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Izinkinga Zesifo Se-Sickle Cell: Okudingeka Ukwazi

Izinkinga Zesifo Se-Sickle Cell: Okudingeka Ukwazi

Kungenzeka ukuthi uke wezwa ngeSickle Cell Disease . Kalula nje, yisimo esithinta indlela umzimba wethu odala ngayo amangqamuzana abomvu egazi . Uyazi, lawa maseli abomvu egazi yiwo athwala umoya-mpilo emizimbeni yethu yonke. Ngokuvamile, lawa maseli ayizicaba, ayindilinga, futhi aguquguqukayo. Kodwa umuntu onesifo se-sickle cell uba namangqamuzana abomvu egazi aqinile, amise okwesikela. Ngakho-ke, lesi simo esingavamile singaholela ezinkingeni eziningi zempilo, noma ' izinkinga '. Kodwa ungakhathazeki, udokotela wakho angasiza ekwelapheni eziningi zalezi zinkinga, futhi avimbele ezinye zazo. Ake sixoxe ngazo ngayinye.

Ubuhlungu - inkinga evame kakhulu

Inkinga evame kakhulu futhi ecasulayo yesifo se-sickle cell ubuhlungu . Lokhu kungenxa yokuthi amangqamuzana amise okwesickle abhajwa emithanjeni yegazi emincane. Cabanga ngalokho okwenzekayo lapho imoto enkulu ibhajwa emgwaqweni omncane. Yilokho okwenzekayo lapho la maseli evimba imithambo yegazi.

Lobuhlungu buvame ukwenzeka emhlane ongezansi, emilenzeni, ezingalweni, esiswini, noma esifubeni. Bungavela ngokuzumayo njengokuhlasela okukhulu (inkinga noma isiqephu). Kwabancane nabadala, ngezinye izikhathi kungaba ubuhlungu besikhathi eside.

Ngokuvamile, uma uhlaselwa ubuhlungu kanje, ungathola impumuzo ngamaphilisi obuhlungu njengeParacetamol noma i-Ibuprofen . Kodwa khumbula, unganiki i-aspirin kunoma ubani oneminyaka engaphansi kwengu-19. Ngezinye izikhathi, uma ubuhlungu bukhulu, udokotela angase akunike umuthi onamandla wokuqeda ubuhlungu ovela eqenjini lama-opioid. Abanye abantu baze badingeke bangeniswe esibhedlela ukuze bathole ukwelashwa.

Udokotela wakho angase ancome amathiphu alandelayo okuvimbela noma ukunciphisa lokhu kuhlaselwa ubuhlungu:

  • Phuza amanzi amaningi.
  • Gwema ukushisa okukhulu nokubanda okukhulu.
  • Ungachithi isikhathi esiningi ezindaweni eziphakeme, njengezindawo ezinezintaba.
  • Umuthi obizwa ngokuthi i-Hydroxyurea usiza ekunciphiseni ukuvama kwalokhu kuhlaselwa ubuhlungu ezinganeni nakubantu abadala.

I-anemia

Lena enye inkinga evamile yesifo se-sickle cell. Yilapho amangqamuzana abomvu egazi anjengesickle efa khona ngokushesha kunamangqamuzana avamile.Ngakho-ke umzimba awukwazi ukwenza amangqamuzana amasha ngesivinini esifanayo nokufa kwawo. Ngenxa yalokho, inani lomoya-mpilo ofinyelela amangqamuzana omzimba liyancipha, futhi ungase uzizwe ukhathele kakhulu, ubuthakathaka, futhi unesiyezi . Ungase futhi ubhekane nezinto ezifana nokushaya kwenhliziyo okusheshayo kanye nobunzima bokuphefumula. Enganeni, i-anemia ingabangela nokukhula okubambezelekile.

Uma i-anemia inzima kakhulu, kungadingeka ukumpontshelwa igazi . Kodwa-ke, ukumpontshelwa igazi njalo kungabangela amazinga ensimbi akhuphuke futhi kulimaze inhliziyo, isibindi, kanye ne-pancreas. Ngakho-ke, udokotela wakho uzohlola amazinga akho ensimbi njalo ukuze asize ekulawuleni. Kwabantu abadala, umuthi i-Hydroxyurea ungasiza futhi nge-anemia.

