Uma ingane yakho itholakale inesifo se-Sickle Cell Disease (SCD), kuyinto evamile ukuzizwa ukhathazekile noma ukhungathekile. Ukuphatha lesi simo kudinga ukuqapha. Namuhla, sifuna ukukhuluma ngenkinga enkulu, engase ibe yingozi empilweni okudingeka uyiqaphele: 'Ukuqothulwa kwe-Splenic.' Nakuba igama lingase lizwakale liyinkimbinkimbi, ukuqonda ukuthi liyini kungakusiza ugcine ingane yakho iphephile.
Kuyini ngempela ukuthuthwa kwe-Splenic?
Ukuze siqonde lokhu, ake sibheke kafushane ukuthi i-SCD isebenza kanjani. Emzimbeni ophilile, amangqamuzana abomvu egazi ayindilinga futhi aguquguquka, okwenza ageleze kalula emithanjeni yegazi. Kodwa-ke, ezinganeni ezine-SCD, ushintsho ku -hemoglobin lubangela ukuthi lawa maseli abe nesimo esiqinile, 'esisikele' noma esicwebezelayo.
Ngenxa yesimo sawo, la maseli awahambi kahle; ayanamathelana futhi angabanjwa ngaphakathi kwemithambo yegazi emincane.
Yilapho inkinga iqala khona. Esitholakala ohlangothini olungaphezulu kwesobunxele lwesisu kukhona isitho esibizwa ngokuthi i -spleen ( i-spleen ). I-spleen isebenza njengesihlungi, isusa amagciwane namaseli amadala egazini lakho. Ezinganeni ezine-SCD, lawa maseli amise okwesikela ayabhajwa ngaphakathi kwemithambo emincane ye-spleen, njengokuminyana kwezimoto emgwaqweni omkhulu.
Uma lokhu kuvinjelwa kwenzeka, igazi okufanele lijikeleze emzimbeni libanjwa ngaphakathi kwe-spleen. I-spleen igcwala igazi, okubangela ukuba ivuvuke ngokushesha. Lesi simo esiyingozi yilokho esikubiza ngokuthi 'i-Splenic Sequestration.'
Njengoba inani elikhulu legazi libhajwa ebhodweni, inani lamaseli abomvu egazi ajikeleza kuwo wonke umzimba liyehla kakhulu, okuholela ekulahlekelweni kwegazi okukhulu. Lokhu kungabangela ingane yakho ukuba ibe buthakathaka kakhulu futhi ibe mhlophe ngokuzumayo.
Izimpawu: Okufanele ukuqaphele njengomzali
Ukuqaphela lezi zimpawu kungakusiza ukuthi uthathe isinyathelo ngokushesha futhi mhlawumbe usindise impilo yengane yakho. Nakuba kuvame kakhulu ezinganeni ezincane, kungenzeka ezigulini ze-SCD zanoma yimuphi ubudala.
| Isibonakaliso | Okufanele ukubheke |
|---|---|
| Ubuhlungu esiswini esingaphezulu kwesobunxele | Lesi yisibonakaliso esivame kakhulu. Uma ingane yakho ikhala ngobuhlungu endaweni lapho kukhona khona udende, naka kakhulu. |
| I-Splenomegaly (ubende obuvuvukile) | Cela udokotela wakho akufundise ukuthi ungayithinta kanjani indawo yengane yakho enobende. Uma izwakala inkulu, iqinile, noma ithambile uma uyithinta, kuyisibonakaliso esiyisixwayiso. |
| Ubuthakathaka nokukhathala okungazelelwe | Uma ingane ebidlala nje ngokuzumayo iba buthaka noma ibuthakathaka kakhulu ukuba ime, hlala uqaphile. |
| Isikhumba esikhanyayo | Hlola izindebe zengane, izinsini, kanye nezandla; uma zibukeka ziphaphathekile ngendlela engavamile, lokhu kuyisibonakaliso se-anemia. |
| Ukuphefumula okusheshayo noma ukushaya kwenhliziyo | Uma umzimba ungenawo umoya-mpilo, inhliziyo namaphaphu kumele asebenze kanzima ukuze abuyisele umoya-mpilo. |
| Ukucasuka | Ngenxa yokuthi ingane ayiphilile kahle emzimbeni, ingase ibe nemizwa engathandeki noma ixakeke ngendlela engavamile. |
| Ukudinwa okukhulu | Uma ingane ilele kakhulu futhi kunzima ukuyivusa, lokhu kuyisibonakaliso esibi kakhulu. |
Isaziso Esibalulekile: Ngezinye izikhathi, ngisho noma kungekho zimpawu ezisobala, ukwehla kwamaseli abomvu egazi kungaba ngokushesha. Uma ubona noma yiziphi zalezi zimpawu, funa usizo lwezokwelapha oluphuthumayo ngokushesha. Lesi simo asinakuphathwa ekhaya.
