhuma kwemithambo yegazi kungenzeka hhayi ngaphansi kwesikhumba kuphela kodwa nangaphakathi emzimbeni (esiswini nasezinso). Ngakho-ke, uma umchamo wezingane ezinalesi sifo uba bomvu, kusho ukuthi izinso zonakele futhi zopha igazi.
💬 Kulashwa kanjani lokhu? Ingabe kudingeka ngilaliswe esibhedlela?
Esikhathini esiningi, lokhu kuzozixazulula ngokwako phakathi namasonto ambalwa. Kodwa-ke, kubalulekile ukubona udokotela wezingane ngoba kudingeka ukuhlolwa komchamo ukuze kuhlolwe umonakalo wezinso kanye nobuhlungu obukhulu bamalunga/isisu kuyinto edingekayo.
I- Henoch-Schonlein purpura, i-HSP, izifo zezingane, amabala esikhumba, i-vasculitis, i-IgA vasculitis, izifo zezingane











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