Inkinga Izimpawu eziyinhloko Okufanele ngikwenze
Ukususwa kwe-Splenic Ubuhlungu besisu obuvela ohlangothini lwesobunxele, ukuphaphatheka, ukozela okukhulu, ukushaya kwenhliziyo okusheshayo. Lesi yisimo esiphuthumayo esisongela ukuphila. Yiya eMnyangweni Wezimo Eziphuthumayo wesibhedlela (ETU) ngokushesha.
Isifo Sesifuba Esibukhali Umkhuhlane, ubunzima bokuphefumula, ubuhlungu besifuba, ukukhwehlela. Lesi futhi yisimo esibucayi kakhulu. Yiya e-Emergency Treatment Unit (ETU) yesibhedlela ngokushesha.

Izifo nezinye izimo eziphuthumayo

Ukuthambekela okukhulu ekuthelelekeni

Abantu abanesifo se-sickle cell, ikakhulukazi izingane ezincane, banamathuba amaningi okuthola izifo. Lokhu kungenxa yokuthi lesi sifo silimaza i-bell . Uyazi, i-bell iyisitho esibalulekile esihlunga amagciwane afana namagciwane egazini lethu. Ngakho-ke uma ingasebenzi kahle, izifo zingangena kalula emzimbeni.

Kubalulekile ukuthola ukwelashwa ngisho nokutheleleka okuncane ngaphambi kokuba kube kubi kakhulu. Uma wena noma ingane yakho inomkhuhlane ongaphezu kuka-101°F (38.3°C), bona udokotela noma uye emnyangweni wezimo eziphuthumayo wesibhedlela (ETU) ngokushesha.

Ukususwa kwe-Splenic

Lesi yisimo esiphuthumayo esisongela ukuphila, ikakhulukazi ezinganeni ezincane. Lokhu kwenzeka lapho amaseli esikela evimba ukugeleza kwegazi eliya embewini. Imbewini iyavuvukala futhi ibe buhlungu. Ezinye izingane zingase zingabi nazimpawu ezinkulu. Kodwa-ke, ezinye zingase zibe nezimpawu ezifana nobuthakathaka, isikhumba esikhanyayo nezindebe, ukozela ngokweqile, ubuhlungu ohlangothini lwesobunxele lwesisu, kanye nokushaya kwenhliziyo okusheshayo . Uma uhlangabezana nalezi zimpawu, iya esibhedlela ngokushesha .

Isifo Sesifuba Esibukhali

Lesi futhi yisimo esibi kakhulu. Yilapho isifo se-sickle cell sivimba khona imithambo yegazi emaphashini. Uma unezimpawu ezifana nomkhuhlane, ubunzima bokuphefumula, ubuhlungu besifuba, nokukhwehlela , hamba esibhedlela ngokushesha. Odokotela bangase bakunike umoya-mpilo, ama-antibiotic, futhi mhlawumbe nokumpontshelwa igazi.

Ezinye izinkinga zesikhathi eside

Isifo se-sickle cell singadala izinkinga ezengeziwe ngokuhamba kwesikhathi.

  • Ukulahlekelwa yithambo (i-Avascular Necrosis): Lapho igazi ligeleza emalungeni amakhulu (njengesinqe) linqunywa, izicubu zamathambo ziqala ukufa. Lokhu kuvamile kubantu abasha nabadala. Ama-painkiller angase anikeze impumuzo, kodwa abanye abantu bangadinga ukuhlinzwa.
  • Ukulimala kwezinye izitho zomzimba: Izinkinga zamehlo, inhliziyo, izinso, nesibindi zisengozini enkulu yokuqhekeka kwegazi kanye nesifo sohlangothi. Yingakho udokotela wakho ezohlola njalo ukusebenza kwalezi zitho zomzimba.

Ukufakelwa Umongo Wethambo kanye Nokwelashwa Kwanamuhla

Kulabo abavame ukubhekana nezinkinga ezinkulu, ukwelashwa okubizwa ngokuthi ukufakelwa umnkantsha kungacatshangelwa. Lokhu kuhilela ukufaka amaseli anempilo esikhundleni samaseli omnkantsha akhiqiza i-sickle-cell. Lokhu kungasiqeda ngokuphelele lesi sifo.

