Ua ʻike anei ʻoe i kahi maʻi e hoʻoulu ai i ka pehu ʻana o nā kīʻaha koko i loko o ka lolo a me ke kaula kuamoʻo? E kamaʻilio kākou e pili ana i (CNS Vasculitis)!

Ua loaʻa anei iā ʻoe kahi ʻeha poʻo nui i hala ʻole no nā lā? A i ʻole ke manaʻo koke nei ʻoe e like me ka mae ʻana o kou kino, me nā mea e like me ka poina ʻana a me ka mae ʻana? I kekahi manawa hiki i kēia ke lilo i mau hōʻailona o kahi maʻi koʻikoʻi, ʻoiai inā ʻaʻole mākou e nānā nui iā lākou. I kēia lā, e kamaʻilio mākou e pili ana i kahi maʻi paʻakikī iki, akā he mea nui loa e hoʻopilikia ana i ko mākou lolo a me ke kaulahao iwi kuamoʻo.

He aha kēia (CNS Vasculitis)? E hoʻomaopopo maʻalahi kākou?

I ka ʻōlelo maʻalahi, ʻo CNS Vasculitis kahi mumū o nā kīʻaha koko i loko o kā mākou ʻōnaehana nerve waena (CNS), ʻo ia hoʻi, ka lolo a me ke kaula spinal . E like me ka wā e loaʻa ai iā mākou kahi ʻeha ma kekahi wahi o ko mākou kino, pehu nā kīʻaha koko e hoʻolako ana i ke koko i ka lolo a me ke kaula spinal mai loko mai. I kekahi manawa kapa nā kauka i kēia "angiitis mua o ka ʻōnaehana nerve waena ". ʻO kekahi inoa ʻē aʻe ʻo "granulomatous angiitis".

E noʻonoʻo e pili ana i ia mea, ua like ko kākou ʻōnaehana nerve waena me ke kikowaena hoʻomalu o ko kākou kino holoʻokoʻa. ʻO nā mea a pau a kākou e hana ai me ka ʻike, mai ka hoʻohana ʻana i kou mau manamana lima e heluhelu i kēia ʻatikala, a hiki i nā mea a pau a kākou e hana ai me ka ʻike ʻole, e like me ka hanu ʻana a me ka helu o ka puʻuwai , ua hoʻomalu ʻia ma ʻaneʻi. No laila he aha ka mea e hana ai inā he pilikia me nā kīʻaha koko ma kahi koʻikoʻi? ʻO ia ke kumu e pono ai kākou e hopohopo e pili ana i kēia maʻi.

Aia kekahi mau ʻano nui o ka CNS Vasculitis?

ʻAe, ua ʻike nā kauka i ʻelua ʻano nui o kēia:

1. ʻO ka Vasculitis CNS mua: Hana ʻia kēia ma kāna iho, me ka ʻole o ka mana o kekahi maʻi ʻē aʻe. ʻO ia hoʻi, ʻaʻohe maʻi ʻē aʻe e hiki ke loaʻa ma ke ʻano he kumu.

2. ʻO ka Vasculitis CNS Lua: Hana ʻia kēia me a i ʻole ma muli o kekahi maʻi ʻē aʻe. I ka ʻōlelo maʻalahi, hoʻoulu ʻia e kahi maʻi mumū a i ʻole kekahi maʻi ʻē aʻe ma kahi ʻē aʻe o ke kino. ʻO nā maʻi Autoimmune ( ʻo ia hoʻi, nā maʻi e hana ai ka ʻōnaehana pale ponoʻī o ko mākou kino e kūʻē iā mākou) a me nā maʻi ʻeha nā kumu maʻamau o kēia ʻano lua.

He aha nā hōʻailona o kēia maʻi? Pehea mākou e ʻike ai?

Hiki ke ʻokoʻa nā hōʻailona o ka CNS Vasculitis mai ke kanaka a ke kanaka, akā aia kekahi mau hōʻailona maʻamau:

• ʻEha poʻo koʻikoʻi a lōʻihi: ʻO kēia ka hōʻailona mua e hiki mai ana i ka noʻonoʻo no nā poʻe he nui. ʻAʻole ia e like me ke poʻo poʻo maʻamau, akā ʻoi aku ka ikaika a hiki ke mau no nā lā.
• Ka poina ʻana a i ʻole ka huikau: E poina koke paha iā ʻoe nā mea a manaʻo ʻoe ua pioloke.
• ʻO ka mae ʻole, nā manaʻo ʻē, a i ʻole nā ​​​​loli i ka hoʻopā ʻana: Hiki i kou mau lālā ke mae, a ʻaʻole paha ʻoe e manaʻo i kekahi mea ke hoʻopā ʻoe iā lākou.
• Ka nāwaliwali o ke kino: He manaʻo o ke kōkua ʻole, ka makemake ʻole e hana i kekahi mea.
• Ka hemahema o ka ʻike: Ka ʻike pohihihi, i kekahi manawa ʻike pālua.
• Nā Hōʻailona o ka maʻi epilepsy (Seizures): Hiki ke nalowale koke ka ʻike a me nā haʻalulu.
• Encephalopathy: Hiki i kēia ke hoʻololi i ke kūlana noʻonoʻo, ke ʻano, a i kekahi manawa e hele wale ana.

Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o kēia mau hōʻailona, ​​​​he mea nui loa ia e ʻimi koke i ke kōkua lapaʻau. No ka mea hiki i kēia ke lilo i mau hōʻailona o nā maʻi ʻē aʻe, he mea nui e ʻike pono i ke kumu o ka pilikia.

He aha nā pilikia e hiki mai ana mai ka CNS Vasculitis?

Hoʻoulu kēia maʻi i nā kīʻaha koko e pehu a lilo i mea nui, e paʻakikī ai ke kahe ʻana o ke koko ma o lākou. I ka hala ʻana o ka manawa, hiki i kēia mumū ke hōʻino i ka lolo a me ke kaula iwi kuamoʻo, e alakaʻi ana i nā pilikia koʻikoʻi, i kekahi manawa he mea hoʻoweliweli i ke ola. ʻO nā mea nui:

• Nā hahau
• Nā hoʻouka ischemic transient (i kapa ʻia hoʻi ʻo "mini-strokes")
• ʻO nā aneurysms o ka lolo (nā ʻōhū e hiki ai ke uhaki i nā kīʻaha koko i loko o ka lolo)

Pono kēia mau pilikia a pau i ka mālama olakino ulia pōpilikia. Inā ʻike ʻoe i nā hōʻailona o ka hahau ʻana a i ʻole ka haki ʻana o ka aneurysm o ka lolo, e hele koke i ka haukapila a kāhea aku paha i ka 1990 (ambulance).

He aha nā kumu o ka CNS Vasculitis?

(CNS Vasculitis) he maʻi autoimmune . I ka ʻōlelo maʻalahi, ʻo ka ʻōnaehana pale o ko mākou kino, nā koa i manaʻo ʻia e pale iā mākou mai ka maʻi, hoʻomaka hewa i ka hoʻouka ʻana i kā mākou mau cell ponoʻī. ʻO ka mea e hana ʻia ma ʻaneʻi, ʻo ia ka hoʻouka ʻana o ka ʻōnaehana pale i ko mākou mau kīʻaha koko ponoʻī.

• Loaʻa i ka poʻe me ka CNS vasculitis mua me ke kumu ʻole, ʻo ia hoʻi, "idiopathically." ʻAʻole hiki ke ʻōlelo pololei i ke kumu.
• ʻO ka maʻamau, ʻo ka lua o ka CNS Vasculitis e hana pū ʻia me nā maʻi ʻē aʻe e hoʻoulu ai i ka mumū i loko o ke kino. Hiki i nā maʻi autoimmune ʻē aʻe a me kekahi mau maʻi ke hoʻoulu iā ia. Eia kekahi mau laʻana:
• ʻO ka Lupus
• ʻO ka granulomatosis me ka polyangiitis
• ʻO ka granulomatosis Eosinophilic me ka polyangiitis (EGPA)
• ʻO ka polyangiitis microscopic
• ʻO ka maʻi ʻo Behçet
• ʻO ka maʻi Sjögren
• Nā maʻi viral: ʻO ka maʻi Epstein-Barr, ka maʻi varicella-zoster (ka maʻi e hoʻoulu ai i nā maʻi e like me ka moa a me ka herpes)
• Nā maʻi bacteria: Tuberculosis, Syphilis

ʻO wai ka mea i pilikia nui i ka loaʻa ʻana o kēia maʻi?

(CNS Vasculitis) ʻOiai hiki i kekahi ke loaʻa iā ia, ʻoi aku ka maʻamau i nā kāne. ʻOiai ʻoi aku ka maʻamau i ka poʻe a puni ka makahiki 50, hiki ke loaʻa kēia maʻi i kēlā me kēia makahiki.

Pehea e ʻike ai nā kauka i ka CNS Vasculitis?

