Ngaba unesifo seSickle Cell? Ngoko ke ukuba uneentlungu esifubeni, musa ukudlala ngathi! Oku kumalunga ne-Acute Chest Syndrome!

Ngaba ngamanye amaxesha ukhe ube neentlungu esifubeni ngequbuliso kwaye ube nobunzima bokuphefumla? Ukuba unale mpawu kunye nokukhohlela kunye nomkhuhlane, ingakumbi ukuba unesifo esibizwa ngokuba yiSickle Cell Disease (SCD) , musa ukusithatha lula. Ezi mpawu zinokuba luphawu lwesifo esibi kakhulu esibizwa ngokuba yiAcute Chest Syndrome. Ungakhathazeki, siza kuthetha ngale nto ngendlela ecacileyo nelula namhlanje.

Yintoni i-Acute Chest Syndrome? Ngamafutshane...

Kulungile, khangela ngoku. Le `Acute Chest Syndrome` yingxaki enokuba yingozi yesifo se-sickle cell (`SCD`) . Ngamafutshane, kuxa unentlungu esifubeni, ukukhwehlela, umkhuhlane, amanqanaba aphantsi eoksijini egazini lakho, kwaye izinto ezingaqhelekanga, ngakumbi ulwelo, ziqala ukuqokelelana kwizicubu zemiphunga (`lung infiltrates`).

Le meko inokuba mandundu ngokukhawuleza . Enyanisweni, le `Acute Chest Syndrome` yeyona nto iphambili ebangela ukulaliswa esibhedlele kwaye ngamanye amaxesha ukufa kwabantu abanesifo se-sickle cell . Ngoko ke, kubaluleke kakhulu ukuqaphela oku.

Ngoku usenokuba uyazibuza ukuba yintoni iSickle Cell Disease (SCD). Masikukhumbuze kancinci ngayo. Sisifo esibangelwa lufuzo . Oko kuthetha ukuba sizuzwe njengelifa. Sichaphazela iproteni kwiiseli zethu ezibomvu zegazi ebizwa ngokuba yi-hemoglobin . Ngelixa iiseli ezibomvu zegazi zomntu ophilileyo zingqukuva, iiseli ezibomvu zegazi zomntu one-SCD zimile njengesikela (njengenyanga). Ngoko ke ezi seli zimile njengesikela azinakudlula kwimithambo yethu yegazi emincinci ngokulula. Emva koko, i-hemoglobin ayinakuthwala ioksijini emzimbeni wonke ngokufanelekileyo. Le yeyona ngxaki iphambili nge-SCD.

Ixhaphake kangakanani i-Acute Chest Syndrome?

Enyanisweni, i-'Acute Chest Syndrome' yimeko eqhelekileyo kubantu abanesifo se-sickle cell ('SCD'). Ngokwezibalo, malunga nesiqingatha sabantu abane-'SCD' baya kuba nale meko ubuncinane kube kanye ebomini babo . Nangona ibonakala ixhaphake kakhulu kubantwana abancinci abaphakathi kweminyaka emi-2 ne-4 ubudala , inokuba nzima kakhulu kubantu abadala kunabantwana . Kukwafunyaniswe ukuba abantu abane-'SCD' kunye ne -asthma basengozini enkulu yokufumana i-'Acute Chest Syndrome' kunabanye.

Kutheni kukho i-Acute Chest Syndrome? Zithini izizathu?

Izazinzulu azikakwazi ukutsho ngokuqinisekileyo ukuba yintoni kanye kanye ebangela i-'Acute Chest Syndrome'. Kodwa zikholelwa ukuba isenokuba ibangelwa yinto enye okanye ezingaphezulu. Makhe sijonge ukuba zeziphi:

• I-Bone Marrow Necrosis: Umhlaza wethambo:Ubusazi na ukuba umongo wethambo yinxalenye ethambileyo nethambileyo engaphakathi kwamathambo ethu amakhulu? Ukuba lo mongo wethambo uyafa ngandlela thile (obizwa ngokuba yi-'necrosis'), iziqwenga zawo ezincinci zinokuqhekeka zingene egazini zihambe emzimbeni wonke. Ukuba ezi ziqwenga ziya emiphungeni, zinokubangela i-'Acute Chest Syndrome'.
• Ukuvaleka kwamafutha: Esinye isizathu esinokubangela ukungasebenzi kakuhle komongo wethambo esikhankanyiweyo apha ngasentla yi- fat embolism. Ngamafutshane, oku kwenzeka xa isuntswana lamafutha (cinga ngalo njengethontsi leoyile) linamathela kwimithambo yegazi lize livale ukuhamba kwegazi . Oku kunokukhokelela kwi-Acute Chest Syndrome.
• Usulelo : Iintsholongwane ezahlukeneyo, ingakumbi i-pneumonia ebangelwa ziibhaktheriya okanye iintsholongwane , zinokubangela isifo sesifuba esibukhali. Iintsholongwane zezona zibangela esi sifo kubantwana abancinci . Nangona kunjalo, kubantu abadala , kusenokwenzeka ukuba zibangelwa yi-fat embolism.

