Ngaba wakha waziva intlungu engaqhelekanga, engacacanga esiswini sakho okanye emqolo ongezantsi? Sinokucinga ukuba kukuhlaselwa yintliziyo okanye ukwenzakala okuncinci emqolo. Nangona kunjalo, namhlanje siza kuthetha ngemeko enokuba neempawu ezifanayo, engaqhelekanga, kodwa kubaluleke kakhulu ukuba sonke siyiqaphele. Oku kubizwa ngokuba yi-retroperitoneal fibrosis. Ngamanye amaxesha ikwabizwa ngokuba sisifo sika-Ormond.
Yintoni iRetroperitoneal Fibrosis? Ngamafutshane...
Ngamafutshane, i-retroperitoneal fibrosis
kukwakheka kwezicubu ezifana nezikrweqe (i-fibrosis) ezijikeleze amalungu akwindawo ebizwa ngokuba yi-retroperitoneum, indawo engasemva kwesisu sethu. Kufana nesikrweqe esakha eluswini lwethu, kodwa kwenzeka ngaphakathi emizimbeni yethu. Ngenxa yokuba yimeko eqhubekayo, iimpawu ezifana neentlungu kunye nokuncipha kokuphuma komchamo zinokuba mandundu ngokuhamba kwexesha.
Kulungile, yintoni le retroperitoneum?
Uninzi lwamalungu angaphakathi esiswini sethu (njengesibindi, isisu, amathumbu) lujikelezwe yi-membrane ekhuselayo ebizwa ngokuba yi-peritoneum.
Isithuba esingasemva kwale peritoneum, esibheke emgogodleni, sibizwa ngokuba yi-retroperitoneum. Le ndawo kulapho:
- Izintso
- Iindawo zenkqubo yomchamo
- Imithambo yegazi emikhulu ethwala igazi ukuya nokubuya emilenzeni (umzekelo, i-vena cava engaphantsi)
- Izitho ezibalulekileyo ezifana neendlala ze-adrenal zilapho.
Oku kuyichaphazela njani imizimba yethu?
Njengoko sele kukhankanyiwe, i-fibrosis, okanye izicubu ezibomvu, ziyakhula kancinci kancinci, zichaphazela amalungu kunye nezinye izakhiwo kwi-retroperitoneum.
Ngokuqhelekileyo, oku kuchaphazela kakhulu ii-ureters, iityhubhu ezithwala umchamo ukusuka kwizintso zethu ukuya kwisinyi. Khawucinge ukuba kwenzeka ntoni xa ezo zicubu ziqinileyo zijikeleza ezi tyhubhu kwaye ziqina? Kufana nokucinezela umbhobho wamanzi, ukuthintela ukuhamba komchamo. Ukuba le meko iba mandundu,
iingxaki ezisongela ubomi ezifana nokungasebenzi kakuhle kwezintso zinokwenzeka.
Ngubani onokuba nethuba elikhulu lokufumana i-retroperitoneal fibrosis?
Le meko
ixhaphake kakhulu kumadoda aphakathi kweminyaka engama-40 ukuya kwengama-60 ubudala. Oku kuthetha ukuba amadoda aphakathi kweminyaka asengozini enkulu kancinci. Ukongeza, kukho nezinye izinto ezininzi ezinobungozi:
- Kwabo basebenza ngezinto ezifana ne-asbestos (ngenxa yokuchatshazelwa zizo).
- Kwabo batshayayo kunyeKwabo basebenzisa iimveliso zecuba .
Yintoni ebangela oku? Izizathu zesifo sika-Ormond
Amaxesha amaninzi,
kunzima ukufumana unobangela othile woku. Kwizonyango, siwubiza ngokuba
yi-idiopathic . Oko kuthetha "isizathu esingaziwayo." Nangona kunjalo, kukho iimeko apho kwenzeka njengengxaki yesinye isifo. Ezinye zezizathu ziquka:
- Amanye amayeza (siza kuthetha ngale nto kancinci).
- Iintlobo zomhlaza , ingakumbi iHodgkin lymphoma kunye ne-non-Hodgkin lymphoma.
- Iimeko zosulelo .
- Unyango lwemitha kwizinto ezinje ngomhlaza.
- Ukonakala kwezicubu ezikuloo ndawo, nokuba kungenxa yotyando okanye enye ingozi.
Zeziphi iintlobo zamayeza ezinokubangela oku?
Kufunyaniswe ukuba le meko inokwenzeka xa amayeza athile esetyenziswa ixesha elide. Nazi imizekelo embalwa:
- Ii-Beta- blockers ludidi lwamayeza asetyenziselwa ukunyanga isifo sentliziyo . Imizekelo ibandakanya i-propranolol, i-metoprolol, kunye ne-atenolol.
- Ii-dopamine antagonists ziziyobisi ezisetyenziselwa ukunyanga izifo zengqondo kunye nesicaphucaphu. Imizekelo: i-methyldopa, i-pergolide.
- Iipilisi zeHydralazine zoxinzelelo lwegazi oluphezulu.
