Chair atanga tho chhuah harsa i ti fo thin em? Stairs i chhoh hian i ke chu chak loin i hria em? A nih loh leh thil i chawi chhuah hian i kutah chakna nei lo ang maiin i inhria em? Hêng thilte hi hahna vanga thil thleng pangngaiah ngai mah ila, a châng chuan hemi hnuaiah hian kan hriat vak loh natna a awm thei a ni. Vawiin hian hetiang natna rapthlak tak hi kan sawi a, mahse hriat chian a phu hle. Chu chu Polymyositis a ni.
A awlsam zawngin Polymyositis chu eng nge ni?
Polymyositis hi a awm lo hle a ni. Autoimmune natna a ni a . Hetiang hian han ngaihtuah teh: kan immune system hi ram venghimtu sipai ang a ni. Chu sipai hna chu pawn lam atanga lo chhuak hrik leh virus do a, kan taksa venhim hi a ni. Mahse Polymyositis-ah chuan he sipai hi a kal sual a, pawn lam hmêlma ai chuan kan taksa ruh hrisel tak takte chu kan bei tan ta a ni.
A awlsam zawngin kan invenna hian min rawn bei mek a ni . Hei hi Myositis an ti a, chu chu taksa ruh natna (inflammation or swelling of the muscles) tihna a ni. Polymyositis -ah chuan "Poly" tih thumal hian "tam tak" tihna a ni. Chumi awmzia chu hetiang dinhmunah hian taksa peng hrang hranga ruh (muscle) te chu a rualin a nghawng thei tihna a ni.
Hei hian kan taksa lairil hnaih ber ruhte a nghawng fo thin. Entir nan:
- Kut (a bik takin kephah leh kutphah) .
- Hips leh thighs te
- Chest leh hnungzang
- Kawng ruh (neck muscle) te
He natna thlentu dik tak hi hriat chian a la ni lo. Tin, a damdawi pawh a la awm lo. Mahse, lungngai suh. Enkawlna leh enkawl dan mumal tak a awm chuan mi tam tak chuan heng natna lanchhuahnate hi an thunun thei a, nun pangngaiin an khawsa thei tawh a ni.
He natna lan chhuah dan engte nge ni?
Polymyositis symptoms hi mi hrang hrangah a inang lo thei. Mahse, a lan chhuah dan tlangpui leh nitin nunah harsatna a thlen thin thenkhat a awm. Table pakhatah han en ila.
| Symptom a ni | A awlsam zawngin sawifiah a ni |
|---|---|
| Muscle chak lohna | Hei hi a symptom ber a ni. A bik takin kekawrte, hip leh kekawrte ruhte chu a chak lo hle. Chair atanga tho chhuak te, stairs chho te, leh rit phurh te chu a harsa ta hle. |
| Muscle na leh a nghet lo | Muscle a na a, khawih pawhin a na a ni. I rilru a na hle thei a, a bik takin zing i thawh hian. |
| Chaw ei harsa (Dysphagia) . | Thlarau ruh chak lohna hian ei leh in tur a ti harsa a, i rilru a buai ang maiin a awm bawk. |
| Thâwk harsa (Dyspnea) . | Chest muscle te a chak lo a nih chuan thawk a harsa a, thawk hah ang maiin a awm thin. |
| Thusawi harsa | Kawng leh kawr ruhte a khawih chuan i aw a danglam thei a, chiang taka sawi a harsa thei bawk. |
| Thil dang pawh a awm | Chauhna awm reng te, ruh na te, chak lohna te, taksa rihna tlahniam te, khawsik te pawh a awm thei bawk. |
A pawimawh ber chu thawk harsa emaw ei leh in emaw ei harsa i tih chuan emergency a ni. Chutiang a nih chuan damdawi in pakhat emergency room (ETU)-ah i kal nghal tur a ni.
Polymyositis vei chhan leh risk factors te chu engte nge ni?
Kan sawi tawh ang khan hei hi a chhan chiang tak hmuh a la ni lo. Mahse, thil ṭhenkhat chuan he dinhmun hi a thlen theihna a tipung thei a ni.
A chhan awm thei te
- Autoimmune natna dang: Autoimmune natna dang `(Lupus)`, `(Rheumatoid arthritis )`, `(Scleroderma)` te i neih tawh chuan Polymyositis i vei theihna a sang zawk.
- Viral infection: A chang chuan viral infection `(COVID-19)`, `(Influenza)` (flu), khawsik, `(HIV)` te hi he natna thlentu a ni thei.
Tute nge risk sang zawk?
- Hmeichhia tan: Hmeichhiain he natna hi mipa aiin a let hnih velin an vei tam zawk.
- Kum 30-60 inkar tan: Kum eng pawha lo awm thei mahse, he natna hi he kum lama mite zingah hian hmuh chhuah a ni ber.
- Autoimmune natna dang nei tan.
Engtin nge hei hi i hmuh theih, Doctor?