Kodwa lokhu akuyona into engenziwa yiwo wonke umuntu. Udinga ukuthola umnikeli onempilo ofanelana nezicubu zakho. Futhi, uma unezinkinga ngezitho ezifana nenhliziyo noma izinso, lokhu kuhlinzwa kungaba yingozi. Kungase kudingeke uhlale esibhedlela isikhathi eside. Ngezinye izikhathi lokhu kwelashwa kungase kungaphumeleli. Ngakho-ke, umndeni kufanele ukhulume nodokotela ngokucophelela bese unquma ukuthi lokhu kwelashwa kuyabafanele yini.

Ngaphezu kwalokho, kunemithi emisha, njenge -Crizanlizumab, engasiza ekunciphiseni ukuhlaselwa ubuhlungu. Buza udokotela wakho ngale mithi futhi.

Umlayezo Wokuya Nawe Ekhaya

  • Isifo se-sickle cell yisimo sofuzo esishintsha isimo samaseli abomvu egazi. Lokhu kungabangela izinkinga ezinkulu njengobuhlungu, ukuntuleka kwegazi kanye nokulimala kwezitho zomzimba.
  • Uma uhlangabezana nezimpawu ezifana nobuhlungu, umkhuhlane, ubunzima bokuphefumula, noma ukuphaphatheka okukhulu, funa iseluleko sezokwelapha ngokushesha noma uye e-Emergency Treatment Unit (ETU) yesibhedlela.
  • Izinkinga eziningi zingalawulwa ngokuphuza amanzi amaningi, ukugcina indlela yokuphila enempilo, kanye nokuthatha imithi (njenge-Hydroxyurea) njengoba udokotela wakho ekuyalele.
  • Kubantwana, kubaluleke kakhulu ukuvimbela ukutheleleka ngokuthola yonke imijovo ngesikhathi nokubanika ama-antibiotic nsuku zonke.
  • Uma unemibuzo noma ukukhathazeka ngesimo sakho noma sengane yakho, xoxa ngaso njalo nodokotela wakho. Ungaphila ngempumelelo nalesi sifo ngaphandle kokwesaba, ngokwaziswa.

Isifo Se-Sickle Cell, i-Anemia, inkinga yobuhlungu, ukufakelwa umnkantsha, impilo yaseSri Lanka
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.

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Izinkinga Zesifo Se-Sickle Cell: Okudingeka Ukwazi

Izinkinga Zesifo Se-Sickle Cell: Okudingeka Ukwazi

Kungenzeka ukuthi uke wezwa ngeSickle Cell Disease . Kalula nje, yisimo esithinta indlela umzimba wethu odala ngayo amangqamuzana abomvu egazi . Uyazi, lawa maseli abomvu egazi yiwo athwala umoya-mpilo emizimbeni yethu yonke. Ngokuvamile, lawa maseli ayizicaba, ayindilinga, futhi aguquguqukayo. Kodwa umuntu onesifo se-sickle cell uba namangqamuzana abomvu egazi aqinile, amise okwesikela. Ngakho-ke, lesi simo esingavamile singaholela ezinkingeni eziningi zempilo, noma ' izinkinga '. Kodwa ungakhathazeki, udokotela wakho angasiza ekwelapheni eziningi zalezi zinkinga, futhi avimbele ezinye zazo. Ake sixoxe ngazo ngayinye.

Ubuhlungu - inkinga evame kakhulu

Inkinga evame kakhulu futhi ecasulayo yesifo se-sickle cell ubuhlungu . Lokhu kungenxa yokuthi amangqamuzana amise okwesickle abhajwa emithanjeni yegazi emincane. Cabanga ngalokho okwenzekayo lapho imoto enkulu ibhajwa emgwaqweni omncane. Yilokho okwenzekayo lapho la maseli evimba imithambo yegazi.

Lobuhlungu buvame ukwenzeka emhlane ongezansi, emilenzeni, ezingalweni, esiswini, noma esifubeni. Bungavela ngokuzumayo njengokuhlasela okukhulu (inkinga noma isiqephu). Kwabancane nabadala, ngezinye izikhathi kungaba ubuhlungu besikhathi eside.

Ngokuvamile, uma uhlaselwa ubuhlungu kanje, ungathola impumuzo ngamaphilisi obuhlungu njengeParacetamol noma i-Ibuprofen . Kodwa khumbula, unganiki i-aspirin kunoma ubani oneminyaka engaphansi kwengu-19. Ngezinye izikhathi, uma ubuhlungu bukhulu, udokotela angase akunike umuthi onamandla wokuqeda ubuhlungu ovela eqenjini lama-opioid. Abanye abantu baze badingeke bangeniswe esibhedlela ukuze bathole ukwelashwa.