- Amayeza afana ne-ergotamine, esetyenziselwa ukunyanga iintloko ezibuhlungu.
- Ezinye iintlungu, ingakumbi ii-analgesics kunye nee-NSAIDs .
Kubalulekile: Ukuba usebenzisa olu hlobo lwamayeza, ungoyiki. Asinguye wonke umntu oza kuba nale meko. Kodwa kubalulekile ukuba uqaphele oku kwaye uthethe nogqirha wakho ngako.
Zithini iimpawu zoku?
Iimpawu zingahluka kumntu nomntu. Kuxhomekeke ekubeni iphi i-fibrosis kwaye inzima kangakanani.
Kwinqanaba lokuqala, ungaziva iintlungu esiswini sakho, emqolo osezantsi, okanye emacaleni. Le ntlungu inokuba ingacacanga, nto leyo ethetha ukuba kunzima ukuyiqonda "apha naphaya," kwaye ingaba yintlungu eqhelekileyo. Ezinye iimpawu ziquka:
- Kunzima ukushukumisa imilenze yakho nokuhambahamba.
- I-Hydrocele: Le yimeko apho amasende amadoda evuvukala khona.
- Ukudumba kwemilenze, iintlungu emilenzeni, okanye utshintsho kumbala wolusu emilenzeni.
- Ukuncipha kokuphuma komchamo.
Ziziphi iingxaki ezinokubakho zesifo sika-Ormond?
Ukuba i-retroperitoneal fibrosis iyaqhubeka, oko kuthetha ukuba izicubu zesilonda ziyanda kwaye ziqala ukucinezela amalungu omzimba, iingxaki
ezahlukeneyo zinokwenzeka. Ezinye zazo zezi:
- I-anemia: Oku kuthetha ukwehla kwenani leeseli ezibomvu zegazi emzimbeni, okanye "ukungabikho kwegazi".
- I-Anuria: Le yimeko apho umchamo ungaphumi konke konke. Le yimeko engxamisekileyo.
- Umzimba orhawuzelelayo.
- I-Jaundice: Ukutyheli kwamehlo nolusu.
- Isicaphucaphu nokuhlanza.
- Iingxaki ze-neurologic.
- Ukufa kwezicubu zamathumbu (necrosis).
- Ukuhla ukusinda.
Ifunyanwa njani i-retroperitoneal fibrosis?
Ukuba unale mpawu, bonana nogqirha aze akuxilonge. Oku kungabandakanya:
- Uvavanyo lomzimba: Ugqirha uza kuchukumisa isisu sakho ukuze ajonge naziphi na izinto ezingaqhelekanga, ezifana namaqhuma.
- Uvavanyo lwegazi: Olu vavanyo lunokufumanisa iimpawu zokuqala zesifo sezintso kunye neengxaki ezifana ne-anemia.
- I-ultrasound yezintso: Ukuba iimpawu zibonisa ingxaki yezintso, olu vavanyo lunokuvavanya i-fibrosis kunye nezinye iingxaki.
- I-CT scan: Oku kunokulinganisa ubukhali be-fibrosis. Kunokunceda ekuthinteleni ezinye iimeko, ezinje ngee-lymph nodes ezivuvukileyo kwi-groin okanye ezinye iithumba.
Ngaba kuyimfuneko ukwenza i-biopsy?
Kwiimeko ezininzi, i-retroperitoneal fibrosis inokufunyaniswa ngovavanyo lwegazi kunye novavanyo lwemifanekiso olukhankanyiweyo apha ngasentla (i-ultrasound, i-CT scan). Nangona kunjalo, kwezinye iimeko ezikhethekileyo
, i-biopsy inokufuneka. Oku kuthetha ukuthatha isiqwenga sesicwili kwaye usihlole phantsi kwe-microscope. Ezi meko ziquka:
- Ukuba kukho urhanelwa lokuba unomhlaza okanye usulelo.
- Ukuba unyango lokuqala aluphumelelanga.
Luhlobo luni lonyango endiludingayo?
Iindlela ezilungileyo zonyango kuwe ziya kuxhomekeka kwindawo kunye nobunzima be-fibrosis. Kwinqanaba lokuqala lesifo sika-Ormond, unyango lwakho lunokuquka:
- IiCorticosteroids:La mayeza anciphisa ngokukhawuleza ukudumba emzimbeni aze ayeke uphuhliso lwe-fibrosis.
- Ii-immunomodulators: La mayeza asebenza ngokutshintsha indlela esebenza ngayo inkqubo yomzimba yokuzikhusela. Oku kunokunciphisa umngcipheko we-fibrosis ophinda ubuye kwixesha elizayo. Nangona kunjalo, ekubeni ii-immunomodulators zinokuthatha iinyanga ezininzi ukusebenza, zinokunikwa kunye ne-corticosteroids.
- Ulawulo lwamayeza: Ngamanye amaxesha, ukuba i-fibrosis ibangelwa yimithi oyithathayo, ugqirha wakho unokutshintsha amayeza okanye anciphise umthamo.
