Ngaba wakha waba neentloko ezibuhlungu ezingapheliyo, ubunzima bokushukumisa amehlo akho, okanye ukulahleka kwesantya ngequbuliso xa uhamba? Mhlawumbi uzibonile ezi mpawu kumntwana wakho. Nangona sihlala singazihoyi ezi ngxaki, ngamanye amaxesha zinokuba ziimpawu zemeko yempilo enzulu. Namhlanje, eNirogi Lanka , sixoxa ngethumba lobuchopho elingaqhelekanga kodwa elibalulekileyo ekufuneka liqondwe elibizwa ngokuba yiPineoblastoma .
Yintoni kanye kanye iPineoblastoma? Ngamafutshane...
Ngamafutshane, iPineoblastoma sisimila esinobungozi (esinomhlaza) esisuka kwi-pineal gland yengqondo yakho. Olu hlobo lwesimila lunamandla kakhulu ; lukhula ngokukhawuleza kwaye lunokusasazeka kwizicwili zobuchopho ezingqongileyo kunye nolwelo olujikeleza ingqondo yakho, nto leyo eyenza ukuba ibe yingxaki enkulu kwezonyango.
Linda, yintoni iPineal Gland?
Masiqale ngezinto ezisisiseko. I-pineal gland sisitho esincinci, esimile okwekhowuni, esilingana ne-pine nut, esikwimbindini wobuchopho bakho. Le gland inoxanduva lokukhupha i-hormone ebizwa ngokuba yi -melatonin . Usenokuba ukhe weva nge-melatonin—ibalulekile ekulawuleni isigqi sakho se-circadian . Cinga ngayo njengewotshi yendalo yangaphakathi yomzimba wakho ekunceda uhlale uphaphile emini kwaye ikukhuthaze ubuthongo ebusuku.
Luhlobo luni lwethumba iPineoblastoma?
I-Pineoblastoma yithumba lobuchopho elikhula ngokukhawuleza . Oogqirha badla ngokulibeka njengethumba lobuchopho elingaphakathi kwentloko leBanga lesi-4 . Ngenxa yokuba lithumba elibi , liyingozi emzimbeni kwaye linokusasazeka.
Ixhaphake kangakanani iPineoblastoma?
I-Pineoblastoma ayiqhelekanga kakhulu . Ngokweengxelo eMelika, ngaphantsi kwe-0.2% yazo zonke iithumba zobuchopho zifunyaniswa njengeethumba ze-pineal gland. Nangona olu hlobo lomhlaza lubonakala kakhulu kubantwana abancinci okanye kubantu abadala abancinci abangaphantsi kweminyaka engama-20 ubudala , kubalulekile ukukhumbula ukuba lunokwenzeka nakweyiphi na iminyaka.
Zithini iimpawu zePineoblastoma?
Makhe sijonge iimpawu ezinokubonakala kule meko:
- Iintloko ezibuhlungu kakhulu : Ezi azizizo iintloko eziqhelekileyo; zihlala zibuhlungu kwaye zihlala zikho.
- Ukudinwa rhoqo : Ukuziva udiniwe kakhulu kangangokuba imisebenzi yemihla ngemihla iba nzima ( Ukudinwa ).
- Ubunzima bokuhamba kwamehlo : Usenokukufumanisa kunzima ukujolisa amehlo akho okanye ukujonga kwicala elithile.
- Iingxaki zokulinganisela kunye nokulungelelanisa : Ukuziva ungazinzile xa uhamba okanye unengxaki yokubamba izinto.
- Utshintsho kwindlela yokuziphatha : Utshintsho olubonakalayo kwimo yengqondo, njengokwanda kokucaphuka, ukuxhalaba, okanye ukuyeka ngequbuliso.
- Isicaphucaphu nokuhlanza .
Ezi mpawu zihlala zibangelwa yimeko ebizwa ngokuba yi -hydrocephalus , apho ulwelo lwe-cerebrospinal luqokelelana khona kwaye lonyusa uxinzelelo ngaphakathi kwengqondo. Nangona ithumba linokusasaza ngolu lwelo liye kwezinye iindawo zeCentral Nervous System (CNS), alisoloko lisasazeka ngaphandle kwe-CNS.
Khawucinge ngomntwana okhalaza ngentloko ebuhlungu rhoqo, engafuni ukudlala, aze abonakale enomsindo ngendlela engaqhelekanga. Abazali basenokungayinaki le nto njengesiqhelo. Nangona kunjalo, ukuba iimpawu ziyaqhubeka, kubalulekile ukubonana nogqirha ngokukhawuleza.
Yintoni ebangela iPineoblastoma?
Isizathu esiyintloko kukukhula okungalawulekiyo nokukhawulezileyo kweeseli ezikhethekileyo kwi-pineal gland eyaziwa ngokuba yi- pinealocytes . Uphando lubonisa ukuba utshintsho lwezakhi zofuzo lubangela ukuba ezi seli zingasebenzi kakuhle kwaye zikhule ngendlela engaqhelekanga.