E ʻike ke kauka i kēia kūlana ma ka nānā ʻana iā ʻoe ma ke kino a me ka hana ʻana i kekahi mau hoʻokolohua kūikawā. E nīnau ʻo ia iā ʻoe e pili ana i kāu mau hōʻailona, ​​e like me ka wā i ʻike mua ai ʻoe iā lākou. E haʻi i kāu kauka inā hele mai kāu mau hōʻailona a hele aku (`recur`), a inā e ʻoi aku ka ʻino i kekahi mau manawa o ka lā a i ʻole i ka wā o kekahi mau hana.

ʻO ka ʻike ʻana i ka CNS Vasculitis i kekahi manawa hiki ke lilo i kaʻina hana o ka hoʻokaʻawale ʻana i nā kūlana ʻē aʻe (diagnosis differential) . ʻO ke ʻano kēia ma mua o ka ʻike maopopo ʻana i kēia kūlana, e hana kāu kauka i kekahi mau hoʻokolohua e hōʻoia ʻaʻole ʻoe i loaʻa i nā kūlana ʻē aʻe, ʻoi aku ka maʻamau. Pono paha ʻoe e hana i kēia mau mea:

• MRI (Kiʻi Hoʻohālikelike Magnetic)
• ʻO ke kiʻi CT (Computered tomography)
• ʻO Angiogram (kahi hoʻokolokolo X-ray kūikawā o nā kīʻaha koko)
• Biopsies (lawe ʻana i kahi ʻāpana o ke kino no ka hoʻokolokolo ʻana)

Pono paha ʻoe e ʻike i kahi rheumatologist, he kauka i loea i ka mālama ʻana i nā kūlana mumū .

He aha nā hōʻailona e kōkua i ka ʻike ʻana i ka CNS Vasculitis?

ʻO nā "Markers" he mau hōʻailona o kahi maʻi. Hiki i kāu kauka ke loaʻa kēia mau mea i loko o kou koko a i ʻole nā ​​​​wai kino ʻē aʻe ma o nā hoʻokolohua hoʻokolohua. Eia kekahi mau hoʻokolohua e hoʻohana ai kāu kauka e ʻimi i nā hōʻailona o ka CNS Vasculitis:

• Nā hoʻāʻo koko e nānā ai i ka anemia.
• Hoʻāʻo ESR (erythrocyte sedimentation rate): He māka no ka mumū i loko o ke kino.
• Hoʻāʻo protein C-reactive (CRP): Nānā i nā māka mumū i hoʻokuʻu ʻia e ke akepaʻa.
• ʻUku lumbar: E lawe i kahi laʻana o kou wai spinal cerebral a nānā i ka helu kiʻekiʻe o nā sela koko keʻokeʻo.

He aha nā lāʻau lapaʻau no kēia?

E paipai paha kāu kauka i nā lāʻau lapaʻau e kāohi i ka mumū. ʻO ka mea nui loa i ka mālama ʻana i ka CNS Vasculitis, ʻo ia ka hōʻemi ʻana i ka pōʻino i hana ʻia i kou lolo a me ke kaula spinal. Pono ka nui o ka poʻe e lawe i ka hui pū ʻana o nā lāʻau lapaʻau i kapa ʻia ʻo corticosteroids (kahi ʻano lāʻau lapaʻau e hōʻemi i ka mumū) a me nā immunosuppressants (nā lāʻau lapaʻau e kāohi i ka ʻōnaehana pale) .

I ka wā mua, e hāʻawi ʻia ʻoe i kahi mahele lāʻau kiʻekiʻe aʻe. Ma hope (ma hope o kekahi mau mahina), hiki i kāu kauka ke hōʻemi i ke alapine o nā inikini a me ka mahele. Ke hoʻāʻo nei kāu mau kauka e hoʻokomo iā ʻoe i kahi pae "remission" kahi e liʻiliʻi ai kāu mau hōʻailona a nalowale loa paha.

Inā loaʻa iā ʻoe ka vasculitis CNS lua, pono ʻoe e lawe i nā lāʻau lapaʻau ʻokoʻa e kāohi i ke kūlana kumu, a kāu kauka e wehewehe ai iā ʻoe.

Āhea wau e ʻike ai i ke kauka?

E mālama i kāu mau hōʻailona. Inā ʻike ʻoe i kekahi mau loli, e kākau i kahi moʻolelo o lākou. E haʻi koke aku i kāu kauka, ʻoiai inā ʻike ʻia kāu mau hōʻailona e hele pinepine mai ana a ʻoi aku ka koʻikoʻi ma mua o ka wā ma mua. E haʻi pū aku i kāu kauka inā ʻike ʻia kekahi lāʻau lapaʻau ʻaʻole e hana a ʻaʻole paha e like me ka wā ma mua.