A chunga i sawi tak symptoms nei doctor i hmuh chuan i symptoms chungchang chipchiar takin a zawt hmasa ang che. Tichuan i taksa ruhte chu a enfiah ang. Hei bakah hian natna chiang taka hriat theih nan test eng emaw zat a ti dawn bawk a ni.
| Fiahna | Hemiah hian eng nge i hmuh? |
|---|---|
| Thisen Test neih a ni | He test hian taksa ruh a chhiat huna thisena enzyme thenkhat chhuak leh kan taksa ngeia antibody siam chhuah chi hrang hrangte a en thin. |
| MRI scan a ni | Hei hian taksa peng hrang hranga hliam leh inflammation ang chi thil chiang takin a hmu thei a ni. |
| EMG test (Electromyography) hmanga enfiah a ni. | Hei hian taksa peng hrang hrangte electrical activity a en a. Hei hian taksa ruh hnathawh danah thil dik lo eng pawh a hmuchhuak thei a ni. |
| Muscle Biopsy tih a ni | Hei hian a natna taksa peng tlemte tak tak lak a, microscope hmanga enfiah a huam a ni. Hei hian taksa ruh (muscle)-a chhiatna thleng dik tak hriat theihna a siam a ni. |
Engtin nge enkawl a nih?
Kan sawi tawh ang khan he natna hi damdawi a la awm lo. Mahse, enkawlna hian taksa peng hrang hranga inflammation control a tum a, symptoms tihtlem a, a pangngai thei ang bera hnathawh theihna tura puih a tum a ni. Mi tam tak chu enkawlna nen remission-ah an kal thin.
Enkawl dan tlangpui engemaw zat a awm a:
- Corticosteroids: Hei hi damdawi class chak tak a ni a, inflammation tihziaawmna a ni. Hei hi enkawlna hmasa ber a ni fo thin.
- Immunosuppressants: Heng damdawi te hian kan taksa hriselna (immune system) hnathawh tlem a tihtlem avangin hna a thawk a, chu chuan kan taksa peng (tissue) tihchhiatna a ti tlem a ni.
- Intravenous immunoglobulin (IVIG): Hei hi enkawlna danglam deuh a ni. Mi hrisel hnen atanga lak i taksa antibodies te chu saline solution hmanga pek a ni. A awlsam zawngin sawi ila, i immune system chu thil dang ngaihtuah tur pek ang mai a ni. I taksa ruh (muscle) a beih zat a ti tlem a ni.
- Physical Therapy: Hei hi a pawimawh hle. Physics therapist chuan i taksa ruh tichaktu tur leh a inthlak danglam theihna tur exercise a zirtir ang che. Hei hian i taksa ruhte a chak loh nan a pui thei a ni.
Engtikah nge Doctor ka hmuh ang?
Chutiang damdawi lam dinhmunah chuan damdawi lam thurawn lak vat a pawimawh hle.
- Muscle thar chak lohna emaw, natna emaw i neih chuan, a bik takin ni engemaw zat chhunga a reh loh chuan doctor pan nghal rawh .
- Enkawlna i dawng tawh a, i natna lan chhuah dan a na zual nia i hriat chuan, emaw, damdawi chuan hna a thawk lo nia i hriat chuan i doctor hnenah hrilh rawh .
| Damdawi in pakhata Emergency Treatment Unit (ETU)-ah kal nghal rawh! | |
|---|---|
| Thâwk harsa i neih emaw, thawk hah ang maia i hriat emaw chuan. | |
| Chaw emaw, in tur emaw i ei harsat emaw, i rilru a buai reng emaw a nih chuan . | |
| Taksa peng pakhat chu a tlangpuiin a che thei lo nghal a nih chuan . | |
Hei hi thlahtu natna a ni em?
Zirna thenkhatah chuan he natna hi genetic link a awm thei tih hmuhchhuah a ni. Chumi awmzia chu chhungkuaa mi tu emaw chuan a neih chuan midangte pawhin an neih theihna chance tlemte an nei thei tihna a ni. Mahse 100% in a la finfiah lo. Chuvangin, he natna hi i neih vang mai mai hian i fate pawhin an vei ngei ang tih i ngaihtuah a ngai lo.
Polymyositis hi dam chhung zawnga natna a ni a, enkawl ngai a ni. Mahse, nun a khap tlat a ngai lo. Damdawi inenkawlna dik, taksa enkawlna leh nunphung tihdanglam a nih chuan mi tam zawk chuan an natna lan chhuah dan chu an thunun thei a, nun hlim takin an hmang thei a ni. A pawimawh ber chu i taksaa inthlak danglamna ngaihven a, a hun taka damdawi lam thurawn lak hi a ni.
Take-Home Thuchah a ni
- Polymyositis hi natna hlauhawm tak a ni a, kan taksa hriselna (immune system) hian kan taksa ruh a bei nasa hle.
- Muscle chak lo, na, ei harsa leh thawk harsa te hi a lan chhuah dan ber a ni.
- Hei hi tihdamna famkim awm lo mah se, damdawi leh taksa enkawlna hmangin a natna lan chhuah dan chu a thunun thei hle.
- Thâwk harsa emaw, ei leh in emaw i neih chuan emergency-ah ngai la, damdawi in Emergency Department (ETU)-ah kal nghal rawh.
- I natna lan chhuah dan emaw, i enkawl dan emaw chungchangah ngaihtuahna i neih chuan i doctor nen zalen takin inbiakna nei rawh.











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