Zithini iimpawu zomntu one-Acute Chest Syndrome?

Iimpawu ze-'Acute Chest Syndrome' zingahluka kumntu nomntu. Kukho umahluko othile, ingakumbi phakathi kwabantwana abancinci nabantu abadala. Abantwana abancinci badla ngokubonisa uninzi lweempawu zosulelo:

• Ukukhwehlela
• Ifiva
• Ukuncipha koxinzelelo lweoksijini egazini (i-hypoxemia)
• Isantya sokuphefumla esingaqhelekanga (i-tachypnea)
• Ukuphefumla (isandi esiphuma esifubeni xa uphefumla)

Abantu abadala nabo banokuba nazo ezi mpawu. Ukongeza, ungaphawula:

• Iintlungu zesifuba , ingakumbi xa uphefumla, zinokwanda.
• Intlungu ebuhlungu, ekhawulezileyo ezingalweni, emilenzeni, nasemqolo ebangelwa kukuvaleka kokuhamba kwegazi (okubizwa ngokuba yi-'vaso-occlusive crisis').
• Ukuqokelelana kolwelo emiphungeni nasesifubeni (i-pleural effusion).
• Ubunzima bokuphefumla (ukuphelelwa ngamandla).

Ukuba unenye okanye ngaphezulu kwezi mpawu, ingakumbi ukuba une-SCD, kubaluleke kakhulu ukufuna ingcebiso kagqirha ngoko nangoko .

Ifunyanwa njani i-Acute Chest Syndrome? (Ukuxilongwa)

Ukuqaphela kwangethuba i-'Acute Chest Syndrome' kunokusindisa ubomi bomntu.Ukuba une-SCD kwaye ulaliswe esibhedlele, kuya kufuneka ujongwe rhoqo kwaye wenze iimvavanyo ezifunekayo. Kukho iimvavanyo ezininzi ezinokunceda oogqirha ukuba bafumanise le ngxaki:

• Uhlalutyo lwegesi yegazi lemithambo: Oku kunokulinganisa amanqanaba e-asidi (pH), ioksijini, kunye ne-carbon dioxide egazini lakho.
• Uvavanyo lwegazi: Uvavanyo olupheleleyo lwegazi lunokubonelela ngolwazi malunga neeseli zakho ezibomvu zegazi, iiseli ezimhlophe zegazi, kunye neeplatelets.
• I-X-reyi yesifuba: Oku kungasetyenziselwa ukujonga usulelo lwemiphunga okanye ukuqokelelwa kwezinto ezingaqhelekanga (ezingena ngaphakathi) esithethe ngazo ngaphambili.
• Iinkcubeko: Olu vavanyo lunceda ekufumaneni iintlobo ezahlukeneyo zosulelo ngokuhlola igazi lakho, i-mucus, okanye olunye ulwelo lomzimba.

Ngokusekelwe kwezi ziphumo zovavanyo kunye neempawu zakho, ugqirha wakho angachaza i-Acute Chest Syndrome njenge -encinci, ephakathi, okanye enzima .

Ziziphi iindlela zonyango lwe-Acute Chest Syndrome?

Kule meko , ukuqala unyango kwangethuba yeyona ndlela ilungileyo yokuthintela iingxaki ezinkulu . Iindlela zonyango ziquka:

• Utofelo-gazi: Oku kuquka ukususa inxalenye yegazi lakho nokukunika igazi okanye iinxalenye zegazi kumntu onikelayo.
• Ulwelo lwe-IV: Oku kunceda ekuthinteleni ukuphelelwa ngamanzi emzimbeni (ukugcinwa kwamanzi), okunokwenza isifo se-sickle cell sibe sibi kakhulu kwaye kwandise intlungu.
• Iintlungu: Amayeza anjenge-'ketorolac' okanye 'opioids' anokunikwa ukulawula iintlungu.
• I-Incentive Spirometer: Esi sixhobo sincinci sikunceda uphefumle nzulu. Sinceda ukugcina imiphunga yakho icocekile kwaye isebenza kakuhle.
• Unyango olongezelelweyo lweoksijini: Ukuba inqanaba leoksijini egazini liphantsi, kunikwa ioksijini.
• Ii-antibiotics: Ukuba le meko ibangelwa lusulelo lwebhaktiriya, kunikwa ii-antibiotics.
• Ii-Antivirals: Ukuba unobangela lusulelo lwentsholongwane, kunikwa amayeza afanelekileyo okulwa neentsholongwane.