Kutholakala kanjani?
Uma usufikile emnyangweni wezimo eziphuthumayo, udokotela wakho uzothatha izinyathelo eziningana ukuqinisekisa isimo:
1. Ukuhlolwa Komzimba : Udokotela uzohlola isisu sengane ukuze ahlole ukuthi ngabe udengezi lukhulisiwe yini.
2. Ukuhlolwa Kwegazi: Lokhu kubalulekile. Kuzothathwa isampula ukuhlola izinga le-hemoglobin ukuze kubonakale ukuthi i-anemia imbi kangakanani, kanye nokubalwa kwamangqamuzana amhlophe egazi kanye nama-platelet.
3. Ezinye Izivivinyo: Kwezinye izimo, izivivinyo zokuthwebula izithombe ezifana ne-X-ray noma i -CT scan zingasetshenziswa ukuze kutholakale umbono ongcono we-spleen.
Ukwelashwa: Ungesabi
Nakuba lokhu kuyisimo esiphuthumayo, kungaphathwa ngempumelelo uma ufuna ukunakekelwa esibhedlela ngokushesha.
Ukwelashwa okuyinhloko ukumpontshelwa igazi . Lokhu kubuyisela inani lamaseli abomvu egazi emzimbeni wengane yakho, kunikeze umoya-mpilo odingwa yizitho zayo. Ezimweni ezimbi kakhulu lapho udengezi lugcwele kakhulu, odokotela kungadingeka futhi baqaphe ngokucophelela amazinga oketshezi.
Kuthiwani uma kwenzeka futhi?
Inselele enkulu nge-Splenic Sequestration ukuthi uma kwenzeka, kunethuba elikhulu lokuthi iphinde ivele . Ezinye izingane zingase zibhekane nalokhu izikhathi eziningi.
Uma kwenzeka izigameko eziphindaphindayo, udokotela wakho angase asikisele ukususwa kwe-spleen (ukususwa kwe-spleen ngokuhlinzwa). Nakuba lokhu kuvimbela izigameko zokuhlukaniswa kwesisu esikhathini esizayo, kuyathinta amasosha omzimba. Udokotela wakho uzokunikeza isiqondiso ngama-antibiotic akhethekile noma imijovo edingekayo ukuvikela ingane yakho uma le nqubo yenziwa.
Umlayezo Wokuya Nawe Ekhaya
- Ukwebiwa kwe-Splenic kuyisimo sezokwelapha esisongela impilo, esiphuthumayo esingathinta izingane ezineSickle Cell Disease.
- Qaphela ubuhlungu besisu, ukuphaphatheka, ukukhathala okukhulu, kanye nobende oluvuvukele.
- Funda ukuthi ungawuhlola kanjani umbende wengane yakho kudokotela wakho; leli khono lingasindisa impilo.
- Uma usola ukuthi ingane yakho ibhekene nalokhu, iya emnyangweni wezimo eziphuthumayo oseduze ngokushesha.
- Ngenxa yokuthi lokhu kunezinga eliphezulu lokuphindaphinda, hlala useduze nethimba lakho lezokwelapha futhi ulandele iseluleko sabo ngokuqinile.
Ukususwa Kwe-Splenic, Isifo Se-Sickle Cell, I-SCD, I-Spleen, I-Anemia, I-Pediatrics, Ukunakekelwa Okuphuthumayo, Ukumpontshelwa Igazi