Olu tshintsho lwemfuza lunokwenzeka ngeendlela ezimbini:
1. Ilifa (utshintsho lwe-germline) : Idluliselwa kubazali ukuya emntwaneni ngexesha lokukhulelwa.
2. Utshintsho olungaqhelekanga : Utshintsho olungalindelekanga oluvela emva kokukhulelwa, apho kungekho mbali yangaphambili yentsapho yale meko.
Ngubani osengozini enkulu yePineoblastoma?
Abantu abathile bajongene nomngcipheko omkhulu wokufumana iPineoblastoma :
- Ukuba une -Retinoblastoma , umhlaza we-retina yeliso, usengozini enkulu.
- Abantu abaneenguqu kwi -RB1 okanye kwi-DICER1 genes nabo basengozini enkulu yokuhlaselwa ngumhlaza . Ezi nguqu zinokufunyanwa njengelifa okanye zingabikho rhoqo.
Ukuba uceba ukuqala usapho kwaye ukhathazekile ngezi zinto zinobungozi, kuyacetyiswa ukuba uthethe nomboneleli wezempilo malunga novavanyo lwemfuza .
Ifunyanwa njani iPineoblastoma?
Oogqirha baxilonga iPineoblastoma ngokudibanisa uvavanyo lweklinikhi kunye novavanyo lokuxilonga:
- Uvavanyo lomzimba : Ugqirha wakho uza kuvavanya iimpawu zakho, imbali yosapho lwakho, aze enze uvavanyo lwemithambo-luvo, kuquka nokujonga ukulungelelaniswa kwamehlo akho.
- Uxilongo oluPhambili :
- Iiskeni zeBrain Magnetic Resonance Imaging ( MRI ).
- Iiskeni zeComputed Tomography (CT).
- Ngamanye amaxesha, kwenziwa iskena sePositron Emission Tomography (PET).
- I -biopsy , apho kuthathwa isampuli encinci yezicubu ukuze ihlolwe ukuqinisekisa uhlobo lwethumba.
- Uvavanyo lwegazi kunye/okanye uvavanyo lolwelo lwe-cerebrospinal ukuze kufunyanwe iimpawu ezithile zethumba.
Ngaba iPineoblastoma inganyangeka?
Le yingxaki eqhelekileyo. Ukuba ndithetha inyani, okwangoku akukho nyango luqhelekileyo lwePineoblastoma . Nangona kunjalo, nceda ungalahli ithemba; kukho iindlela ezahlukeneyo zonyango. Ukuba ithumba alisasazekanga, ukususwa ngotyando kudla ngokuba linyathelo lokuqala.
Ngenxa yokuba iPineoblastoma luhlobo lomhlaza olunobundlongondlongo, kunzima ukunyanga. Iingxaki zinokubakho, kwaye ukuqikelela kwangaphambili kunokuchaphazeleka. Ngaphezu koko, kusoloko kukho ithuba lokuba umhlaza uphinde ubuye emva konyango.
Ziziphi iindlela zonyango lwePineoblastoma?
Unyango lwePineoblastoma lungabandakanya oku kulandelayo:
- Utyando : Utyando ludla ngokwenziwa ukuze kususwe inxalenye okanye lonke ithumba. Ugqirha wakho uza kuchaza ngokweenkcukacha inkqubo kunye neengozi ezinxulumene nayo.
- Utyando lweHydrocephalus : Ukuze kuncitshiswe ukwakheka kolwelo (ulwelo lwe-cerebrospinal) olujikeleze ingqondo, kunokufakwa i-shunt—ityhubhu encinci—ukuze kukhutshwe ulwelo olugqithisileyo kwaye kuncitshiswe uxinzelelo.
- Unyango lweMisebe : Olu lolona nyango luqhelekileyo emva kotyando. Unyango lweMisebe lunokunceda ukunciphisa izicubu zethumba eziseleyo okanye ukutshabalalisa iiseli zomhlaza.
- I-Chemotherapy : Xa isetyenziswa kunye notyando kunye ne-radiation, i-chemotherapy inokunceda ukunciphisa ithumba ngaphambi kotyando okanye isuse iiseli zomhlaza eziseleyo emva koko.
- I-High-Dose Chemotherapy kunye ne-Autologous Stem Cell Transplant : Kule nkqubo, ii-stem cells zakho ziyaqokelelwa ngaphambi kokuba ufumane i-high-dose chemotherapy. Ezi seli emva koko zifakwa emzimbeni wakho ukuze zincede inkqubo yakho ibuyele esiqhelweni emva konyango.
Njengoko uphando lwezonyango luqhubeka, unokufumana ithuba lokuthatha inxaxheba kwiimvavanyo zeklinikhi. Ezi zinokubandakanya ukuvavanya unyango olutsha olujoliswe kulo okanye unyango lwe-immunotherapy.
Ngubani okwiqela lakho lokhathalelo?
Ukuba ufunyaniswe unePineoblastoma, iqela lakho lokhathalelo eNirogi Lanka lingabandakanya:
- Ingcali yezifo zengqondo
- Ingcali yomhlaza
- Ingcali yomhlaza wemisebe
- Ugqirha weengqondo
Ngaba kukho iziphumo ebezingalindelekanga kwezi ndlela zonyango?