E haʻi aku kāu kauka iā ʻoe i ka pinepine o kou pono e ʻike i kāu kauka, e hana i nā hoʻokolohua koko, a i ʻole e hana i nā hoʻokolohua ʻē aʻe.

Inā loaʻa iā ʻoe kekahi o nā hōʻailona ma lalo nei, e hele koke i ka haukapila a kāhea aku paha i ka 1990:

• Inā manaʻo ʻoe ua loaʻa iā ʻoe nā hōʻailona o ka hahau ʻana a i ʻole ka haki ʻana o ka aneurysm o ka lolo .
• Inā pilikia ʻoe i ka hanu ʻana.
• ʻAʻohe pilikia inā e ʻino koke kou ʻike, a inā e nalowale koke kou ʻike.

Inā loaʻa iaʻu (Central Nervous System Vasculitis), he aha kaʻu e manaʻo ai?

ʻAʻohe lāʻau lapaʻau no ka CNS Vasculitis. Eia nō naʻe, hiki i nā poʻe he nui ke komo i loko o nā manawa lōʻihi o ka hoʻomaha ʻana ma hope o ka loaʻa ʻana o ka hui pū ʻana o nā lāʻau lapaʻau e pono ai no lākou. Hiki i kekahi poʻe ke hele i nā mahina a i ʻole nā ​​​​makahiki me ka ʻole o nā hōʻailona, ​​​​a laila hoʻi mai nā hōʻailona.

ʻAʻole pinepine ka hopena koʻikoʻi o ka CNS Vasculitis i kou manaʻolana ola. Eia nō naʻe, he paʻakikī ke ʻōlelo maopopo. No ka mea, hiki i ka CNS Vasculitis ke hoʻoulu i nā pilikia koʻikoʻi e like me ka hahau ʻana a me ka aneurysm. Inā loaʻa kēlā mau pilikia, ʻoi aku ka kiʻekiʻe o ka make ma mua o ka maʻamau.

Inā he mau hopohopo kāu e pili ana i kou olakino a i ʻole pehea ka hopena o ka CNS Vasculitis i kou ola, e kamaʻilio me kāu kauka.

Hiki ke weliweli kekahi maʻi e hoʻopilikia ana i kāu ʻōnaehana nerve waena (CNS). ʻOi loa aku i ka wā e ʻike ai ʻoe e hoʻouka ana kāu ʻōnaehana pale ponoʻī i kou lolo a me ke kaula spinal. Akā ʻo ka nūhou maikaʻi, hiki i ka hapa nui o ka poʻe me CNS Vasculitis ke loaʻa i kahi hui pū ʻana o nā lāʻau lapaʻau e kāohi ana iā ia. Ke loaʻa iā ʻoe ka lāʻau kūpono nou, hiki i kāu kauka ke kōkua iā ʻoe e hōʻemi i ka hopena o kāu mau hōʻailona i kou ola.

E hoʻomanaʻo, ʻaʻole ia he mea maikaʻi ʻole ke nīnau i nā nīnau e pili ana i kou olakino. E kamaʻilio me kāu kauka e pili ana i kou mau hopohopo a pau. E pane ʻo ia i kāu mau nīnau a pau, e hāʻawi iā ʻoe i ka hilinaʻi i nā mea e hana nei i loko o kou kino, a e kōkua iā ʻoe e hoʻokele iā ia.

ʻO ka leka koʻikoʻi loa e lawe i ka home

He maʻi koʻikoʻi akā hiki ke mālama ʻia (CNS Vasculitis). ʻO ka mea nui loa, ʻo ia ke ʻimi i ke kōkua lapaʻau i ka wā e ʻike ai ʻoe i nā hōʻailona a lawe i ka lāʻau i kuhikuhi ʻia. I ka wā e noho ai me kēia maʻi, he mea nui loa ia e mālama i kahi pilina maikaʻi me kāu kauka. Ma ka hahai ʻana i kā lākou ʻōlelo aʻo a me ka haʻi ʻana iā lākou e pili ana i nā loli āu e ʻike nei, hiki iā ʻoe ke ola me ka holomua me kēia maʻi. Mai makaʻu, ʻaʻole ʻoe hoʻokahi. Me ke alakaʻi lapaʻau kūpono, hiki ke mālama maikaʻi ʻia kēia kūlana.

ʻO ka Vasculitis CNS, ka ʻōnaehana nerve waena, ka mumū o nā kīʻaha koko, ka lolo, ke kaula spinal, nā maʻi autoimmune, ka ʻeha poʻo