Ngaba umngcipheko wokuba ne-Acute Chest Syndrome ungancitshiswa?

Ukuba unesifo se-sickle cell (SCD), kubalulekile ukuthetha neqela lakho lezonyango malunga neendlela zokuthintela i-Acute Chest Syndrome. Banokucebisa izinto ezifana nezi:

• Ukufutha ibhotile rhoqo: Nangona kunokubonakala ngathi yinto elula, oku kunceda ukugcina iindlela zakho zomoya zicocekile kwaye kunciphisa ukuqokelelwa kolwelo olungafunekiyo olujikeleze imiphunga yakho.
• Ukuzilolonga rhoqo: Oku kunokunyusa amandla emiphunga yakho.
• Utofelo-gazi oluqhelekileyo: Abanye abantu banokulufuna olu.
• Ukusebenzisa amayeza anjenge-`Hydroxyurea` okanye i-`L-glutamine`: La mayeza anokunceda ukunciphisa iintlungu nokunciphisa umngcipheko wokulaliswa esibhedlele rhoqo. Nangona kunjalo, la mayeza afanele athathwe kuphela phantsi kwengcebiso kagqirha.

Iyintoni imbono (ukuchacha) yomntu onesi sifo?

Kubalulekile ukufuna unyango ngokukhawuleza xa kuvela i-'Acute Chest Syndrome'. Ukungaphumeleli ukwenza njalo kunokukhokelela kwiingxaki ezinkulu ezifana nezi:

• I-Acute Respiratory Distress Syndrome (ARDS): Le yimeko enzima yemiphunga enokuba yingozi ebomini.
• Utshintsho kwimeko yengqondo.
• Ukulimala kwezintso.
• Ukungasebenzi kakuhle kwesibindi.
• Ukungasebenzi kakuhle kwamalungu amaninzi.
• Ukungaphumeleli ngokupheleleyo kokuphefumla.
• Intlungu enzima kakhulu.
• Ngelishwa, nokufa kunokwenzeka.

Ngokwezibalo, izinga lokufa kwabantu abadala ngenxa ye-'Acute Chest Syndrome' limalunga ne-4% . Phakathi kwabantwana, eli nani limalunga ne- 1% . Oku kuthetha ukuba ubomi obuninzi bunokusindiswa ngonyango lwangethuba.

Kwakhona, khumbula ukuba nokuba i-'Acute Chest Syndrome' inyangwa kwaye inyangwe ngempumelelo, umntu one-'SCD' usenokuphinda abe nale meko kwixesha elizayo .

Ndinesifo se-sickle cell. Ndingenza ntoni ukuba ndifumana iimpawu ze-Acute Chest Syndrome?

Le yeyona nto ibalulekileyo. Ukuba une-SCD kwaye uqala ukuba nazo naziphi na iimpawu ze-Acute Chest Syndrome (iintlungu zesifuba, ukuphefumla kancinci, ukukhohlela, umkhuhlane), musa ukulibazisa umzuzu kwaye funa ingcebiso kagqirha ngoko nangoko .

• Xelela oogqirha ukuba unesifo se-sickle cell xa usiya kwigumbi likaxakeka okanye kwenye indawo yonyango.
• Cela i-X-ray yesifuba ngoko nangoko . Oku kunokuqinisekisa ngokukhawuleza ukuba unayo na i-Acute Chest Syndrome kwaye uqalise unyango ngokukhawuleza.

Khumbula, ukwenza izinto ngokukhawuleza ngexesha elinje kunokunceda kakhulu ekusindiseni ubomi bakho.

Umyalezo Wokuya Ekhaya

Ngoku uyazi ukuba i-'Acute Chest Syndrome', ebesithetha ngayo, yingxaki enokuba yingozi yesifo se-sickle cell. Iimpawu eziphambili ziintlungu zesifuba, ukuphefumla kancinci, ukukhohlela, kunye nomkhuhlane . Ukuba unesifo se-sickle cell, funa ingcebiso kagqirha ngokukhawuleza ukuba ufumana naziphi na kwezi mpawu.Ungalibali ukwazisa oogqirha bakho ukuba unesifo se-sickle cell. Ukuxilongwa kwangoko kunye nonyango olukhawulezileyo zezona ndlela zilungileyo zokuzikhusela kule meko. Hlala usempilweni! I-Acute Chest Syndrome, Isifo se-Sickle Cell, Intlungu yesifuba, Ubunzima bokuphefumla, I-Acute Chest Syndrome, Isifo se-Sickle Cell, Usulelo lweMiphunga