Ewe, ezinye iindlela zonyango, ingakumbi imitha, zinokubangela iziphumo ebezingalindelekanga. Ezi zinokuchaphazela ukusebenza kwe-endocrine yakho, kuquka:
- Ukukhula
- Amanqanaba amandla
- Ukuchuma
Ngaphambi kokuba uqale unyango, thetha nogqirha wakho ngeziphumo ebezingalindelekanga . Baza kukujonga rhoqo baze bathathe amanyathelo afunekayo ukulawula naziphi na iingxaki ezivelayo.
Ngaba ungasinda kwiPineoblastoma?
Ewe, izigulane ezininzi ziyasinda kwiPineoblastoma. Izinga lokusinda kweminyaka emihlanu kwiPineoblastoma liqala kwi -60% ukuya kwi-69.5% . Nangona olu xilongo lunokutshintsha ubomi, kukho unyango olusebenzayo oluyilelwe ukukunceda uphile kakuhle kwaye wandise ubomi bakho.
Yintoni ingqikelelo yePineoblastoma?
Emva kokuba uxilongiwe, ugqirha wakho uza kuxoxa ngesifo sakho. Nangona kungekho "nyango" lunye, kukho iindlela ezininzi zonyango. Iziphumo zesigulana zixhomekeke kwizinto ezifana nempilo iyonke, indlela umzimba wakho osabela ngayo kunyango, kunye nesantya sokukhula kwesi sifo .
Emva kokuba uxilongiwe, uza kuba nexesha lokubonana nogqirha ukuze iqela lakho lezonyango likwazi ukujonga iziphumo ebezingalindelekanga kwaye linike inkxaso efunekayo.
Ngaba iPineoblastoma ingathintelwa?
Ngelishwa, okwangoku akukho ndlela eyaziwayo yokuthintela iPineoblastoma .
Ufanele uye nini kugqirha?
Ukuba wena okanye umntwana wakho nifumana iimpawu zePineoblastoma, ezifana nezi:
- Intloko ebuhlungu engapheliyo
- Utshintsho kwindlela yokuziphatha
- Ubunzima bokuhamba kwamehlo
Nceda ubone ugqirha ngokukhawuleza.
Ukuba okwangoku ufumana unyango kwaye ufumana iziphumo ezingezizo ezintsha, yazisa iqela lakho lokhathalelo. Ukuba ukhathazekile ngokukhula okanye uphuhliso lomntwana wakho ngexesha lonyango, xoxa ngezi zinto ziqwalaselweyo nogqirha wezingane okanye ugqirha wezifo zomhlaza.
Ndingayibuza yiphi imibuzo ugqirha wam?
Xa udibana nogqirha wakho, kuyanceda ukubuza oku:
- Ucebisa luphi unyango?
- Ingaba umhlaza usasazekile?
- Ngaba kufuneka ndityandwe?
- Zithini iziphumo ebezingalindelekanga ezinokubakho ngenxa yolu nyango?
- Ithini ingqikelelo yam?
Ukuva igama elithi "umhlaza" kunokuba yinto eyoyikisayo neyoyikisayo. Kuqhelekile ukuba uzive wothukile okanye uxhalabile ngekamva. Musa ukuziva uwedwa. Iqela lakho lezonyango eNirogi Lanka lilapha ukukunceda uhambe kwesi sifo kwaye ukhethe isicwangciso sonyango esifanelekileyo kuwe. Thembela kubahlobo bakho kunye nosapho lwakho ukuze ufumane inkxaso. Uphando oluqhubekayo malunga nonyango olutsha lwePineoblastoma luyaqhubeka nokunika ithemba.
Umyalezo Wokuya Ekhaya
- I-Pineoblastoma sisimila esingaqhelekanga nesikhula ngokukhawuleza esikhula kwi-pineal gland yengqondo.
- Iimpawu ezifana neentloko ebuhlungu, iingxaki zokubona, ukulahlekelwa kukulinganisela, kunye notshintsho kwindlela yokuziphatha zinokwenzeka, rhoqo ngenxa ye -hydrocephalus (ukwakheka kolwelo engqondweni).
- Unobangela udla ngokuba yimfuza; abantu abane-Retinoblastoma okanye i-RB1/DICER1 gene mutations basengozini enkulu.
- Ukuxilongwa kubandakanya i-MRI, i-CT scans, kunye ne-biopsies.
- Nangona kunzima, unyango olusebenzayo olufana notyando, i-radiation, kunye ne-chemotherapy ziyafumaneka.
- Ukuba ubona iimpawu, funa ingcebiso kagqirha ngoko nangoko . Musa ukuthandabuza ukubuza imibuzo.
- Hlala unethemba kwaye uqine; awuwedwa kolu hambo.
Siyathemba ukuba olu lwazi luluncedo. Ukuba uneengxaki malunga nempilo yakho, nceda ucwangcise idinga kunye neengcali zempilo.