Udokotela wakho angase ancome amathiphu alandelayo okuvimbela noma ukunciphisa lokhu kuhlaselwa ubuhlungu:

  • Phuza amanzi amaningi.
  • Gwema ukushisa okukhulu nokubanda okukhulu.
  • Ungachithi isikhathi esiningi ezindaweni eziphakeme, njengezindawo ezinezintaba.
  • Umuthi obizwa ngokuthi i-Hydroxyurea usiza ekunciphiseni ukuvama kwalokhu kuhlaselwa ubuhlungu ezinganeni nakubantu abadala.

I-anemia

Lena enye inkinga evamile yesifo se-sickle cell. Yilapho amangqamuzana abomvu egazi anjengesickle efa khona ngokushesha kunamangqamuzana avamile.Ngakho-ke umzimba awukwazi ukwenza amangqamuzana amasha ngesivinini esifanayo nokufa kwawo. Ngenxa yalokho, inani lomoya-mpilo ofinyelela amangqamuzana omzimba liyancipha, futhi ungase uzizwe ukhathele kakhulu, ubuthakathaka, futhi unesiyezi . Ungase futhi ubhekane nezinto ezifana nokushaya kwenhliziyo okusheshayo kanye nobunzima bokuphefumula. Enganeni, i-anemia ingabangela nokukhula okubambezelekile.

Uma i-anemia inzima kakhulu, kungadingeka ukumpontshelwa igazi . Kodwa-ke, ukumpontshelwa igazi njalo kungabangela amazinga ensimbi akhuphuke futhi kulimaze inhliziyo, isibindi, kanye ne-pancreas. Ngakho-ke, udokotela wakho uzohlola amazinga akho ensimbi njalo ukuze asize ekulawuleni. Kwabantu abadala, umuthi i-Hydroxyurea ungasiza futhi nge-anemia.

Inkinga Izimpawu eziyinhloko Okufanele ngikwenze
Ukususwa kwe-Splenic Ubuhlungu besisu obuvela ohlangothini lwesobunxele, ukuphaphatheka, ukozela okukhulu, ukushaya kwenhliziyo okusheshayo. Lesi yisimo esiphuthumayo esisongela ukuphila. Yiya eMnyangweni Wezimo Eziphuthumayo wesibhedlela (ETU) ngokushesha.
Isifo Sesifuba Esibukhali Umkhuhlane, ubunzima bokuphefumula, ubuhlungu besifuba, ukukhwehlela. Lesi futhi yisimo esibucayi kakhulu. Yiya e-Emergency Treatment Unit (ETU) yesibhedlela ngokushesha.

Izifo nezinye izimo eziphuthumayo

Ukuthambekela okukhulu ekuthelelekeni

Abantu abanesifo se-sickle cell, ikakhulukazi izingane ezincane, banamathuba amaningi okuthola izifo. Lokhu kungenxa yokuthi lesi sifo silimaza i-bell . Uyazi, i-bell iyisitho esibalulekile esihlunga amagciwane afana namagciwane egazini lethu. Ngakho-ke uma ingasebenzi kahle, izifo zingangena kalula emzimbeni.

Kubalulekile ukuthola ukwelashwa ngisho nokutheleleka okuncane ngaphambi kokuba kube kubi kakhulu. Uma wena noma ingane yakho inomkhuhlane ongaphezu kuka-101°F (38.3°C), bona udokotela noma uye emnyangweni wezimo eziphuthumayo wesibhedlela (ETU) ngokushesha.

Ukususwa kwe-Splenic

Lesi yisimo esiphuthumayo esisongela ukuphila, ikakhulukazi ezinganeni ezincane. Lokhu kwenzeka lapho amaseli esikela evimba ukugeleza kwegazi eliya embewini. Imbewini iyavuvukala futhi ibe buhlungu. Ezinye izingane zingase zingabi nazimpawu ezinkulu. Kodwa-ke, ezinye zingase zibe nezimpawu ezifana nobuthakathaka, isikhumba esikhanyayo nezindebe, ukozela ngokweqile, ubuhlungu ohlangothini lwesobunxele lwesisu, kanye nokushaya kwenhliziyo okusheshayo . Uma uhlangabezana nalezi zimpawu, iya esibhedlela ngokushesha .