Ukuba i-fibrosis iqhubekile, kunokufuneka olunye unyango:
- Utyando: Kusenokufuneka utyando ukuze kususwe izicubu ze-fibrotic kunye nokulungisa nawuphi na umonakalo kwizicubu ezijikelezileyo.
- Iistenti: Njengoko bekutshiwo ngaphambili, ukuba i-ureter ivaliwe, isixhobo esincinci esifana netyhubhu (i-stent) singafakwa ngaphakathi kuyo ukuze sihlale sivulekile.
Sikuthintela njani ukuphuhliswa kwe-retroperitoneal fibrosis?
Ekubeni le meko idla ngokuba yinto engaqhelekanga,
kunzima ukuyithintela ngokupheleleyo. Nangona kunjalo, ekubeni amanye amayeza aziwa ukuba abangela le nto, ugqirha wakho uya kukujonga iimpawu ze-fibrosis, ingakumbi ukuba uzithatha ixesha elide.
Ngaba amathuba okuba oku kwenzeke kwakhona angancitshiswa emva konyango?
Ukuba kufuneka wenze utyando, ngamanye amaxesha umaleko wezicubu ezinamafutha ujikeleza i-ureter ngexesha lotyando. Kuthiwa oku kwenza kube nzima ukuba i-fibrosis iphinde ivele.
Ndiza kuziva bhetele kungekudala kangakanani?
Ukuba usela amayeza afana ne-corticosteroids, okanye emva kokulawula amayeza
, ungaqala ukuziva ungcono kwiiveki ezimbalwa. Nangona kunjalo, ukuba udinga ii-immunomodulators, ii-stents, okanye utyando, kuya kuthatha ixesha elide ukuba uphile.
Iyintoni imbono yabantu abane-retroperitoneal fibrosis?
Uninzi lwabantu luyachacha ngokupheleleyo. Ithuba elihle lonyango oluphumelelayo
kuxa isifo sifunyenwe kwangethuba. Nangona kunjalo, kubalulekile ukukhumbula ukuba i-fibrosis inokuphinda ivele emva kweenyanga okanye iminyaka emva konyango.
Kunjani ukuphila nesifo sika-Ormond?
Kwabo baneengxaki ezincinci,
kuya kufuneka uqhubeke uphantsi kweliso likagqirha. Oku kuthetha ukuba kuya kufuneka ubone ugqirha wakho rhoqo ukuze ujonge iimpawu zokuba isifo sibuya.
Kwenzeka ntoni emva kotyando ukulungisa ukuvaleka komchamo?
I-Hydronephrosis inokwenzeka xa, kwiintsuku ezimbalwa emva kotyando, oogqirha bekhupha umchamo oqokelelene kwizintso zakho ngequbuliso.Qaphela ingxaki ebizwa ngokuba yi-"urinary retention." Xa umchamo obuvaleleke emzimbeni uphuma ngequbuliso, oku kulandelayo kunokwenzeka:
- Ukungalingani kwe-electrolyte emzimbeni.
- Ukuphelelwa ngamanzi emzimbeni.
- Ukothuka kwe-Hypovolemic (imeko ebangelwa kukuncipha komthamo wegazi).
I-Retroperitoneal fibrosis, okanye isifo sika-Ormond, yimeko apho izicubu ezifana nezibazi zenzeka ngasemva kwesisu. Abantu abasebenzisa amayeza athile basengozini enkulu yokuhlaselwa yile meko. Ukuba ufunyenwe unale meko, thetha nogqirha wakho ngayo nayiphi na imibuzo okanye iinkxalabo onokuba nazo. Bakho ukuze bakuncede.
Izinto ezibalulekileyo ekufuneka uzikhumbule (Umyalezo Wokuya Ekhaya)
Kulungile, ngoku siyaqonda ngcono ukuba yintoni iRetroperitoneal Fibrosis.
Nangona ingaqhelekanga, kubaluleke kakhulu ukuyiqonda.- Khumbula, esi sisicwili esityebileyo esijikeleza amalungu afanele ukuba angaphakathi esiswini, ukuya kumqolo.
- Idla ngokuchaphazela i-ureters kwaye inokonakalisa izintso.
- Isizathu asisoloko sicacile, kodwa izinto ezifana namayeza athile, umhlaza, kunye nosulelo nazo zinokuba zizizathu.
- Kubalulekile ukufuna ingcebiso kagqirha ukuba uneempawu ezifana nentlungu yesisu/umqolo engacacanga kunye nokuncipha komchamo.
- Kukho unyango olufanelekileyo xa lufunyenwe kwangethuba. Ngoko ke musa ukuzityeshela iimpawu.
- Ukuba unemibuzo malunga noku, ungoyiki ukubuza ugqirha wakho.
Siyathemba ukuba olu lwazi luza kukunceda. Hlala usempilweni!
I-Retroperitoneal Fibrosis, isifo sika-Ormond, isifo sezintso, iintlungu zesisu, iingxaki zomchamo, i-fibrosis, utyando
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