Isifo Sesifuba Esibukhali

Lesi futhi yisimo esibi kakhulu. Yilapho isifo se-sickle cell sivimba khona imithambo yegazi emaphashini. Uma unezimpawu ezifana nomkhuhlane, ubunzima bokuphefumula, ubuhlungu besifuba, nokukhwehlela , hamba esibhedlela ngokushesha. Odokotela bangase bakunike umoya-mpilo, ama-antibiotic, futhi mhlawumbe nokumpontshelwa igazi.

Ezinye izinkinga zesikhathi eside

Isifo se-sickle cell singadala izinkinga ezengeziwe ngokuhamba kwesikhathi.

  • Ukulahlekelwa yithambo (i-Avascular Necrosis): Lapho igazi ligeleza emalungeni amakhulu (njengesinqe) linqunywa, izicubu zamathambo ziqala ukufa. Lokhu kuvamile kubantu abasha nabadala. Ama-painkiller angase anikeze impumuzo, kodwa abanye abantu bangadinga ukuhlinzwa.
  • Ukulimala kwezinye izitho zomzimba: Izinkinga zamehlo, inhliziyo, izinso, nesibindi zisengozini enkulu yokuqhekeka kwegazi kanye nesifo sohlangothi. Yingakho udokotela wakho ezohlola njalo ukusebenza kwalezi zitho zomzimba.

Ukufakelwa Umongo Wethambo kanye Nokwelashwa Kwanamuhla

Kulabo abavame ukubhekana nezinkinga ezinkulu, ukwelashwa okubizwa ngokuthi ukufakelwa umnkantsha kungacatshangelwa. Lokhu kuhilela ukufaka amaseli anempilo esikhundleni samaseli omnkantsha akhiqiza i-sickle-cell. Lokhu kungasiqeda ngokuphelele lesi sifo.

Kodwa lokhu akuyona into engenziwa yiwo wonke umuntu. Udinga ukuthola umnikeli onempilo ofanelana nezicubu zakho. Futhi, uma unezinkinga ngezitho ezifana nenhliziyo noma izinso, lokhu kuhlinzwa kungaba yingozi. Kungase kudingeke uhlale esibhedlela isikhathi eside. Ngezinye izikhathi lokhu kwelashwa kungase kungaphumeleli. Ngakho-ke, umndeni kufanele ukhulume nodokotela ngokucophelela bese unquma ukuthi lokhu kwelashwa kuyabafanele yini.

Ngaphezu kwalokho, kunemithi emisha, njenge -Crizanlizumab, engasiza ekunciphiseni ukuhlaselwa ubuhlungu. Buza udokotela wakho ngale mithi futhi.

Umlayezo Wokuya Nawe Ekhaya

  • Isifo se-sickle cell yisimo sofuzo esishintsha isimo samaseli abomvu egazi. Lokhu kungabangela izinkinga ezinkulu njengobuhlungu, ukuntuleka kwegazi kanye nokulimala kwezitho zomzimba.
  • Uma uhlangabezana nezimpawu ezifana nobuhlungu, umkhuhlane, ubunzima bokuphefumula, noma ukuphaphatheka okukhulu, funa iseluleko sezokwelapha ngokushesha noma uye e-Emergency Treatment Unit (ETU) yesibhedlela.
  • Izinkinga eziningi zingalawulwa ngokuphuza amanzi amaningi, ukugcina indlela yokuphila enempilo, kanye nokuthatha imithi (njenge-Hydroxyurea) njengoba udokotela wakho ekuyalele.
  • Kubantwana, kubaluleke kakhulu ukuvimbela ukutheleleka ngokuthola yonke imijovo ngesikhathi nokubanika ama-antibiotic nsuku zonke.
  • Uma unemibuzo noma ukukhathazeka ngesimo sakho noma sengane yakho, xoxa ngaso njalo nodokotela wakho. Ungaphila ngempumelelo nalesi sifo ngaphandle kokwesaba, ngokwaziswa.

Isifo Se-Sickle Cell, i-Anemia, inkinga yobuhlungu, ukufakelwa umnkantsha, impilo yaseSri Lanka
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.

Engeza amazwana akho

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